With the CF Research News, we aim to bridge the gap between people with CF and the researchers investigating CF and how best to treat those with the condition.
We want to provide access to patients, parents, relatives, friends and caregivers of patients with CF to all scientific work mainly published in the Journal of Cystic Fibrosis (JCF).

All PDF files published hereunder are lay version summaries of work published in the JCF.

September 2019

Title: A two-center analysis of hyperpolarized 129Xe lung MRI in stable pediatric cystic fibrosis: Potential as a biomarker for multi-site trials.
References
Couch MJ, Thomen R, Kanhere N, Hu R, Ratjen F, Woods J, Santyr G
Title: International approaches for delivery of positive newborn bloodspot screening results for CF
References
J Cyst Fibros. 2019 Sep;18(5):614-621. doi: 10.1016/j.jcf.2019.04.004. Epub 2019 Apr 30.

September 2019

Title: Micronutrient intake in children with cystic fibrosis in Sydney, Australia
References
J Cyst Fibros. 2019 Sep 14. pii: S1569-1993(19)30885-9. doi: 10.1016/j.jcf.2019.08.028. 

September 2019

Title: A critical review of definitions used to describe Pseudomonas aeruginosa microbiological status in patients with Cystic Fibrosis for application in clinical trials
References
J Cyst Fibros. 2019 Sep 13. pii: S1569-1993(19)30867-7. doi: 10.1016/j.jcf.2019.08.014.

September 2019

Title: The impact of chest computed tomography and chest radiography on clinical management of cystic fibrosis lung disease
References
J Cyst Fibros. 2019 Sep 4. pii: S1569-1993(19)30837-9. doi: 10.1016/j.jcf.2019.08.005.

August 2019

Title: Whole-blood transcriptomic responses to lumacaftor/ivacaftor therapy in cystic fibrosis.
References
J Cyst Fibros. 2019 Aug 29. pii: S1569-1993(19)30868-9. doi: 10.1016/j.jcf.2019.08.021. 

August 2019

Title: Addressing the Burden of Illness in Adults with Cystic Fibrosis with Screening and Triage: An Early Intervention Model of Palliative Care
References
J Cyst Fibros. 2019 Aug 27. pii: S1569-1993(19)30841-0. doi: 10.1016/j.jcf.2019.08.009

August 2019

Title: Dysregulated insulin in pancreatic insufficient cystic fibrosis with post-prandial hypoglycemia.
References
J Cyst Fibros. 2019 Aug 8. pii: S1569-1993(19)30827-6. doi: 10.1016/j.jcf.2019.07.006

July 2019

Title: Incretin dysfunction and hyperglycemia in cystic fibrosis: role of acyl-ghrelin
References
J Cyst Fibros. 2019 Jul;18(4):557-565. doi: 10.1016/j.jcf.2019.01.010. 
Title: Randomized Controlled Study of Aerosolized Hypertonic Xylitol Versus Hypertonic Saline in Hospitalized Patients with Pulmonary Exacerbation of Cystic Fibrosis
References
J Cyst Fibros. 2019 Jul 18. pii: S1569-1993(19)30821-5. doi: 10.1016/j.jcf.2019.06.016
Title: Ventilation and perfusion assessed by functional MRI in children with CF: reproducibility in comparison to lung function
References
J Cyst Fibros. 2019 Jul;18(4):543-550. doi: 10.1016/j.jcf.2018.10.003. Epub 2018 Oct 20.

July 2019

Title: Theranostics by testing CFTR modulators in patient-derived materials: the current status and a proposal for subjects with rare CFTR mutations
References
J Cyst Fibros. 2019 Jul 17. pii: S1569-1993(19)30814-8. doi: 10.1016/j.jcf.2019.06.010. 

