With the CF Research News, we aim to bridge the gap between people with CF and the researchers investigating CF and how best to treat those with the condition.
We want to provide access to patients, parents, relatives, friends and caregivers of patients with CF to all scientific work mainly published in the Journal of Cystic Fibrosis (JCF).

All PDF files published hereunder are lay version summaries of work published in the JCF.

November 2022

Title: Using inhaled aztreonam in the treatment of exacerbations of cystic fibrosis
References
J Cyst Fibros. 2021 Nov;20(6):994-1002. doi: 10.1016/j.jcf.2020.12.012. Epub 2021 Jan 7.
Theme
Care of patients with CF, Lung Disease and Infection

May 2022

Title: How does chronic rhinosinusitis impact quality of life of cystic fibrosis patients?
References
J Cyst Fibros. 2022 May 31;S1569-1993(22)00146-1. doi: 10.1016/j.jcf.2022.05.008.
 
Theme
Care of patients with CF, Pulmonology

May 2022

Title: Evaluation of a biochemical cystic fibrosis newborn screening protocol using IRT and PAP
References
J Cyst Fibros. 2022 May;21(3):422-433. doi: 10.1016/j.jcf.2021.10.007. Epub 2021 Nov 9.
 
Theme
False-positives, Newborn screening

May 2022

Title: Adjusting the dose of triple therapy (Elexacaftor/Tezacaftor/Ivacaftor) to reduce mental health side effects
References
J Cyst Fibros. 2022 May 15;S1569-1993(22)00111-4. doi: 10.1016/j.jcf.2022.05.001. Online ahead of print.
 
Theme
Care of patients with CF, Psychosocial, Pulmonology

May 2022

Title: Patients with F508del/5T;TG12 CFTR genotype
References
J Cyst Fibros. 2022 May 4;S1569-1993(22)00109-6. doi: 10.1016/j.jcf.2022.04.020.
Theme
Care of patients with CF, Diagnosis/Screening

April 2022

Title: How the number of kinds of antibiotics chosen to treat Pseudomonas during an exacerbation affect recovery
References
J Cyst Fibros. 2022 Apr 21;S1569-1993(22)00096-0. doi: 10.1016/j.jcf.2022.04.006.
Theme
Care of patients with CF, Lung Disease and Infection, Pulmonology

April 2022

Title: Coping and Length of Life in Cystic Fibrosis
References
J Cyst Fibros. 2022 Apr 20;S1569-1993(22)00100-X. doi: 10.1016/j.jcf.2022.04.011.
Theme
Care of patients with CF, Psychosocial

April 2022

Title: Current Prices versus Minimum Costs of Production for CFTR Modulators
References
J Cyst Fibros. 2022 Apr 16;S1569-1993(22)00090-X. doi: 10.1016/j.jcf.2022.04.007.
 
Theme
Care of patients with CF, Psychosocial
Title: How ivacaftor changes inflammation and protein levels in the bloodstream of people with CF and the G551D mutation
References
J Cyst Fibros. 2022 Apr 16;S1569-1993(22)00089-3. doi: 10.1016/j.jcf.2022.03.012.
Theme
Care of patients with CF, Endocrinology, Nutrition/Gastroenterology, Pulmonology

April 2022

Title: Inflammation and infection change what mucus is made of, how much gets made, and how much it can dissolve
References
J Cyst Fibros. 2022 Apr 15;S1569-1993(22)00097-2. doi: 10.1016/j.jcf.2022.04.008.
Theme
CFTR/Basic Science, Lung Disease and Infection

April 2022

Title: Immune response after COVID-19 vaccination in cystic fibrosis patients
References
J Cyst Fibros. 2022 Apr 14;S1569-1993(22)00094-7. doi: 10.1016/j.jcf.2022.04.004.
Theme
Care of patients with CF, Immunology

April 2022

Title: Maternal Trikafta use during pregnancy and breastfeeding improved outcomes for a baby with CF
References
J Cyst Fibros. 2022 Apr 11;S1569-1993(22)00095-9. doi: 10.1016/j.jcf.2022.04.005.
Theme
Care of patients with CF, Parents, Pregnancy with CF

April 2022

Title: Magnetic Resonance Imaging Detects Improvements of Pulmonary and Paranasal Sinus Abnormalities in Response to Elexacaftor/Tezacaftor/Ivacaftor Therapy in Adults with Cystic Fibrosis
References
J Cyst Fibros. 2022 Apr 7;S1569-1993(22)00088-1. doi: 10.1016/j.jcf.2022.03.011.

