With the CF Research News, we aim to bridge the gap between people with CF and the researchers investigating CF and how best to treat those with the condition.
We want to provide access to patients, parents, relatives, friends and caregivers of patients with CF to all scientific work mainly published in the Journal of Cystic Fibrosis (JCF).

All PDF files published hereunder are lay version summaries of work published in the JCF.

November 2022

Title: The effects of Trikafta/Kaftrio on people with CF who have mutations other than the most common CF mutation (F508del)
References
J Cyst Fibros. 2022 Nov 10;S1569-1993(22)01393-5. doi: 10.1016/j.jcf.2022.10.011.
Theme
Care of patients with CF, Lung Disease and Infection, Pulmonology

October 2022

Title: Best therapeutic approaches to treat everyone with CF
References
J Cyst Fibros. 2022 Oct 30;S1569-1993(22)01389-3. doi: 10.1016/j.jcf.2022.10.007.
Theme
CFTR/Basic Science

October 2022

Title: Gastrointestinal symptom burden in cystic fibrosis
References
J Cyst Fibros. 2022 Oct 29;S1569-1993(22)01388-1. doi: 10.1016/j.jcf.2022.10.006.
 
Theme
Care of patients with CF, Nutrition/Gastroenterology

October 2022

Title: Effect of ETI on CF Gastrointestinal Disease
References
J Cyst Fibros. 2022 Oct 21;S1569-1993(22)01384-4. doi: 10.1016/j.jcf.2022.10.003.
Theme
Care of patients with CF, Nutrition/Gastroenterology

October 2022

Title: The risk of developing bowel cancer in people with cystic fibrosis, or cystic fibrosis causing mutations.
References
J Cyst Fibros. 2022 Oct 14;S1569-1993(22)01383-2. doi: 10.1016/j.jcf.2022.10.001.
Theme
Care of patients with CF

October 2022

Title: New guidelines on non CF disorders related to the CFTR gene
References
J Cyst Fibros. 2022 Oct 8;S1569-1993(22)00691-9. doi: 10.1016/j.jcf.2022.09.011.
Theme
Diagnosis/Screening

September 2022

Title: What happened to outcomes of Australians with CF during the first year of the COVID pandemic?
References
J Cyst Fibros. 2022 Sep 16;S1569-1993(22)00685-3. doi: 10.1016/j.jcf.2022.09.006.
Theme
Care of patients with CF, Epidemiology/Models of care, Lung Disease and Infection

September 2022

Title: The CFTR protein impacts energy usage in mouse brown fat
References
J Cyst Fibros. 2022 Sep 7;S1569-1993(22)00649-X. doi: 10.1016/j.jcf.2022.08.012.
Theme
CFTR/Basic Science, Endocrinology, Nutrition/Gastroenterology

September 2022

Title: Increased blood glucose during the night is associated with a lower pulmonary function in adults but not in children with cystic fibrosis.
References
J Cyst Fibros. 2022 Sep 3;S1569-1993(22)00653-1. doi: 10.1016/j.jcf.2022.08.016.
Theme
Diabetes

August 2022

Title: How does early eradication of Pseudomonas affect lung function?
References
J Cyst Fibros. 2022 Aug 19;S1569-1993(22)00645-2. doi: 10.1016/j.jcf.2022.08.007.
Theme
Care of patients with CF, Lung Disease and Infection

August 2022

Title: A step forward in the development of a safe anti-inflammatory molecule for the chronic respiratory disease of people with CF
References
J Cyst Fibros. 2022 Aug 13;S1569-1993(22)00642-7. doi: 10.1016/j.jcf.2022.08.005.
Theme
CFTR/Basic Science, Lung Disease and Infection
Title: How do people with CF experience pain and other symptoms?
References
J Cyst Fibros. 2022 Aug 13;S1569-1993(22)00643-9. doi: 10.1016/j.jcf.2022.08.006.
Theme
Care of patients with CF

