With the CF Research News, we aim to bridge the gap between people with CF and the researchers investigating CF and how best to treat those with the condition.
We want to provide access to patients, parents, relatives, friends and caregivers of patients with CF to all scientific work mainly published in the Journal of Cystic Fibrosis (JCF).

All PDF files published hereunder are lay version summaries of work published in the JCF.

May 2018

Title: Primary sclerosing cholangitis is associated with abnormalities in CFTR.
Authors
Werlin S, Scotet V, Uguen K, Audrezet MP, Cohen M, Yaakov Y, Safadi R, Ilan Y, Konikoff F, Galun E, Mizrahi M, Slae M, Sayag S, Cohen-Cymberknoh M, Wilschanski M, Ferec C
References
J Cyst Fibros. 2018 May 26. pii: S1569-1993(18)30115-2. doi: 10.1016/j.jcf.2018.04.005.
Keywords
CFTR-related disorder, Nasal potential difference, New generation sequencing, Primary sclerosing cholangitis
PDF icon CF Research News Article
Scientific Abstract

May 2018

Title: Emergence of livestock-associated MRSA isolated from cystic fibrosis patients: result of a Belgian national survey
Authors
Dodémont M, Argudín MA, Willekens J, Vanderhelst E, Pierard D, Miendje Deyi VY, Hanssens L, Franckx H, Schelstraete P, Leroux-Roels I, Nonhoff C, Deplano A, Knoop C, Malfroot A, Denis O
References
J Cyst Fibros. 2018 May 24. pii: S1569-1993(18)30577-0. doi: 10.1016/j.jcf.2018.04.008.
Keywords
CC398, LA-MRSA, Small colony variant, spa-typing
PDF icon CF Research News Article
Scientific Abstract
Title: Multicentre Standardisation of Chest MRI as Radiation-Free Outcome Measure of Lung Disease in Young Children with Cystic Fibrosis
Authors
Mark O. Wielpütz, Oyunbileg von Stackelberg, Mirjam Stahl, Bertram J. Jobst, Monika Eichinger, Michael U. Puderbach, Lutz Nährlich, Sandra Barth, Christian Schneider, Matthias V. Kopp, Isabell Ricklefs, Michael Buchholz, Burkhard Tümmler, Christian Dopfer
References
J Cyst Fibros. 2018 May 24. pii: S1569-1993(18)30581-2. doi: 10.1016/j.jcf.2018.05.003. 
Keywords
Airway disease, Functional lung imaging, Lung perfusion, Magnetic Resonance Imaging
PDF icon CF Research News Article
Scientific Abstract

May 2018

Title: Strategies for newborn screening for cystic fibrosis: A systematic review of health economic evaluations.
Authors
Schmidt M, Werbrouck A, Verhaeghe N, De Wachter E, Simoens S, Annemans L, Putman K
References
J Cyst Fibros. 2018 May;17(3):306-315. doi: 10.1016/j.jcf.2018.03.002
Keywords
Health economic evaluation, Newborn screening, Systematic review
PDF icon CF Research News Article
Scientific Abstract
Title: Audiometric assessment of paediatric patients with cystic fibrosis
Authors
Kreicher KL, Bauschard MJ, Clemmens CS, Riva CM, Meyer TA.
References
J Cyst Fibros. 2018 May;17(3):383-390. doi: 10.1016/j.jcf.2017.10.007. Epub 2017 Dec 27
Keywords
Audiogram, Conductive hearing loss, Hearing loss, Otitis media, Sensorineural hearing loss
PDF icon CF Research News Article
Scientific Abstract
Title: Comparison of ex vivo and in vitro intestinal cystic fibrosis models to measure CFTR-dependent ion channel activity.
Authors
Zomer-van Ommen DD, de Poel E, Kruisselbrink E, Oppelaar H, Vonk AM, Janssens HM, van der Ent CK, Hagemeijer MC, Beekman JM
References
J Cyst Fibros. 2018 May;17(3):316-324. doi: 10.1016/j.jcf.2018.02.007.
Keywords
Biopsies, CFTR, Differentiation, Donor-matched, Electrophysiology, Monolayers, Organoids
PDF icon CF Research News Article
Scientific Abstract

May 2018

Title: Precision Medicine in Action: The Impact of Ivacaftor on Cystic Fibrosis-Related Hospitalizations
Authors
Feng LB, Grosse SD, Green RF, Fink AK, Sawicki GS
References
Health Aff (Millwood). 2018 May;37(5):773-779. doi: 10.1377/hlthaff.2017.1554.
Keywords
Precision medicine, Rare disease, real world evidence
PDF icon CF Research News Article
Scientific Abstract

May 2018

Title: Health insurance and use of recommended routine care in adults with cystic fibrosis
Authors
Li SS, Hayes D Jr, Tobias JD, Morgan WJ, Tumin D.
References
Clin Respir J. 2018 May;12(5):1981-1988. doi: 10.1111/crj.12767.
Keywords
Medicaid, Medicare, access to care, health care disparities, health insurance
PDF icon CF Research News Article
Scientific Abstract

May 2018

Title: A prospective analysis of unplanned patient-initiated contacts in an adult cystic fibrosis centre.
Authors
Burnet E, Hubert D, Champreux J, Honoré I, Kanaan R, Panzo R, Burgel PR
References
J Cyst Fibros. 2018 May 7. pii: S1569-1993(18)30116-4. doi: 10.1016/j.jcf.2018.04.006
Keywords
Ambulatory care, Contact frequency, Continuity of care, Outpatient, Patient-initiated contact, Telephone triage
PDF icon CF Research News Article
Scientific Abstract

May 2018

Title: Dietary intake of energy-dense, nutrient-poor and nutrient-dense food sources in children with cystic fibrosis
Authors
Rosie Sutherland, Tamarah Katz, Victoria Liu, Justine Quintano, Rebecca Brunner, Chai Wei Tong, Clare E. Collins, Chee Y. Ooi
References
https://doi.org/10.1016/j.jcf.2018.03.011
Keywords
Diet, Nutrition, FFQ, Paediatric
PDF icon CF Research News Article
Scientific Abstract