With the CF Research News, we aim to bridge the gap between people with CF and the researchers investigating CF and how best to treat those with the condition.
We want to provide access to patients, parents, relatives, friends and caregivers of patients with CF to all scientific work mainly published in the Journal of Cystic Fibrosis (JCF).

All PDF files published hereunder are lay version summaries of work published in the JCF.

July 2019

Title: Supersonic Shear-Wave Elastography and APRI for the detection and staging of liver disease in paediatric cystic fibrosis
References
J Cyst Fibros. 2019 Jul 11. pii: S1569-1993(19)30820-3. doi: 10.1016/j.jcf.2019.06.017.

June 2019

Title: Dissociation of Systemic and Mucosal Autoimmunity in Cystic Fibrosis
References
J Cyst Fibros. 2019 Jun 28. pii: S1569-1993(19)30807-0. doi: 10.1016/j.jcf.2019.06.006. 
Title: Dissociation of Systemic and Mucosal Autoimmunity in Cystic Fibrosis
References
J Cyst Fibros. 2019 Jun 28. pii: S1569-1993(19)30807-0. doi: 10.1016/j.jcf.2019.06.006. 

June 2019

Title: Variation in lung function and nutritional decline in cystic fibrosis by genotype: An analysis of the Canadian Cystic Fibrosis Registry
References
J Cyst Fibros. 2019 Jun 25. pii: S1569-1993(19)30812-4. doi: 10.1016/j.jcf.2019.06.007
Title: Variation in lung function and nutritional decline in cystic fibrosis by genotype: An analysis of the Canadian Cystic Fibrosis Registry
References
J Cyst Fibros. 2019 Jun 25. pii: S1569-1993(19)30812-4. doi: 10.1016/j.jcf.2019.06.007

June 2019

Title: Do current clinical trials in cystic fibrosis match the priorities of patients and clinicans? A systematic review.
References
J Cyst Fibros. 2019 Jun 21. pii: S1569-1993(19)30806-9. doi: 10.1016/j.jcf.2019.06.005.

June 2019

Title: Disease Progression in Patients with Cystic Fibrosis Treated with Ivacaftor: Data From National US and UK Registries
References
J Cyst Fibros. 2019 Jun 10. pii: S1569-1993(19)30767-2. doi: 10.1016/j.jcf.2019.05.015. 

June 2019

Title: Antisense oligonucleotide eluforsen is safe and improves respiratory symptoms in F508DEL cystic fibrosis.
References
J Cyst Fibros. 2019 Jun 7. pii: S1569-1993(19)30766-0. doi: 10.1016/j.jcf.2019.05.014

June 2019

Title: Non-fasting bioelectrical impedance analysis in cystic fibrosis: Implications for clinical practice and research
References
J Cyst Fibros. 2019 Jun 5. pii: S1569-1993(19)30772-6. doi: 10.1016/j.jcf.2019.05.018
Title: Blood Biomarkers to Predict Short-term Pulmonary Exacerbation Risk in Children and Adolescents with CF: A Pilot Study
References
J Cyst Fibros. 2019 Jun 5. pii: S1569-1993(19)30774-X. doi: 10.1016/j.jcf.2019.05.020.
Title: Abnormal Pro-Gly-Pro pathway and airway neutrophilia in pediatric cystic fibrosis
References
J Cyst Fibros. 2019 Jun 5. pii: S1569-1993(19)30769-6. doi: 10.1016/j.jcf.2019.05.017

May 2019

Title: The use of antimicrobial susceptibility testing in pediatric cystic fibrosis pulmonary exacerbations
References
J Cyst Fibros. 2019 May 28. pii: S1569-1993(19)30764-7. doi: 10.1016/j.jcf.2019.05.012.

May 2019

Title: GLPG1837, a CFTR potentiator, in p.Gly551Asp (G551D)-CF patients: An open-label, single-arm, phase 2a study (SAPHIRA1)
References
J Cyst Fibros. 2019 May 27. pii: S1569-1993(19)30111-0. doi: 10.1016/j.jcf.2019.05.006. 

