With the CF Research News, we aim to bridge the gap between people with CF and the researchers investigating CF and how best to treat those with the condition.
We want to provide access to patients, parents, relatives, friends and caregivers of patients with CF to all scientific work mainly published in the Journal of Cystic Fibrosis (JCF).

All PDF files published hereunder are lay version summaries of work published in the JCF.

October 2021

Title: Lung infection by Pseudomonas aeruginosa in children with cystic fibrosis: risk factors and impact on lung function
References
J Cyst Fibros. 2021 Oct 7;S1569-1993(21)01422-3. doi: 10.1016/j.jcf.2021.09.017.
Theme
Lung Disease and Infection

October 2021

Title: A review of sweat testing in Ireland in the era of modern CF care
References
J Cyst Fibros. 2021 Oct 4;S1569-1993(21)01417-X. doi: 10.1016/j.jcf.2021.09.012.
Theme
Diagnosis/Screening

September 2021

Title: Sense of Smell in People with Cystic Fibrosis: Impact of Modulator Therapy
References
J Cyst Fibros. 2021 Sep 28;S1569-1993(21)01419-3. doi: 10.1016/j.jcf.2021.09.014.
Theme
Care of patients with CF, Nutrition/Gastroenterology

September 2021

Title: Using a digital system, CFHealthHub, to automatically record the use of preventative inhaled treatments as to compare the amount of medicines collected from pharmacy to the amount actually used.
References
J Cyst Fibros. 2021 Sep 23;S1569-1993(21)01408-9. doi: 10.1016/j.jcf.2021.09.007.
Theme
Care of patients with CF

September 2021

Title: Drug development for Cystic Fibrosis patients carrying the 3849+10kb C-to-T splicing mutation
References
J Cyst Fibros. 2021 Sep;20(5):865-875. doi: 10.1016/j.jcf.2021.06.003. Epub 2021 Jul 2.
Theme
CFTR/Basic Science

September 2021

Title: Can cough swabs be used to identify bacterial infections in patient with cystic fibrosis.
References
J Cyst Fibros. 2021 Sep 18;S1569-1993(21)01372-2. doi: 10.1016/j.jcf.2021.08.031.

September 2021

Title: Study that tested the effects of a new drug called acebilustat in adultswith cystic fibrosis
References
J Cyst Fibros. 2021 Sep 16;S1569-1993(21)01348-5. doi: 10.1016/j.jcf.2021.08.007.

September 2021

Title: The effect of ETI (Trikafta™) on blood sugars in adults with cystic fibrosis
References
J Cyst Fibros. 2021 Sep 13;S1569-1993(21)01377-1. doi: 10.1016/j.jcf.2021.09.001.

September 2021

Title: A review of three studies examining different aspects of pulmonary exacerbation treatment
References
J Cyst Fibros. 2021 Sep 6;S1569-1993(21)01365-5. doi: 10.1016/j.jcf.2021.08.024.
Theme
Care of patients with CF, Epidemiology/Models of care

September 2021

Title: Treatment patterns in people with cystic fibrosis: have they changed since the introduction of ivacaftor?
References
J Cyst Fibros. 2021 Sep 5;S1569-1993(21)01355-2. doi: 10.1016/j.jcf.2021.08.014.
Theme
Care of patients with CF, Epidemiology/Models of care

September 2021

Title: New perspectives on physical exercise training in adults and children with cystic fibrosis
References
J Cyst Fibros. 2021 Sep 4;S1569-1993(21)01345-X. doi: 10.1016/j.jcf.2021.08.004

September 2021

Title: Clinical presentation and basic defect of the CFTR genotype p.Phe508del / p.Arg117His in a mother and her monozygous twin daughters
References
J Cyst Fibros. 2021 Sep 3;S1569-1993(21)01359-X. doi: 10.1016/j.jcf.2021.08.018.

August 2021

Title: Survival in cystic fibrosis after need for mechanical life support.
References
J Cyst Fibros. 2021 Aug 31;S1569-1993(21)01357-6. doi: 10.1016/j.jcf.2021.08.016.
Title: Clofazimine use for treatment of mycobacteria in children with and without cystic fibrosis
References
J Cyst Fibros. 2021 Aug 31;S1569-1993(21)01351-5. doi: 10.1016/j.jcf.2021.08.010.

