April 2017
Title: A Multiple Reader Scoring System for Nasal Potential Difference Parameters
Authors George M. Solomon, Bo Liu, Isabelle Sermet-Gaudelus, Isabelle Fajac, Michael Wilschanski, Francois Vermeulen, Steven M. Rowe
References J Cyst Fibros. 2017 Apr 29. pii: S1569-1993(17)30141-8
Keywords CFTR, Clinical trial outcomes, Nasal potential difference
April 2017
Title: Standardized Treatment of Pulmonary Exacerbations (STOP) study: Observations at the initiation of intravenous antibiotics for cystic fibrosis pulmonary exacerbations.
Authors Sanders DB, Solomon GM, Beckett VV, West NE, Daines CL, Heltshe SL, VanDevanter DR, Spahr JE, Gibson RL, Nick JA, Marshall BC, Flume PA, Goss CH; STOP Study Group.
References J Cyst Fibros. 2017 Apr 28. pii: S1569-1993(17)30101-7.
Keywords FEV(1), Pseudomonas aeruginosa, Symptoms
April 2017
Title: Standardized Treatment of Pulmonary exacerbations (STOP) study: Physician treatment practices and outcomes for individuals with cystic fibrosis with pulmonary exacerbations.
Authors West NE, Beckett VV, Jain R, Sanders DB, Nick JA, Heltshe SL, Dasenbrook EC, VanDevanter DR, Solomon GM, Goss CH, Flume PA; STOP investigators.
References J Cyst Fibros. 2017 Apr 27. pii: S1569-1993(17)30099-1.
Keywords antibiotic therapy, Physician treatment practices, Pulmonary exacerbations
April 2017
Title: Increased Risk of PTLD in Lung Transplant Recipients with Cystic Fibrosis
Authors Erin M. Lowery, William Adams, Shellee A. Grim, Nina M. Clark, Leah Edwards, Jennifer E. Layden
References J Cyst Fibros. 2017 Apr 26. pii: S1569-1993(17)30096-6. doi: 10.1016/j.jcf.2017.03.013.
Keywords Ebstein–Barr virus, Post transplant lymphoproliferative disorder
April 2017
Title: Does current reporting of lung function by the UK cystic fibrosis registry allow a fair comparison of adult centres?
Authors Nightingale JA, Osmond C
References J Cyst Fibros. 2017 Apr 24. pii: S1569-1993(17)30103-0.
Keywords Clinical epidemiology, Respiratory measurement
April 2017
Title: Risk Factors for Persistent Methicillin-resistant Staphylococcus aureus Infection in Cystic Fibrosis
Authors Jennings MT, Dasenbrook EC, Lechtzin N, Boyle MP, Merlo CA
References J Cyst Fibros. 2017 Apr 23. pii: S1569-1993(17)30106-6.
Keywords Epidemiology, MRSA
April 2017
Title: Feasibility and normal values of an integrated conductivity (Nanoduct) sweat test system in healthy newborns
Authors Kuehni CE, Schindler M, Mazur A, Malzacher A, Hornung R, Barben J.
References J Cyst Fibros. 2017 Apr 22. pii: S1569-1993(17)30098-X.
Keywords Conductivity, Newborn screening, Sweat test
April 2017
Title: Rationalizing endpoints for prospective studies of pulmonary exacerbation treatment response in cystic fibrosis
Authors VanDevanter DR, Heltshe SL, Spahr J, Beckett VV, Daines CL, Dasenbrook EC, Gibson RL, Jain R, Sanders DB, Goss CH, Flume PA; STOP Study Group.
References J Cyst Fibros. 2017 Apr 21. pii: S1569-1993(17)30100-5
Keywords Clinical trial, endpoints, Exacerbation, Sample size
April 2017
Title: Survival Comparison of Patients With Cystic Fibrosis in Canada and the United States: A Population-Based Cohort Study.
Authors Stephenson AL, Sykes J, Stanojevic S, Quon BS, Marshall BC, Petren K, Ostrenga J, Fink AK, Elbert A, Goss CH.
References Ann Intern Med. 2017 Apr 18;166(8):537-546. doi: 10.7326/M16-0858. Epub 2017 Mar 14.
Title: Survival Comparison of Patients With Cystic Fibrosis in Canada and the United States: A Population-Based Cohort Study.
Authors Stephenson AL, Sykes J, Stanojevic S, Quon BS, Marshall BC, Petren K, Ostrenga J, Fink AK, Elbert A, Goss CH.
References Ann Intern Med. 2017 Apr 18;166(8):537-546. doi: 10.7326/M16-0858. Epub 2017 Mar 14.
April 2017
Title: CFTR-dependent defect in alternatively-activated macrophages in cystic fibrosis
Authors Abdullah Al Tarique, Peter D Sly, Patrick G Holt, Anthony Bosco, Robert S Ware, Jayden Logan, Scott C Bell, Claire E Wainwright, Emmanuelle Fantino.
References J Cyst Fibros. 2017 Apr 17. pii: S1569-1993(17)30094-2.
Keywords Alternatively activated macrophages, CFTR, CFTR inhibitors, Classically activated macrophages, Endocytosis, IL-13 receptor, Monocyte-derived macrophages, Phagocytosis
April 2017
Title: Age-dependent variation of fecal calprotectin in cystic fibrosis and healthy children.
Authors Garg M, Leach ST, Coffey MJ, Katz T, Strachan R, Pang T, Needham B, Lui K, Ali F, Day AS, Appleton L, Moeeni V, Jaffe A, Ooi CY
References J Cyst Fibros. 2017 Apr 14. pii: S1569-1993(17)30093-0
Keywords Calprotectin, Gastrointestinal inflammation, Leukocyte L1 antigen complex, Pediatrics, S100 proteins
April 2017
Title: A treatment evaluator tool to monitor the real-world effectiveness of inhaled aztreonam lysine in cystic fibrosis.
Authors Plant BJ, Downey DG, Eustace JA, Gunaratnam C, Haworth CS, Jones AM, McKone EF, Peckham DG, Ketchell RI, Bilton D.
References J Cyst Fibros. 2017 Apr 6. pii: S1569-1993(17)30031-0.
Keywords Aztreonam, Evaluation tool, forced expiratory volume, intravenous antibiotics
April 2017
Title: Monocyte derived macrophages from CF pigs exhibit increased inflammatory responses at birth
Authors Paemka L, McCullagh BN, Abou Alaiwa MH, Stoltz DA, Dong Q, Randak CO, Gray RD, McCray PB Jr.
References J Cyst Fibros. 2017 Apr 1. pii: S1569-1993(17)30090-5
Keywords CFTR, Inflammation, Lipopolysaccharide, Macrophage, Monocyte