August 2022

Title: Partner Perspectives on Women’s Sexual and Reproductive Healthcare in Cystic Fibrosis
References
J Cyst Fibros. 2022 Aug 12;S1569-1993(22)00641-5. doi: 10.1016/j.jcf.2022.08.003.
Theme
Care of patients with CF, Pregnancy with CF, Psychosocial

August 2022

Title: Predicting Risk-Adjusted Incidence Rates of Methicillin-Resistant Staphylococcus aureus and Pseudomonas aeruginosa in the Cystic Fibrosis Programs in the United States
References
J Cyst Fibros. 2022 Aug 10;S1569-1993(22)00639-7. doi: 10.1016/j.jcf.2022.08.002.
Theme
Care of patients with CF, Epidemiology/Models of care, Lung Disease and Infection

July 2022

Title: Comparing continuous glucose monitoring to self-monitoring of blood glucose in the management of cystic fibrosis related diabetes; a systematic review and meta-analysis
References
J Cyst Fibros. 2022 Jul 26;S1569-1993(22)00633-6. doi: 10.1016/j.jcf.2022.07.013.
Theme
Care of patients with CF, Diabetes, Epidemiology/Models of care

July 2022

Title: How might cystic fibrosis care change because of telehealth and CFTR modulators
References
J Cyst Fibros. 2022 Jul 22;S1569-1993(22)00600-2. doi: 10.1016/j.jcf.2022.07.002.
Theme
Care of patients with CF, Epidemiology/Models of care

July 2022

Title: Two mutations in one CFTR gene copy can influence each other and thereby disease characteristics
References
J Cyst Fibros. 2022 Jul;21(4):644-651. doi: 10.1016/j.jcf.2022.05.013. Epub 2022 Jun 9.
Theme
Care of patients with CF, CFTR/Basic Science
Title: A Study Characterizing Sweat Chloride after CFTR Modulators in People with Cystic Fibrosis
References
J Cyst Fibros. 2022 Jul 21;S1569-1993(22)00625-7. doi: 10.1016/j.jcf.2022.07.008.
Theme
CFTR/Basic Science
Title: Are we missing Aspergillus in airway samples due to bacteria that may also be present?
References
J Cyst Fibros. 2022 Jul 21;S1569-1993(22)00627-0. doi: 10.1016/j.jcf.2022.07.009.
Theme
Care of patients with CF, Microbiology

July 2022

Title: The assessment of quality of care from the patient perspective
References
J Cyst Fibros. 2022 Jul 13;S1569-1993(22)00622-1. doi: 10.1016/j.jcf.2022.07.004.
Theme
Care of patients with CF

July 2022

Title: CFTR modulators: A case where Triple therapy induced rash resolved on its own, without stopping the drug
References
J Cyst Fibros. 2022 Jul 12;S1569-1993(22)00598-7. doi: 10.1016/j.jcf.2022.06.011.
Theme
Care of patients with CF

July 2022

Title: People with cystic fibrosis-related diabetes do not have a lower exercise capacity compared to those without diabetes: data from an international multicenter study
References
J Cyst Fibros. 2022 Jul 5;S1569-1993(22)00599-9. doi: 10.1016/j.jcf.2022.06.012.
Theme
Diabetes, Exercise

July 2022

Title: Vitamin D and liver stiffness measurements – Are they players in Cystic Fibrosis liver disease?
References
J Cyst Fibros. 2022 Jul 3;S1569-1993(22)00596-3. doi: 10.1016/j.jcf.2022.06.009.
Theme
Care of patients with CF, Diagnosis/Screening, Nutrition/Gastroenterology

June 2022

Title: ivacaftor does not change gut bacteria, inflammation or pancreas function
References
J Cyst Fibros. 2022 Jun 25;S1569-1993(22)00589-6. doi: 10.1016/j.jcf.2022.06.002
Theme
Care of patients with CF, Microbiology, Nutrition/Gastroenterology

