With the CF Research News, we aim to bridge the gap between people with CF and the researchers investigating CF and how best to treat those with the condition.
We want to provide access to patients, parents, relatives, friends and caregivers of patients with CF to all scientific work mainly published in the Journal of Cystic Fibrosis (JCF).

All PDF files published hereunder are lay version summaries of work published in the JCF.

August 2020

Title: The implementation of an aminoglycoside induced ototoxicity algorithm for people with cystic fibrosis
References
J Cyst Fibros. 2020 Aug 15;S1569-1993(20)30817-1. doi: 10.1016/j.jcf.2020.08.002. Online ahead of print.

August 2020

Title: Projecting the impact of delayed access to elexacaftor/tezacaftor/ivacaftor for people with Cystic Fibrosis
References
J Cyst Fibros. 2020 Aug 5;S1569-1993(20)30809-2. doi: 10.1016/j.jcf.2020.07.017. Online ahead of print.

August 2020

Title: Azithromycin and Tezacaftor/Ivacaftor is associated with first-degree heart block in an adult with Cystic Fibrosis
References
J Cyst Fibros. 2020 Aug 4;S1569-1993(20)30808-0. doi: 10.1016/j.jcf.2020.07.016. Online ahead of print.

July 2020

Title: The impact of the COVID-19 pandemic on the emotional well-being and home treatment of Belgian patients with cystic fibrosis, including transplanted patients and children
References
J Cyst Fibros. 2020 Jul 31;S1569-1993(20)30815-8. doi: 10.1016/j.jcf.2020.07.022. Online ahead of print.

July 2020

Title: Citrullination of extracellular histone H3.1 reduces antibacterial activity and exacerbates its proteolytic degradation
References
J Cyst Fibros. 2020 Jul 26;S1569-1993(20)30802-X. doi: 10.1016/j.jcf.2020.07.010. Online ahead of print.

July 2020

Title: Prospective cohort study of ototoxicity in persons with cystic fibrosis following a single course of intravenous tobramycin
References
J Cyst Fibros . 2020 Jul 23;S1569-1993(20)30793-1. doi: 10.1016/j.jcf.2020.07.001. Online ahead of print.

July 2020

Title: Evaluating assumptions of definition-based pulmonary exacerbation endpoints in cystic fibrosis clinical trials
References
J Cyst Fibros. 2020 Jul 15;S1569-1993(20)30800-6. doi: 10.1016/j.jcf.2020.07.008.
 

July 2020

Title: Efficacy and safety of ataluren in patients with nonsense-mutation cystic fibrosis not receiving chronic inhaled aminoglycosides: the international, randomized, double-blind, placebo-controlled Ataluren Confirmatory Trial in Cystic Fibrosis (ACT CF)
References
J Cyst Fibros. 2020 Jul;19(4):595-601. doi: 10.1016/j.jcf.2020.01.007. Epub 2020 Jan 23.
Title: CFTR modulator therapy for cystic fibrosis caused by the rare c.3700A>G mutation
References
J Cyst Fibros . 2020 Jul 14;S1569-1993(20)30795-5. doi: 10.1016/j.jcf.2020.07.003.

July 2020

Title: Evaluation of airway and circulating inflammatory biomarkers for cystic fibrosis drug development
References
J Cyst Fibros . 2020 Jul 1;S1569-1993(20)30782-7. doi: 10.1016/j.jcf.2020.06.017.

June 2020

Title: A disruption of innervation around CF tissues results in low amount of VIP before CF disease has produced damage to the lungs and small intestine.
References
J Cyst Fibros. 2020 Jun 26;S1569-1993(20)30777-3. doi: 10.1016/j.jcf.2020.06.013. Online ahead of print

June 2020

Title: Fibrocyte accumulation in the lungs of cystic fibrosis patients
References
J Cyst Fibros. 2020 Jun 24;S1569-1993(20)30756-6. doi: 10.1016/j.jcf.2020.06.011. Online ahead of print.