March 2022

Title: What makes lung function fall between childhood and adolescence
References
J Cyst Fibros. 2022 Mar 24;S1569-1993(22)00085-6. doi: 10.1016/j.jcf.2022.03.008.
Theme
Care of patients with CF, Lung Disease and Infection, Pulmonology

March 2022

Title: Cystic fibrosis liver disease – A clinical challenge in the era of improved outcomes.
References
J Cyst Fibros. 2022 Mar;21(2):202-211. doi: 10.1016/j.jcf.2021.07.014. Epub 2021 Aug 8.
Theme
Care of patients with CF, Nutrition/Gastroenterology
Title: Serodiagnostic as a complement to bacterial culture in identification of Mycobacterium abscessus infections in cystic fibrosis patients
References
J Cyst Fibros. 2022 Mar;21(2):353-360. doi: 10.1016/j.jcf.2021.08.019. Epub 2021 Sep 10.
Theme
Biomarkers, Lung Disease and Infection, Microbiology
Title: Multi-Organ MRI in Cystic Fibrosis
References
J Cyst Fibros. 2022 Mar;21(2):e148-e157. doi: 10.1016/j.jcf.2021.11.006.
Theme
Care of patients with CF, Imaging

March 2022

Title: Elexacaftor-Tezacaftor- Ivacaftor improves sinonasal sinus in cystic fibrosis
References
J Cyst Fibros. 2022 Mar 14;S1569-1993(22)00051-0. doi: 10.1016/j.jcf.2022.03.002.
Theme
Care of patients with CF

March 2022

Title: Reduced levels of nitric oxide in cystic fibrosis airways may be caused by interleukin-1 beta
References
J Cyst Fibros. 2022 Mar 5;S1569-1993(22)00049-2. doi: 10.1016/j.jcf.2022.02.017.
Theme
Care of patients with CF, Immunology

March 2022

Title: Intracranial mucous benign cyst causing bulging eye in a child with cystic fibrosis: a case report.
References
J Cyst Fibros. 2022 Mar 1;S1569-1993(22)00048-0. doi: 10.1016/j.jcf.2022.02.016.
Theme
Care of patients with CF

February 2022

Title: Evaluation of a novel compound, AZD5634, in healthy volunteers and patients with cystic fibrosis
References
J Cyst Fibros. 2022 Feb 26;S1569-1993(22)00042-X. doi: 10.1016/j.jcf.2022.02.010.
Theme
Clinical Trials, Pulmonology

February 2022

Title: The impact of the first wave of the COVID-19 pandemic on people with cystic fibrosis in New York
References
J Cyst Fibros. 2022 Feb 21;S1569-1993(22)00044-3. doi: 10.1016/j.jcf.2022.02.012.
Theme
Care of patients with CF, Lung Disease and Infection, Psychosocial

February 2022

Title: Human airway cell models to study genes contributing to CF lung disease
References
J Cyst Fibros. 2022 Feb 18;S1569-1993(22)00039-X. doi: 10.1016/j.jcf.2022.02.007.
Theme
CFTR/Basic Science
Title: Tezacaftor/Ivacaftor in Children ≥6 Years of Age With F508del and Residual Function Changes in CFTR.
References
J Cyst Fibros. 2022 Feb 18;S1569-1993(22)00033-9. doi: 10.1016/j.jcf.2022.02.003.
 
Theme
Care of patients with CF, Clinical Trials, Pulmonology

February 2022

Title: Measuring CFTR function and relating it to health.
References
J Cyst Fibros. 2022 Feb 17;S1569-1993(22)00035-2. doi: 10.1016/j.jcf.2022.02.001.
Theme
Care of patients with CF

February 2022

Title: Health Changes in People with CF the Year After Having a Child
References
J Cyst Fibros. 2022 Feb 15;S1569-1993(22)00038-8. doi: 10.1016/j.jcf.2022.02.006.
Theme
Care of patients with CF, Pregnancy with CF, Pulmonology

February 2022

Title: Men’s Sexual and Reproductive Health in Cystic Fibrosis in the Era Highly Effective Modulator Therapies: A Qualitative Study
References
J Cyst Fibros. 2022 Feb 12;S1569-1993(22)00034-0. doi: 10.1016/j.jcf.2022.02.002.
 
