With the CF Research News, we aim to bridge the gap between people with CF and the researchers investigating CF and how best to treat those with the condition.
We want to provide access to patients, parents, relatives, friends and caregivers of patients with CF to all scientific work mainly published in the Journal of Cystic Fibrosis (JCF).

All PDF files published hereunder are lay version summaries of work published in the JCF.

April 2021

Title: Meconium Ileus due to GUCY2C gene mutations in three unrelated South Indian families
References
J Cyst Fibros. 2021 Apr 18;S1569-1993(21)00105-3. doi: 10.1016/j.jcf.2021.03.023.

April 2021

Title: Incidence of SARS-CoV-2 in people with cystic fibrosis in Europe between February and June 2020.
References
Journal of Cystic Fibrosis 2021; April 17.  DOI: https://doi.org/10.1016/j.jcf.2021.03.017
 

April 2021

Title: Optimising equity of access: how should we allocate slots to the most competitive trials in Cystic Fibrosis (CF)?
References
J Cyst Fibros. 2021 Apr 16;S1569-1993(21)00109-0. doi: 10.1016/j.jcf.2021.03.027. 

April 2021

Title: Trends in the use of healthcare resources over time and the associated costs for people with cystic fibrosis?
References
J Cyst Fibros. 2021 Apr 14;S1569-1993(21)00107-7. doi: 10.1016/j.jcf.2021.03.025.

April 2021

Title: Peripheral lung effect of elexacaftor/tezacaftor/ivacaftor in adult cystic fibrosis
References
J Cyst Fibros. 2021 Apr 6;S1569-1993(21)00098-9. doi: 10.1016/j.jcf.2021.03.016

April 2021

Title: The role of the “PTM-CODE” in restoring F50del-CFTR functionality
References
J Cyst Fibros. 2021 Apr 1;S1569-1993(21)00086-2. doi: 10.1016/j.jcf.2021.03.010.
Title: Nasal high-flow therapy as an adjunct to exercise in patients with cystic fibrosis: A pilot feasibility trial
References
J Cyst Fibros. 2021 Apr 1;S1569-1993(21)00054-0. doi: 10.1016/j.jcf.2021.03.005. 

March 2021

Title: Elevated blood glucose during exacerbations of cystic fibrosis lung disease is associated with poor recovery of lung function.
References
Cyst Fibros. 2021 Mar 26;S1569-1993(21)00053-9. doi: 10.1016/j.jcf.2021.03.004.

March 2021

Title: Emergence and impact of oprD mutations in Pseudomonas aeruginosa strains in cystic fibrosis
References
J Cyst Fibros. 2021 Mar 25;S1569-1993(21)00056-4. doi: 10.1016/j.jcf.2021.03.007.

March 2021

Title: Impact of Trikafta on mothers and babies during pregnancy and lactation
References
J Cyst Fibros. 2021 Mar 21;S1569-1993(21)00055-2. doi: 10.1016/j.jcf.2021.03.006.

March 2021

Title: The Proteostatic Network Chaperome is Downregulated in F508del Homozygote Cystic Fibrosis
References
J Cyst Fibros. 2021 Mar;20(2):356-363. doi: 10.1016/j.jcf.2020.12.018. Epub 2021 Jan 23.

March 2021

Title: Adverse events in clinical trials in children with CF
References
J Cyst Fibros. 2021 Mar 18;S1569-1993(21)00048-5. doi: 10.1016/j.jcf.2021.02.013.

March 2021

Title: Efficacy and safety of inhaled dry-powder mannitol in adults with cystic fibrosis: An international, randomized controlled study
References
J Cyst Fibros. 2021 Mar 11;S1569-1993(21)00046-1. doi: 10.1016/j.jcf.2021.02.011.

March 2021

Title: The Effect of Oral and Intravenous Antimicrobials on Pulmonary Exacerbation Recovery in Cystic Fibrosis
References
J Cyst Fibros. 2021 Mar 5;S1569-1993(21)00047-3. doi: 10.1016/j.jcf.2021.02.012.

