With the CF Research News, we aim to bridge the gap between people with CF and the researchers investigating CF and how best to treat those with the condition.
We want to provide access to patients, parents, relatives, friends and caregivers of patients with CF to all scientific work mainly published in the Journal of Cystic Fibrosis (JCF).

All PDF files published hereunder are lay version summaries of work published in the JCF.

November 2023

Title: Changes in cholesterol levels in people with cystic fibrosis after starting highly effective modulators
References
J Cyst Fibros. 2023 Nov;22(6):1024-1026. doi: 10.1016/j.jcf.2023.10.002. Epub 2023 Oct 12

October 2023

Title: Frequency of urinary and anal incontinence in patient suffering from cystic fibrosis and their impact on quality of life
References
J Cyst Fibros. 2023 Oct 29:S1569-1993(23)01659-4. doi: 10.1016/j.jcf.2023.10.011.

October 2023

Title: Unlocking the Secrets of Cystic Fibrosis: A Genetic Study of people with CF in Germany
References
J Cyst Fibros. 2023 Oct 20:S1569-1993(23)00928-1. doi: 10.1016/j.jcf.2023.10.009.

October 2023

Title: Pulmonary exacerbation treatment location
References
J Cyst Fibros. 2023 Oct 5:S1569-1993(23)00926-8. doi: 10.1016/j.jcf.2023.10.004.

October 2023

Title: Repeating bacterial cultures in people with cystic fibrosis (CF) hospitalised with chest exacerbations may not be useful
References
J Cyst Fibros. 2023 Oct 12:S1569-1993(23)00930-X. doi: 10.1016/j.jcf.2023.10.007.

October 2023

Title: Testing the Usability, Acceptability, and Appropriateness of a Web-Based Reproductive Decision Support Tool for Cystic Fibrosis
References
J Cyst Fibros. 2023 Oct 11:S1569-1993(23)00924-4. doi: 10.1016/j.jcf.2023.10.003.

October 2023

Title: Impact of Highly Effective Modulator Therapy on Sinus Disease and Health Status: 2-year Follow-up
References
J Cyst Fibros. 2023 Oct 5:S1569-1993(23)00917-7. doi: 10.1016/j.jcf.2023.09.013.

October 2023

Title: Understanding patient views on use of Trikafta after lung transplant
References
J Cyst Fibros. 2023 Oct 3:S1569-1993(23)00921-9. doi: 10.1016/j.jcf.2023.09.017.

September 2023

Title: How long after treatment do people with cystic fibrosis no longer have Burkholderia cepacia complex in their sputum samples?
References
J Cyst Fibros. 2023 Sep 27:S1569-1993(23)00920-7. doi: 10.1016/j.jcf.2023.09.016.

September 2023

Title: Using Home Spirometry Devices to Watch Over Children with Cystic Fibrosis: Can It Help Detect and Treat Pulmonary Exacerbations and Improve 1-Year Lung Function?
References
J Cyst Fibros. 2023 Sep 23:S1569-1993(23)00911-6. doi: 10.1016/j.jcf.2023.09.007.
Title: Changes in pancreatic enzyme function for children with cystic fibrosis while taking modulators (Trikafta®, Orkambi®, Symdeco®, and Kalydeco®)
References
J Cyst Fibros. 2023 Sep 26:S1569-1993(23)00909-8. doi: 10.1016/j.jcf.2023.09.005.

September 2023

Title: A Review of Cystic Fibrosis Sinus and Nasal Disease response to CFTR Modulator Therapy
References
J Cyst Fibros. 2023 Sep 8:S1569-1993(23)00877-9. doi: 10.1016/j.jcf.2023.08.009.

September 2023

Title: Making the diagnosis of nontuberculous mycobacteria (NTM) lung disease standard with the PREDICT study
References
J Cyst Fibros. 2023 Sep 2:S1569-1993(23)00876-7. doi: 10.1016/j.jcf.2023.08.007.

August 2023

Title: What do people with cystic fibrosis eat? – A systematic review
References
J Cyst Fibros. 2023 Aug 28:S1569-1993(23)00874-3. doi: 10.1016/j.jcf.2023.08.004.

August 2023

Title: A mini-pancreas model shows its activity is dependent on chloride
References
J Cyst Fibros. 2023 Aug 24:S1569-1993(23)00872-X. doi: 10.1016/j.jcf.2023.08.003.