May 2019

Title: Pilot study to test inhaled nitric oxide in cystic fibrosis patients with refractory Mycobacterium abscessus lung infection.
References
J Cyst Fibros. 2019 May 22. pii: S1569-1993(19)30104-3. doi: 10.1016/j.jcf.2019.05.002.

May 2019

Title: Study of 109 Achromobacter spp. isolates from 9 French CF centres reveals the circulation of a multiresistant clone of A. xylosoxidans belonging to ST 137
References
J Cyst Fibros. 2019 May 16. pii: S1569-1993(19)30065-7. doi: 10.1016/j.jcf.2019.04.005

April 2019

Title: Assessment of endothelial function is reproducible in patients with cystic fibrosis.
References
J Cyst Fibros. 2019 Apr 4. pii: S1569-1993(19)30062-1. doi: 10.1016/j.jcf.2019.03.011

March 2019

Title: The impact of cystic fibrosis-related diabetes on health-related quality of life
References
J Cyst Fibros. 2019 Mar 29. pii: S1569-1993(19)30060-8. doi: 10.1016/j.jcf.2019.03.007. 

March 2019

Title: Markers of bone turnover are reduced in patients with CF related diabetes; the role of glucose.
References
J Cyst Fibros. 2019 Mar 27. pii: S1569-1993(18)30809-9. doi: 10.1016/j.jcf.2019.01.004

March 2019

Title: Aligning patients’ needs towards a comprehensive CF research program
References
J Cyst Fibros. 2019 Mar 26. pii: S1569-1993(18)30857-9. doi: 10.1016/j.jcf.2019.03.008.
Title: Physical activity and associations with clinical outcome measures in adults with cystic fibrosis; a systematic review.
References
J Cyst Fibros. 2019 Mar 26. pii: S1569-1993(18)30898-1. doi: 10.1016/j.jcf.2019.03.003.

March 2019

Title: Assessment of stability and fluctuations of cultured lower airway bacterial communities in people with cystic fibrosis
References
J Cyst Fibros. 2019 Mar 21. pii: S1569-1993(19)30052-9. doi: 10.1016/j.jcf.2019.02.012. 

March 2019

Title: 3D Printing and the Cystic Fibrosis Lung
References
J Cyst Fibros. 2019 Mar;18(2):278-279. doi: 10.1016/j.jcf.2018.09.004. 
Title: Cystic fibrosis related diabetes is not independently associated with increased Stenotrophomonas maltophilia infection: longitudinal data from the UK CF Registry
References
J Cyst Fibros. 2019 Mar;18(2):294-298. doi: 10.1016/j.jcf.2018.10.011. Epub 2018 Oct 25

March 2019

Title: The Effects of Cycled Inhaled Aztreonam on the Cystic Fibrosis (CF) Lung Microbiome
References
J Cyst Fibros. 2019 Mar 8. pii: S1569-1993(19)30028-1. doi: 10.1016/j.jcf.2019.02.010

February 2019

Title: Abnormal Preschool Lung Clearance Index (LCI) reflects clinical status and predicts lower spirometry later in childhood in Cystic Fibrosis.
References
J Cyst Fibros. 2019 Feb 28. pii: S1569-1993(19)30025-6. doi: 10.1016/j.jcf.2019.02.007.

February 2019

Title: Early respiratory viral infections in infants with cystic fibrosis
References
Deschamp AR, Hatch JE, Slaven JE, Gebregziabher N, Storch G, Hall GL, Stick S, Ranganathan S, Ferkol TW, Davis SD.