Theme
Care of patients with CF, Psychosocial
Title: CFTR modulator therapy alters sphingolipid profiles in blood from people with cystic fibrosis
References
J Cyst Fibros. 2022 Feb 12;S1569-1993(22)00037-6. doi: 10.1016/j.jcf.2022.02.005.
Theme
Nutrition/Gastroenterology
Title: Cystic fibrosis outcomes with Tricare Insurance
References
J Cyst Fibros. 2022 Feb 12;S1569-1993(22)00036-4. doi: 10.1016/j.jcf.2022.02.004.
 
Theme
Care of patients with CF, Psychosocial

February 2022

Title: Worldwide Estimates of Cystic Fibrosis Diagnosis and Treatment Access
References
J Cyst Fibros. 2022 Feb 3;S1569-1993(22)00031-5. doi: 10.1016/j.jcf.2022.01.009.
Theme
Care of patients with CF, Diagnosis/Screening, Epidemiology/Models of care

February 2022

Title: Elexacaftor-tezacaftor-ivacaftor provides continued health improvement in lung transplant candidates with cystic fibrosis
References
J Cyst Fibros. 2022 Feb 2;S1569-1993(22)00032-7. doi: 10.1016/j.jcf.2022.01.012.
Theme
Care of patients with CF, Transplantation

January 2022

Title: Use of swelling tests in mini-guts to help determine eligibility for treatment with Trikafta for a CF patient with a rare mutation
References
J Cyst Fibros. 2022 Jan 30;S1569-1993(22)00028-5. doi: 10.1016/j.jcf.2022.01.008.
Theme
Care of patients with CF

January 2022

Title: Measuring how the drug elexacaftor/tezacaftor/ivacaftor affects the muscles of breathing, using dynamic chest radiography
References
J Cyst Fibros. 2022 Jan 28;S1569-1993(22)00027-3. doi: 10.1016/j.jcf.2022.01.007.
Theme
Care of patients with CF, Imaging, Pulmonology

January 2022

Title: Patient and program characteristics which influence screening for bone mineral disease in people with Cystic Fibrosis
References
J Cyst Fibros. 2022 Jan 24;S1569-1993(22)00029-7. doi: 10.1016/j.jcf.2022.01.011.
Theme
Bone health, Care of patients with CF, Diagnosis/Screening
Title: Results from a clinical trial of the natural therapeutic alginate OligoG against Burkholderia lung infection in people with cystic fibrosis.
References
J Cyst Fibros. 2022 Jan 24;S1569-1993(22)00024-8. doi: 10.1016/j.jcf.2022.01.003.
Theme
Clinical Trials, Lung Disease and Infection, Microbiology

January 2022

Title: Using safe sampling and DNA tests to diagnose lung infections in children with cystic fibrosis
References
J Cyst Fibros. 2022 Jan 22;S1569-1993(22)00023-6. doi: 10.1016/j.jcf.2022.01.006.
Theme
Care of patients with CF, Lung Disease and Infection, Microbiology

January 2022

Title: Description of children who changed diagnosis from indeterminate newborn screening to cystic fibrosis
References
J Cyst Fibros. 2022 Jan;21(1):e23-e27. doi: 10.1016/j.jcf.2021.06.012. 
Theme
Newborn screening
Title: Comparing four different definitions of chronic pseudomonas infection in people with cystic fibrosis
References
J Cyst Fibros. 2022 Jan;21(1):40-44. doi: 10.1016/j.jcf.2021.07.020. Epub 2021 Aug 13.
Theme
Epidemiology/Models of care, Lung Disease and Infection, Microbiology

January 2022

Title: Guidance for Sweat Testing in Europe
References
J Cyst Fibros. 2022 Jan 19;S1569-1993(22)00025-X. doi: 10.1016/j.jcf.2022.01.004.
Theme
Diagnosis/Screening

January 2022

Title: Wrinkling of the palms on exposure to water in cystic fibrosis patients treated with ivacaftor
References
J Cyst Fibros. 2022 Jan 18;S1569-1993(22)00026-1. doi: 10.1016/j.jcf.2022.01.005.
Theme
CFTR/Basic Science

January 2022

Title: Exploring health care provider attitudes and perspectives related to men’s sexual and reproductive health in cystic fibrosis
References
J Cyst Fibros. 2022 Jan 5;S1569-1993(21)02176-7. doi: 10.1016/j.jcf.2021.12.016.
Theme
Care of patients with CF, Psychosocial