July 2019

Title: Speeding up access to new drugs for Cystic Fibrosis: Considerations for clinical trial design and delivery
References
 2019 Jul 11. pii: S1569-1993(19)30815-X. doi: 10.1016/j.jcf.2019.06.011.
Title: Supersonic Shear-Wave Elastography and APRI for the detection and staging of liver disease in paediatric cystic fibrosis
References
J Cyst Fibros. 2019 Jul 11. pii: S1569-1993(19)30820-3. doi: 10.1016/j.jcf.2019.06.017.

June 2019

Title: Dissociation of Systemic and Mucosal Autoimmunity in Cystic Fibrosis
References
J Cyst Fibros. 2019 Jun 28. pii: S1569-1993(19)30807-0. doi: 10.1016/j.jcf.2019.06.006. 
Title: Dissociation of Systemic and Mucosal Autoimmunity in Cystic Fibrosis
References
J Cyst Fibros. 2019 Jun 28. pii: S1569-1993(19)30807-0. doi: 10.1016/j.jcf.2019.06.006. 

June 2019

Title: Variation in lung function and nutritional decline in cystic fibrosis by genotype: An analysis of the Canadian Cystic Fibrosis Registry
References
J Cyst Fibros. 2019 Jun 25. pii: S1569-1993(19)30812-4. doi: 10.1016/j.jcf.2019.06.007
Title: Variation in lung function and nutritional decline in cystic fibrosis by genotype: An analysis of the Canadian Cystic Fibrosis Registry
References
J Cyst Fibros. 2019 Jun 25. pii: S1569-1993(19)30812-4. doi: 10.1016/j.jcf.2019.06.007

June 2019

Title: Do current clinical trials in cystic fibrosis match the priorities of patients and clinicans? A systematic review.
References
J Cyst Fibros. 2019 Jun 21. pii: S1569-1993(19)30806-9. doi: 10.1016/j.jcf.2019.06.005.

June 2019

Title: Disease Progression in Patients with Cystic Fibrosis Treated with Ivacaftor: Data From National US and UK Registries
References
J Cyst Fibros. 2019 Jun 10. pii: S1569-1993(19)30767-2. doi: 10.1016/j.jcf.2019.05.015. 

June 2019

Title: Antisense oligonucleotide eluforsen is safe and improves respiratory symptoms in F508DEL cystic fibrosis.
References
J Cyst Fibros. 2019 Jun 7. pii: S1569-1993(19)30766-0. doi: 10.1016/j.jcf.2019.05.014

June 2019

Title: Non-fasting bioelectrical impedance analysis in cystic fibrosis: Implications for clinical practice and research
References
J Cyst Fibros. 2019 Jun 5. pii: S1569-1993(19)30772-6. doi: 10.1016/j.jcf.2019.05.018
Title: Blood Biomarkers to Predict Short-term Pulmonary Exacerbation Risk in Children and Adolescents with CF: A Pilot Study
References
J Cyst Fibros. 2019 Jun 5. pii: S1569-1993(19)30774-X. doi: 10.1016/j.jcf.2019.05.020.
Title: Abnormal Pro-Gly-Pro pathway and airway neutrophilia in pediatric cystic fibrosis
References
J Cyst Fibros. 2019 Jun 5. pii: S1569-1993(19)30769-6. doi: 10.1016/j.jcf.2019.05.017

May 2019

Title: The use of antimicrobial susceptibility testing in pediatric cystic fibrosis pulmonary exacerbations
References
J Cyst Fibros. 2019 May 28. pii: S1569-1993(19)30764-7. doi: 10.1016/j.jcf.2019.05.012.

May 2019

Title: GLPG1837, a CFTR potentiator, in p.Gly551Asp (G551D)-CF patients: An open-label, single-arm, phase 2a study (SAPHIRA1)
References
J Cyst Fibros. 2019 May 27. pii: S1569-1993(19)30111-0. doi: 10.1016/j.jcf.2019.05.006. 
Title: GLPG1837, a CFTR potentiator, in p.Gly551Asp (G551D)-CF patients: An open-label, single-arm, phase 2a study (SAPHIRA1)
References
J Cyst Fibros. 2019 May 27. pii: S1569-1993(19)30111-0. doi: 10.1016/j.jcf.2019.05.006. 