February 2019

Title: Inhaled antibiotic use is associated with Scedosporium/Lomentospora species isolation in cystic fibrosis
References
Pediatr Pulmonol. 2019 Feb;54(2):133-140

February 2019

Title: Social Support is Associated with Fewer Reported Symptoms and Decreased Treatment Burden in Adults with Cystic Fibrosis
References
J Cyst Fibros. 2019 Feb 13. pii: S1569-1993(19)30017-7. doi: 10.1016/j.jcf.2019.01.013
Title: Do patients with cystic fibrosis participating in clinical trials demonstrate placebo response? A meta-analysis.
References
J Cyst Fibros. 2019 Feb 13. pii: S1569-1993(18)30833-6. doi: 10.1016/j.jcf.2019.02.003

February 2019

Title: CT evaluation of hyperattenuating mucus to diagnose allergic bronchopulmonary aspergillosis in the special condition of cystic fibrosis
References
J Cyst Fibros. 2019 Feb 12. pii: S1569-1993(18)30902-0. doi: 10.1016/j.jcf.2019.02.002.

February 2019

Title: Lumacaftor-rescued F508del-CFTR has a modified bicarbonate permeability
References
J Cyst Fibros. 2019 Feb 6. pii: S1569-1993(18)30927-5. doi: 10.1016/j.jcf.2019.01.012.

February 2019

Title: Methylomic correlates of autophagy activity in cystic fibrosis
References
J Cyst Fibros. 2019 Feb 5. pii: S1569-1993(18)30824-5. doi: 10.1016/j.jcf.2019.01.011

January 2019

Title: The main mechanism associated with progression of glucose intolerance in older patients with cystic fibrosis is insulin resistance and not reduced insulin secretion capacity.
References
J Cyst Fibros. 2019 Jan 30. pii: S1569-1993(19)30015-3. doi: 10.1016/j.jcf.2019.01.009
Title: Hyperbaric oxygen treatment increases killing of aggregating Pseudomonas aeruginosa isolates from cystic fibrosis patients
References
J Cyst Fibros. 2019 Jan 30. pii: S1569-1993(19)30011-6. doi: 10.1016/j.jcf.2019.01.005. 
Title: Antimicrobial susceptibility testing (AST) and associated clinical outcomes in individuals with cystic fibrosis: A systematic review.
References
J Cyst Fibros. 2019 Jan 30. pii: S1569-1993(19)30014-1. doi: 10.1016/j.jcf.2019.01.008.

January 2019

Title: Visceral Adipose Tissue is Associated with Poor Diet Quality and Higher Fasting Glucose in Adults with Cystic Fibrosis
References
J Cyst Fibros. 2019 Jan 18. pii: S1569-1993(18)30812-9. doi: 10.1016/j.jcf.2019.01.002

January 2019

Title: Application of Multiple Event Analysis as an alternative approach to studying pulmonary exacerbations as an outcome measure
References
J Cyst Fibros. 2019 Jan 11. pii: S1569-1993(18)30943-3. doi: 10.1016/j.jcf.2018.12.005

January 2019

Title: Systemic levels of anti-PAD4 autoantibodies correlate with airway obstruction in cystic fibrosis
References
J Cyst Fibros. 2019 Jan 10. pii: S1569-1993(18)30971-8. doi: 10.1016/j.jcf.2018.12.010

December 2018

Title: Measuring Recovery in Health-Related Quality of Life During and After Pulmonary Exacerbations in Patients with Cystic Fibrosis
References
J Cyst Fibros. 2018 Dec 23. pii: S1569-1993(18)30942-1. doi: 10.1016/j.jcf.2018.12.004.

December 2018

Title: Isogenic cell models of cystic fibrosis-causing variants in natively expressing pulmonary epithelial cells.
References
J Cyst Fibros. 2018 Dec 15. pii: S1569-1993(18)30940-8. doi: 10.1016/j.jcf.2018.12.001. 

December 2018

Title: Cirrhosis associated with decreased survival and a 10-year lower median age at death of cystic fibrosis patients in the Netherlands
References
J Cyst Fibros. 2018 Dec 14. pii: S1569-1993(18)30937-8. doi: 10.1016/j.jcf.2018.11.009.