June 2022

Title: Eruption of brown moles following Trikafta/Kaftrio treatment for cystic fibrosis
References
J Cyst Fibros. 2022 Jun 16;S1569-1993(22)00591-4. doi: 10.1016/j.jcf.2022.06.003.
Theme
Care of patients with CF
Title: Elexacaftor-Tezacaftor-Ivacaftor (ETI) improve stomach, gullet, nose and throat symptoms in people with advanced CF
References
J Cyst Fibros. 2022 Jun 16;S1569-1993(22)00591-4. doi: 10.1016/j.jcf.2022.06.003.
Theme
Care of patients with CF, Nutrition/Gastroenterology

May 2022

Title: How does chronic rhinosinusitis impact quality of life of cystic fibrosis patients?
References
J Cyst Fibros. 2022 May 31;S1569-1993(22)00146-1. doi: 10.1016/j.jcf.2022.05.008.
 
Theme
Care of patients with CF, Pulmonology

May 2022

Title: Long-term health effects of real-world use of ivacaftor by people with cystic fibrosis who have non-G551D-CFTR gating mutations
References
J Cyst Fibros. 2022 May 22;S1569-1993(22)00141-2. doi: 10.1016/j.jcf.2022.05.007.
Theme
Care of patients with CF, Pulmonology

May 2022

Title: Evaluation of a biochemical cystic fibrosis newborn screening protocol using IRT and PAP
References
J Cyst Fibros. 2022 May;21(3):422-433. doi: 10.1016/j.jcf.2021.10.007. Epub 2021 Nov 9.
 
Theme
False-positives, Newborn screening

May 2022

Title: The Association of Area Deprivation and State Child Health with Respiratory Outcomes of Pediatric Patients with Cystic Fibrosis in the United States
References
Pediatr Pulmonol. 2021 May;56(5):883-890. doi: 10.1002/ppul.25192. Epub 2020 Dec 14.
Theme
Care of patients with CF, Psychosocial, Pulmonology
Title: Adjusting the dose of triple therapy (Elexacaftor/Tezacaftor/Ivacaftor) to reduce mental health side effects
References
J Cyst Fibros. 2022 May 15;S1569-1993(22)00111-4. doi: 10.1016/j.jcf.2022.05.001. Online ahead of print.
 
Theme
Care of patients with CF, Psychosocial, Pulmonology

May 2022

Title: A rapid sweat test for chloride and bicarbonate to confirm the diagnosis of infants with cystic fibrosis
References
J Cyst Fibros. 2022 May 13;S1569-1993(22)00112-6. doi: 10.1016/j.jcf.2022.05.004.
Theme
Diagnosis/Screening

May 2022

Title: Breakdown of lung proteins causes structural damage in cystic fibrosis lungs
References
J Cyst Fibros. 2022 May 4;S1569-1993(22)00106-0. doi: 10.1016/j.jcf.2022.04.016.
Theme
Imaging, Lung Disease and Infection
Title: Patients with F508del/5T;TG12 CFTR genotype
References
J Cyst Fibros. 2022 May 4;S1569-1993(22)00109-6. doi: 10.1016/j.jcf.2022.04.020.
Theme
Care of patients with CF, Diagnosis/Screening

May 2022

Title: Respiratory viral infections and chest CT (computer tomography scan) changes in infants with CF
References
J Cyst Fibros. 2022 May 3;S1569-1993(22)00103-5. doi: 10.1016/j.jcf.2022.04.014.
Theme
Care of patients with CF, Imaging, Lung Disease and Infection

April 2022

Title: Use of the CFTR modulator combination elexacaftor/tezacaftor/ivacaftor after lung transplant
References
J Cyst Fibros. 2022 Apr 23;S1569-1993(22)00098-4. doi: 10.1016/j.jcf.2022.04.009.
Theme
Care of patients with CF, Diabetes, Lung Disease and Infection, Nutrition/Gastroenterology, Transplantation