June 2020

Title: Clinical response to lumacaftor-ivacaftor in patients with cystic fibrosis according to baseline lung function
References
J Cyst Fibros. 2020 Jun 23;S1569-1993(20)30752-9. doi: 10.1016/j.jcf.2020.06.012. Online ahead of print.

June 2020

Title: Lumacaftor/ivacaftor improves liver cholesterol metabolism but does not influence hypocholesterolemia in patients with cystic fibrosis
References
J Cyst Fibros. 2020 Jun 22;S1569-1993(20)30779-7. doi: 10.1016/j.jcf.2020.06.015. Online ahead of print

June 2020

Title: Influenza B outbreak at an adult cystic fibrosis centre - clinical impact and factors influencing spread
References
J Cyst Fibros. 2020 Jun 19;S1569-1993(20)30124-7. doi: 10.1016/j.jcf.2020.04.011.

June 2020

Title: In vitro 3D culture lung model from expanded primary cystic fibrosis human airway cells
References
J Cyst Fibros. 2020 Jun 18;S1569-1993(20)30151-X. doi: 10.1016/j.jcf.2020.05.007. Online ahead of print.

June 2020

Title: Antimicrobial resistance: concerns of healthcare providers and people with CF
References
J Cyst Fibros . 2020 Jun 17;S1569-1993(20)30159-4. doi: 10.1016/j.jcf.2020.05.009

June 2020

Title: Newborn screening alone insufficient to improve pulmonary outcomes for cystic fibrosis
References
J Cyst Fibros . 2020 Jun 13;S1569-1993(20)30731-1. doi: 10.1016/j.jcf.2020.06.002. 
Title: The fungal airway microbiome in cystic fibrosis and non-cystic fibrosis bronchiectasis
References
J Cyst Fibros. 2020 Jun 13;S1569-1993(20)30163-6. doi: 10.1016/j.jcf.2020.05.013.
Title: Immunotyping of clinically divergent p.Phe508del homozygous monozygous cystic fibrosis twins
References
J Cyst Fibros. 2020 Jun 13;S1569-1993(20)30754-2. doi: 10.1016/j.jcf.2020.06.009.
Title: Tezacaftor/ivacaftor in people with cystic fibrosis heterozygous for minimal function CFTR mutations
References
J Cyst Fibros . 2020 Jun 13;S1569-1993(20)30128-4. doi: 10.1016/j.jcf.2020.04.015.

June 2020

Title: Defective BACH1/HO-1 regulatory circuits in cystic fibrosis bronchial epithelial cells
References
J Cyst Fibros . 2020 Jun 11;S1569-1993(20)30150-8. doi: 10.1016/j.jcf.2020.05.006. Online ahead of print.
Title: Accumulation and persistence of Ivacaftor in airway epithelia with prolonged treatment
References
J Cyst Fibros . 2020 Jun 11;S1569-1993(20)30123-5. doi: 10.1016/j.jcf.2020.04.010.

June 2020

Title: Clinimetric evaluation of muscle function tests for individuals with cystic fibrosis: A systematic review
References
J Cyst Fibros . 2020 Jun 10;S1569-1993(20)30164-8. doi: 10.1016/j.jcf.2020.05.014.

June 2020

Title: Building global development strategies for cf therapeutics during a transitional cftr modulator era
References
J Cyst Fibros . 2020 Jun 7;S1569-1993(20)30161-2. doi: 10.1016/j.jcf.2020.05.011. Online ahead of print.

June 2020

Title: Pseudomonas aeruginosa antimicrobial susceptibility test (AST) results and pulmonary exacerbation treatment responses in cystic fibrosis
References
J Cyst Fibros . 2020 Jun 4;S1569-1993(20)30152-1. doi: 10.1016/j.jcf.2020.05.008

June 2020

Title: Clinical effects of the three CFTR potentiator treatments curcumin, genistein and ivacaftor in patients with the CFTR-S1251N gating mutation
References
J Cyst Fibros. 2020 Jun 1;S1569-1993(20)30127-2. doi: 10.1016/j.jcf.2020.04.014. Online ahead of print.