December 2018

Title: Depletion of BAFF cytokine exacerbates infection in Pseudomonas aeruginosa infected mice
References
J Cyst Fibros. 2018 Dec 7. pii: S1569-1993(18)30864-6. doi: 10.1016/j.jcf.2018.11.015. 

December 2018

Title: Prevalence and diversity of filamentous fungi in the airways of cystic fibrosis patients - A Dutch, multicentre study.
References
J Cyst Fibros. 2018 Dec 1. pii: S1569-1993(18)30939-1. doi: 10.1016/j.jcf.2018.11.012.
Theme
Epidemiology/Models of care

November 2018

Title: Non-Invasive Ventilation and Clinical Outcomes in Cystic Fibrosis: findings from the UK CF Registry
References
J Cyst Fibros. 2018 Nov 28. pii: S1569-1993(18)30934-2. doi: 10.1016/j.jcf.2018.11.006.

November 2018

Title: Pre-transplant factors associated with mortality after lung transplantation in cystic fibrosis: A systematic review and meta-analysis
References

November 2018

Title: Urinary Metabolomics Reveals Unique Metabolic Signatures in Infants with Cystic Fibrosis
References
J Cyst Fibros. 2018 Nov 23. pii: S1569-1993(18)30916-0. doi: 10.1016/j.jcf.2018.10.016

November 2018

Title: Cystic fibrosis is associated with an increased risk of Barrett’s esophagus
References
J Cyst Fibros. 2018 Nov 22. pii: S1569-1993(18)30933-0. doi: 10.1016/j.jcf.2018.11.005
Title: Dental and periodontal manifestations in patients with cystic fibrosis - A systematic review
References
J Cyst Fibros. 2018 Nov 22. pii: S1569-1993(18)30935-4. doi: 10.1016/j.jcf.2018.11.007.

November 2018

Title: Eluforsen: a potential new treatment option for people with cystic fibrosis (CF) due to the F508del gene mutation?
References
J Cyst Fibros. 2018 Nov 19. pii: S1569-1993(18)30914-7. doi: 10.1016/j.jcf.2018.10.015

November 2018

Title: Use of telavancin in adolescent patients with cystic fibrosis and prior intolerance to vancomycin: A case series.
References
J Cyst Fibros. 2018 Nov;17(6):e48-e50. doi: 10.1016/j.jcf.2018.08.003.

November 2018

Title: Clinical outcomes in U.S. infants with cystic fibrosis from 2001 to 2012
References
Pediatr Pulmonol. 2018 Nov;53(11):1492-1497. doi: 10.1002/ppul.2416

November 2018

Title: Comparison of Lung Clearance Index Determined by Washout of N2 and SF6 in Infants and Preschool Children with Cystic Fibrosis
References
J Cyst Fibros. 2018 Nov 9. pii: S1569-1993(18)30929-9. doi: 10.1016/j.jcf.2018.11.001

November 2018

Title: Glycosaminoglycans are differentially involved in bacterial binding to healthy and cystic fibrosis lung cells.
References
J Cyst Fibros. 2018 Nov 8. pii: S1569-1993(18)30920-2. doi: 10.1016/j.jcf.2018.10.017. 

November 2018

Title: Validation of the French 3-year prognostic score using the Canadian Cystic Fibrosis registry.
References
J Cyst Fibros. 2018 Nov 2. pii: S1569-1993(18)30911-1. doi: 10.1016/j.jcf.2018.10.014

October 2018

Title: Antibody response against Mycobacterium avium complex in cystic fibrosis patients measured by a novel IgG ELISA test
References
J Cyst Fibros. 2018 Nov 29. pii: S1569-1993(18)30938-X. doi: 10.1016/j.jcf.2018.11.011. [

October 2018

Title: Failure to conceive in women with CF is associated with pancreatic insufficiency and advancing age
References
J Cyst Fibros. 2018 Oct 23. pii: S1569-1993(18)30867-1. doi: 10.1016/j.jcf.2018.10.009.