July 2023

Title: A Search Begins for the Role of CircRNAs in Cystic Fibrosis
References
J Cyst Fibros. 2023 Jul;22(4):683-693. doi: 10.1016/j.jcf.2023.04.021. Epub 2023 May 2
Title: Improvement of Pulmonary Function After Implementation of a Standardized Cystic Fibrosis Care Algorithm
References
J Cyst Fibros. 2023 Jul;22(4):710-714. doi: 10.1016/j.jcf.2023.03.016. Epub 2023 Apr 8.
Title: Bacterial infections and the antibiotics prescribed for children with cystic fibrosis-related pulmonary exacerbations
References
J Cyst Fibros. 2023 Jul;22(4):630-635. doi: 10.1016/j.jcf.2023.02.001. Epub 2023 Feb 26.

July 2023

Title: Response to oral antibiotic treatment in people with cystic fibrosis
References
J Cyst Fibros. 2023 Jul 18;S1569-1993(23)00829-9. doi: 10.1016/j.jcf.2023.06.015.
Theme
Care of patients with CF, Lung Disease and Infection

July 2023

Title: Comparing how effective and safe 14 days and 28 days of inhaled aztreonam were at getting rid of a Pseudomonas bacterial lung infection.
References
J Cyst Fibros. 2023 Jul 14:S1569-1993(23)00821-4. doi: 10.1016/j.jcf.2023.06.008.

July 2023

Title: CFTR modulator therapy may improve lipid levels in children and adolescents with cystic fibrosis.
References
J Cyst Fibros. 2023 Jul 13:S1569-1993(23)00831-7. doi: 10.1016/j.jcf.2023.07.001.

July 2023

Title: Ivacaftor impacts nutrition and growth status in 4 to 24 month old children within the first 12 weeks
References
J Cyst Fibros. 2023 Jul 10;S1569-1993(23)00114-5. doi: 10.1016/j.jcf.2023.04.010.
Theme
Care of patients with CF, Nutrition/Gastroenterology

July 2023

Title: Successful treatment of a blockage in the lower portion of the small intestine in patients with cystic fibrosis using a solution administered during a colonoscopy.
References
J Cyst Fibros. 2023 Jul 8;S1569-1993(23)00828-7. doi: 10.1016/j.jcf.2023.06.014
Theme
Care of patients with CF, Imaging, Nutrition/Gastroenterology

July 2023

Title: CF Mutation Presents with Intestinal Obstruction in Newborns and Later Pancreatic Sufficiency
References
J Cyst Fibros. 2023 Jul 7;S1569-1993(23)00045-0. doi: 10.1016/j.jcf.2023.02.002.
Theme
Care of patients with CF, Diagnosis/Screening, Newborn screening

July 2023

Title: STOP Codon mutations are associated with more severe disease from childhood in people with cystic fibrosis
References
J Cyst Fibros. 2023 Jul 6:S1569-1993(23)00819-6. doi: 10.1016/j.jcf.2023.06.005.
Title: Changes in weight and how much you eat after starting triple modulator therapy in adults with cystic fibrosis
References
J Cyst Fibros. 2023 Jul 6;S1569-1993(23)00824-X. doi: 10.1016/j.jcf.2023.06.010.
Theme
Nutrition/Gastroenterology
Title: Airway infection increases Pseudomonas aeruginosa acquisition
References
J Cyst Fibros. 2023 Jul 6;S1569-1993(23)00822-6. doi: 10.1016/j.jcf.2023.06.007
Theme
Lung Disease and Infection, Microbiology

July 2023

Title: Gilbert’s syndrome post elexacaftor/tezacaftor/ivacaftor
References
J Cyst Fibros. 2023 Jul 1:S1569-1993(23)00827-5. doi: 10.1016/j.jcf.2023.06.013.