March 2021

Title: Chronic incretin-based therapy in cystic fibrosis-related diabetes: a tale of 3 patients treated with sitagliptin for over 5 years
References
J Cyst Fibros. 2021 Mar 2;S1569-1993(21)00040-0. doi: 10.1016/j.jcf.2021.02.005.
Title: SLC26A9 SNP rs7512462 is not associated with lung disease severity or lung function response to ivacaftor in cystic fibrosis patients with G551D-CFTR
References
J Cyst Fibros. 2021 Mar 2;S1569-1993(21)00042-4. doi: 10.1016/j.jcf.2021.02.007.

February 2021

Title: “Il faut continuer à poser des questions” patient reported outcome measures in cystic fibrosis: An anthropological perspective
References
J Cyst Fibros. 2021 Feb 26;S1569-1993(21)00044-8. doi: 10.1016/j.jcf.2021.02.009.
 
Title: Limb muscle size and contractile function in adults with cystic fibrosis: A systematic review and meta-analysis
References
J Cyst Fibros. 2021 Feb 26;S1569-1993(21)00045-X. doi: 10.1016/j.jcf.2021.02.010

February 2021

Title: Performing an exercise capacity test, known as the modified shuttle test, can help to detect the risk of being hospitalized in youths with cystic fibrosis
References

February 2021

Title: Neutrophil Dysfunction in Cystic Fibrosis
References
J Cyst Fibros. 2021 Feb 13;S1569-1993(21)00035-7. doi: 10.1016/j.jcf.2021.01.012.

February 2021

Title: Measuring the impact of CFTR modulation on sweat chloride in cystic fibrosis: Rationale and design of the CHEC-SC Study
References
J Cyst Fibros. 2021 Feb 8;S1569-1993(21)00034-5. doi: 10.1016/j.jcf.2021.01.011.

February 2021

Title: Targeting G542X CFTR Nonsense Alleles With ELX-02 Restores CFTR Function in Human-Derived Intestinal Organoids
References
J Cyst Fibros. 2021 Feb 5;S1569-1993(21)00028-X. doi: 10.1016/j.jcf.2021.01.009.

January 2021

Title: Attitudes of Pain and Opioids Prescription Practices in U.S. Cystic Fibrosis Centers
References
J Cyst Fibros. 2021 Jan;20(1):127-132. doi: 10.1016/j.jcf.2020.07.021. Epub 2020 Aug 11

January 2021

Title: Alpha-1 Antitrypsin for Cystic Fibrosis Complicated by Severe Cytokinemic COVID-19
References
J Cyst Fibros. 2021 Jan;20(1):31-35. doi: 10.1016/j.jcf.2020.11.012.
Title: Emerging preclinical modulators developed for F508del-CFTR have the potential to be effective for ORKAMBI resistant processing mutants
References
J Cyst Fibros. 2021 Jan;20(1):106-119. doi: 10.1016/j.jcf.2020.07.015. Epub 2020 Jul 30.
Title: ACT with CF: A telehealth and in-person feasibility study to address anxiety and depressive symptoms among people with cystic fibrosis
References
J Cyst Fibros. 2021 Jan;20(1):133-139. doi: 10.1016/j.jcf.2020.11.013. Epub 2020 Dec 2.

January 2021

Title: Comparing oral glucose tolerance test and continuous glucose monitoring
References
J Cyst Fibros. 2021 Jan 18;S1569-1993(21)00002-3. doi: 10.1016/j.jcf.2021.01.002.

January 2021

Title: Changes in airway inflammation with pseudomonas eradication in early cystic fibrosis
References
J Cyst Fibros . 2021 Jan 15;S1569-1993(20)30947-4. doi: 10.1016/j.jcf.2020.12.015. 

January 2021

Title: Is hyperpolarised gas magnetic resonance imaging a valid and reliable tool to detect lung health in cystic fibrosis patients? A COSMIN systematic review.
References
J Cyst Fibros. 2021 Jan 13;S1569-1993(20)30952-8. doi: 10.1016/j.jcf.2020.12.020.