August 2021

Title: Comparing lung function testing at home vs in the clinic.
References
J Cyst Fibros. 2021 Aug 30;S1569-1993(21)01354-0. doi: 10.1016/j.jcf.2021.08.013.
Theme
Clinical Trials

August 2021

Title: The influence of cystic fibrosis on work ability of affected patients
References
J Cyst Fibros. 2021 Aug 29;S1569-1993(21)01352-7. doi: 10.1016/j.jcf.2021.08.011.

August 2021

Title: How did new infections with important bacteria change over time across U.S. CF care centers
References
J Cyst Fibros. 2021 Aug 26;S1569-1993(21)01350-3. doi: 10.1016/j.jcf.2021.08.009.
Title: Review of pregnancy in cystic fibrosis
References
J Cyst Fibros. 2021 Aug 26;S1569-1993(21)01338-2. doi: 10.1016/j.jcf.2021.07.019.

August 2021

Title: Orkambi may improve liver disease in people with CF
References
J Cyst Fibros. 2021 Aug 25;S1569-1993(21)01337-0. doi: 10.1016/j.jcf.2021.07.018.

August 2021

Title: A study of the drug riociguat as a possible treatment for people with cystic fibrosis
References
J Cyst Fibros. 2021 Aug 19;S1569-1993(21)01329-1. doi: 10.1016/j.jcf.2021.07.015.
Title: Do cystic fibrosis patients have an abnormal innate immune response to pathogens?
References
J Cyst Fibros. 2021 Aug 19;S1569-1993(21)01343-6. doi: 10.1016/j.jcf.2021.08.002.

August 2021

Title: Use of elexacaftor/tezacaftor/ivacaftor in liver transplant patients with cystic fibrosis
References
J Cyst Fibros. 2021 Aug 9;S1569-1993(21)01336-9. doi: 10.1016/j.jcf.2021.07.017.

August 2021

Title: “Coping and Learning to Manage Stress with CF” a Telehealth Pilot Intervention
References
J Cyst Fibros. 2021 Aug 5;S1569-1993(21)01326-6. doi: 10.1016/j.jcf.2021.07.012.
Title: Do bone active therapy and lung disease influence the skeletal outcome after transplantation?
References
J Cyst Fibros. 2021 Aug 5;S1569-1993(21)01327-8. doi: 10.1016/j.jcf.2021.07.013

August 2021

Title: Is elexacaftor/tezacaftor/ivacaftor always better than ezacaftor/ivacaftor?
References
J Cyst Fibros. 2021 Aug 1;S1569-1993(21)01304-7. doi: 10.1016/j.jcf.2021.07.006.

July 2021

Title: Different approaches to Aspergillus-related conditions in people with cystic fibrosis
References
J Cyst Fibros. 2021 Jul 28;S1569-1993(21)01306-0. doi: 10.1016/j.jcf.2021.07.008.

July 2021

Title: Urinary tract infections in cystic fibrosis patients
References
J Cyst Fibros. 2021 Jul 27;S1569-1993(21)01303-5. doi: 10.1016/j.jcf.2021.07.005

July 2021

Title: Utilization of Electronic Patient-Reported Outcome Measures in Cystic Fibrosis Research
References
J Cyst Fibros. 2021 Jul 22;S1569-1993(21)01299-6. doi: 10.1016/j.jcf.2021.07.002.

July 2021

Title: Review of abnormal Stomach and Intestinal Movement in Cystic Fibrosis
References
J Cyst Fibros. 2021 Jul;20(4):578-585. doi: 10.1016/j.jcf.2021.05.016. Epub 2021 Jun 17.
Title: Stopping exposure to smoke improves breathing and nutritional outcomes in children and adolescents with cystic fibrosis
References
J Cyst Fibros. 2021 Jul;20(4):618-624. doi: 10.1016/j.jcf.2021.06.014. Epub 2021 Jul 17.

July 2021

Title: Disease burden in people with cystic fibrosis heterozygous for F508del and a minimal function mutation
References
J Cyst Fibros. 2021 Jul 19;S1569-1993(21)01300-X. doi: 10.1016/j.jcf.2021.07.003.
Title: Disease burden in people with cystic fibrosis heterozygous for F508del and a minimal function mutation
References
J Cyst Fibros. 2021 Jul 19;S1569-1993(21)01300-X. doi: 10.1016/j.jcf.2021.07.003.

July 2021

Title: Drug-Induced Liver Injury from Elexacaftor/Ivacaftor/Tezacaftor
References
J Cyst Fibros. 2021 Jul 16;S1569-1993(21)01297-2. doi: 10.1016/j.jcf.2021.07.001.