June 2023

Title: What happens to muscle, fat and body mass index between 8 and 18 years of age in children with cystic fibrosis
References
J Cyst Fibros. 2023 Jun 24;S1569-1993(23)00817-2. doi: 10.1016/j.jcf.2023.06.003.
Theme
Care of patients with CF, Nutrition/Gastroenterology, Pulmonology

June 2023

Title: Anxiety and Depression Symptom Patterns over 6 years in one Pediatric CF Center
References
J Cyst Fibros. 2023 Jun 29;S1569-1993(23)00823-8. doi: 10.1016/j.jcf.2023.06.009.
Theme
Care of patients with CF, Psychosocial
Title: Weight A Minute: Exploring the effect on total weight, fat and fat-free weight after the initiation of Elexacaftor/ Tezacaftor/ Ivacaftor in adults with CF
References
J Cyst Fibros. . 2023 Jun 23;S1569-1993(23)00180-7. doi: 10.1016/j.jcf.2023.06.002.
Theme
Care of patients with CF, Diabetes, Nutrition/Gastroenterology

June 2023

Title: Elexacaftor/Tezacaftor/Ivacaftor improves CFTR activity and pulmonary function in Cystic Fibrosis Patients carrying the N1303K Mutation
References
J Cyst Fibros. 2023 Jun 16;S1569-1993(23)00178-9. doi: 10.1016/j.jcf.2023.06.001.
Theme
Pulmonology
Title: Elexacaftor/Tezacaftor/Ivacaftor improves CFTR activity and pulmonary function in Cystic Fibrosis Patients carrying the N1303K Mutation
References
J Cyst Fibros. 2023 Jun 16;S1569-1993(23)00178-9. doi: 10.1016/j.jcf.2023.06.001.
Theme
Care of patients with CF, Clinical Trials, Pulmonology

June 2023

Title: Molecular fingerprinting of Pseudomonas aeruginosa from PWCF, and a UK reference laboratory investigation into frequency of cross-infection
References
J Cyst Fibros. 2023 Jun 2;S1569-1993(23)00176-5. doi: 10.1016/j.jcf.2023.05.017.
Theme
Microbiology

May 2023

Title: People with CF who take part in clinical trials do not represent the general CF population well
References
Theme
Clinical Trials

May 2023

Title: How to interpret changes in home spirometry when people are feeling well?
References
J Cyst Fibros. 2023 May 25;S1569-1993(23)00141-8. doi: 10.1016/j.jcf.2023.05.011.
Theme
Care of patients with CF, Pulmonology
Title: Male female differences after elexacaftor/tezacaftor/ivacaftor
References
J Cyst Fibros. 2023 May 25;S1569-1993(23)00139-X. doi: 10.1016/j.jcf.2023.05.009.
Theme
Epidemiology/Models of care, Pulmonology

May 2023

Title: Simplified method for cystic fibrosis sweat testing using microneedle patches is effective in human study.
References
 Cyst Fibros. 2023 May 24;S1569-1993(23)00120-0. doi: 10.1016/j.jcf.2023.04.014.
Theme
Diagnosis/Screening

May 2023

Title: Nutritional Considerations for a New Era: A CF Foundation Position Paper
References
J Cyst Fibros. 2023 May 23;S1569-1993(23)00140-6. doi: 10.1016/j.jcf.2023.05.010.
 
Theme
Care of patients with CF, Exercise, Nutrition/Gastroenterology

May 2023

Title: People with CF face high costs of CF care which have implications for debt, access to health care, adequate food, and other necessities of life.
References
J Cyst Fibros. 2023 May;22(3):471-477. doi: 10.1016/j.jcf.2023.01.002. Epub 2023 Jan 27.
Theme
Care of patients with CF, Psychosocial

May 2023

Title: Understanding sleep in young adults with cystic fibrosis (CF) taking elexacaftor/tezacaftor/ivacaftor (ETI)
References
J Cyst Fibros. 2023 May 18;S1569-1993(23)00135-2. doi: 10.1016/j.jcf.2023.05.005.
Theme
Psychosocial
Title: Understanding sleep in young adults with cystic fibrosis (CF) taking elexacaftor/tezacaftor/ivacaftor (ETI)
References
J Cyst Fibros. 2023 May 18;S1569-1993(23)00135-2. doi: 10.1016/j.jcf.2023.05.005.

May 2023

Title: Eradication of Nontuberculous Mycobacteria in People with Cystic Fibrosis Treated with Elexacaftor/Tezacaftor/Ivacaftor
References
J Cyst Fibros. 2023 May 10;S1569-1993(23)00133-9. doi: 10.1016/j.jcf.2023.05.003.
Theme
Care of patients with CF, Microbiology

May 2023

Title: Use of Cystic Fibrosis inhaled medication after Elexacaftor/Tezacaftor/Ivacaftor in comparison to before
References
J Cyst Fibros. 2023 May 9;S1569-1993(23)00131-5. doi: 10.1016/j.jcf.2023.05.001.
 