May 2019

Title: Pilot study to test inhaled nitric oxide in cystic fibrosis patients with refractory Mycobacterium abscessus lung infection.
References
J Cyst Fibros. 2019 May 22. pii: S1569-1993(19)30104-3. doi: 10.1016/j.jcf.2019.05.002.

May 2019

Title: Peak OGTT glucose is associated with lower lung function in young children with cystic fibrosis.
References
J Cyst Fibros. 2019 May 21. pii: S1569-1993(18)30791-4. doi: 10.1016/j.jcf.2019.05.005. 
Title: Peak OGTT glucose is associated with lower lung function in young children with cystic fibrosis.
References
J Cyst Fibros. 2019 May 21. pii: S1569-1993(18)30791-4. doi: 10.1016/j.jcf.2019.05.005. 
Title: Peak OGTT glucose is associated with lower lung function in young children with cystic fibrosis.
References
J Cyst Fibros. 2019 May 21. pii: S1569-1993(18)30791-4. doi: 10.1016/j.jcf.2019.05.005. 
Title: Correspondence between Lung Function and Symptom Measures from the Cystic Fibrosis Respiratory Symptom Diary–Chronic Respiratory Infection Symptom Score (CFRSD-CRISS)
References
J Cyst Fibros. 2019 May 21. pii: S1569-1993(19)30113-4. doi: 10.1016/j.jcf.2019.05.009. 

May 2019

Title: Lung transplant referral for individuals with cystic fibrosis: Cystic Fibrosis Foundation consensus guidelines
References
J Cyst Fibros. 2019 May;18(3):321-333. doi: 10.1016/j.jcf.2019.03.002. Epub 2019 Mar 27.
Title: High airborne level of Aspergillus fumigatus and presence of azole-resistant TR34/L98H isolates in the home of a cystic fibrosis patient harbouring chronic colonisation with azole-resistant H285Y A. fumigatus.
References
J Cyst Fibros. 2019 May;18(3):364-367. doi: 10.1016/j.jcf.2019.01.001. Epub 2019 Jan 9.
Title: Predictive factors for lumacaftor/ivacaftor clinical response.
References
J Cyst Fibros. 2019 May;18(3):368-374. doi: 10.1016/j.jcf.2018.12.011. Epub 2018 Dec 28.
 
Title: Differential Expression of Genes and Receptors in Monocytes from Patients with Cystic Fibrosis.
References
J Cyst Fibros. 2019 May;18(3):342-348. doi: 10.1016/j.jcf.2018.07.012. Epub 2018 Sep 1.

May 2019

Title: Study of 109 Achromobacter spp. isolates from 9 French CF centres reveals the circulation of a multiresistant clone of A. xylosoxidans belonging to ST 137
References
J Cyst Fibros. 2019 May 16. pii: S1569-1993(19)30065-7. doi: 10.1016/j.jcf.2019.04.005

May 2019

Title: Deep Learning to Automate Brasfield Chest Radiographic Scoring for Cystic Fibrosis
References
J Cyst Fibros. 2019 May 2. pii: S1569-1993(19)30075-X. doi: 10.1016/j.jcf.2019.04.016. 

April 2019

Title: An open-label extension study of ivacaftor in children with CF and a CFTR gating mutation initiating treatment at age 2-5 years (KLIMB).
References
J Cyst Fibros. 2019 Apr 30. pii: S1569-1993(19)30061-X. doi: 10.1016/j.jcf.2019.03.009.

