With the CF Research News, we aim to bridge the gap between people with CF and the researchers investigating CF and how best to treat those with the condition.
We want to provide access to patients, parents, relatives, friends and caregivers of patients with CF to all scientific work mainly published in the Journal of Cystic Fibrosis (JCF).

All PDF files published hereunder are lay version summaries of work published in the JCF.

June 2023

Title: What happens to muscle, fat and body mass index between 8 and 18 years of age in children with cystic fibrosis
Authors
Jade K. Tran, Chee Y. Ooi, Katrina Blazek, Tamarah Katz
References
J Cyst Fibros. 2023 Jun 24;S1569-1993(23)00817-2. doi: 10.1016/j.jcf.2023.06.003.
Theme
Care of patients with CF, Nutrition/Gastroenterology, Pulmonology
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Scientific Abstract

June 2023

Title: Anxiety and Depression Symptom Patterns over 6 years in one Pediatric CF Center
Authors
Michelle Hjelm, Elizabeth Hente, Jamie Miller, Susan Moore, James Peugh, David V Swetland, Dawit G Tadesse, Md Monir Hossain, Christopher Siracusa, Stephanie S Filigno
References
J Cyst Fibros. 2023 Jun 29;S1569-1993(23)00823-8. doi: 10.1016/j.jcf.2023.06.009.
Keywords
anxiety, depression, Generalized anxiety disorder questionnaire, mental health, Patient health questionnaire
Theme
Care of patients with CF, Psychosocial
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Scientific Abstract
Title: Weight A Minute: Exploring the effect on total weight, fat and fat-free weight after the initiation of Elexacaftor/ Tezacaftor/ Ivacaftor in adults with CF
Authors
David Proud, Jamie Duckers
References
J Cyst Fibros. . 2023 Jun 23;S1569-1993(23)00180-7. doi: 10.1016/j.jcf.2023.06.002.
Theme
Care of patients with CF, Diabetes, Nutrition/Gastroenterology
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Scientific Abstract

June 2023

Title: Telehealth in CF: what are the top 10 research papers that can help inform best practices?
Authors
Tamara Vagg, Shivanthan Shanthikumar, Hisham Ibrahim, Paul O'Regan, Wendy W Chapman, Laura Kirwan, Sarath C Ranganathan, Barry J Plant
References
J Cyst Fibros. 2023 Jul;22(4):598-606. doi: 10.1016/j.jcf.2023.05.012. Epub 2023 May 23.
Keywords
Best practices, Expert weighting, Guidance; Novel scoring, Telehealth
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Scientific Abstract

June 2023

Title: Elexacaftor/Tezacaftor/Ivacaftor improves CFTR activity and pulmonary function in Cystic Fibrosis Patients carrying the N1303K Mutation
Authors
Ido Sadras, Eitan Kerem, Galit Livnat, Ifat Sarouk, Oded Breuer, Joel Reiter, Alex Gileles-Hillel, Ori Inbar, Michael Cohen, Ayelet Gamliel, Noemie Stanleigh, Tarini Gunawardena, Claire Bartlett, Tanja Gonska, Theo Moraes, Paul D W Eckford, , Christine E Bear, Felix Ratjen, Batsheva Kerem, Michael Wilschanski, Michal Shteinberg, Malena Cohen-Cymberknoh
References
J Cyst Fibros. 2023 Jun 16;S1569-1993(23)00178-9. doi: 10.1016/j.jcf.2023.06.001.
Theme
Pulmonology
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Scientific Abstract
Title: Elexacaftor/Tezacaftor/Ivacaftor improves CFTR activity and pulmonary function in Cystic Fibrosis Patients carrying the N1303K Mutation
Authors
Ido Sadras, Eitan Kerem, Galit Livnat, Ifat Sarouk, Oded Breuer, Joel Reiter, Alex Gileles-Hillel, Ori Inbar, Michael Cohen, Ayelet Gamliel, Noemie Stanleigh, Tarini Gunawardena, Claire Bartlett, Tanja Gonska, Theo Moraes, Paul D W Eckford,, Christine E Bear, Felix Ratjen, Batsheva Kerem, Michael Wilschanski, Michal Shteinberg, Malena Cohen-Cymberknoh
References
J Cyst Fibros. 2023 Jun 16;S1569-1993(23)00178-9. doi: 10.1016/j.jcf.2023.06.001.
Theme
Care of patients with CF, Clinical Trials, Pulmonology
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Scientific Abstract

June 2023

Title: Molecular fingerprinting of Pseudomonas aeruginosa from PWCF, and a UK reference laboratory investigation into frequency of cross-infection
Authors
Dervla T D Kenna, Zoë Payne, David A Lee, Ann-Marie Keane, Jack Turton, Dania V Zamarreño, Ulf Schaefer, Katie L Hopkins, Danièle Meunier, Rishi Dhillon, Jamie Duckers, Lorraine Speight, Jane F Turton
References
J Cyst Fibros. 2023 Jun 2;S1569-1993(23)00176-5. doi: 10.1016/j.jcf.2023.05.017.
Keywords
Cross-infection, Liverpool epidemic strain, Pseudomonas aeruginosa, Whole genome sequencing
Theme
Microbiology
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Scientific Abstract