October 2018

Title: SWATH label-free proteomics for cystic fibrosis research
References
J Cyst Fibros. 2018 Oct 19. pii: S1569-1993(18)30855-5. doi: 10.1016/j.jcf.2018.10.004.
 
Title: SWATH label-free proteomics for cystic fibrosis research
References
J Cyst Fibros. 2018 Oct 19. pii: S1569-1993(18)30855-5. doi: 10.1016/j.jcf.2018.10.004.
 
Title: Prevalence, geographic risk factor, and development of a standardized protocol for fungal isolation in cystic fibrosis: Results from the international prospective study “MFIP”
References
J Cyst Fibros. 2018 Oct 19. pii: S1569-1993(18)30839-7. doi: 10.1016/j.jcf.2018.10.001

October 2018

Title: Seasonal fluctuation of lung function in cystic fibrosis: A national register-based study in two northern European populations
References
J Cyst Fibros. 2018 Oct 18. pii: S1569-1993(18)30858-0. doi: 10.1016/j.jcf.2018.10.006. 

October 2018

Title: Disparities in Mortality of Hispanic Patients with Cystic Fibrosis in the United States. A National and Regional Cohort Study
References
Am J Respir Crit Care Med. 2018 Oct 15;198(8):1055-1063. doi: 10.1164/rccm.201711-2357OC.

October 2018

Title: Combined antifungal therapy is superior to monotherapy in pulmonary scedosporiosis in cystic fibrosis
References
J Cyst Fibros. 2018 Oct 5. pii: S1569-1993(18)30794-X. doi: 10.1016/j.jcf.2018.08.012

September 2018

Title: Phenotypic spectrum of patients with cystic fibrosis and cystic fibrosis-related disease carrying p.Arg117His
References
J Cyst Fibros. 2018 Sep 29. pii: S1569-1993(18)30800-2. doi: 10.1016/j.jcf.2018.09.002

September 2018

Title: Human epididymis protein 4 (HE4) levels inversely correlate with lung function improvement (delta FEV1) in cystic fibrosis patients receiving ivacaftor treatment.
References
J Cyst Fibros. 2018 Sep 26. pii: S1569-1993(18)30795-1. doi: 10.1016/j.jcf.2018.08.013.
Title: Mental Health screening in cystic fibrosis centres across Europe
References
J Cyst Fibros. 2018 Sep 26. pii: S1569-1993(18)30801-4. doi: 10.1016/j.jcf.2018.09.003

September 2018

Title: The Q359K/T360K mutation causes cystic fibrosis in Georgian Jews.
References
J Cyst Fibros. 2018 Sep;17(5):e41-e45. doi: 10.1016/j.jcf.2018.06.008. Epub 2018 Jul 20.

September 2018

Title: Repeated Hot Water and Steam Disinfection of Pari LC Plus® Nebulizers Alters Nebulizer Output
References
J Cyst Fibros. 2018 Sep 14. pii: S1569-1993(18)30753-7. doi: 10.1016/j.jcf.2018.08.005.

September 2018

Title: Higher Interleukin-7 serum concentrations in patients with cystic fibrosis correlate with impaired lung function
References

September 2018

Title: Rate and Predictors of Prescription of Lumacaftor – Ivacaftor in the 18 Months Following Approval in the United States
References
J Cyst Fibros. 2018 Sep 7. pii: S1569-1993(18)30755-0. doi: 10.1016/j.jcf.2018.08.007.

September 2018

Title: Breathlessness catastrophizing relates to poorer quality of life in adults with cystic fibrosis
References
J Cyst Fibros. 2018 Sep 6. pii: S1569-1993(18)30756-2. doi: 10.1016/j.jcf.2018.08.008

August 2018

Title: Investigating the effects of long-term dornase alfa use on lung function using registry data.
References
J Cyst Fibros. 2018 Aug 29. pii: S1569-1993(18)30747-1. doi: 10.1016/j.jcf.2018.08.004

August 2018

Title: Correspondence between symptoms and preference-based health status measures in the STOP study.
References
J Cyst Fibros. 2018 Aug 28. pii: S1569-1993(18)30743-4. doi: 10.1016/j.jcf.2018.08.001.