May 2020

Title: A longitudinal assessment of non-Invasive biomarkers to diagnose and predict Ccystic Fibrosis-Associated Liver Disease
References
J Cyst Fibros . 2020 May 30;S1569-1993(20)30133-8. doi: 10.1016/j.jcf.2020.05.002.
Title: Disruption of the extracellular polymeric network of Pseudomonas aeruginosa biofilms by alginate lyase enhances pathogen eradication by antibiotics
References
J Cyst Fibros . 2020 May 30;S1569-1993(20)30119-3. doi: 10.1016/j.jcf.2020.04.006.
 
Title: Metabolomics profiling of tobacco exposure in children with cystic fibrosis
References
J Cyst Fibros . 2020 May 30;S1569-1993(20)30134-X. doi: 10.1016/j.jcf.2020.05.003.

May 2020

Title: Circulating CRP and calprotectin to diagnose CF pulmonary exacerbations
References
J Cyst Fibros. 2020 May 28;S1569-1993(20)30129-6. doi: 10.1016/j.jcf.2020.04.016.

May 2020

Title: Testicular Pain Following Initiation of Elexacaftor/Tezacaftor/Ivacaftor in Males With Cystic Fibrosis
References
J Cyst Fibros. 2020 May 26;S1569-1993(20)30130-2. doi: 10.1016/j.jcf.2020.04.017

May 2020

Title: Global assessment of the integrated stress response in CF patient-derived airway and intestinal tissues
References
J Cyst Fibros. 2020 May 22;S1569-1993(20)30118-1. doi: 10.1016/j.jcf.2020.04.005.

May 2020

Title: Females with Cystic Fibrosis have a larger decrease in sweat chloride in response to lumacaftor/ivacaftor compared to males
References
J Cyst Fibros. 2020 May 21;S1569-1993(20)30135-1. doi: 10.1016/j.jcf.2020.05.004

May 2020

Title: Distal Intestinal Obstruction Syndrome resolved by dissolution with Coca-Cola® via colonoscopy in a cystic fibrosis patient
References
J Cyst Fibros . 2020 May 20;S1569-1993(20)30132-6. doi: 10.1016/j.jcf.2020.05.001. Online ahead of print. 

May 2020

Title: Glucose ingestion in cystic fibrosis induces severe redox imbalance: a potential role in diabetes
References
J Cyst Fibros. 2020 May;19(3):476-482. doi: 10.1016/j.jcf.2020.02.010. Epub 2020 Feb 27.
Title: Effect of one-year lumacaftor-ivacaftor treatment on glucose tolerance abnormalities in cystic fibrosis patients
References
J Cyst Fibros . 2020 Mar 19;S1569-1993(20)30073-4. doi: 10.1016/j.jcf.2020.03.002.

May 2020

Title: Average Rate of Lung Function Decline in Adults with Cystic Fibrosis in the United Kingdom: Data from the UK CF Registry
References
J Cyst Fibros. 2020 May 4;S1569-1993(20)30121-1. doi: 10.1016/j.jcf.2020.04.008.

April 2020

Title: A multinational report to characterise SARs-CoV-2 infection in people with cystic fibrosis
References
J Cyst Fibros. 2020 Apr 25;S1569-1993(20)30125-9. doi: 10.1016/j.jcf.2020.04.01

April 2020

Title: Use of a mobile application for self-management of pancreatic enzyme replacement therapy is associated with improved gastro-intestinal related quality of life in children with Cystic Fibrosis
References
J Cyst Fibros . 2020 Jul;19(4):562-568. doi: 10.1016/j.jcf.2020.04.001. Epub 2020 Apr 22

April 2020

Title: “Mild” CFTR genetic variants might be associated with a lower than expected probability of developing CF
References
J Cyst Fibros . 2020 Apr 20;S1569-1993(20)30098-9. doi: 10.1016/j.jcf.2020.03.019.