Theme
Care of patients with CF, Epidemiology/Models of care, Pulmonology

May 2023

Title: Understanding Joint Problems in Cystic Fibrosis: Defining Stages of Arthritis with Ultrasound and Clinical Assessment
References
J Cyst Fibros. 2023 May 5;S1569-1993(23)00116-9. doi: 10.1016/j.jcf.2023.04.011.
Theme
Care of patients with CF, Imaging

May 2023

Title: Understanding the relationship between secondhand smoke exposure and lung function in children with cystic fibrosis
References
J Cyst Fibros. 2023 May 2;S1569-1993(23)00126-1. doi: 10.1016/j.jcf.2023.04.020.
Theme
Care of patients with CF, Pulmonology
Title: Changes in blood levels of vitamins A, D and E after starting Kaftrio
References
J Cyst Fibros. 2023 May 2;S1569-1993(23)00125-X. doi: 10.1016/j.jcf.2023.04.019.
Theme
Care of patients with CF, Nutrition/Gastroenterology

April 2023

Title: Inhaled mRNA therapy for treatment of Cystic Fibrosis: Results of an Early Phase Clinical Trial
References
J Cyst Fibros. 2023 Apr 28;S1569-1993(23)00112-1. doi: 10.1016/j.jcf.2023.04.008
Theme
Care of patients with CF, Clinical Trials, Pulmonology

April 2023

Title: Variability of the sweat test in children with Cystic Fibrosis previously with an inconclusive diagnosis Vito Terlizzi, Daniela Dolce
References
J Cyst Fibros. 2023 Apr 26;S1569-1993(23)00122-4. doi: 10.1016/j.jcf.2023.04.018.
Theme
Care of patients with CF, Diagnosis/Screening, Parents, Psychosocial

April 2023

Title: Is it cost-effective to use genetic tools to predict how well patients with cystic fibrosis will respond to treatment?
References
J Cyst Fibros. 2023 Apr 24;S1569-1993(23)00119-4. doi: 10.1016/j.jcf.2023.04.013.
Theme
Care of patients with CF, Epidemiology/Models of care
Title: Willingness of people taking elexacaftor/tezacaftor/ivacaftor to be in new CFTR modulator studies
References
J Cyst Fibros. 2023 Apr 24;S1569-1993(23)00096-6. doi: 10.1016/j.jcf.2023.04.007.
Theme
Clinical Trials

April 2023

Title: The combination elexacaftor/tezacaftor/ivacaftor (eti) alters the lipid composition of the lung cells irrespective of CFTR mutation
References
J Cyst Fibros. 2023 Apr 21;S1569-1993(23)00115-7. doi: 10.1016/j.jcf.2023.04.012.
Theme
CFTR/Basic Science
Title: Cumulative ototoxicity of tobramycin
References
J Cyst Fibros. 2023 Apr 21;S1569-1993(23)00092-9. doi: 10.1016/j.jcf.2023.04.002.
Theme
Care of patients with CF, Lung Disease and Infection

April 2023

Title: A mobile app for self-management of CF and improved patient-centred care
References
J Cyst Fibros. 2023 Apr 19;S1569-1993(23)00113-3. doi: 10.1016/j.jcf.2023.04.009.
Theme
Epidemiology/Models of care

April 2023

Title: Impact of the De-escalation of Supportive Therapies in Patients with Cystic Fibrosis Taking Elexacaftor, Tezacaftor, Ivacaftor
References
J Cyst Fibros. 2023 Apr 15;S1569-1993(23)00082-6. doi: 10.1016/j.jcf.2023.03.018.
Theme
Care of patients with CF

April 2023

Title: Children and Adolescents with CF who have a patchy liver on a research ultrasound (US) are at increased risk of developing advanced CF liver disease
References
J Cyst Fibros. 2023 Apr 7;S1569-1993(23)00083-8. doi: 10.1016/j.jcf.2023.03.019
Theme
Imaging, Nutrition/Gastroenterology

April 2023

Title: Impact of unplanned pregnancies in cystic fibrosis
References
J Cyst Fibros. 2023 Apr 5;S1569-1993(23)00084-X. doi: 10.1016/j.jcf.2023.03.020.
Theme
Care of patients with CF, Pregnancy with CF, Pulmonology

March 2023

Title: How the discovery of new white blood cell subtypes can improve our understanding of lung disease progression in adult CF patients?
References
J Cyst Fibros. 2023 Mar 25;S1569-1993(23)00072-3. doi: 10.1016/j.jcf.2023.03.009.
Theme
CFTR/Basic Science, Immunology, Lung Disease and Infection