April 2019

Title: Early glucose abnormalities are associated with pulmonary inflammation in young children with cystic fibrosis
References
J Cyst Fibros. 2019 Apr 26. pii: S1569-1993(18)30897-X. doi: 10.1016/j.jcf.2019.03.010. 
Title: Early glucose abnormalities are associated with pulmonary inflammation in young children with cystic fibrosis
References
J Cyst Fibros. 2019 Apr 26. pii: S1569-1993(18)30897-X. doi: 10.1016/j.jcf.2019.03.010. 
Title: Early glucose abnormalities are associated with pulmonary inflammation in young children with cystic fibrosis
References
J Cyst Fibros. 2019 Apr 26. pii: S1569-1993(18)30897-X. doi: 10.1016/j.jcf.2019.03.010. 
Title: Mucoid Pseudomonas aeruginosa and regional inflammation in the cystic fibrosis lung
References
J Cyst Fibros. 2019 Apr 26. pii: S1569-1993(19)30069-4. doi: 10.1016/j.jcf.2019.04.009.
Title: Mucoid Pseudomonas aeruginosa and regional inflammation in the cystic fibrosis lung
References
J Cyst Fibros. 2019 Apr 26. pii: S1569-1993(19)30069-4. doi: 10.1016/j.jcf.2019.04.009.

April 2019

Title: Oxidative Stress and Abnormal Bioactive Lipids in Early Cystic Fibrosis Lung Disease.
References
J Cyst Fibros. 2019 Apr 25. pii: S1569-1993(19)30071-2. doi: 10.1016/j.jcf.2019.04.011. 

April 2019

Title: Assessment of endothelial function is reproducible in patients with cystic fibrosis.
References
J Cyst Fibros. 2019 Apr 4. pii: S1569-1993(19)30062-1. doi: 10.1016/j.jcf.2019.03.011

March 2019

Title: The impact of cystic fibrosis-related diabetes on health-related quality of life
References
J Cyst Fibros. 2019 Mar 29. pii: S1569-1993(19)30060-8. doi: 10.1016/j.jcf.2019.03.007. 

March 2019

Title: Markers of bone turnover are reduced in patients with CF related diabetes; the role of glucose.
References
J Cyst Fibros. 2019 Mar 27. pii: S1569-1993(18)30809-9. doi: 10.1016/j.jcf.2019.01.004

March 2019

Title: Aligning patients’ needs towards a comprehensive CF research program
References
J Cyst Fibros. 2019 Mar 26. pii: S1569-1993(18)30857-9. doi: 10.1016/j.jcf.2019.03.008.
Title: Physical activity and associations with clinical outcome measures in adults with cystic fibrosis; a systematic review.
References
J Cyst Fibros. 2019 Mar 26. pii: S1569-1993(18)30898-1. doi: 10.1016/j.jcf.2019.03.003.

March 2019

Title: Assessment of stability and fluctuations of cultured lower airway bacterial communities in people with cystic fibrosis
References
J Cyst Fibros. 2019 Mar 21. pii: S1569-1993(19)30052-9. doi: 10.1016/j.jcf.2019.02.012. 

March 2019

Title: 3D Printing and the Cystic Fibrosis Lung
References
J Cyst Fibros. 2019 Mar;18(2):278-279. doi: 10.1016/j.jcf.2018.09.004. 
Title: Cystic fibrosis related diabetes is not independently associated with increased Stenotrophomonas maltophilia infection: longitudinal data from the UK CF Registry
References
J Cyst Fibros. 2019 Mar;18(2):294-298. doi: 10.1016/j.jcf.2018.10.011. Epub 2018 Oct 25

March 2019

Title: The Effects of Cycled Inhaled Aztreonam on the Cystic Fibrosis (CF) Lung Microbiome
References
J Cyst Fibros. 2019 Mar 8. pii: S1569-1993(19)30028-1. doi: 10.1016/j.jcf.2019.02.010

February 2019

Title: Abnormal Preschool Lung Clearance Index (LCI) reflects clinical status and predicts lower spirometry later in childhood in Cystic Fibrosis.
References
J Cyst Fibros. 2019 Feb 28. pii: S1569-1993(19)30025-6. doi: 10.1016/j.jcf.2019.02.007.

February 2019

Title: Early respiratory viral infections in infants with cystic fibrosis
References
Deschamp AR, Hatch JE, Slaven JE, Gebregziabher N, Storch G, Hall GL, Stick S, Ranganathan S, Ferkol TW, Davis SD.

