May 2019
Title: The use of antimicrobial susceptibility testing in pediatric cystic fibrosis pulmonary exacerbations
Authors Cogen JD, Whitlock KB, Gibson RL, Hoffman LR, VanDevanter DR
References J Cyst Fibros. 2019 May 28. pii: S1569-1993(19)30764-7. doi: 10.1016/j.jcf.2019.05.012.
Keywords Antimicrobial susceptibility testing, Antimicrobial switching, Pediatrics, Pulmonary exacerbations
May 2019
Title: GLPG1837, a CFTR potentiator, in p.Gly551Asp (G551D)-CF patients: An open-label, single-arm, phase 2a study (SAPHIRA1)
Authors Davies JC, Van de Steen O, van Koningsbruggen-Rietschel S, Drevinek P, Derichs N, McKone EF, Kanters D, Allamassey L, Namour F, de Kock H, Conrath K.
References J Cyst Fibros. 2019 May 27. pii: S1569-1993(19)30111-0. doi: 10.1016/j.jcf.2019.05.006.
Keywords CFTR modulator, G551D, GLPG1837, Gating mutation, Ivacaftor
Title: GLPG1837, a CFTR potentiator, in p.Gly551Asp (G551D)-CF patients: An open-label, single-arm, phase 2a study (SAPHIRA1)
Authors Davies JC, Van de Steen O, van Koningsbruggen-Rietschel S, Drevinek P, Derichs N, McKone EF, Kanters D, Allamassey L, Namour F, de Kock H, Conrath K
References J Cyst Fibros. 2019 May 27. pii: S1569-1993(19)30111-0. doi: 10.1016/j.jcf.2019.05.006.
May 2019
Title: Pilot study to test inhaled nitric oxide in cystic fibrosis patients with refractory Mycobacterium abscessus lung infection.
Authors Bentur L, Gur M, Ashkenazi M, Livnat-Levanon G, Mizrahi M, Tal A, Ghaffari A, Geffen Y, Aviram M, Efrati O
References J Cyst Fibros. 2019 May 22. pii: S1569-1993(19)30104-3. doi: 10.1016/j.jcf.2019.05.002.
Keywords Inhaled nitric oxide, Mycobacterium abscessus
May 2019
Title: Peak OGTT glucose is associated with lower lung function in young children with cystic fibrosis.
Authors Prentice BJ, Chelliah A, Ooi CY, Hameed S, Verge CF, Plush L, Widger J.
References J Cyst Fibros. 2019 May 21. pii: S1569-1993(18)30791-4. doi: 10.1016/j.jcf.2019.05.005.
Keywords Abnormal glucose tolerance, CFRD, CGM, Child, Cystic fibrosis-related diabetes, Growth
Title: Peak OGTT glucose is associated with lower lung function in young children with cystic fibrosis.
Authors Prentice BJ, Chelliah A, Ooi CY, Hameed S, Verge CF, Plush L, Widger J.
References J Cyst Fibros. 2019 May 21. pii: S1569-1993(18)30791-4. doi: 10.1016/j.jcf.2019.05.005.
Keywords Abnormal glucose tolerance, CFRD, CGM, Child, Cystic fibrosis-related diabetes, Growth
Title: Peak OGTT glucose is associated with lower lung function in young children with cystic fibrosis.
Authors Prentice BJ, Chelliah A, Ooi CY, Hameed S, Verge CF, Plush L, Widger J.
References J Cyst Fibros. 2019 May 21. pii: S1569-1993(18)30791-4. doi: 10.1016/j.jcf.2019.05.005.
Keywords Abnormal glucose tolerance, CFRD, CGM, Child, Cystic fibrosis-related diabetes, Growth
Title: Correspondence between Lung Function and Symptom Measures from the Cystic Fibrosis Respiratory Symptom Diary–Chronic Respiratory Infection Symptom Score (CFRSD-CRISS)
Authors Laura S. Gold, Donald L. Patrick, Ryan N. Hansen, Christopher H. Goss, and Larry Kessler
References J Cyst Fibros. 2019 May 21. pii: S1569-1993(19)30113-4. doi: 10.1016/j.jcf.2019.05.009.