January 2022

Title: Neutrophils do not produce more oxidants when stimulated to fight infections in cystic fibrosis
References
J Cyst Fibros. 2022 Jan 3;S1569-1993(21)02175-5. doi: 10.1016/j.jcf.2021.12.015.
Theme
Lung Disease and Infection

December 2021

Title: Treatment of Idiopathic Chronic Pancreatitis (ICP) with ivacaftor in a Cystic Fibrosis (CF) carrier who also had a second inherited risk factor for pancreatitis called Methylmalonic Acidemia
References
J Cyst Fibros. 2021 Dec 30;S1569-1993(21)02174-3. doi: 10.1016/j.jcf.2021.12.013.
Theme
Nutrition/Gastroenterology

December 2021

Title: Antisense oligonucleotide as a novel therapy for people with CF affected by the W1282X mutation
References
J Cyst Fibros. 2021 Dec 28;S1569-1993(21)02172-X. doi: 10.1016/j.jcf.2021.12.012.
Theme
CFTR/Basic Science
Title: Is Body Mass Index Associated with Better Lung Function in Children with Pancreatic-Sufficient Cystic Fibrosis?
References
J Cyst Fibros. 2021 Dec 28;S1569-1993(21)02173-1. doi: 10.1016/j.jcf.2021.12.014.
Theme
Care of patients with CF, Lung Disease and Infection, Nutrition/Gastroenterology

December 2021

Title: Looking at lung disease over time in young children with CF
References
J Cyst Fibros. 2021 Dec 24;S1569-1993(21)02168-8. doi: 10.1016/j.jcf.2021.12.009.
Theme
Imaging, Lung Disease and Infection, Pulmonology
Title: Looking at lung disease over time in young children with CF
References
J Cyst Fibros. 2021 Dec 24;S1569-1993(21)02168-8. doi: 10.1016/j.jcf.2021.12.009.
Title: Results of a clinical evaluation of the safety and efficacy of the therapeutic drug candidate Roscovitine in people with cystic fibrosis.
References
J Cyst Fibros. 2021 Dec 24;S1569-1993(21)02167-6. doi: 10.1016/j.jcf.2021.10.013.
Theme
Lung Disease and Infection, Microbiology

December 2021

Title: A simple blood test to detect how severe liver disease is in children with CF
References
J Cyst Fibros. 2021 Dec 22;S1569-1993(21)02171-8. doi: 10.1016/j.jcf.2021.10.014.
Theme
Biomarkers, Nutrition/Gastroenterology

December 2021

Title: Advanced but not mild liver disease is a predictor of decreased survival in children with cystic fibrosis, with far greater impact in females: A 27-year real-life cohort study
References
J Cyst Fibros. 2021 Dec 20;S1569-1993(21)02156-1. doi: 10.1016/j.jcf.2021.11.015.
Theme
Diabetes, Nutrition/Gastroenterology
Title: Improving conclusions after newborn screening for babies with no clear diagnosis
References
J Cyst Fibros. 2021 Dec 20;S1569-1993(21)02169-X. doi: 10.1016/j.jcf.2021.12.010
Theme
Newborn screening

December 2021

Title: Measuring inflammation in blood during exacerbation treatment
References
J Cyst Fibros. 2021 Dec 18;S1569-1993(21)02160-3. doi: 10.1016/j.jcf.2021.12.003.
Theme
Biomarkers, Care of patients with CF, Lung Disease and Infection, Pulmonology

December 2021

Title: Magnetic resonance imaging of the gastrointestinal tract shows reduced small bowel motility and altered chyme in cystic fibrosis compared to controls
References
J Cyst Fibros. 2021 Dec 15;S1569-1993(21)02166-4. doi: 10.1016/j.jcf.2021.12.007.
Theme
Imaging, Nutrition/Gastroenterology
Title: Nutritional health and lung transplantation in cystic fibrosis
References
J Cyst Fibros. 2021 Dec 15;S1569-1993(21)02159-7. doi: 10.1016/j.jcf.2021.12.001.
Theme
Care of patients with CF, Nutrition/Gastroenterology, Transplantation

December 2021

Title: Two cases of heart attacks in young women with cystic fibrosis and diabetes
References
J Cyst Fibros. 2021 Dec 12;S1569-1993(21)02154-8. doi: 10.1016/j.jcf.2021.11.013.
Theme
Diabetes