February 2019

Title: Inhaled antibiotic use is associated with Scedosporium/Lomentospora species isolation in cystic fibrosis
References
Pediatr Pulmonol. 2019 Feb;54(2):133-140

February 2019

Title: Social Support is Associated with Fewer Reported Symptoms and Decreased Treatment Burden in Adults with Cystic Fibrosis
References
J Cyst Fibros. 2019 Feb 13. pii: S1569-1993(19)30017-7. doi: 10.1016/j.jcf.2019.01.013
Title: Do patients with cystic fibrosis participating in clinical trials demonstrate placebo response? A meta-analysis.
References
J Cyst Fibros. 2019 Feb 13. pii: S1569-1993(18)30833-6. doi: 10.1016/j.jcf.2019.02.003

February 2019

Title: CT evaluation of hyperattenuating mucus to diagnose allergic bronchopulmonary aspergillosis in the special condition of cystic fibrosis
References
J Cyst Fibros. 2019 Feb 12. pii: S1569-1993(18)30902-0. doi: 10.1016/j.jcf.2019.02.002.

February 2019

Title: Lumacaftor-rescued F508del-CFTR has a modified bicarbonate permeability
References
J Cyst Fibros. 2019 Feb 6. pii: S1569-1993(18)30927-5. doi: 10.1016/j.jcf.2019.01.012.

February 2019

Title: Methylomic correlates of autophagy activity in cystic fibrosis
References
J Cyst Fibros. 2019 Feb 5. pii: S1569-1993(18)30824-5. doi: 10.1016/j.jcf.2019.01.011

January 2019

Title: The main mechanism associated with progression of glucose intolerance in older patients with cystic fibrosis is insulin resistance and not reduced insulin secretion capacity.
References
J Cyst Fibros. 2019 Jan 30. pii: S1569-1993(19)30015-3. doi: 10.1016/j.jcf.2019.01.009
Title: Hyperbaric oxygen treatment increases killing of aggregating Pseudomonas aeruginosa isolates from cystic fibrosis patients
References
J Cyst Fibros. 2019 Jan 30. pii: S1569-1993(19)30011-6. doi: 10.1016/j.jcf.2019.01.005. 
Title: Antimicrobial susceptibility testing (AST) and associated clinical outcomes in individuals with cystic fibrosis: A systematic review.
References
J Cyst Fibros. 2019 Jan 30. pii: S1569-1993(19)30014-1. doi: 10.1016/j.jcf.2019.01.008.

January 2019

Title: Visceral Adipose Tissue is Associated with Poor Diet Quality and Higher Fasting Glucose in Adults with Cystic Fibrosis
References
J Cyst Fibros. 2019 Jan 18. pii: S1569-1993(18)30812-9. doi: 10.1016/j.jcf.2019.01.002

January 2019

Title: Application of Multiple Event Analysis as an alternative approach to studying pulmonary exacerbations as an outcome measure
References
J Cyst Fibros. 2019 Jan 11. pii: S1569-1993(18)30943-3. doi: 10.1016/j.jcf.2018.12.005

January 2019

Title: Systemic levels of anti-PAD4 autoantibodies correlate with airway obstruction in cystic fibrosis
References
J Cyst Fibros. 2019 Jan 10. pii: S1569-1993(18)30971-8. doi: 10.1016/j.jcf.2018.12.010

December 2018

Title: Measuring Recovery in Health-Related Quality of Life During and After Pulmonary Exacerbations in Patients with Cystic Fibrosis
References
J Cyst Fibros. 2018 Dec 23. pii: S1569-1993(18)30942-1. doi: 10.1016/j.jcf.2018.12.004.

December 2018

Title: Isogenic cell models of cystic fibrosis-causing variants in natively expressing pulmonary epithelial cells.
References
J Cyst Fibros. 2018 Dec 15. pii: S1569-1993(18)30940-8. doi: 10.1016/j.jcf.2018.12.001. 