January 2021

Title: Designing the GALAXY study: Partnering with the cystic fibrosis community to optimize assessment of gastrointestinal symptoms
References
J Cyst Fibros. 2021 Jan 12;S1569-1993(20)30953-X. doi: 10.1016/j.jcf.2020.12.021. 

January 2021

Title: Relationship between airway dysbiosis, inflammation and lung function in adults with cystic fibrosis
References
J Cyst Fibros. 2021 Jan 8;S1569-1993(20)30954-1. doi: 10.1016/j.jcf.2020.12.022.

January 2021

Title: Significant functional differences in differentiated Conditionally Reprogrammed (CRC)- and Feeder-free Dual SMAD inhibited-expanded human nasal epithelial cells
References
J Cyst Fibros. 2021 Jan 4;S1569-1993(20)30951-6. doi: 10.1016/j.jcf.2020.12.019.

December 2020

Title: Pilot study suggests that the gut bacteria in people with CF change with CFTR modulator therapy
References
J Cyst Fibros. 2020 Dec 31;S1569-1993(20)30934-6. doi: 10.1016/j.jcf.2020.12.002. 

December 2020

Title: Men's health in the modern era of cystic fibrosis
References
J Cyst Fibros. 2020 Dec 26;S1569-1993(20)30945-0. doi: 10.1016/j.jcf.2020.12.013. 

December 2020

Title: Psychological distress in adults with and without cystic fibrosis during the COVID-19 lockdown
References
J Cyst Fibros. 2020 Dec 23;S1569-1993(20)30948-6. doi: 10.1016/j.jcf.2020.12.016. 

December 2020

Title: Elexacafator/tezacaftor/ivacaftor Resolves Subfertility in Females with CF: A Two Center Case Series
References
J Cyst Fibros. 2020 Dec 19;S1569-1993(20)30943-7. doi: 10.1016/j.jcf.2020.12.011.

December 2020

Title: Vitamin D supplementation in patients with cystic fibrosis: A systematic review and meta-analysis
References
J Cyst Fibros. 2020 Dec 18;S1569-1993(20)30940-1. doi: 10.1016/j.jcf.2020.12.008. 
Title: The association between the function of the cellular salt channel cystic fibrosis transmembrane conductance regulator and lung function in people with cystic fibrosis
References
J Cyst Fibros. 2020 Dec 18;S1569-1993(20)30941-3. doi: 10.1016/j.jcf.2020.12.009.

December 2020

Title: Assessing the effect of adding chelating agent (Tris-CaEDTA) to nebulised tobramycin for improving bacterial killing and lung function in cystic fibrosis patients with Pseudomonas aeruginosa lung infection.
References
J Cyst Fibros. 2020 Dec 16;S1569-1993(20)30936-X. doi: 10.1016/j.jcf.2020.12.004.
Title: Ototoxicity in Cystic Fibrosis Patients Receiving Intravenous Tobramycin for Acute Pulmonary Exacerbation
References
J Cyst Fibros. 2020 Dec 16;S1569-1993(20)30930-9. doi: 10.1016/j.jcf.2020.11.020.

December 2020

Title: The impact of SARS-CoV-2 on the cystic fibrosis foundation therapeutics development network
References
J Cyst Fibros. 2020 Dec 15;S1569-1993(20)30939-5. doi: 10.1016/j.jcf.2020.12.007.
Title: A phase 3, randomized, double-blind, parallel-group study to evaluate tezacaftor/ivacaftor in people with cystic fibrosis heterozygous
References
J Cyst Fibros. 2020 Dec 15;S1569-1993(20)30906-1. doi: 10.1016/j.jcf.2020.11.003.

December 2020

Title: Impact of biofilm formation and azoles' susceptibility in Scedosporium/Lomentospora species using an in vitro model that mimics the cystic fibrosis patients' airway environment
References
J Cyst Fibros. 2020 Dec 14;S1569-1993(20)30933-4. doi: 10.1016/j.jcf.2020.12.001.