July 2021

Title: A Short extension to multiple breath washout provides additional indications of blocked and severely diseased airways in people with CF: a pilot study
References
J Cyst Fibros. 2021 Jul 15;S1569-1993(21)01298-4. doi: 10.1016/j.jcf.2021.06.013.

July 2021

Title: Opioid Pain Management Among Adults with CF: Survey Results
References
J Cyst Fibros. 2021 Jul 10;S1569-1993(21)01291-1. doi: 10.1016/j.jcf.2021.06.007.

July 2021

Title: Genetics of immunity against the Pseudomonas aeruginosa bacteria in people with cystic fibrosis
References
J Cyst Fibros. 2021 Jul 7;S1569-1993(21)01295-9. doi: 10.1016/j.jcf.2021.06.011.

June 2021

Title: How does the cystic fibrosis drug ivacaftor move in the body during pregnancy and breastfeeding?
References
J Cyst Fibros. 2021 Jun 27;S1569-1993(21)01289-3. doi: 10.1016/j.jcf.2021.06.005.

June 2021

Title: Use of LCI to monitor CFTR Modulator effect in people with CF
References
J Cyst Fibros. 2021 Jun 25;S1569-1993(21)01286-8. doi: 10.1016/j.jcf.2021.06.002.

June 2021

Title: How changes in health insurance coverage for young children with CF can impact important health outcomes, such as lung function at 6 years of age
References
J Cyst Fibros. 2021 Jun 23;S1569-1993(21)01290-X. doi: 10.1016/j.jcf.2021.06.006.
Theme
Care of patients with CF

June 2021

Title: Effect of elexacaftor-texacaftor-ivacaftor in cystic fibrosis patients with advanced lung disease
References
J Cyst Fibros. 2021 Jun 21;S1569-1993(21)00160-0. doi: 10.1016/j.jcf.2021.05.009

June 2021

Title: Using an Antibiotic Treatment Called Amikacin Liposome Inhalation Suspension (or ALIS) for Chronic Infection With Pseudomonas aeruginosa in People With Cystic Fibrosis for 2 years
References
J Cyst Fibros. 2021 Jun 15;S1569-1993(21)00164-8. doi: 10.1016/j.jcf.2021.05.013.

June 2021

Title: Complications relating to the heart and blood vessels in people with Cystic Fibrosis: A Review of the Literature
References
J Cyst Fibros. 2021 Jun 14;S1569-1993(21)00126-0. doi: 10.1016/j.jcf.2021.04.016.

June 2021

Title: Cystic fibrosis-related diabetes (CFRD) and cognitive ability (memory, attention and task switching) in adults with cystic fibrosis
References
J Cyst Fibros. 2021 Jun 13;S1569-1993(21)00124-7. doi: 10.1016/j.jcf.2021.04.014.
Title: Liver toxicity with triple therapy in cystic fibrosis: when it is worth taking the risk.
References
J Cyst Fibros. 2021 Jun 13;S1569-1993(21)00174-0. doi: 10.1016/j.jcf.2021.05.017.

June 2021

Title: New drug for cystic fibrosis does not significantly interfere with another drug that prevents organ rejection
References
J Cyst Fibros. 2021 Jun 12;S1569-1993(21)00159-4. doi: 10.1016/j.jcf.2021.05.008.

June 2021

Title: What do different bacteria together do to the lung epithelium in Cystic Fibrosis
References
J Cyst Fibros. 2021 Jun 7;S1569-1993(21)00122-3. doi: 10.1016/j.jcf.2021.04.012.

June 2021

Title: Comparison of gene editing methods to correct the W1282X mutation
References
J Cyst Fibros. 2021 Jun 5;S1569-1993(21)00167-3. doi: 10.1016/j.jcf.2021.05.014.
Title: Appearance and behaviour of methicillin resistant Staphylococcus aureus (MRSA) from early and chronic infection in cystic fibrosis (CF)
References
J Cyst Fibros. 2021 Jun 5;S1569-1993(21)00168-5. doi: 10.1016/j.jcf.2021.05.015.

June 2021

Title: Effect of inhaled antibiotic therapy with levofloxacin in people with cystic fibrosis
References
J Cyst Fibros. 2021 Jun 4;S1569-1993(21)00051-5. doi: 10.1016/j.jcf.2021.03.002.