April 2020

Title: Resting energy expenditure in cystic fibrosis patients decreases after lung transplantation, which improves applicability of prediction equations for energy requirement
References
J Cyst Fibros. 2020 Apr 11. pii: S1569-1993(20)30092-8. doi: 10.1016/j.jcf.2020.03.013. 

April 2020

Title: Caring for gender diverse youth with cystic fibrosis
References
J Cyst Fibros. 2020 Apr 5;S1569-1993(20)30074-6. doi: 10.1016/j.jcf.2020.03.003.

March 2020

Title: Antibiofilm and mucolytic action of nitric oxide delivered as a gas or via macromolecular donor using in vitro and ex vivo models
References
J Cyst Fibros. 2020 Mar 20;S1569-1993(20)30075-8. doi: 10.1016/j.jcf.2020.03.004
Title: Go for It, Dream Big, Work Hard and Persist': A Message to the Next Generation of CF Leaders in Recognition of International Women's Day 2020
References
J Cyst Fibros. 2020 Mar 7;S1569-1993(20)30070-9. doi: 10.1016/j.jcf.2020.02.021.

March 2020

Title: Total bacterial load, inflammation, and structural lung disease in paediatric cystic fibrosis
References

J Cyst Fibros. 2020 Mar 18; - DOI: 10.1016/j.jcf.2020.03.008

March 2020

Title: Intrinsic Alterations in Peripheral Neutrophils From Cystic Fibrosis Newborn Piglets
References
J Cyst Fibros. 2020 Mar 9;S1569-1993(20)30065-5. doi: 10.1016/j.jcf.2020.02.016.

March 2020

Title: Outcomes of pregnancy in women with cystic fibrosis (CF) taking CFTR modulators - an international survey
References
J Cyst Fibros 2020 Mar 6 -  doi: 10.1016/j.jcf.2020.02.018.

March 2020

Title: Ebselen attenuates tobramycin-induced ototoxicity in mice
References
J Cyst Fibros. 2020 Mar 5;S1569-1993(20)30063-1. doi: 10.1016/j.jcf.2020.02.014.

February 2020

Title: Finding the Relevance of Antimicrobial Stewardship for Cystic Fibrosis
References
J Cyst Fibros. 2020 Feb 29;S1569-1993(20)30059-X. doi: 10.1016/j.jcf.2020.02.012.

February 2020

Title: Glucose abnormalities detected by continuous glucose monitoring are common in young children with Cystic Fibrosis
References
J Cyst Fibros. 2020 Feb 25;S1569-1993(20)30057-6. doi: 10.1016/j.jcf.2020.02.009.
Theme
False-positives, Imaging, Immunology, Lung Disease and Infection, Microbiology, Newborn screening, Nutrition/Gastroenterology, Parents, Physiotherapy/Exercise testing, Pregnancy with CF, Psychosocial, Pulmonology

February 2020

Title: Tobacco smoke exposure and socioeconomic factors are independent predictors of pulmonary decline in pediatric cystic fibrosis
References
J Cyst Fibros. 2020 Feb 17;S1569-1993(20)30049-7. doi: 10.1016/j.jcf.2020.02.004.

February 2020

Title: Amplifiers co-translationally enhance CFTR biosynthesis via PCBP1-mediated regulation of CFTR mRNA
References
J Cyst Fibros . 2020 Feb 14;S1569-1993(20)30052-7. doi: 10.1016/j.jcf.2020.02.006.
Title: In Vivo demonstration of Pseudomonas aeruginosa biofilms as independent pharmacological microcompartments
References
J Cyst Fibros . 2020 Feb 14;S1569-1993(20)30033-3. doi: 10.1016/j.jcf.2020.01.009.