December 2018

Title: Cirrhosis associated with decreased survival and a 10-year lower median age at death of cystic fibrosis patients in the Netherlands
References
J Cyst Fibros. 2018 Dec 14. pii: S1569-1993(18)30937-8. doi: 10.1016/j.jcf.2018.11.009.

December 2018

Title: Depletion of BAFF cytokine exacerbates infection in Pseudomonas aeruginosa infected mice
References
J Cyst Fibros. 2018 Dec 7. pii: S1569-1993(18)30864-6. doi: 10.1016/j.jcf.2018.11.015. 

December 2018

Title: Prevalence and diversity of filamentous fungi in the airways of cystic fibrosis patients - A Dutch, multicentre study.
References
J Cyst Fibros. 2018 Dec 1. pii: S1569-1993(18)30939-1. doi: 10.1016/j.jcf.2018.11.012.
Theme
Epidemiology/Models of care

November 2018

Title: Non-Invasive Ventilation and Clinical Outcomes in Cystic Fibrosis: findings from the UK CF Registry
References
J Cyst Fibros. 2018 Nov 28. pii: S1569-1993(18)30934-2. doi: 10.1016/j.jcf.2018.11.006.

November 2018

Title: Pre-transplant factors associated with mortality after lung transplantation in cystic fibrosis: A systematic review and meta-analysis
References

November 2018

Title: Urinary Metabolomics Reveals Unique Metabolic Signatures in Infants with Cystic Fibrosis
References
J Cyst Fibros. 2018 Nov 23. pii: S1569-1993(18)30916-0. doi: 10.1016/j.jcf.2018.10.016

November 2018

Title: Cystic fibrosis is associated with an increased risk of Barrett’s esophagus
References
J Cyst Fibros. 2018 Nov 22. pii: S1569-1993(18)30933-0. doi: 10.1016/j.jcf.2018.11.005
Title: Dental and periodontal manifestations in patients with cystic fibrosis - A systematic review
References
J Cyst Fibros. 2018 Nov 22. pii: S1569-1993(18)30935-4. doi: 10.1016/j.jcf.2018.11.007.

November 2018

Title: Eluforsen: a potential new treatment option for people with cystic fibrosis (CF) due to the F508del gene mutation?
References
J Cyst Fibros. 2018 Nov 19. pii: S1569-1993(18)30914-7. doi: 10.1016/j.jcf.2018.10.015

November 2018

Title: Use of telavancin in adolescent patients with cystic fibrosis and prior intolerance to vancomycin: A case series.
References
J Cyst Fibros. 2018 Nov;17(6):e48-e50. doi: 10.1016/j.jcf.2018.08.003.

November 2018

Title: Clinical outcomes in U.S. infants with cystic fibrosis from 2001 to 2012
References
Pediatr Pulmonol. 2018 Nov;53(11):1492-1497. doi: 10.1002/ppul.2416

November 2018

Title: Comparison of Lung Clearance Index Determined by Washout of N2 and SF6 in Infants and Preschool Children with Cystic Fibrosis
References
J Cyst Fibros. 2018 Nov 9. pii: S1569-1993(18)30929-9. doi: 10.1016/j.jcf.2018.11.001

November 2018

Title: Glycosaminoglycans are differentially involved in bacterial binding to healthy and cystic fibrosis lung cells.
References
J Cyst Fibros. 2018 Nov 8. pii: S1569-1993(18)30920-2. doi: 10.1016/j.jcf.2018.10.017. 

November 2018

Title: Validation of the French 3-year prognostic score using the Canadian Cystic Fibrosis registry.
References
J Cyst Fibros. 2018 Nov 2. pii: S1569-1993(18)30911-1. doi: 10.1016/j.jcf.2018.10.014

October 2018

Title: Antibody response against Mycobacterium avium complex in cystic fibrosis patients measured by a novel IgG ELISA test
References
J Cyst Fibros. 2018 Nov 29. pii: S1569-1993(18)30938-X. doi: 10.1016/j.jcf.2018.11.011. [

October 2018

Title: Failure to conceive in women with CF is associated with pancreatic insufficiency and advancing age
References
J Cyst Fibros. 2018 Oct 23. pii: S1569-1993(18)30867-1. doi: 10.1016/j.jcf.2018.10.009.