December 2020

Title: Environmental risks of Pseudomonas aeruginosa-What to advise patients and parents
References
J Cyst Fibros. 2020 Dec 12;S1569-1993(20)30937-1. doi: 10.1016/j.jcf.2020.12.005. Online ahead of print.

December 2020

Title: Organoids for personalized treatment of Cystic Fibrosis: Professional perspectives on the ethics and governance of organoid biobanking
References
J Cyst Fibros. 2020 Dec 7;S1569-1993(20)30921-8. doi: 10.1016/j.jcf.2020.11.015.

December 2020

Title: Phages as immunomodulators and their promising use as anti-inflammatory agents in a cftr loss-of-function zebrafish model
References
J Cyst Fibros. 2020 Dec 6;S1569-1993(20)30927-9. doi: 10.1016/j.jcf.2020.11.017.

December 2020

Title: Sensitive structural and functional measurements and 1-year pulmonary outcomes in pediatric cystic fibrosis
References
J Cyst Fibros. 2020 Dec 4;S1569-1993(20)30929-2. doi: 10.1016/j.jcf.2020.11.019. 

December 2020

Title: MyCyFapp clinical trial sub-study on change in PERT and fat absorption
References
J Cyst Fibros. 2020 Dec 2;S1569-1993(20)30926-7. doi: 10.1016/j.jcf.2020.11.016.
Title: CFTR plays an important role in the regulation of vascular resistance and high-fructose/salt-diet induced hypertension in mice
References
J Cyst Fibros. 2020 Dec 2;S1569-1993(20)30920-6. doi: 10.1016/j.jcf.2020.11.014.

December 2020

Title: YKL-40 as a clinical biomarker in adult patients with CF: Implications of a CHI3L1 single nucleotide polymorphism in disease severity.
References
J Cyst Fibros. 2020 Dec 1;S1569-1993(20)30914-0. doi: 10.1016/j.jcf.2020.11.011.

November 2020

Title: Updated guidance on the care of children with an inconclusive diagnosis after newborn screening
References
J Cyst Fibros. 2020 Nov 27;S1569-1993(20)30909-7. doi: 10.1016/j.jcf.2020.11.006.

November 2020

Title: The cystic fibrosis gut as a potential source of multidrug resistant pathogens
References
J Cyst Fibros. 2020 Nov 26;S1569-1993(20)30912-7. doi: 10.1016/j.jcf.2020.11.009.
Title: Prostaglandin E2 and phagocytosis of inhaled particulate matter by airway macrophages in cystic fibrosis
References
J Cyst Fibros. 2020 Nov 26;S1569-1993(20)30913-9. doi: 10.1016/j.jcf.2020.11.010.

November 2020

Title: Long term clinical effectiveness of ivacaftor in people with the G551D CFTR mutation
References
J Cyst Fibros. 2020 Nov 25;S1569-1993(20)30911-5. doi: 10.1016/j.jcf.2020.11.008. 
Title: Lumacaftor/ivacaftor in people with cystic fibrosis with an A455E-CFTR mutation
References
J Cyst Fibros. 2020 Nov 25;S1569-1993(20)30910-3. doi: 10.1016/j.jcf.2020.11.007.

November 2020

Title: Long-term azithromycin use is not associated with QT prolongation in children with cystic fibrosis
References
J Cyst Fibros. 2020 Nov 24;S1569-1993(20)30908-5. doi: 10.1016/j.jcf.2020.11.005.

November 2020

Title: Predicting effects of mutations on CFTR’s mRNA
References
J Cyst Fibros. 2020 Dec 16;S1569-1993(20)30935-8. doi: 10.1016/j.jcf.2020.12.003.

November 2020

Title: Defective immunometabolism pathways in cystic fibrosis macrophages
References
J Cyst Fibros. 2020 Nov 15;S1569-1993(20)30880-8. doi: 10.1016/j.jcf.2020.10.006.