April 2022

Title: How the number of kinds of antibiotics chosen to treat Pseudomonas during an exacerbation affect recovery
References
J Cyst Fibros. 2022 Apr 21;S1569-1993(22)00096-0. doi: 10.1016/j.jcf.2022.04.006.
Theme
Care of patients with CF, Lung Disease and Infection, Pulmonology

April 2022

Title: Coping and Length of Life in Cystic Fibrosis
References
J Cyst Fibros. 2022 Apr 20;S1569-1993(22)00100-X. doi: 10.1016/j.jcf.2022.04.011.
Theme
Care of patients with CF, Psychosocial

April 2022

Title: Current Prices versus Minimum Costs of Production for CFTR Modulators
References
J Cyst Fibros. 2022 Apr 16;S1569-1993(22)00090-X. doi: 10.1016/j.jcf.2022.04.007.
 
Theme
Care of patients with CF, Psychosocial
Title: How ivacaftor changes inflammation and protein levels in the bloodstream of people with CF and the G551D mutation
References
J Cyst Fibros. 2022 Apr 16;S1569-1993(22)00089-3. doi: 10.1016/j.jcf.2022.03.012.
Theme
Care of patients with CF, Endocrinology, Nutrition/Gastroenterology, Pulmonology

April 2022

Title: Inflammation and infection change what mucus is made of, how much gets made, and how much it can dissolve
References
J Cyst Fibros. 2022 Apr 15;S1569-1993(22)00097-2. doi: 10.1016/j.jcf.2022.04.008.
Theme
CFTR/Basic Science, Lung Disease and Infection

April 2022

Title: Immune response after COVID-19 vaccination in cystic fibrosis patients
References
J Cyst Fibros. 2022 Apr 14;S1569-1993(22)00094-7. doi: 10.1016/j.jcf.2022.04.004.
Theme
Care of patients with CF, Immunology

April 2022

Title: Maternal Trikafta use during pregnancy and breastfeeding improved outcomes for a baby with CF
References
J Cyst Fibros. 2022 Apr 11;S1569-1993(22)00095-9. doi: 10.1016/j.jcf.2022.04.005.
Theme
Care of patients with CF, Parents, Pregnancy with CF

April 2022

Title: Magnetic Resonance Imaging Detects Improvements of Pulmonary and Paranasal Sinus Abnormalities in Response to Elexacaftor/Tezacaftor/Ivacaftor Therapy in Adults with Cystic Fibrosis
References
J Cyst Fibros. 2022 Apr 7;S1569-1993(22)00088-1. doi: 10.1016/j.jcf.2022.03.011.

March 2022

Title: High blood eosinophil counts are linked with worse symptoms in adults with cystic fibrosis
References
J Cyst Fibros. 2022 Mar 31;S1569-1993(22)00086-8. doi: 10.1016/j.jcf.2022.03.009.
Theme
Biomarkers, Care of patients with CF, Lung Disease and Infection

March 2022

Title: Club cell secretory protein is reduced in children with cystic fibrosis who have severe lung disease
References
J Cyst Fibros. 2022 Mar 30;S1569-1993(22)00084-4. doi: 10.1016/j.jcf.2022.03.007.
Theme
Biomarkers, Care of patients with CF, Lung Disease and Infection

March 2022

Title: What makes lung function fall between childhood and adolescence
References
J Cyst Fibros. 2022 Mar 24;S1569-1993(22)00085-6. doi: 10.1016/j.jcf.2022.03.008.
Theme
Care of patients with CF, Lung Disease and Infection, Pulmonology

March 2022

Title: Cystic fibrosis liver disease – A clinical challenge in the era of improved outcomes.
References
J Cyst Fibros. 2022 Mar;21(2):202-211. doi: 10.1016/j.jcf.2021.07.014. Epub 2021 Aug 8.
Theme
Care of patients with CF, Nutrition/Gastroenterology
Title: Serodiagnostic as a complement to bacterial culture in identification of Mycobacterium abscessus infections in cystic fibrosis patients
References
J Cyst Fibros. 2022 Mar;21(2):353-360. doi: 10.1016/j.jcf.2021.08.019. Epub 2021 Sep 10.
Theme
Biomarkers, Lung Disease and Infection, Microbiology
Title: Multi-Organ MRI in Cystic Fibrosis
References
J Cyst Fibros. 2022 Mar;21(2):e148-e157. doi: 10.1016/j.jcf.2021.11.006.
Theme
Care of patients with CF, Imaging