June 2021

Title: Can a new blood test be used to screen for CF-related diabetes ?
References
J Cyst Fibros. 2021 Jun 2;S1569-1993(21)00161-2. doi: 10.1016/j.jcf.2021.05.010.
Title: Evaluating Pulmonary Exacerbation Treatment Differences in Women and Men with CF
References
J Cyst Fibros. 2021 Jun 2;S1569-1993(21)00163-6. doi: 10.1016/j.jcf.2021.05.012.

June 2021

Title: Respiratory symptoms are not more frequent or severe in infants with CF compared to healthy infants.
References
J Cyst Fibros. 2021 Jun 1;S1569-1993(21)00116-8. doi: 10.1016/j.jcf.2021.04.006.

May 2021

Title: The effect of lumacaftor-ivacaftor on mucus clearance
References
J Cyst Fibros. 2021 May 31;S1569-1993(21)00131-4. doi: 10.1016/j.jcf.2021.05.004.

May 2021

Title: How frequent is the condition of overweight among patients with cystic fibrosis in Italy?
References
J Cyst Fibros. 2021 May 27;S1569-1993(21)00129-6. doi: 10.1016/j.jcf.2021.05.002.

May 2021

Title: Sleep in children and youth with cystic fibrosis: A review of the research
References
J Cyst Fibros. 2021 May 23;S1569-1993(21)00132-6. doi: 10.1016/j.jcf.2021.05.005.

May 2021

Title: Early signs of Cystic Fibrosis Related Diabetes (CFRD) and low amount of the neuropeptide VIP in ΔF508-CF mice.
References
J Cyst Fibros. 2021 May 22;S1569-1993(21)00133-8. doi: 10.1016/j.jcf.2021.05.006.

May 2021

Title: Pseudomonas aeruginosa infection, but not CFTR modulator therapy affects circulating regulatory T cells in an adult population with cystic fibrosis
References
J Cyst Fibros. 2021 May 21;S1569-1993(21)00128-4. doi: 10.1016/j.jcf.2021.05.001.

May 2021

Title: SARS-CoV2 infection in CF patient colonized by Burkholderia cenocepacia
References
J Cyst Fibros. 2021 May;20(3):e29-e31. doi: 10.1016/j.jcf.2021.03.024. Epub 2021 Apr 8.

May 2021

Title: Quality of life and health outcomes in children with CF aged 5 years
References
J Cyst Fibros. 2020 May;19(3):483-491. doi: 10.1016/j.jcf.2020.02.022. Epub 2020 Mar 9.

May 2021

Title: Boosting the rescue of faulty CFTR with phosphate
References
J Cyst Fibros. 2021 May 18;S1569-1993(21)00123-5. doi: 10.1016/j.jcf.2021.04.013.

May 2021

Title: CF Pancreatic Duct Secretions Can Alter Islet Function
References
J Cyst Fibros. 2021 May 17;S1569-1993(21)00120-X. doi: 10.1016/j.jcf.2021.04.010.
Title: Focusing on tiny compounds in exhaled breath, can they help detect bacteria in people with cystic fibrosis?
References
J Cyst Fibros. 2021 May 17;S1569-1993(21)00125-9. doi: 10.1016/j.jcf.2021.04.015.
Title: Aquagenic wrinkling in children under two years of age: Could this be a potential clinical referral tool for cystic fibrosis among non-screened populations?
References
J Cyst Fibros. 2021 May 17;S1569-1993(21)00112-0. doi: 10.1016/j.jcf.2021.04.002.

May 2021

Title: How does infection with Pseudomonas and Aspergillus affect people with cystic fibrosis? A study using UK registry data.
References
J Cyst Fibros. 2021 May 3;S1569-1993(21)00117-X. doi: 10.1016/j.jcf.2021.04.007.

April 2021

Title: Microbiota diversity in CF chronic sinusitis
References
J Cyst Fibros. 2021 Apr 27;S1569-1993(21)00104-1. doi: 10.1016/j.jcf.2021.03.022.

April 2021

Title: Risk factors for joint inflammation and joint pain in cystic fibrosis
References
J Fibros . 2021 May 22;S1569-1993(21)00130-2. doi: 10.1016/j.jcf.2021.05.003.

April 2021

Title: A study to understand which factors are important to people with Cystic Fibrosis when deciding whether to take part in clinical trials
References
J Cyst Fibros. 2021 Apr 21;S1569-1993(21)00103-X. doi: 10.1016/j.jcf.2021.03.021.