November 2020

Title: Airway epithelial stem cell chimerism in cystic fibrosis lung transplant recipients
References
J Cyst Fibros. 2020 Nov 10;S1569-1993(20)30881-X. doi: 10.1016/j.jcf.2020.09.013.

November 2020

Title: The virtual CF clinic – what this means for sputum microbiology
References
J Cyst Fibros. 2020 Nov 6;S1569-1993(20)30879-1. doi: 10.1016/j.jcf.2020.10.005.

November 2020

Title: Early acquisition and conversion of Pseudomonas aeruginosa in Hispanic youth with cystic fibrosis in the United States
References
J Cyst Fibros. 2020 Nov 5;S1569-1993(20)30876-6. doi: 10.1016/j.jcf.2020.10.002.

November 2020

Title: The global impact of SARS-CoV-2 in 181 people with cystic fibrosis
References
J Cyst Fibros. 2020 Nov 4;S1569-1993(20)30877-8. doi: 10.1016/j.jcf.2020.10.003

October 2020

Title: Long-term bone mineral density changes and fractures in lung transplant recipients with cystic fibrosis
References
J Cyst Fibros. 2020 Oct; 21  2020DOI:https://doi.org/10.1016/j.jcf.2020.09.012

October 2020

Title: Prospective longitudinal association between repeated multiple breath washout measurements and computed tomography scores in children with cystic fibrosis
References
J Cyst Fibros. 2020 Oct 4;2121. doi: 10.1016/j.jcf.2020.09.010. 

October 2020

Title: Tobacco smoke exposure limits the therapeutic benefit of tezacaftor/ivacaftor in pediatric patients with cystic fibrosis
References
J Cyst Fibros. 2020 Oct 3;S1569-1993(20)30870-5. doi: 10.1016/j.jcf.2020.09.011. Online ahead of print.

September 2020

Title: Safety and Efficacy of Lenabasum in a Phase 2 Randomized, Placebo-Controlled Trial in Adults with Cystic Fibrosis
References
J Cyst Fibros. 2020 Sep 30;S1569-1993(20)30873-0. doi: 10.1016/j.jcf.2020.09.008.

September 2020

Title: Evidence of early increased sialylation of airway mucins and defective mucociliary clearance in CFTR-/- deficient piglets
References
J Cyst Fibros. 2020 Sep 23;S1569-1993(20)30868-7. doi: 10.1016/j.jcf.2020.09.009.

September 2020

Title: A phase 3, double-blind, parallel-group study to evaluate the efficacy and safety of tezacaftor in combination with ivacaftor in participants 6 through 11 years of age with cystic fibrosis homozygous for F508del or heterozygous for the F508del-CFTR mutati
References
J Cyst Fibros . 2020 Sep 21;S1569-1993(20)30811-0. doi: 10.1016/j.jcf.2020.07.023.

September 2020

Title: Anti-inflammatory effects of lenabasum, a cannabinoid receptor type 2 agonist, on macrophages from cystic fibrosis
References
J Cyst Fibros. 2020 Sep;19(5):823-829. doi: 10.1016/j.jcf.2020.03.015. Epub 2020 May 6. 

September 2020

Title: What is the value of lung function testing in infants with cystic fibrosis?
References
 J Cyst Fibros. 2020 Sep 17;S1569-1993(20)30867-5. doi: 10.1016/j.jcf.2020.09.005. Online ahead of print.

September 2020

Title: Trends in nontuberculous mycobacteria infection in children and young people with cystic fibrosis
References
J Cyst Fibros. 2020 Sep 16;S1569-1993(20)30872-9. doi: 10.1016/j.jcf.2020.09.007.

September 2020

Title: Sputum for viral diagnosis in cystic fibrosis patients
References
J Cyst Fibros. 2020 Sep 14;S1569-1993(20)30865-1. doi: 10.1016/j.jcf.2020.09.003.