February 2020

Title: Predictive Effects of Low Birth Weight and Small for Gestational Age Status on Respiratory and Nutritional Outcomes in Cystic Fibrosis
References
J Cyst Fibros  2020 Feb 12 - DOI: 10.1016/j.jcf.2020.02.003
Title: Lymphocyte responses to Mycobacterium tuberculosis and Mycobacterium bovis are similar between BCG-vaccinated patients with cystic fibrosis and healthy controls
References
J Cyst Fibros  2020 Feb 12  DOI: 10.1016/j.jcf.2020.01.013

February 2020

Title: Minimal change in structural, functional and inflammatory markers of lung disease in newborn screened infants with cystic fibrosis at one year
References
J Cyst Fibros . 2020 Feb 7;S1569-1993(20)30031-X. doi: 10.1016/j.jcf.2020.01.006.
Title: Pseudomonas Aeruginosa Antibody Response in Cystic Fibrosis Decreases Rapidly Following Lung Transplantation
References
J Cyst Fibros  2020 Feb 7 -  DOI: 10.1016/j.jcf.2020.01.012

January 2020

Title: Identification of Mycobacterium Porcinum in Patients With Cystic Fibrosis: Pathogen or Contaminant?
References
J Cyst Fibros 2020 Jan 22 - 10.1016/j.jcf.2020.01.004

January 2020

Title: Glycaemic control and FEV1 recovery during pulmonary exacerbations in paediatric cystic fibrosis-related diabetes
References
J Cyst Fibros  2020 Jan 21 -  DOI: 10.1016/j.jcf.2019.12.016

January 2020

Title: Cystic Fibrosis Related Diabetes; Glucose challenge test; Oral glucose tolerance test.
References
Saba Sheikh, A Russell Localio, Andrea Kelly, Ronald C Rubenstein

January 2020

Title: Pregnancy outcomes in women with cystic fibrosis and poor pulmonary function
References
J Cyst Fibros. 2020 Jan;19(1):80-83. doi: 10.1016/j.jcf.2019.06.003. Epub 2019 Jul 1.
Title: Inactivation of CFTR by CRISPR/Cas9 alters transcriptional regulation of inflammatory pathways and other networks
References
J Cyst Fibros. 2020 Jan;19(1):34-39. doi: 10.1016/j.jcf.2019.05.003.

January 2020

Title: Sputum trypsin-like protease activity relates to clinical outcome in cystic fibrosis.
References
J Cyst Fibros  2020 Jan 10 - DOI: 10.1016/j.jcf.2019.12.014

January 2020

Title: Clinical effect of lumacaftor/ivacaftor in F508del homozygous CF patients with FEV1 ≥90% predicted at baseline
References
J Cyst Fibros 2020 Jan 7 - DOI: 10.1016/j.jcf.2019.12.015

January 2020

Title: Developing a smartphone application to support social connectedness and wellbeing in young people with cystic fibrosis
References
J Cyst Fibros  2020 Jan 6 - DOI: 10.1016/j.jcf.2019.12.011

January 2020

Title: Adherence to lumacaftor-ivacaftor therapy in patients with cystic fibrosis in France
References
J Cyst Fibros. 2020 Jan 2 doi: 10.1016/j.jcf.2019.09.018. Online ahead of print.

December 2019

Title: Rapid lung function decline in adults with early-stage cystic fibrosis lung disease
References
J Cyst Fibros  2019 Dec 20 -  DOI: 10.1016/j.jcf.2019.12.005
Title: Utilizing centralized biorepository samples for biomarkers of cystic fibrosis lung disease severity
References
J Cyst Fibros  2019 Dec 20 -  DOI: 10.1016/j.jcf.2019.12.007

December 2019

Title: Prevalence of unmet palliative care needs in adults with cystic fibrosis
References
J Cyst Fibros. 2019 Dec 18;S1569-1993(19)30978-6. doi: 10.1016/j.jcf.2019.11.010

December 2019

Title: Structured Surveillance of Achromobacter, Pandoraea and Ralstonia Species From Patients in England With Cystic Fibrosis
References
J Cyst Fibros 2019 Dec 17 -  DOI: 10.1016/j.jcf.2019.11.005

December 2019

Title: Lumacaftor/ivacaftor reduces exacerbations in adults homozygous for Phe508del mutation with severe lung disease
References
J Cyst Fibros. 2019 Dec 15;S1569-1993(19)30985-3. doi: 10.1016/j.jcf.2019.12.006.