April 2021

Title: Meconium Ileus due to GUCY2C gene mutations in three unrelated South Indian families
References
J Cyst Fibros. 2021 Apr 18;S1569-1993(21)00105-3. doi: 10.1016/j.jcf.2021.03.023.

April 2021

Title: Incidence of SARS-CoV-2 in people with cystic fibrosis in Europe between February and June 2020.
References
Journal of Cystic Fibrosis 2021; April 17.  DOI: https://doi.org/10.1016/j.jcf.2021.03.017
 

April 2021

Title: Optimising equity of access: how should we allocate slots to the most competitive trials in Cystic Fibrosis (CF)?
References
J Cyst Fibros. 2021 Apr 16;S1569-1993(21)00109-0. doi: 10.1016/j.jcf.2021.03.027. 

April 2021

Title: Trends in the use of healthcare resources over time and the associated costs for people with cystic fibrosis?
References
J Cyst Fibros. 2021 Apr 14;S1569-1993(21)00107-7. doi: 10.1016/j.jcf.2021.03.025.

April 2021

Title: Bio-informatic analyses clarify how blood vessel malfunction may happen in people with cystic fibrosis
References
J Cyst Fibros. 2021 Apr 13;S1569-1993(21)00101-6. doi: 10.1016/j.jcf.2021.03.019.

April 2021

Title: Infant with cystic fibrosis has normal pancreas function and was missed by newborn screening after mom stayed on CFTR modulator therapy during pregnancy.
References
J Cyst Fibros. 2021 Apr 9;S1569-1993(21)00100-4. doi: 10.1016/j.jcf.2021.03.018.

April 2021

Title: Peripheral lung effect of elexacaftor/tezacaftor/ivacaftor in adult cystic fibrosis
References
J Cyst Fibros. 2021 Apr 6;S1569-1993(21)00098-9. doi: 10.1016/j.jcf.2021.03.016

April 2021

Title: The role of the “PTM-CODE” in restoring F50del-CFTR functionality
References
J Cyst Fibros. 2021 Apr 1;S1569-1993(21)00086-2. doi: 10.1016/j.jcf.2021.03.010.
Title: Nasal high-flow therapy as an adjunct to exercise in patients with cystic fibrosis: A pilot feasibility trial
References
J Cyst Fibros. 2021 Apr 1;S1569-1993(21)00054-0. doi: 10.1016/j.jcf.2021.03.005. 

March 2021

Title: Elevated blood glucose during exacerbations of cystic fibrosis lung disease is associated with poor recovery of lung function.
References
Cyst Fibros. 2021 Mar 26;S1569-1993(21)00053-9. doi: 10.1016/j.jcf.2021.03.004.

March 2021

Title: Does having Exophiala in sputum samples make a difference to health in CF?
References
J Cyst Fibros. 2021 Mar 25;S1569-1993(21)00088-6. doi: 10.1016/j.jcf.2021.03.012.
Title: Emergence and impact of oprD mutations in Pseudomonas aeruginosa strains in cystic fibrosis
References
J Cyst Fibros. 2021 Mar 25;S1569-1993(21)00056-4. doi: 10.1016/j.jcf.2021.03.007.

March 2021

Title: Impact of Trikafta on mothers and babies during pregnancy and lactation
References
J Cyst Fibros. 2021 Mar 21;S1569-1993(21)00055-2. doi: 10.1016/j.jcf.2021.03.006.

March 2021

Title: The Proteostatic Network Chaperome is Downregulated in F508del Homozygote Cystic Fibrosis
References
J Cyst Fibros. 2021 Mar;20(2):356-363. doi: 10.1016/j.jcf.2020.12.018. Epub 2021 Jan 23.

March 2021

Title: Adverse events in clinical trials in children with CF
References
J Cyst Fibros. 2021 Mar 18;S1569-1993(21)00048-5. doi: 10.1016/j.jcf.2021.02.013.

March 2021

Title: Does Using Home Spirometry Lower Healthcare Costs of Care for people with cystic fibrosis?
References
J Cyst Fibros. 2021 Mar 11;S1569-1993(21)00049-7. doi: 10.1016/j.jcf.2021.02.014.
Title: Efficacy and safety of inhaled dry-powder mannitol in adults with cystic fibrosis: An international, randomized controlled study
References
J Cyst Fibros. 2021 Mar 11;S1569-1993(21)00046-1. doi: 10.1016/j.jcf.2021.02.011.

