With the CF Research News, we aim to bridge the gap between people with CF and the researchers investigating CF and how best to treat those with the condition.
We want to provide access to patients, parents, relatives, friends and caregivers of patients with CF to all scientific work mainly published in the Journal of Cystic Fibrosis (JCF).

All PDF files published hereunder are lay version summaries of work published in the JCF.

July 2016

Title: Ursodeoxycholic acid treatment is associated with improvement of liver stiffness in cystic fibrosis patients.
Authors
van der Feen C, van der Doef HP, van der Ent CK, Houwen RH
References
J Cyst Fibros. 2016 Jul 29. pii: S1569-1993(16)30566-5.
Keywords
Cystic fibrosis liver disease, Fibroscan, Liver stiffness measurement, Ursodeoxycholic acid
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Scientific abstract

July 2016

Title: Hyperpolarized 129Xe for investigation of mild cystic fibrosis lung disease in pediatric patients.
Authors
Thomen RP, Walkup LL, Roach DJ, Cleveland ZI, Clancy JP, Woods JC
References
J Cyst Fibros. 2016 Jul 28. pii: S1569-1993(16)30565-3.
Keywords
Hyperpolarized, MRI, Pediatric
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Scientific abstract

July 2016

Title: Ivacaftor and symptoms of extra-oesophageal reflux in patients with cystic fibrosis and G551D mutation
Authors
Gemma L Zeybel, Jeffrey P Pearson, Amaran Krishnan, Stephen J Bourke, Simon Doe, Alan Anderson, Shoaib Faruqi, Alyn H Morice, Rhys Jones, Mellissa McDonnell, Mujdat Zeybel, Peter W Dettmar, Malcolm Brodlie, Chris Ward
References
J Cyst Fibros. 2016 Jul 27. pii: S1569-1993(16)30561-6
Keywords
CFTR potentiator, G551D, Gastrointestinal, Real life data
Theme
Nutrition/Gastroenterology
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Scientific abstract

July 2016

Title: The Effects of Ivacaftor on CF Fatty Acid Metabolism: An Analysis from the GOAL Study
Authors
Michael Glenn O’Connor, Adam Seegmiller
References
J Cyst Fibros. 2016 Jul 26. pii: S1569-1993(16)30563-X.
Keywords
Fatty acids, Ivacaftor, Prostaglandin E
Theme
Nutrition/Gastroenterology
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Scientific abstract

July 2016

Title: Limitations to providing adult cystic fibrosis care in Europe: Results of a care centre survey
Authors
Susan Madge, Scott C Bell, Pierre- Régis Burgel, Karleen De Rijcke, Francesco Blasi, J. Stuart Elborn
References
J Cyst Fibros. 2016 Jul 25. pii: S1569-1993(16)30558-6
Keywords
Adults, Eastern Europe, Service provision, Western Europe
Theme
Epidemiology/Models of care
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July 2016

Title: A Product of Immunoreactive Trypsinogen and Pancreatitis-Associated Protein as Second Tier Strategy in Cystic Fibrosis Newborn Screening
Authors
Sophia Weidler, Konrad H. Stopsack, Jutta Hammermann, Olaf Sommerburg, Marcus A. Mall, Georg F. Hoffmann, Dirk Kohlmüller, Jürgen G. Okun, Milan Macek Jr., Felix Votava, Veronika Krulišová, Miroslava Balaščaková, Veronika Skalická, Min Ae Lee-Kirsch, Marina Stopsack
References
J Cyst Fibros. 2016 Jul 22. pii: S1569-1993(16)30559-8
Keywords
Cutoff, Immunoreactive trypsinogen, Newborn screening, Pancreatitis-associated protein
Theme
Diagnosis/Screening
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Scientific abstract

July 2016

Title: The Cystic Fibrosis Foundation Patient Registry. Design and Methods of a National Observational Disease Registry
Authors
Knapp EA, Fink AK, Goss CH, Sewall A, Ostrenga J, Dowd C, Elbert A, Petren KM, Marshall BC
References
Ann Am Thorac Soc. 2016 Jul;13(7):1173-9. doi: 10.1513/AnnalsATS.201511-781OC.
Keywords
registries
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Scientific Abstract