November 2019

Title: Antimicrobial Susceptibility Testing in Cystic Fibrosis: A Delphi approach to defining best practices
References
J Cyst Fibros. 2019 Oct 31. pii: S1569-1993(19)30919-1. doi: 10.1016/j.jcf.2019.10.006.

November 2019

Title: Ivacaftor in Cystic Fibrosis With Residual Function: Lung Function Results From an N-of-1 Study
References
J Cyst Fibros. 2019 Nov 26. pii: S1569-1993(19)30897-5. doi: 10.1016/j.jcf.2019.09.013.

November 2019

Title: Integrating the multiple breath washout test into international multicentre trials.
References
J Cyst Fibros. 2019 Nov 23. pii: S1569-1993(19)30968-3. doi: 10.1016/j.jcf.2019.11.006.

November 2019

Title: Answering the call to address cystic fibrosis treatment burden in the era of highly effective CFTR modulator therapy
References
J Cyst Fibros  2019 Nov 21 -  DOI: 10.1016/j.jcf.2019.11.007
Title: Streptococcus pseudopneumoniae, an opportunistic pathogen in patients with cystic fibrosis
References
J Cyst Fibros. 2019 Nov 20. pii: S1569-1993(19)30966-X. doi: 10.1016/j.jcf.2019.11.004.

November 2019

Title: Lavage lipidomics signatures in children with cystic fibrosis and protracted bacterial bronchitis
References
J Cyst Fibros. 2019 Nov;18(6):790-795. doi: 10.1016/j.jcf.2019.04.012. Epub 2019 Apr 25.
Title: The role of endothelial cells in cystic fibrosis
References
J Cyst Fibros. 2019 Nov;18(6):752-761. doi: 10.1016/j.jcf.2019.07.005

November 2019

Title: Can Exercise Replace Airway Clearance Techniques in Cystic Fibrosis? A Survey of Patients and Healthcare Professionals
References
J Cyst Fibros 2019 Nov 15 - DOI: 10.1016/j.jcf.2019.10.026

November 2019

Title: Characterising burden of treatment in cystic fibrosis to identify priority areas for clinical trials
References
J Cyst Fibros. 2019 Nov 14. pii: S1569-1993(19)30961-0. doi: 10.1016/j.jcf.2019.10.025

November 2019

Title: Prevalence and factors associated with overweight and obesity in adults with cystic fibrosis: A single-center analysis
References
J Cyst Fibros. 2019 Nov 11. pii: S1569-1993(19)30922-1. doi: 10.1016/j.jcf.2019.10.004.

November 2019

Title: Regional differences in infection and structural lung disease in infants and young children with cystic fibrosis
References
J Cyst Fibros. 2019 Nov 6. pii: S1569-1993(19)30933-6. doi: 10.1016/j.jcf.2019.10.018.

November 2019

Title: Insights into the variability of Nasal Potential Difference, a biomarker of CFTR activity
References
J Cyst Fibros. 2019 Nov 4. pii: S1569-1993(19)30899-9. doi: 10.1016/j.jcf.2019.09.015. 

November 2019

Title: The implications of dysglycaemia on aerobic exercise and ventilatory function in cystic fibrosis
References
J Cyst Fibros . 2019 Nov 2;S1569-1993(19)30895-1. doi: 10.1016/j.jcf.2019.09.014.