March 2021

Title: The Effect of Oral and Intravenous Antimicrobials on Pulmonary Exacerbation Recovery in Cystic Fibrosis
References
J Cyst Fibros. 2021 Mar 5;S1569-1993(21)00047-3. doi: 10.1016/j.jcf.2021.02.012.

March 2021

Title: Chronic incretin-based therapy in cystic fibrosis-related diabetes: a tale of 3 patients treated with sitagliptin for over 5 years
References
J Cyst Fibros. 2021 Mar 2;S1569-1993(21)00040-0. doi: 10.1016/j.jcf.2021.02.005.
Title: SLC26A9 SNP rs7512462 is not associated with lung disease severity or lung function response to ivacaftor in cystic fibrosis patients with G551D-CFTR
References
J Cyst Fibros. 2021 Mar 2;S1569-1993(21)00042-4. doi: 10.1016/j.jcf.2021.02.007.

February 2021

Title: “Il faut continuer à poser des questions” patient reported outcome measures in cystic fibrosis: An anthropological perspective
References
J Cyst Fibros. 2021 Feb 26;S1569-1993(21)00044-8. doi: 10.1016/j.jcf.2021.02.009.
 
Title: Limb muscle size and contractile function in adults with cystic fibrosis: A systematic review and meta-analysis
References
J Cyst Fibros. 2021 Feb 26;S1569-1993(21)00045-X. doi: 10.1016/j.jcf.2021.02.010

February 2021

Title: Defining key outcomes to evaluate performance of newborn screening programmes for cystic fibrosis
References
J Cyst Fibros. 2021 Feb 23;S1569-1993(21)00041-2. doi: 10.1016/j.jcf.2021.02.006.
Title: Performing an exercise capacity test, known as the modified shuttle test, can help to detect the risk of being hospitalized in youths with cystic fibrosis
References

February 2021

Title: Outcomes of cystic fibrosis pulmonary exacerbations treated with antibiotics with activity against anaerobic bacteria
References
J Cyst Fibros. 2021 Feb 18;S1569-1993(21)00036-9. doi: 10.1016/j.jcf.2021.02.001.

February 2021

Title: Neutrophil Dysfunction in Cystic Fibrosis
References
J Cyst Fibros. 2021 Feb 13;S1569-1993(21)00035-7. doi: 10.1016/j.jcf.2021.01.012.

February 2021

Title: Airways glutathione S-transferase omega-1 and inflammation in cystic fibrosis
References
J Cyst Fibros. 2021 Feb 11;S1569-1993(21)00033-3. doi: 10.1016/j.jcf.2021.01.010.

February 2021

Title: Measuring the impact of CFTR modulation on sweat chloride in cystic fibrosis: Rationale and design of the CHEC-SC Study
References
J Cyst Fibros. 2021 Feb 8;S1569-1993(21)00034-5. doi: 10.1016/j.jcf.2021.01.011.

February 2021

Title: Targeting G542X CFTR Nonsense Alleles With ELX-02 Restores CFTR Function in Human-Derived Intestinal Organoids
References
J Cyst Fibros. 2021 Feb 5;S1569-1993(21)00028-X. doi: 10.1016/j.jcf.2021.01.009.

January 2021

Title: Attitudes of Pain and Opioids Prescription Practices in U.S. Cystic Fibrosis Centers
References
J Cyst Fibros. 2021 Jan;20(1):127-132. doi: 10.1016/j.jcf.2020.07.021. Epub 2020 Aug 11

January 2021

Title: Experience of COVID-19 during the first wave in children with cystic fibrosis worldwide.
References
J Cyst Fibros. 2021 Jan;20(1):25-30. doi: 10.1016/j.jcf.2020.11.021. Epub 2020 Dec 3.
Title: Alpha-1 Antitrypsin for Cystic Fibrosis Complicated by Severe Cytokinemic COVID-19
References
J Cyst Fibros. 2021 Jan;20(1):31-35. doi: 10.1016/j.jcf.2020.11.012.
Title: Emerging preclinical modulators developed for F508del-CFTR have the potential to be effective for ORKAMBI resistant processing mutants
References
J Cyst Fibros. 2021 Jan;20(1):106-119. doi: 10.1016/j.jcf.2020.07.015. Epub 2020 Jul 30.