March 2023

Title: Autoimmunity (a condition where the body's immune system mistakes its own healthy tissues as foreign and attacks them) in People with Cystic Fibrosis
References
J Cyst Fibros. 2023 Mar 23;S1569-1993(23)00071-1. doi: 10.1016/j.jcf.2023.03.007.
Theme
Immunology
Title: Cervical mucus quality in females with and without cystic fibrosis
References
J Cyst Fibros. 2023 Mar 23;S1569-1993(23)00077-2. doi: 10.1016/j.jcf.2023.03.013.
Theme
Endocrinology, Pregnancy with CF
Title: What do dietitians, doctors and physiotherapists think about the management of people with CF who are living with overweight and obesity?
References
J Cyst Fibros. 2023 Mar 23;S1569-1993(23)00075-9. doi: 10.1016/j.jcf.2023.03.011.
Theme
Care of patients with CF, Nutrition/Gastroenterology

March 2023

Title: Year in Review (2022): Modulators and COVID-19: the story does on
References
J Cyst Fibros. 2023 Mar;22(2):188-192. doi: 10.1016/j.jcf.2023.03.001. Epub 2023 Mar 6.
Theme
Bone health, Care of patients with CF, Imaging, Lung Disease and Infection, Nutrition/Gastroenterology, Psychosocial, Pulmonology, Transplantation
Title: Effects of elexacaftor/tezacaftor/ivacaftor on liver tests in cystic fibrosis
References
J Cyst Fibros. 2023 Mar;22(2):256-262. doi: 10.1016/j.jcf.2023.01.007. Epub 2023 Jan 19.
Theme
CFTR/Basic Science, Nutrition/Gastroenterology
Title: Sharing decisions about family goals: A study exploring women’s experiences and needs for support.
References
J Cyst Fibros. 2023 Mar;22(2):207-216. doi: 10.1016/j.jcf.2023.02.007. Epub 2023 Feb 28.
Theme
Care of patients with CF, Pregnancy with CF, Psychosocial
Title: An overview of CFTR modulators and pancreas function
References
J Cyst Fibros. 2023 Mar;22(2):193-200. doi: 10.1016/j.jcf.2022.08.008.
Theme
Care of patients with CF, Nutrition/Gastroenterology
Title: Two-year follow-up results from an ongoing study on the safety and effectiveness of elexacaftor/tezacaftor/ivacaftor when used in real-world settings by people with cystic fibrosis
References
J Cyst Fibros. 2023 Mar 22;S1569-1993(23)00066-8. doi: 10.1016/j.jcf.2023.03.002.
Theme
Clinical Trials, Pulmonology

March 2023

Title: A letter in response to the recently published article entitled “Effect of elexacaftor/tezacaftor/ivacaftor on annual rate of lung function decline in people with cystic fibrosis
References
J Cyst Fibros. 2023 Mar 20;S1569-1993(23)00076-0. doi: 10.1016/j.jcf.2023.03.012.
Theme
Pulmonology

March 2023

Title: Postage of sputum samples from home to clinic can be used for microbiology surveillance
References
J Cyst Fibros. 2023 Mar 16;S1569-1993(23)00073-5. doi: 10.1016/j.jcf.2023.03.008.
Theme
Microbiology

March 2023

Title: Understanding Medical Traumatic Stress in Cystic Fibrosis from the Viewpoints of Patients, Families, and Providers
References
J Cyst Fibros. 2023 Mar 14;S1569-1993(22)01427-8. doi: 10.1016/j.jcf.2022.12.008.

March 2023

Title: Association between nebulizer therapies adherence and visit-to-visit variability of lung function in patients with cystic fibrosis
References
J Cyst Fibros. 2023 Mar 13;S1569-1993(23)00070-X. doi: 10.1016/j.jcf.2023.03.006.
Theme
Pulmonology

March 2023

Title: How does telehealth impact the health of children with cystic fibrosis
References
J Cyst Fibros. 2023 Mar 6;S1569-1993(23)00068-1. doi: 10.1016/j.jcf.2023.03.003.
Theme
Care of patients with CF, Epidemiology/Models of care