October 2019

Title: Infection Prevention and Control in Patients With Cystic Fibrosis (CF): Results From a Survey in 35 German CF Treatment Centers
References
J Cyst Fibros  2019 Oct 31  pii: S1569-1993(19)30925-7. DOI: 10.1016/j.jcf.2019.10.012
Title: Cystic fibrosis related diabetes in Europe: Prevalence, risk factors and outcome
References
J Cyst Fibros. 2019 Oct 31. pii: S1569-1993(19)30916-6. doi: 10.1016/j.jcf.2019.10.009

October 2019

Title: Minimal detectable change and minimal clinically important differences in modified shuttle walk test in children and adolescents with cystic fibrosis
References
J Cyst Fibros. 2019 Oct 30. pii: S1569-1993(19)30915-4. doi: 10.1016/j.jcf.2019.10.007.
Title: Cystic Fibrosis in Black African Children
References
J Cyst Fibros. 2019 Oct 30. pii: S1569-1993(19)30891-4. doi: 10.1016/j.jcf.2019.09.007. 
Title: Occurrence, outcomes and predictors of portal hypertension in cystic fibrosis: a longitudinal prospective birth cohort study.
References
J Cyst Fibros. 2019 Oct 30. pii: S1569-1993(19)30900-2. doi: 10.1016/j.jcf.2019.09.016

October 2019

Title: Intraoperative extracorporeal membrane oxygenation for lung transplantation in cystic fibrosis patients: predictors and impact on outcome
References
J Cyst Fibros. 2019 Oct 29. pii: S1569-1993(19)30930-0. doi: 10.1016/j.jcf.2019.10.016

October 2019

Title: Risk factors for progression of structural lung disease in school-age children with cystic fibrosis
References
J Cyst Fibros  2019 Oct 28 -  DOI: 10.1016/j.jcf.2019.10.014
Title: Differences in clinical outcomes of paediatric cystic fibrosis patients with and without meconium ileus.
References
J Cyst Fibros. 2019 Oct 28. pii: S1569-1993(19)30892-6. doi: 10.1016/j.jcf.2019.09.008.

October 2019

Title: Infection with Prevotella nigrescens induces Toll-like Receptor 2 signalling and low levels of p65 mediated inflammation in Cystic Fibrosis bronchial epithelial cells
References
J Cyst Fibros. 2019 Oct 10. pii: S1569-1993(19)30889-6. doi: 10.1016/j.jcf.2019.09.005.
 

October 2019

Title: GLPG2737 in lumacaftor/ivacaftor-treated CF subjects homozygous for the F508del mutation: A randomized phase 2A trial (PELICAN).
References
J Cyst Fibros. 2019 Oct 5. pii: S1569-1993(19)30890-2. doi: 10.1016/j.jcf.2019.09.006.

September 2019

Title: Decreased mRNA and protein stability of W1282X limits response to modulator therapy
References
J Cyst Fibros. 2019 Sep;18(5):606-613. doi: 10.1016/j.jcf.2019.02.009. Epub 2019 Feb 23.
Title: CFTR activity is enhanced by the novel corrector GLPG2222, given with and without ivacaftor in two randomized trials
References
J Cyst Fibros. 2019 Sep;18(5):700-707. doi: 10.1016/j.jcf.2019.04.014.
Title: A two-center analysis of hyperpolarized 129Xe lung MRI in stable pediatric cystic fibrosis: Potential as a biomarker for multi-site trials.
References
Couch MJ, Thomen R, Kanhere N, Hu R, Ratjen F, Woods J, Santyr G
Title: International approaches for delivery of positive newborn bloodspot screening results for CF
References
J Cyst Fibros. 2019 Sep;18(5):614-621. doi: 10.1016/j.jcf.2019.04.004. Epub 2019 Apr 30.

September 2019

Title: Micronutrient intake in children with cystic fibrosis in Sydney, Australia
References
J Cyst Fibros. 2019 Sep 14. pii: S1569-1993(19)30885-9. doi: 10.1016/j.jcf.2019.08.028.