December 2021

Title: Bacterial communities relate to gut function and transit in the cystic fibrosis gut
References
J Cyst Fibros. 2021 Dec 8;S1569-1993(21)02155-X. doi: 10.1016/j.jcf.2021.11.014.
Theme
Imaging, Microbiology, Nutrition/Gastroenterology

December 2021

Title: A new path for CF clinical trials through the use of historical controls
References
J Cyst Fibros. 2021 Dec 5;S1569-1993(21)02138-X. doi: 10.1016/j.jcf.2021.11.007.
Theme
Clinical Trials, Epidemiology/Models of care

November 2021

Title: Effects of CFTR Modulators on Metabolic Parameters
References
J Cyst Fibros. 2021 Nov 30;S1569-1993(21)02153-6. doi: 10.1016/j.jcf.2021.11.012
Theme
Care of patients with CF, Diabetes, Endocrinology, Nutrition/Gastroenterology

November 2021

Title: Outcomes after IV antibiotics for pulmonary exacerbations at home or in the hospital
References
J Cyst Fibros. 2021 Nov 29;S1569-1993(21)02151-2. doi: 10.1016/j.jcf.2021.11.009.
Theme
Care of patients with CF, Lung Disease and Infection

November 2021

Title: Changes in inpatient episodes following the introduction of modulator therapy across different age groups in the USA
References
J Cyst Fibros. 2021 Nov;20(6):e114-e117. doi: 10.1016/j.jcf.2021.08.003. Epub 2021 Sep 25.
Theme
Psychosocial

November 2021

Title: Evaluating the sodium status in relation to your age will be possible with a single spot urine.
References
J Cyst Fibros. 2021 Nov 18;S1569-1993(21)02130-5. doi: 10.1016/j.jcf.2021.11.002.
Theme
Care of patients with CF, Nutrition/Gastroenterology

November 2021

Title: A microengineered laboratory model of human CF lung
References
J Cyst Fibros. 2021 Nov 16;S1569-1993(21)02106-8. doi: 10.1016/j.jcf.2021.10.004.
Theme
CFTR/Basic Science

November 2021

Title: Cystic fibrosis patients and health care professionals’ evaluation of a remote follow up solution with digital questionnaires and phone consultations developed due to the COVID19 pandemic.
References
J Cyst Fibros. 2021 Nov 13;S1569-1993(21)02112-3. doi: 10.1016/j.jcf.2021.10.010.
Theme
Care of patients with CF

November 2021

Title: An in-depth study of the CFTR gene enables selection of CFTR therapies for almost all individuals with CF
References
J Cyst Fibros. 2021 Nov 12;S1569-1993(21)02113-5. doi: 10.1016/j.jcf.2021.10.011.
Theme
Care of patients with CF, CFTR/Basic Science

November 2021

Title: What do we already know and what do we need to study next when looking at markers of inflammation in sputum in CF trials?
References
J Cyst Fibros. 2021 Nov 9;S1569-1993(21)02111-1. doi: 10.1016/j.jcf.2021.10.009.
Theme
Biomarkers

November 2021

Title: How effective are exercise interventions at increasing physical activity in people with Cystic Fibrosis?
References
J Cyst Fibros. 2021 Nov 6;S1569-1993(21)02110-X. doi: 10.1016/j.jcf.2021.10.008.
Theme
Care of patients with CF, Exercise

October 2021

Title: Arm muscle area as an early indicator of worsening nutritional status in children - a single centre experience
References
J Cyst Fibros. 2021 Oct 30;S1569-1993(21)02108-1. doi: 10.1016/j.jcf.2021.10.006.
Theme
Care of patients with CF, Nutrition/Gastroenterology

October 2021

Title: Clofazimine has no influence on the blood concentrations of tezacaftor-ivacaftor in a patient with cystic fibrosis.
References
J Cyst Fibros. 2021 Oct 29;S1569-1993(21)02105-6. doi: 10.1016/j.jcf.2021.10.003.
Theme
Care of patients with CF, Lung Disease and Infection

October 2021

Title: The effect of CFTR modulation with elexacaftor-tezacaftor-ivacaftor on the anxiety sweat rate in people with cystic fibrosis
References
J Cyst Fibros. 2021 Oct 28;S1569-1993(21)02107-X. doi: 10.1016/j.jcf.2021.10.005.
Theme
Diagnosis/Screening