March 2022

Title: Elexacaftor-Tezacaftor- Ivacaftor improves sinonasal sinus in cystic fibrosis
References
J Cyst Fibros. 2022 Mar 14;S1569-1993(22)00051-0. doi: 10.1016/j.jcf.2022.03.002.
Theme
Care of patients with CF

March 2022

Title: Reduced levels of nitric oxide in cystic fibrosis airways may be caused by interleukin-1 beta
References
J Cyst Fibros. 2022 Mar 5;S1569-1993(22)00049-2. doi: 10.1016/j.jcf.2022.02.017.
Theme
Care of patients with CF, Immunology

March 2022

Title: Intracranial mucous benign cyst causing bulging eye in a child with cystic fibrosis: a case report.
References
J Cyst Fibros. 2022 Mar 1;S1569-1993(22)00048-0. doi: 10.1016/j.jcf.2022.02.016.
Theme
Care of patients with CF

February 2022

Title: Evaluation of a novel compound, AZD5634, in healthy volunteers and patients with cystic fibrosis
References
J Cyst Fibros. 2022 Feb 26;S1569-1993(22)00042-X. doi: 10.1016/j.jcf.2022.02.010.
Theme
Clinical Trials, Pulmonology

February 2022

Title: The impact of the first wave of the COVID-19 pandemic on people with cystic fibrosis in New York
References
J Cyst Fibros. 2022 Feb 21;S1569-1993(22)00044-3. doi: 10.1016/j.jcf.2022.02.012.
Theme
Care of patients with CF, Lung Disease and Infection, Psychosocial

February 2022

Title: Human airway cell models to study genes contributing to CF lung disease
References
J Cyst Fibros. 2022 Feb 18;S1569-1993(22)00039-X. doi: 10.1016/j.jcf.2022.02.007.
Theme
CFTR/Basic Science
Title: Tezacaftor/Ivacaftor in Children ≥6 Years of Age With F508del and Residual Function Changes in CFTR.
References
J Cyst Fibros. 2022 Feb 18;S1569-1993(22)00033-9. doi: 10.1016/j.jcf.2022.02.003.
 
Theme
Care of patients with CF, Clinical Trials, Pulmonology

February 2022

Title: Measuring CFTR function and relating it to health.
References
J Cyst Fibros. 2022 Feb 17;S1569-1993(22)00035-2. doi: 10.1016/j.jcf.2022.02.001.
Theme
Care of patients with CF

February 2022

Title: Health Changes in People with CF the Year After Having a Child
References
J Cyst Fibros. 2022 Feb 15;S1569-1993(22)00038-8. doi: 10.1016/j.jcf.2022.02.006.
Theme
Care of patients with CF, Pregnancy with CF, Pulmonology

February 2022

Title: Men’s Sexual and Reproductive Health in Cystic Fibrosis in the Era Highly Effective Modulator Therapies: A Qualitative Study
References
J Cyst Fibros. 2022 Feb 12;S1569-1993(22)00034-0. doi: 10.1016/j.jcf.2022.02.002.
 
Theme
Care of patients with CF, Psychosocial
Title: CFTR modulator therapy alters sphingolipid profiles in blood from people with cystic fibrosis
References
J Cyst Fibros. 2022 Feb 12;S1569-1993(22)00037-6. doi: 10.1016/j.jcf.2022.02.005.
Theme
Nutrition/Gastroenterology
Title: Cystic fibrosis outcomes with Tricare Insurance
References
J Cyst Fibros. 2022 Feb 12;S1569-1993(22)00036-4. doi: 10.1016/j.jcf.2022.02.004.
 