September 2020

Title: Delayed glucose peak and elevated 1-hour glucose on the oral glucose tolerance test identify youth with cystic fibrosis with lower oral disposition index
References
J Cyst Fibros. 2020 Sep 11;2111. doi: 10.1016/j.jcf.2020.08.020. Online ahead of print.
Title: Delayed glucose peak and elevated 1-hour glucose on the oral glucose tolerance test identify youth with cystic fibrosis with lower oral disposition index
References
J Cyst Fibros. 2020 Sep 11;2111. doi: 10.1016/j.jcf.2020.08.020. Online ahead of print.

September 2020

Title: Baseline CF disease severity has an adverse impact on pregnancy and infant outcomes, but does not impact disease progression
References
J Cyst Fibros. 2020 Sep 9;S1569-1993(20)30864-X. doi: 10.1016/j.jcf.2020.09.002.

September 2020

Title: Lumacaftor/ivacaftor therapy fails to increase insulin secretion in F508del/F508del CF patients
References
J Cyst Fibros. 2020 Sep 8;S1569-1993(20)30862-6. doi: 10.1016/j.jcf.2020.09.001. 

September 2020

Title: Factors influencing clinical trial participation for adult and pediatric patients with cystic fibrosis
References
J Cyst Fibros. 2020 Sep 5;S1569-1993(20)30857-2. doi: 10.1016/j.jcf.2020.08.019. Online ahead of print.

September 2020

Title: Aerosolized lancovutide in adolescents (≥12 years) and adults with cystic fibrosis - a randomized trial
References
J Cyst Fibros. 2020 Sep 1;S1569-1993(20)30830-4. doi: 10.1016/j.jcf.2020.08.014.

August 2020

Title: Immune response of polarized cystic fibrosis airway epithelial cells infected with Influenza A virus
References
J Cyst Fibros. 2020 Aug 29;S1569-1993(20)30827-4. doi: 10.1016/j.jcf.2020.08.012. Online ahead of print.

August 2020

Title: Recommended shielding against COVID-19 impacts physical activity levels in adults with cystic fibrosis
References
J Cyst Fibros. 2020 Aug 28;S1569-1993(20)30828-6. doi: 10.1016/j.jcf.2020.08.013

August 2020

Title: Extensive CFTR sequencing through NGS in Brazilian individuals with cystic fibrosis: unravelling regional discrepancies in the country
References
J Cyst Fibros. 2020 Aug 17;S1569-1993(20)30822-5. doi: 10.1016/j.jcf.2020.08.007.

August 2020

Title: The implementation of an aminoglycoside induced ototoxicity algorithm for people with cystic fibrosis
References
J Cyst Fibros. 2020 Aug 15;S1569-1993(20)30817-1. doi: 10.1016/j.jcf.2020.08.002. Online ahead of print.

August 2020

Title: Long-term safety study of colistimethate sodium (Colobreathe®): Findings from the UK Cystic Fibrosis Registry
References
J Cyst Fibros. 2020 Aug 14;S1569-1993(20)30816-X. doi: 10.1016/j.jcf.2020.08.001. Online ahead of print.

August 2020

Title: Changes in symptom scores as a potential clinical endpoint for studies of cystic fibrosis pulmonary exacerbation treatment
References
J Cyst Fibros. 2020 Aug 13;S1569-1993(20)30820-1. doi: 10.1016/j.jcf.2020.08.006. Online ahead of print.

August 2020

Title: Decreased survival in cystic fibrosis patients with a positive screen for depression
References
J Cyst Fibros. 2020 Aug 12;S1569-1993(20)30812-2. doi: 10.1016/j.jcf.2020.07.020.

August 2020

Title: SARS-CoV-2 seroprevalence in a Belgian cohort of patients with cystic fibrosis
References
J Cyst Fibros. 2020 Aug 11;S1569-1993(20)30821-3. doi: 10.1016/j.jcf.2020.08.005

August 2020

Title: Screening for Nontuberculous mycobacteria (NTM) in people with Cystic Fibrosis
References
J Cyst Fibros. 2020 Aug; 9

August 2020

Title: Projecting the impact of delayed access to elexacaftor/tezacaftor/ivacaftor for people with Cystic Fibrosis
References
J Cyst Fibros. 2020 Aug 5;S1569-1993(20)30809-2. doi: 10.1016/j.jcf.2020.07.017. Online ahead of print.