October 2021

Title: Exploring new treatment options for people with cystic fibrosis with severe stop mutations
References
J Cyst Fibros. 2021 Oct 16;S1569-1993(21)01425-9. doi: 10.1016/j.jcf.2021.09.020.
Theme
CFTR/Basic Science

October 2021

Title: Damage in the cell lining of the airways in cystic fibrosis
References
J Cyst Fibros. 2021 Oct 14;S1569-1993(21)01424-7. doi: 10.1016/j.jcf.2021.09.019.
Theme
CFTR/Basic Science, Lung Disease and Infection

October 2021

Title: Is it possible to monitor young people with cystic fibrosis at home? Results of the CLIMB-CF study
References
J Cyst Fibros. 2021 Oct 8;S1569-1993(21)01423-5. doi: 10.1016/j.jcf.2021.09.018.
Theme
Care of patients with CF, Clinical Trials

October 2021

Title: Lung infection by Pseudomonas aeruginosa in children with cystic fibrosis: risk factors and impact on lung function
References
J Cyst Fibros. 2021 Oct 7;S1569-1993(21)01422-3. doi: 10.1016/j.jcf.2021.09.017.
Theme
Lung Disease and Infection

October 2021

Title: A review of sweat testing in Ireland in the era of modern CF care
References
J Cyst Fibros. 2021 Oct 4;S1569-1993(21)01417-X. doi: 10.1016/j.jcf.2021.09.012.
Theme
Diagnosis/Screening

October 2021

Title: Features of Salt Imbalance and Pseudo Barter Syndrome in hospitalized Children and Young Adults with Cystic Fibrosis.
References
J Cyst Fibros. 2021 Oct 2;S1569-1993(21)01418-1. doi: 10.1016/j.jcf.2021.09.013.
Theme
Care of patients with CF, Endocrinology

September 2021

Title: Sense of Smell in People with Cystic Fibrosis: Impact of Modulator Therapy
References
J Cyst Fibros. 2021 Sep 28;S1569-1993(21)01419-3. doi: 10.1016/j.jcf.2021.09.014.
Theme
Care of patients with CF, Nutrition/Gastroenterology

September 2021

Title: A summary of previously-published research looking at the length of treatment of acute infections and exacerbations in people with cystic fibrosis
References
J Cyst Fibros. 2021 Sep 27;S1569-1993(21)01358-8. doi: 10.1016/j.jcf.2021.08.017.
Theme
Care of patients with CF, Lung Disease and Infection

September 2021

Title: A serious consideration about the wise use of the new, highly efficient, very expensive, treatment for cystic fibrosis (Trikafta©/Kaftrio©)
References
J Cyst Fibros. 2021 Sep 25;S1569-1993(21)01416-8. doi: 10.1016/j.jcf.2021.09.011.
Theme
Psychosocial

September 2021

Title: Using a digital system, CFHealthHub, to automatically record the use of preventative inhaled treatments as to compare the amount of medicines collected from pharmacy to the amount actually used.
References
J Cyst Fibros. 2021 Sep 23;S1569-1993(21)01408-9. doi: 10.1016/j.jcf.2021.09.007.
Theme
Care of patients with CF

September 2021

Title: Prevalence, management and outcome of Italian infants with cystic fibrosis screening positive inconclusive diagnosis
References
J Cyst Fibros. 2021 Sep;20(5):828-834. doi: 10.1016/j.jcf.2021.03.015.
Theme
Newborn screening
Title: Drug levels and dosing recommendations for antibiotics used to treat Mycobacterium avium complex in people with cystic fibrosis.
References
J Cyst Fibros. 2021 Sep;20(5):772-778. doi: 10.1016/j.jcf.2021.04.011. Epub 2021 May 21.
Theme
Care of patients with CF, Lung Disease and Infection, Microbiology
Title: Drug development for Cystic Fibrosis patients carrying the 3849+10kb C-to-T splicing mutation
References
J Cyst Fibros. 2021 Sep;20(5):865-875. doi: 10.1016/j.jcf.2021.06.003. Epub 2021 Jul 2.
Theme
CFTR/Basic Science

September 2021

Title: Testicular pain following initiation of elexacaftor/tezacaftor/ivacaftor in males with cystic fibrosis
References
J Cyst Fibros. 2020 Sep;19(5):e39-e41. doi: 10.1016/j.jcf.2020.04.017.
Theme
Care of patients with CF, Psychosocial

September 2021

Title: Can cough swabs be used to identify bacterial infections in patient with cystic fibrosis.
References
J Cyst Fibros. 2021 Sep 18;S1569-1993(21)01372-2. doi: 10.1016/j.jcf.2021.08.031.