Theme
Care of patients with CF, Psychosocial

February 2022

Title: Worldwide Estimates of Cystic Fibrosis Diagnosis and Treatment Access
References
J Cyst Fibros. 2022 Feb 3;S1569-1993(22)00031-5. doi: 10.1016/j.jcf.2022.01.009.
Theme
Care of patients with CF, Diagnosis/Screening, Epidemiology/Models of care

February 2022

Title: Elexacaftor-tezacaftor-ivacaftor provides continued health improvement in lung transplant candidates with cystic fibrosis
References
J Cyst Fibros. 2022 Feb 2;S1569-1993(22)00032-7. doi: 10.1016/j.jcf.2022.01.012.
Theme
Care of patients with CF, Transplantation

January 2022

Title: Use of swelling tests in mini-guts to help determine eligibility for treatment with Trikafta for a CF patient with a rare mutation
References
J Cyst Fibros. 2022 Jan 30;S1569-1993(22)00028-5. doi: 10.1016/j.jcf.2022.01.008.
Theme
Care of patients with CF

January 2022

Title: Measuring how the drug elexacaftor/tezacaftor/ivacaftor affects the muscles of breathing, using dynamic chest radiography
References
J Cyst Fibros. 2022 Jan 28;S1569-1993(22)00027-3. doi: 10.1016/j.jcf.2022.01.007.
Theme
Care of patients with CF, Imaging, Pulmonology

January 2022

Title: Patient and program characteristics which influence screening for bone mineral disease in people with Cystic Fibrosis
References
J Cyst Fibros. 2022 Jan 24;S1569-1993(22)00029-7. doi: 10.1016/j.jcf.2022.01.011.
Theme
Bone health, Care of patients with CF, Diagnosis/Screening
Title: Results from a clinical trial of the natural therapeutic alginate OligoG against Burkholderia lung infection in people with cystic fibrosis.
References
J Cyst Fibros. 2022 Jan 24;S1569-1993(22)00024-8. doi: 10.1016/j.jcf.2022.01.003.
Theme
Clinical Trials, Lung Disease and Infection, Microbiology

January 2022

Title: Using safe sampling and DNA tests to diagnose lung infections in children with cystic fibrosis
References
J Cyst Fibros. 2022 Jan 22;S1569-1993(22)00023-6. doi: 10.1016/j.jcf.2022.01.006.
Theme
Care of patients with CF, Lung Disease and Infection, Microbiology

January 2022

Title: Description of children who changed diagnosis from indeterminate newborn screening to cystic fibrosis
References
J Cyst Fibros. 2022 Jan;21(1):e23-e27. doi: 10.1016/j.jcf.2021.06.012. 
Theme
Newborn screening
Title: Comparing four different definitions of chronic pseudomonas infection in people with cystic fibrosis
References
J Cyst Fibros. 2022 Jan;21(1):40-44. doi: 10.1016/j.jcf.2021.07.020. Epub 2021 Aug 13.
Theme
Epidemiology/Models of care, Lung Disease and Infection, Microbiology

January 2022

Title: Guidance for Sweat Testing in Europe
References
J Cyst Fibros. 2022 Jan 19;S1569-1993(22)00025-X. doi: 10.1016/j.jcf.2022.01.004.
Theme
Diagnosis/Screening

January 2022

Title: Wrinkling of the palms on exposure to water in cystic fibrosis patients treated with ivacaftor
References
J Cyst Fibros. 2022 Jan 18;S1569-1993(22)00026-1. doi: 10.1016/j.jcf.2022.01.005.
Theme
CFTR/Basic Science

January 2022

Title: Exploring health care provider attitudes and perspectives related to men’s sexual and reproductive health in cystic fibrosis
References
J Cyst Fibros. 2022 Jan 5;S1569-1993(21)02176-7. doi: 10.1016/j.jcf.2021.12.016.
Theme
Care of patients with CF, Psychosocial