August 2020

Title: Azithromycin and Tezacaftor/Ivacaftor is associated with first-degree heart block in an adult with Cystic Fibrosis
References
J Cyst Fibros. 2020 Aug 4;S1569-1993(20)30808-0. doi: 10.1016/j.jcf.2020.07.016. Online ahead of print.

August 2020

Title: Heat acclimation improves sweat gland function and lowers sweat sodium concentration in an adult with cystic fibrosis
References
J Cyst Fibros. 2020 Aug 2;S1569-1993(20)30804-3. doi: 10.1016/j.jcf.2020.07.013.

July 2020

Title: Clinical characteristics and outcomes associated with Inquilinus infection in cystic fibrosis
References
J Cyst Fibros. 2020 Jul 31;S1569-1993(20)30803-1. doi: 10.1016/j.jcf.2020.07.011. Online ahead of print.
Title: The impact of the COVID-19 pandemic on the emotional well-being and home treatment of Belgian patients with cystic fibrosis, including transplanted patients and children
References
J Cyst Fibros. 2020 Jul 31;S1569-1993(20)30815-8. doi: 10.1016/j.jcf.2020.07.022. Online ahead of print.

July 2020

Title: Biliary disease and cholecystectomy after initiation of elexacaftor/ivacaftor/tezacaftor in adults with cystic fibrosis
References
J Cyst Fibros. 2020 Jul 29;S1569-1993(20)30806-7. doi: 10.1016/j.jcf.2020.07.014.

July 2020

Title: Developing Innovative GastroEnterology Specialty Training: the DIGEST model for expanding cystic fibrosis gastroenterologic expertise
References
J Cyst Fibros. 2020 Jul 28;S1569-1993(20)30805-5. doi: 10.1016/j.jcf.2020.07.012.

July 2020

Title: Citrullination of extracellular histone H3.1 reduces antibacterial activity and exacerbates its proteolytic degradation
References
J Cyst Fibros. 2020 Jul 26;S1569-1993(20)30802-X. doi: 10.1016/j.jcf.2020.07.010. Online ahead of print.

July 2020

Title: Prospective cohort study of ototoxicity in persons with cystic fibrosis following a single course of intravenous tobramycin
References
J Cyst Fibros . 2020 Jul 23;S1569-1993(20)30793-1. doi: 10.1016/j.jcf.2020.07.001. Online ahead of print.

July 2020

Title: Screening practices for nontuberculous mycobacteria at US cystic fibrosis centers
References
J Cyst Fibros. 2020 Jul;19(4):569-574. doi: 10.1016/j.jcf.2020.02.013. Epub 2020 Mar 13.

July 2020

Title: Effect of highly effective modulator treatment on sinonasal symptoms in cystic fibrosis
References
J Cyst Fibros. 2020 Jul 18;S1569-1993(20)30794-3. doi: 10.1016/j.jcf.2020.07.002.

July 2020

Title: Evaluating assumptions of definition-based pulmonary exacerbation endpoints in cystic fibrosis clinical trials
References
J Cyst Fibros. 2020 Jul 15;S1569-1993(20)30800-6. doi: 10.1016/j.jcf.2020.07.008.
 

July 2020

Title: Efficacy and safety of ataluren in patients with nonsense-mutation cystic fibrosis not receiving chronic inhaled aminoglycosides: the international, randomized, double-blind, placebo-controlled Ataluren Confirmatory Trial in Cystic Fibrosis (ACT CF)
References
J Cyst Fibros. 2020 Jul;19(4):595-601. doi: 10.1016/j.jcf.2020.01.007. Epub 2020 Jan 23.