July 2017
Title: Poor recovery from a pulmonary exacerbation does not lead to accelerated FEV1 decline
Authors Don B. Sanders, Zhanhai Li,c, Qianqian Zhao, Philip Farrell
References J Cyst Fibros. 2017 Jul 29. pii: S1569-1993(17)30818-4. doi: 10.1016/j.jcf.2017.07.003
Keywords Epidemiology, FEV1, Pulmonary exacerbation
July 2017
Title: Air pollution exposure is associated with MRSA acquisition in young U.S. children with cystic fibrosis
Authors Psoter KJ, DeRoos AJ, Wakefield J, Mayer J, Rosenfeld M.
References BMC Pulm Med. 2017 Jul 27;17(1):106. doi: 10.1186/s12890-017-0449-8.
Keywords Achromobacter xylosoxidans, Air pollution, Fine particulate matter, MRSA, Staphylococcus aureus, Stenotrophomonas maltophilia
Title: Tracheal diverticula in advanced cystic fibrosis: Prevalence, features, and outcomes after lung transplantation.
Authors Siddhartha G. Kapnadak, Gregory A. Kicska, Kathleen A. Ramos, Desiree A. Marshall, Tamara Y. Carroll, Sudhakar N. Pipavath, Michael S. Mulligan, Christopher H. Goss, Moira L. Aitken
References J Cyst Fibros. 2017 Jul 27. pii: S1569-1993(17)30830-5. doi: 10.1016/j.jcf.2017.07.015.
Keywords Lung diseases, Lung transplantation, Pseudomonas infections, Tomography, x-ray computed, Tracheal diverticulum
July 2017
Title: Age-related levels of fecal M2-pyruvate kinase in children with cystic fibrosis and healthy children 0 to 10years old.
Authors Garg M, Leach ST, Pang T, Needham B, Coffey MJ, Katz T, Strachan R, Widger J, Field P, Belessis Y, Chuang S, Day AS, Jaffe A, Ooi CY.
References J Cyst Fibros. 2017 Jul 25. pii: S1569-1993(17)30826-3. doi: 10.1016/j.jcf.2017.07.011.
Keywords Biomarkers, Gastrointestinal inflammation, Intestinal neoplasms, Pediatrics, Pyruvate kinase
July 2017
Title: Increased Prevalence of Colonic Adenomas in Patients with Cystic Fibrosis
Authors Hegagi M, Aaron SD, James P, Goel R, Chatterjee A
References J Cyst Fibros. 2017 Jul 22. pii: S1569-1993(17)30824-X. doi: 10.1016/j.jcf.2017.07.009
Keywords adenoma, colonoscopy
July 2017
Title: Bile salt stimulated lipase, Cystic fibrosis, Enzyme therapy, NMR spectroscopy, Pancreatic insufficiency, Titrimetric enzyme assay
Authors Elena Venuti, Dmitry Shishmarev, Philip W. Kuchel, Shoma Dutt, Caron S. Blumenthal, and Kevin J. Gaskin1
References J Cyst Fibros. 2017 Jul 21. pii: S1569-1993(17)30820-2. doi: 10.1016/j.jcf.2017.07.005
Keywords Bile salt stimulated lipase, Enzyme therapy, NMR spectroscopy, pancreatic insufficiency, Titrimetric enzyme assay
Title: Analytical and Biological Variation in Repeated Sweat Chloride Concentrations in Clinical Trials for CFTR Modulator Therapy
Authors VA LeGrys, TC Moon, J Laux, MJ Rock, F Accurso
References J Cyst Fibros. 2017 Jul 21. pii: S1569-1993(17)30823-8. doi: 10.1016/j.jcf.2017.07.008
Keywords Analytical variation, Biological variation, Index of individuality, Reference change value, sweat chloride
July 2017
Title: Differences between WHO AND CDC early growth measurements in the assessment of Cystic Fibrosis clinical outcomes.
Authors Usatin D, Yen EH, McDonald C, Asfour F, Pohl J, Robson J
References J Cyst Fibros. 2017 Jul;16(4):503-509. doi: 10.1016/j.jcf.2016.12.001
Keywords Forced Expiratory Volume in 1second percent predicted (FEV1(pp)), Growth standards, Survival, Weight-for-length (WFL)
Title: Outcomes associated with antibiotic regimens for treatment of Mycobacterium abscessus in cystic fibrosis patients.
Authors DaCosta A, Jordan CL, Giddings O, Lin FC, Gilligan P, Esther CR Jr
References J Cyst Fibros. 2017 Jul;16(4):483-487. doi: 10.1016/j.jcf.2017.04.013. Epub 2017 May 8
Keywords Mycobacterium abscessus, Nontuberculous mycobacterium
Title: Macronutrient Intake in Preschoolers with Cystic Fibrosis and the Relationship between Macronutrients and Growth
Authors Stephanie S. Filigno, Shannon M. Robson, Rhonda D. Szczesniak, Leigh A. Chamberlin, Meredith A. Baker, Stephanie M. Sullivan, John Kroner, Scott W. Powers
References J Cyst Fibros. 2017 Jul;16(4):519-524. doi: 10.1016/j.jcf.2017.01.010. Epub 2017 Feb 6.
Keywords Behavioral intervention, Children, Nutrition
Title: Worsening anxiety and depression after initiation of lumacaftor/ivacaftor combination therapy in adolescent females with cystic fibrosis
Authors Cameron J. McKinzie, Jennifer L. Goralski, Terry L. Noah, George Z. Retsch-Bogart, Mary Beth Prieur
References J Cyst Fibros. 2017 Jul;16(4):525-527. doi: 10.1016/j.jcf.2017.05.008. Epub 2017 Jun 8.
July 2017
Title: Lower exhaled nitric oxide in infants with Cystic Fibrosis compared to healthy controls
Authors Insa Korten, Margot Liechti, Florian Singer, Gaudenz Hafen, Isabelle Rochat, Pinelopi Anagnostopoulou, Dominik Müller-Suter, Jakob Usemann, Alexander Moeller, Urs Frey, Philipp Latzin, Carmen Casaulta for the SCILD7 and BILD study group
July 2017
Title: Detection of CFTR Function and Modulation in Primary Human Nasal Cell Spheroids
Authors John J. Brewington, Erin T. Filbrandt, F. J. LaRosa III, Alicia J. Ostmann, Lauren M. Strecker, Rhonda D. Szczesniak, John P. Clancy
References J Cyst Fibros. 2017 Jul 13. pii: S1569-1993(17)30812-3. doi: 10.1016/j.jcf.2017.06.010.
Keywords CFTR, Modulator, Organoid, Personalized model system
July 2017
Title: Retrospective observational study of French patients with cystic fibrosis and a Gly551Asp-CFTR mutation after 1 and 2 years of treatment with ivacaftor in a real-world setting
Authors Hubert D, Dehillotte C, Munck A, David V, Baek J, Mely L, Dominique S, Ramel S, Danner Boucher I, Lefeuvre S, Reynaud Q, Colomb-Jung V, Bakouboula P, Lemonnier L
References J Cyst Fibros. 2017 Jul 12. pii: S1569-1993(17)30816-0. doi: 10.1016/j.jcf.2017.07.001
Keywords CFTR modulators, Lumacaftor