January 2022

Title: Neutrophils do not produce more oxidants when stimulated to fight infections in cystic fibrosis
References
J Cyst Fibros. 2022 Jan 3;S1569-1993(21)02175-5. doi: 10.1016/j.jcf.2021.12.015.
Theme
Lung Disease and Infection

December 2021

Title: Treatment of Idiopathic Chronic Pancreatitis (ICP) with ivacaftor in a Cystic Fibrosis (CF) carrier who also had a second inherited risk factor for pancreatitis called Methylmalonic Acidemia
References
J Cyst Fibros. 2021 Dec 30;S1569-1993(21)02174-3. doi: 10.1016/j.jcf.2021.12.013.
Theme
Nutrition/Gastroenterology

December 2021

Title: Antisense oligonucleotide as a novel therapy for people with CF affected by the W1282X mutation
References
J Cyst Fibros. 2021 Dec 28;S1569-1993(21)02172-X. doi: 10.1016/j.jcf.2021.12.012.
Theme
CFTR/Basic Science
Title: Is Body Mass Index Associated with Better Lung Function in Children with Pancreatic-Sufficient Cystic Fibrosis?
References
J Cyst Fibros. 2021 Dec 28;S1569-1993(21)02173-1. doi: 10.1016/j.jcf.2021.12.014.
Theme
Care of patients with CF, Lung Disease and Infection, Nutrition/Gastroenterology

December 2021

Title: Looking at lung disease over time in young children with CF
References
J Cyst Fibros. 2021 Dec 24;S1569-1993(21)02168-8. doi: 10.1016/j.jcf.2021.12.009.
Theme
Imaging, Lung Disease and Infection, Pulmonology
Title: Looking at lung disease over time in young children with CF
References
J Cyst Fibros. 2021 Dec 24;S1569-1993(21)02168-8. doi: 10.1016/j.jcf.2021.12.009.
Title: Results of a clinical evaluation of the safety and efficacy of the therapeutic drug candidate Roscovitine in people with cystic fibrosis.
References
J Cyst Fibros. 2021 Dec 24;S1569-1993(21)02167-6. doi: 10.1016/j.jcf.2021.10.013.
Theme
Lung Disease and Infection, Microbiology

December 2021

Title: A simple blood test to detect how severe liver disease is in children with CF
References
J Cyst Fibros. 2021 Dec 22;S1569-1993(21)02171-8. doi: 10.1016/j.jcf.2021.10.014.
Theme
Biomarkers, Nutrition/Gastroenterology

December 2021

Title: Advanced but not mild liver disease is a predictor of decreased survival in children with cystic fibrosis, with far greater impact in females: A 27-year real-life cohort study
References
J Cyst Fibros. 2021 Dec 20;S1569-1993(21)02156-1. doi: 10.1016/j.jcf.2021.11.015.
Theme
Diabetes, Nutrition/Gastroenterology
Title: Improving conclusions after newborn screening for babies with no clear diagnosis
References
J Cyst Fibros. 2021 Dec 20;S1569-1993(21)02169-X. doi: 10.1016/j.jcf.2021.12.010
Theme
Newborn screening

December 2021

Title: Measuring inflammation in blood during exacerbation treatment
References
J Cyst Fibros. 2021 Dec 18;S1569-1993(21)02160-3. doi: 10.1016/j.jcf.2021.12.003.
Theme
Biomarkers, Care of patients with CF, Lung Disease and Infection, Pulmonology

December 2021

Title: Magnetic resonance imaging of the gastrointestinal tract shows reduced small bowel motility and altered chyme in cystic fibrosis compared to controls
References
J Cyst Fibros. 2021 Dec 15;S1569-1993(21)02166-4. doi: 10.1016/j.jcf.2021.12.007.
Theme
Imaging, Nutrition/Gastroenterology
Title: Nutritional health and lung transplantation in cystic fibrosis
References
J Cyst Fibros. 2021 Dec 15;S1569-1993(21)02159-7. doi: 10.1016/j.jcf.2021.12.001.
Theme
Care of patients with CF, Nutrition/Gastroenterology, Transplantation