September 2021

Title: Study that tested the effects of a new drug called acebilustat in adultswith cystic fibrosis
References
J Cyst Fibros. 2021 Sep 16;S1569-1993(21)01348-5. doi: 10.1016/j.jcf.2021.08.007.

September 2021

Title: The effect of ETI (Trikafta™) on blood sugars in adults with cystic fibrosis
References
J Cyst Fibros. 2021 Sep 13;S1569-1993(21)01377-1. doi: 10.1016/j.jcf.2021.09.001.

September 2021

Title: Defining constipation in patients with Cystic Fibrosis following criteria delineated by the European Society for Paediatric Gastroenterology Hepatology and Nutrition
References
J Cyst Fibros. 2021 Sep 9;S1569-1993(21)01362-X. doi: 10.1016/j.jcf.2021.08.021.
Theme
Care of patients with CF, Nutrition/Gastroenterology
Title: Defining constipation in patients with Cystic Fibrosis following criteria delineated by the European Society for Paediatric Gastroenterology Hepatology and Nutrition
References
J Cyst Fibros. 2021 Sep 9;S1569-1993(21)01362-X. doi: 10.1016/j.jcf.2021.08.021.

September 2021

Title: A review of three studies examining different aspects of pulmonary exacerbation treatment
References
J Cyst Fibros. 2021 Sep 6;S1569-1993(21)01365-5. doi: 10.1016/j.jcf.2021.08.024.
Theme
Care of patients with CF, Epidemiology/Models of care

September 2021

Title: Treatment patterns in people with cystic fibrosis: have they changed since the introduction of ivacaftor?
References
J Cyst Fibros. 2021 Sep 5;S1569-1993(21)01355-2. doi: 10.1016/j.jcf.2021.08.014.
Theme
Care of patients with CF, Epidemiology/Models of care

September 2021

Title: New perspectives on physical exercise training in adults and children with cystic fibrosis
References
J Cyst Fibros. 2021 Sep 4;S1569-1993(21)01345-X. doi: 10.1016/j.jcf.2021.08.004

September 2021

Title: Needle-free bubble test
References
J Cyst Fibros. 2021 Sep 3;S1569-1993(21)01353-9. doi: 10.1016/j.jcf.2021.08.012.
Theme
Care of patients with CF, Diagnosis/Screening
Title: Clinical presentation and basic defect of the CFTR genotype p.Phe508del / p.Arg117His in a mother and her monozygous twin daughters
References
J Cyst Fibros. 2021 Sep 3;S1569-1993(21)01359-X. doi: 10.1016/j.jcf.2021.08.018.

August 2021

Title: Survival in cystic fibrosis after need for mechanical life support.
References
J Cyst Fibros. 2021 Aug 31;S1569-1993(21)01357-6. doi: 10.1016/j.jcf.2021.08.016.
Title: Clofazimine use for treatment of mycobacteria in children with and without cystic fibrosis
References
J Cyst Fibros. 2021 Aug 31;S1569-1993(21)01351-5. doi: 10.1016/j.jcf.2021.08.010.

August 2021

Title: Comparing lung function testing at home vs in the clinic.
References
J Cyst Fibros. 2021 Aug 30;S1569-1993(21)01354-0. doi: 10.1016/j.jcf.2021.08.013.
Theme
Clinical Trials

August 2021

Title: The influence of cystic fibrosis on work ability of affected patients
References
J Cyst Fibros. 2021 Aug 29;S1569-1993(21)01352-7. doi: 10.1016/j.jcf.2021.08.011.

August 2021

Title: How did new infections with important bacteria change over time across U.S. CF care centers
References
J Cyst Fibros. 2021 Aug 26;S1569-1993(21)01350-3. doi: 10.1016/j.jcf.2021.08.009.
Title: Review of pregnancy in cystic fibrosis
References
J Cyst Fibros. 2021 Aug 26;S1569-1993(21)01338-2. doi: 10.1016/j.jcf.2021.07.019.

August 2021

Title: Orkambi may improve liver disease in people with CF
References
J Cyst Fibros. 2021 Aug 25;S1569-1993(21)01337-0. doi: 10.1016/j.jcf.2021.07.018.