October 2018

Title: SWATH label-free proteomics for cystic fibrosis research
References
J Cyst Fibros. 2018 Oct 19. pii: S1569-1993(18)30855-5. doi: 10.1016/j.jcf.2018.10.004.
 
Title: SWATH label-free proteomics for cystic fibrosis research
References
J Cyst Fibros. 2018 Oct 19. pii: S1569-1993(18)30855-5. doi: 10.1016/j.jcf.2018.10.004.
 
Title: Prevalence, geographic risk factor, and development of a standardized protocol for fungal isolation in cystic fibrosis: Results from the international prospective study “MFIP”
References
J Cyst Fibros. 2018 Oct 19. pii: S1569-1993(18)30839-7. doi: 10.1016/j.jcf.2018.10.001

October 2018

Title: Seasonal fluctuation of lung function in cystic fibrosis: A national register-based study in two northern European populations
References
J Cyst Fibros. 2018 Oct 18. pii: S1569-1993(18)30858-0. doi: 10.1016/j.jcf.2018.10.006. 

October 2018

Title: Disparities in Mortality of Hispanic Patients with Cystic Fibrosis in the United States. A National and Regional Cohort Study
References
Am J Respir Crit Care Med. 2018 Oct 15;198(8):1055-1063. doi: 10.1164/rccm.201711-2357OC.

October 2018

Title: Combined antifungal therapy is superior to monotherapy in pulmonary scedosporiosis in cystic fibrosis
References
J Cyst Fibros. 2018 Oct 5. pii: S1569-1993(18)30794-X. doi: 10.1016/j.jcf.2018.08.012

September 2018

Title: Phenotypic spectrum of patients with cystic fibrosis and cystic fibrosis-related disease carrying p.Arg117His
References
J Cyst Fibros. 2018 Sep 29. pii: S1569-1993(18)30800-2. doi: 10.1016/j.jcf.2018.09.002

September 2018

Title: Human epididymis protein 4 (HE4) levels inversely correlate with lung function improvement (delta FEV1) in cystic fibrosis patients receiving ivacaftor treatment.
References
J Cyst Fibros. 2018 Sep 26. pii: S1569-1993(18)30795-1. doi: 10.1016/j.jcf.2018.08.013.
Title: Mental Health screening in cystic fibrosis centres across Europe
References
J Cyst Fibros. 2018 Sep 26. pii: S1569-1993(18)30801-4. doi: 10.1016/j.jcf.2018.09.003

September 2018

Title: The Q359K/T360K mutation causes cystic fibrosis in Georgian Jews.
References
J Cyst Fibros. 2018 Sep;17(5):e41-e45. doi: 10.1016/j.jcf.2018.06.008. Epub 2018 Jul 20.

September 2018

Title: Repeated Hot Water and Steam Disinfection of Pari LC Plus® Nebulizers Alters Nebulizer Output
References
J Cyst Fibros. 2018 Sep 14. pii: S1569-1993(18)30753-7. doi: 10.1016/j.jcf.2018.08.005.

September 2018

Title: Higher Interleukin-7 serum concentrations in patients with cystic fibrosis correlate with impaired lung function
References

September 2018

Title: Rate and Predictors of Prescription of Lumacaftor – Ivacaftor in the 18 Months Following Approval in the United States
References
J Cyst Fibros. 2018 Sep 7. pii: S1569-1993(18)30755-0. doi: 10.1016/j.jcf.2018.08.007.

September 2018

Title: Breathlessness catastrophizing relates to poorer quality of life in adults with cystic fibrosis
References
J Cyst Fibros. 2018 Sep 6. pii: S1569-1993(18)30756-2. doi: 10.1016/j.jcf.2018.08.008