December 2021

Title: Two cases of heart attacks in young women with cystic fibrosis and diabetes
References
J Cyst Fibros. 2021 Dec 12;S1569-1993(21)02154-8. doi: 10.1016/j.jcf.2021.11.013.
Theme
Diabetes

December 2021

Title: Bacterial communities relate to gut function and transit in the cystic fibrosis gut
References
J Cyst Fibros. 2021 Dec 8;S1569-1993(21)02155-X. doi: 10.1016/j.jcf.2021.11.014.
Theme
Imaging, Microbiology, Nutrition/Gastroenterology

December 2021

Title: A new path for CF clinical trials through the use of historical controls
References
J Cyst Fibros. 2021 Dec 5;S1569-1993(21)02138-X. doi: 10.1016/j.jcf.2021.11.007.
Theme
Clinical Trials, Epidemiology/Models of care

November 2021

Title: Effects of CFTR Modulators on Metabolic Parameters
References
J Cyst Fibros. 2021 Nov 30;S1569-1993(21)02153-6. doi: 10.1016/j.jcf.2021.11.012
Theme
Care of patients with CF, Diabetes, Endocrinology, Nutrition/Gastroenterology

November 2021

Title: Outcomes after IV antibiotics for pulmonary exacerbations at home or in the hospital
References
J Cyst Fibros. 2021 Nov 29;S1569-1993(21)02151-2. doi: 10.1016/j.jcf.2021.11.009.
Theme
Care of patients with CF, Lung Disease and Infection

November 2021

Title: Using inhaled aztreonam in the treatment of exacerbations of cystic fibrosis
References
J Cyst Fibros. 2021 Nov;20(6):994-1002. doi: 10.1016/j.jcf.2020.12.012. Epub 2021 Jan 7.
Theme
Care of patients with CF, Lung Disease and Infection
Title: Changes in inpatient episodes following the introduction of modulator therapy across different age groups in the USA
References
J Cyst Fibros. 2021 Nov;20(6):e114-e117. doi: 10.1016/j.jcf.2021.08.003. Epub 2021 Sep 25.
Theme
Psychosocial

November 2021

Title: Evaluating the sodium status in relation to your age will be possible with a single spot urine.
References
J Cyst Fibros. 2021 Nov 18;S1569-1993(21)02130-5. doi: 10.1016/j.jcf.2021.11.002.
Theme
Care of patients with CF, Nutrition/Gastroenterology

November 2021

Title: A microengineered laboratory model of human CF lung
References
J Cyst Fibros. 2021 Nov 16;S1569-1993(21)02106-8. doi: 10.1016/j.jcf.2021.10.004.
Theme
CFTR/Basic Science

November 2021

Title: Cystic fibrosis patients and health care professionals’ evaluation of a remote follow up solution with digital questionnaires and phone consultations developed due to the COVID19 pandemic.
References
J Cyst Fibros. 2021 Nov 13;S1569-1993(21)02112-3. doi: 10.1016/j.jcf.2021.10.010.
Theme
Care of patients with CF

November 2021

Title: An in-depth study of the CFTR gene enables selection of CFTR therapies for almost all individuals with CF
References
J Cyst Fibros. 2021 Nov 12;S1569-1993(21)02113-5. doi: 10.1016/j.jcf.2021.10.011.
Theme
Care of patients with CF, CFTR/Basic Science

November 2021

Title: What do we already know and what do we need to study next when looking at markers of inflammation in sputum in CF trials?
References
J Cyst Fibros. 2021 Nov 9;S1569-1993(21)02111-1. doi: 10.1016/j.jcf.2021.10.009.
Theme
Biomarkers

November 2021

Title: How effective are exercise interventions at increasing physical activity in people with Cystic Fibrosis?
References
J Cyst Fibros. 2021 Nov 6;S1569-1993(21)02110-X. doi: 10.1016/j.jcf.2021.10.008.
Theme
Care of patients with CF, Exercise