August 2018

Title: DNA-analysis, Extended CFTR-gene analysis, Immuno-reactive trypsin, Newborn screening, Pancreatitis-associated protein,Validity
References
J Cyst Fibros. 2018 Aug 23. pii: S1569-1993(18)30705-7. doi: 10.1016/j.jcf.2018.07.008
Title: Lumacaftor/Ivacaftor reduces pulmonary exacerbations in patients irrespective of initial changes in FEV1.
References
J Cyst Fibros. 2018 Aug 23. pii: S1569-1993(18)30719-7. doi: 10.1016/j.jcf.2018.07.011. 

August 2018

Title: Rescue of CFTR NBD2 mutants N1303K and S1235R is influenced by the functioning of the autophagosome
References
J Cyst Fibros. 2018 Jun 20. pii: S1569-1993(18)30621-0. doi: 10.1016/j.jcf.2018.05.016.

August 2018

Title: Eradication of Persistent Methicillin-resistant Staphylococcus aureus Infection in Cystic Fibrosis
References
J Cyst Fibros. 2018 Aug 18. pii: S1569-1993(18)30702-1. doi: 10.1016/j.jcf.2018.07.005

August 2018

Title: Antisense oligonucleotide targeting of mRNAs encoding ENaC subunits α, β, and ɣ improves cystic fibrosis-like disease in mice
References
J Cyst Fibros. 2018 Aug 10. pii: S1569-1993(18)30703-3. doi: 10.1016/j.jcf.2018.07.006
Title: Continuous glucose monitoring in youth with cystic fibrosis treated with lumacaftor-ivacaftor
References
J Cyst Fibros. 2018 Aug 10. pii: S1569-1993(18)30718-5. doi: 10.1016/j.jcf.2018.07.010

July 2018

Title: Respiratory rate in infants with cystic fibrosis throughout the first year of life and association with lung clearance index measured shortly after birth
References
J Cyst Fibros. 2018 Jul 27. pii: S1569-1993(18)30696-9. doi: 10.1016/j.jcf.2018.07.002.

July 2018

Title: R560S: a class II CFTR mutation that is not rescued by current modulators
References
J Cyst Fibros. 2018 Jul 18. pii: S1569-1993(18)30643-X. doi: 10.1016/j.jcf.2018.07.001

July 2018

Title: Prevalence of hypoglycemia during oral glucose tolerance testing in adults with cystic fibrosis and risk of developing cystic fibrosis-related diabetes.
References
J Cyst Fibros. 2018 Jul;17(4):536-541. doi: 10.1016/j.jcf.2018.03.009. Epub 2018 Apr 19.

July 2018

Title: Impact of a program ensuring consistent response to acute drops in lung function in children with cystic fibrosis.
References
J Cyst Fibros. 2018 Jul 13. pii: S1569-1993(18)30628-3. doi: 10.1016/j.jcf.2018.06.003. 

July 2018

Title: Age-Related differences in Dental Caries and Associated Risk Factors in Individuals with Cystic Fibrosis Ages 6-20 years: A Pilot Study
References
J Cyst Fibros. 2018 Jul 10. pii: S1569-1993(18)30642-8. doi: 10.1016/j.jcf.2018.06.009.

July 2018

Title: Establishment of a ΔF508-CF promyelocytic cell line for cystic fibrosis research and drug screening
References

July 2018

Title: Italian and North American dietary intake after ivacaftor treatment for Cystic Fibrosis Gating Mutations.
References
J Cyst Fibros. 2018 Jul 5. pii: S1569-1993(18)30629-5. doi: 10.1016/j.jcf.2018.06.004

June 2018

Title: A Specialized Method of Sputum Collection and Processing for Therapeutic Interventions in Cystic Fibrosis
References
J Cyst Fibros. 2018 Jun 27. pii: S1569-1993(18)30625-8. doi: 10.1016/j.jcf.2018.06.001. 