March 2023

Title: Models of Cystic Fibrosis care after lung transplant
References
J Cyst Fibros. 2023 Mar 5;S1569-1993(23)00059-0. doi: 10.1016/j.jcf.2023.02.011.
Theme
Care of patients with CF, Epidemiology/Models of care, Transplantation

February 2023

Title: Investigating the diagnostic potential of small cell particles in the blood of people with CF
References
J Cyst Fibros. 2023 Feb 27;S1569-1993(23)00056-5. doi: 10.1016/j.jcf.2023.02.005.
Theme
CFTR/Basic Science
Title: More favorable growth profiles in early childhood are associated with higher lung function at age six
References
J Cyst Fibros. 2023 Feb 27;S1569-1993(23)00060-7. doi: 10.1016/j.jcf.2023.02.008.
Theme
Care of patients with CF, Nutrition/Gastroenterology

February 2023

Title: Suicide Attempts in Adolescents with Cystic Fibrosis on Elexacaftor/Tezacaftor/Ivacaftor Therapy
References
J Cyst Fibros. 2023 Feb 7;S1569-1993(23)00023-1. doi: 10.1016/j.jcf.2023.01.015.
Theme
Care of patients with CF, Psychosocial

February 2023

Title: CFTR modulators: a new therapeutic approach but not for all CF patients
References
J Cyst Fibros. 2023 Feb 2;S1569-1993(23)00020-6. doi: 10.1016/j.jcf.2023.01.012.
Theme
Care of patients with CF, Nutrition/Gastroenterology

January 2023

Title: Diabetes is associated with an increased burden of tummy and bowel symptoms in adults with cystic fibrosis
References
J Cyst Fibros. 2023 Jan 27;S1569-1993(23)00018-8. doi: 10.1016/j.jcf.2023.01.010.
Theme
Care of patients with CF, Diabetes, Nutrition/Gastroenterology

January 2023

Title: The Completion of Airway Clearance Therapy at School in a Group of Pediatric Patients with Cystic Fibrosis
References
J Cyst Fibros. 2023 Jan 24;S1569-1993(23)00007-3. doi: 10.1016/j.jcf.2023.01.006.
Theme
Care of patients with CF, Parents, Psychosocial, Pulmonology

January 2023

Title: Bariatric surgery in a patient with cystic fibrosis and diabetes: a case report
References
J Cyst Fibros. 2023 Jan 22;S1569-1993(23)00009-7. doi: 10.1016/j.jcf.2023.01.008.
Theme
Care of patients with CF, Diabetes, Endocrinology, Nutrition/Gastroenterology

January 2023

Title: Bone health after lung transplantation in patients with cystic fibrosis
References
J Cyst Fibros. 2023 Jan 18;S1569-1993(23)00005-X. doi: 10.1016/j.jcf.2023.01.003.
Theme
Bone health, Care of patients with CF, Pulmonology, Transplantation

January 2023

Title: Examining the potential for drug interactions with Trikafta®/Kaftrio® in people with cystic fibrosis
References
J Cyst Fibros. 2023 Jan 16;S1569-1993(23)00004-8. doi: 10.1016/j.jcf.2023.01.005.
Theme
Care of patients with CF

January 2023

Title: Lung infection in people with advanced cystic fibrosis lung disease
References
J Cyst Fibros. 2023 Jan 8;S1569-1993(23)00002-4. doi: 10.1016/j.jcf.2023.01.001.
Theme
CFTR/Basic Science, Microbiology

January 2023

Title: CFTR in the pancreas, the intestine and the kidney: Function, dysfunction and potential future remedies
References
J Cyst Fibros. 2023 Mar;22 Suppl 1:S17-S22. doi: 10.1016/j.jcf.2022.12.017. Epub 2023 Jan 6.
Theme
CFTR/Basic Science, Nutrition/Gastroenterology
Title: What happens with CFTR inside human cells affected by cystic fibrosis and how the latest CF drugs change the effects
References
J Cyst Fibros. 2023 Jan 6;S1569-1993(22)01435-7. doi: 10.1016/j.jcf.2022.12.015.
Theme
CFTR/Basic Science

December 2022

Title: The Presence of Clostridioides difficile in Stool Samples of Children with Cystic Fibrosis
References
J Cyst Fibros. 2022 Dec 28;S1569-1993(22)01434-5. doi: 10.1016/j.jcf.2022.12.014.
Theme
Microbiology, Nutrition/Gastroenterology
Title: Fundamental and translational research in Cystic Fibrosis – why we still need it
References
J Cyst Fibros. 2022 Dec 26;S1569-1993(22)01430-8. doi: 10.1016/j.jcf.2022.12.010.
Theme
CFTR/Basic Science