Keywords Cystic Fibrosis Respiratory Symptom Diary - Chronic Respiratory Infection Symptom Score, Lung function, Pulmonary exacerbations
May 2019
Title: Lung transplant referral for individuals with cystic fibrosis: Cystic Fibrosis Foundation consensus guidelines
Authors Ramos KJ, Smith PJ, McKone EF, Pilewski JM, Lucy A, Hempstead SE, Tallarico E, Faro A, Rosenbluth DB, Gray AL, Dunitz JM; CF Lung Transplant Referral Guidelines Committee.
References J Cyst Fibros. 2019 May;18(3):321-333. doi: 10.1016/j.jcf.2019.03.002. Epub 2019 Mar 27.
Keywords Advanced lung disease, Communication, Lung transplant, Modifiable barriers, Referral, Transplant
Title: High airborne level of Aspergillus fumigatus and presence of azole-resistant TR34/L98H isolates in the home of a cystic fibrosis patient harbouring chronic colonisation with azole-resistant H285Y A. fumigatus.
Authors J Cyst Fibros. 2019 May;18(3):364-367. doi: 10.1016/j.jcf.2019.01.001. Epub 2019 Jan 9. Paluch M, Lejeune S, Hecquet E, Prévotat A, Deschildre A, Fréalle E
References J Cyst Fibros. 2019 May;18(3):364-367. doi: 10.1016/j.jcf.2019.01.001. Epub 2019 Jan 9.
Keywords Aspergillus fumigatus, Azole-resistance, Indoor mould exposure
Title: Predictive factors for lumacaftor/ivacaftor clinical response.
Authors Masson A, Schneider-Futschik EK, Baatallah N, Nguyen-Khoa T, Girodon E, Hatton A, Flament T, Le Bourgeois M, Chedevergne F, Bailly C, Kyrilli S, Achimastos D, Hinzpeter A, Edelman A, Sermet-Gaudelus I.
References J Cyst Fibros. 2019 May;18(3):368-374. doi: 10.1016/j.jcf.2018.12.011. Epub 2018 Dec 28.
Title: Differential Expression of Genes and Receptors in Monocytes from Patients with Cystic Fibrosis.
Authors Abdullah A Tarique, Peter D Sly, Diana G Cardenas, Lin Luo, Jennifer L Stow, Scott C Bell, Claire E Wainwright, Emmanuelle Fantino
References J Cyst Fibros. 2019 May;18(3):342-348. doi: 10.1016/j.jcf.2018.07.012. Epub 2018 Sep 1.
Keywords Cox-2, Gamma-chain receptor, IL-13/IL-4 receptor, IRF4, LRP1, MMP28, MMP9, Macrophage polarization, Monocyte-derived macrophages (MDMs), Monocytes, TIMP-1, TLR4
May 2019
Title: Study of 109 Achromobacter spp. isolates from 9 French CF centres reveals the circulation of a multiresistant clone of A. xylosoxidans belonging to ST 137
Authors Lucie Amoureux, Juliette Sauge, Benoit Sarret, Matthieu Lhoumeau, Audrey Bajard, Jennifer Tetu, Julien Bador, Catherine Neuwirth; MucoMicrobes group
References J Cyst Fibros. 2019 May 16. pii: S1569-1993(19)30065-7. doi: 10.1016/j.jcf.2019.04.005
Keywords Achromobacter, Identification, MLST, Resistance, ST 137, nrdA
May 2019
Title: Deep Learning to Automate Brasfield Chest Radiographic Scoring for Cystic Fibrosis
Authors Evan J. Zucker, Zachary A. Barnes, Matthew P. Lungren, Yekaterina Shpanskaya, Jayne M. Seekins, Safwan S. Halabi, David B. Larson
References J Cyst Fibros. 2019 May 2. pii: S1569-1993(19)30075-X. doi: 10.1016/j.jcf.2019.04.016.
Keywords Brasfield, Chest, Deep convolutional neural network, Deep learning, Radiograph