June 2018

Title: RNA sequencing data from neutrophils of patients with cystic fibrosis reveals potential for developing biomarkers for pulmonary exacerbations
References

June 2018

Title: Electrochemical measurement of membrane cholesterol correlates with CFTR function and is HDAC6-dependent
References
J Cyst Fibros. 2018 Jun 22. pii: S1569-1993(18)30630-1. doi: 10.1016/j.jcf.2018.06.005

June 2018

Title: Resistin is elevated in cystic fibrosis sputum and correlates negatively with lung function.
References
J Cyst Fibros. 2018 Jun 21. pii: S1569-1993(18)30623-4. doi: 10.1016/j.jcf.2018.05.018.
Title: AGTR2 absence or antagonism prevents cystic fibrosis pulmonary manifestations
References
J Cyst Fibros. 2018 Jun 21. pii: S1569-1993(18)30618-0. doi: 10.1016/j.jcf.2018.05.013.

June 2018

Title: SPX-101 is stable in and retains function after exposure to cystic fibrosis sputum.
References
J Cyst Fibros. 2018 Jun 20. pii: S1569-1993(18)30627-1. doi: 10.1016/j.jcf.2018.06.002

June 2018

Title: Characteristics and outcomes of oral antibiotic treated pulmonary exacerbations in children with cystic fibrosis.
References
J Cyst Fibros. 2018 Jun 16. pii: S1569-1993(18)30620-9. doi: 10.1016/j.jcf.2018.05.015. 

June 2018

Title: Likelihood-based analysis of outcome-dependent sampling designs with longitudinal data.
References
Stat Med. 2018 Jun 15;37(13):2120-2133. doi: 10.1002/sim.7633.

June 2018

Title: Combination potentiator ('co-potentiator') therapy for CF caused by CFTR mutants, including N1303K, that are poorly responsive to single potentiators.
References
J Cyst Fibros. 2018 Jun 11. pii: S1569-1993(18)30592-7. doi: 10.1016/j.jcf.2018.05.010.

June 2018

Title: Physiological and pharmacological characterization of the N1303K mutant CFTR.
References
J Cyst Fibros. 2018 Jun 7. pii: S1569-1993(18)30593-9. doi: 10.1016/j.jcf.2018.05.011. 

June 2018

Title: Continuous glucose monitoring guided insulin therapy is associated with improved clinical outcomes in cystic fibrosis-related diabetes.
References
J Cyst Fibros. 2018 Jun 6. pii: S1569-1993(18)30587-3. doi: 10.1016/j.jcf.2018.05.005. 

June 2018

Title: Interleukin-1 is associated with inflammation and structural lung disease in young children with cystic fibrosis
References
J Cyst Fibros. 2018 Jun 5. pii: S1569-1993(18)30588-5. doi: 10.1016/j.jcf.2018.05.006

June 2018

Title: Measured fetal and neonatal exposure to Lumacaftor and Ivacaftor during pregnancy and while breastfeeding
References
J Cyst Fibros. 2018 Jun 1. pii: S1569-1993(18)30591-5. doi: 10.1016/j.jcf.2018.05.009. 

May 2018

Title: Primary sclerosing cholangitis is associated with abnormalities in CFTR.
References
J Cyst Fibros. 2018 May 26. pii: S1569-1993(18)30115-2. doi: 10.1016/j.jcf.2018.04.005.

May 2018

Title: Emergence of livestock-associated MRSA isolated from cystic fibrosis patients: result of a Belgian national survey
References
J Cyst Fibros. 2018 May 24. pii: S1569-1993(18)30577-0. doi: 10.1016/j.jcf.2018.04.008.