December 2022

Title: Safety and efficacy of extended treatment with tezacaftor/ivacaftor
References
J Cyst Fibros. 2022 Dec 27;S1569-1993(22)01426-6. doi: 10.1016/j.jcf.2022.12.006
Theme
Pulmonology

December 2022

Title: Pulmonary exacerbation groupings based on blood inflammation in Cystic Fibrosis
References
J Cyst Fibros. 2022 Dec 24;S1569-1993(22)01433-3. doi: 10.1016/j.jcf.2022.12.013.
Theme
Care of patients with CF, Lung Disease and Infection, Pulmonology

December 2022

Title: Effect of variants in the CFTR gene on the CFTR transcripts and protein to improve patients care.
References
J Cyst Fibros. 2022 Dec 23;S1569-1993(22)01423-0. doi: 10.1016/j.jcf.2022.12.003.
Theme
Care of patients with CF, CFTR/Basic Science

December 2022

Title: Experiences of people with cystic fibrosis living without Trikafta/Kaftrio
References
J Cyst Fibros. 2022 Dec 20;S1569-1993(22)01428-X. doi: 10.1016/j.jcf.2022.12.007.
Theme
Care of patients with CF, Psychosocial

December 2022

Title: Study of how the G1244E cystic fibrosis mutation modifies the CFTR function and response to available CFTR modulators
References
J Cyst Fibros. 2022 Dec 19;S1569-1993(22)01425-4. doi: 10.1016/j.jcf.2022.12.005.
Theme
CFTR/Basic Science

December 2022

Title: Risk of Human papilloma virus infection and of cervical lesions in females with cystic fibrosis
References
J Cyst Fibros. 2022 Dec 14;S1569-1993(22)01415-1. doi: 10.1016/j.jcf.2022.11.005.
Theme
Care of patients with CF, Microbiology, Transplantation

December 2022

Title: Clinician Perspectives on Assessing for Disordered Eating and Body Image Disturbance in Adolescents and Young Adults with Cystic Fibrosis
References
J Cyst Fibros. 2022 Dec 2;S1569-1993(22)01416-3. doi: 10.1016/j.jcf.2022.11.006.
Theme
Care of patients with CF, Psychosocial

November 2022

Title: Mutations carrying premature termination mutations are improved by ELX-02
References
J Cyst Fibros. 2022 Nov 16;S1569-1993(22)01411-4. doi: 10.1016/j.jcf.2022.11.002.
Theme
Care of patients with CF, Exercise

November 2022

Title: The effects of Trikafta/Kaftrio on people with CF who have mutations other than the most common CF mutation (F508del)
References
J Cyst Fibros. 2022 Nov 10;S1569-1993(22)01393-5. doi: 10.1016/j.jcf.2022.10.011.
Theme
Care of patients with CF, Lung Disease and Infection, Pulmonology

October 2022

Title: Best therapeutic approaches to treat everyone with CF
References
J Cyst Fibros. 2022 Oct 30;S1569-1993(22)01389-3. doi: 10.1016/j.jcf.2022.10.007.
Theme
CFTR/Basic Science

October 2022

Title: Gastrointestinal symptom burden in cystic fibrosis
References
J Cyst Fibros. 2022 Oct 29;S1569-1993(22)01388-1. doi: 10.1016/j.jcf.2022.10.006.
 
Theme
Care of patients with CF, Nutrition/Gastroenterology

October 2022

Title: Effect of ETI on CF Gastrointestinal Disease
References
J Cyst Fibros. 2022 Oct 21;S1569-1993(22)01384-4. doi: 10.1016/j.jcf.2022.10.003.
Theme
Care of patients with CF, Nutrition/Gastroenterology

October 2022

Title: The risk of developing bowel cancer in people with cystic fibrosis, or cystic fibrosis causing mutations.
References
J Cyst Fibros. 2022 Oct 14;S1569-1993(22)01383-2. doi: 10.1016/j.jcf.2022.10.001.
Theme
Care of patients with CF

October 2022

Title: New guidelines on non CF disorders related to the CFTR gene
References
J Cyst Fibros. 2022 Oct 8;S1569-1993(22)00691-9. doi: 10.1016/j.jcf.2022.09.011.
Theme
Diagnosis/Screening