With the CF Research News, we aim to bridge the gap between people with CF and the researchers investigating CF and how best to treat those with the condition.
We want to provide access to patients, parents, relatives, friends and caregivers of patients with CF to all scientific work mainly published in the Journal of Cystic Fibrosis (JCF).

All PDF files published hereunder are lay version summaries of work published in the JCF.

March 2017

Title: A 3-year prognostic score for adults with cystic fibrosis.
Authors
Nkam L, Lambert J, Latouche A, Bellis G, Burgel PR, Hocine MN
References
J Cyst Fibros. 2017 Mar 18. pii: S1569-1993(17)30087-5
Keywords
Logistic model, Prognostic factors, Prognostic score, Registry data
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Scientific Abstract

March 2017

Title: Nutritional status, nutrient intake and use of enzyme supplements in paediatric patients with Cystic Fibrosis; a European multicentre study with reference to current guidelines
Authors
Calvo-Lerma J, Hulst JM, Asseiceira I, Claes I, Garriga M, Colombo C, Fornés V, Woodcock S, Martins T, Boon M, Ruperto M, Walet S, Speziali C, Witters P, Masip E, Barreto C, de Boeck K, Ribes-Koninckx C; MyCyFAPP Project.
References
J Cyst Fibros. 2017 Mar 17. pii: S1569-1993(17)30088-7
Theme
Nutrition/Gastroenterology
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Scientific Abstract

March 2017

Title: When is too little care, too much harm in cystic fibrosis? Psychological and ethical approaches to the problem.
Authors
Massie J, Morgan A, Gillam L
References
J Cyst Fibros. 2017 Mar;16(2):299-303
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Scientific Abstract
Title: Clostridium difficile carriage in adult cystic fibrosis (CF); implications for patients with CF and the potential for transmission of nosocomial infection.
Authors
DG Burke, MJ Harrison, C Fleming, M McCarthy, C Shortt, I Sulaiman, DM Murphy, JA Eustace, F Shanahan, C Hill, C Stanton, MC Rea, RP Ross, BJ Plant
References
 2017 Mar;16(2):291-298.
Keywords
Clostridium difficile, Nosocomial infection, Transmission
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Scientific Abstract

March 2017

Title: Nonparametric analysis of competing risks data with event category missing at random.
Authors
Gouskova NA, Lin FC, Fine JP
References
Biometrics. 2017 Mar;73(1):104-113. doi: 10.1111/biom.12547.
Keywords
Competing risks, Missing event category, Nadaraya-Watson estimator, Nonparametric estimation
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Scientific Abstract
Title: Real-life initiation of lumacaftor/ivacaftor combination in adults with cystic fibrosis homozygous for the Phe508del CFTR mutation and severe lung disease
Authors
Hubert D, Chiron R, Camara B, Grenet D, Prévotat A, Bassinet L, Dominique S, Rault G, Macey J, Honoré I, Kanaan R, Leroy S, Desmazes Dufeu N, Burgel PR.
References
J Cyst Fibros. 2017 Mar 15. pii: S1569-1993(17)30086-3
Keywords
CFTR correctors, Lumacaftor/ivacaftor
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March 2017

Title: Technological advances shed light on left ventricular cardiac disturbances in cystic fibrosis
Authors
Sayyid ZN, Sellers ZM
References
J Cyst Fibros. 2017 Mar 14. pii: S1569-1993(17)30080-2
Keywords
Echocardiography, Heart function, Left ventricle
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Scientific Abstract
Title: The CF-CARES primary palliative care model: A CF-specific structured assessment of symptoms, distress, and coping. distress, and coping.
Authors
Friedman D, Linnemann RW, Altstein LL, Islam S, Bach KT, Lamb C, Volpe J, Doolittle C, St John A, O'Malley PJ, Sawicki GS, Georgiopoulos AM, Yonker LM, Moskowitz SM.
References
J Cyst Fibros. 2017 Mar 14. pii: S1569-1993(17)30077-2.
Keywords
anxiety, Chronic symptom burden, depression, Palliative care, Symptom prevalence
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Title: Immediate Effects of Lumacaftor/Ivacaftor Administration on Lung Function in Patients with Severe Cystic Fibrosis Lung Disease
Authors
Natalia Popowicz, Jamie Wood, Anna Tai, Sue Morey, Siobhain Mulrennan
References
 2017 Mar 14. pii: S1569-1993(17)30075-9
Keywords
Ivacaftor, Lumacaftor, Lung function, adverse events
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Scientific Abstract

March 2017

Title: Feasibility of placebo-controlled trial designs for new CFTR modulator evaluation
Authors
Donald R. VanDevanter, Nicole Mayer-Hamblett, Michael Boyle
References
J Cyst Fibros. 2017 Mar 8. pii: S1569-1993(17)30078-4
Keywords
Enrollment, Modulator, Placebo, Trial design
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Scientific Abstract
Title: Association between glucose intolerance and bacterial colonisation in an adult population with cystic fibrosis, emergence of Stenotrophomonas maltophilia.
Authors
Lehoux Dubois, C., Boudreau, V., Tremblay, F., Lavoie A., Berthiaume Y., Rabasa-Lhoret, R., Coriati, A.
References
J Cyst Fibros. 2017 Mar 8. pii: S1569-1993(17)30025-5.
Keywords
Cystic fibrosis related diabetes, Infections, Pathogens, Pulmonary exacerbations, Stenotrophomonas maltophilia
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Scientific Abstract

March 2017

Title: Pilot trial of tobramycin inhalation powder in cystic fibrosis patients with chronic Burkholderia cepacia complex infection
Authors
Valerie Waters, Yvonne Yau, Trevor Beaudoin, Jillian Wettlaufer, Sean Kevin Tom, Nancy McDonald, Leena Rizvi, Michelle Klingel, Felix Ratjen, Elizabeth Tullis
References
J Cyst Fibros. 2017 Mar 2. pii: S1569-1993(17)30074-7. 
Keywords
Burkholderia cepacia, Inhaled tobramycin
Theme
CFTR/Basic Science
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Scientific Abstract
Title: Peripheral muscle abnormalities in cystic fibrosis: etiology, clinical implications and response to therapeutic interventions
Authors
Mathieu Gruet, Thierry Troosters, Samuel Verges
References
J Cyst Fibros. 2017 Mar 2. pii: S1569-1993(17)30032-2.
Keywords
Aerobic function, CFTR, Exercise interventions, Muscle function, Muscle metabolism, nutritional status
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Scientific Abstract