All Resources

This page provides filters and search facilities across all types of CF resources contained within the ECFS website.

Additionally, you can visit the specific resource type pages as follows:

More information on CF publications can be found here: Publications

May 2022

Title: How does chronic rhinosinusitis impact quality of life of cystic fibrosis patients?
Authors
Daniel J Lee, Jenna Sykes, Katherine Griffin, Christopher W Noel, Brian Hyung, Kamalprit Chokar, Christopher Mkl Yao, Elizabeth Tullis, John M Lee
References
J Cyst Fibros. 2022 May 31;S1569-1993(22)00146-1. doi: 10.1016/j.jcf.2022.05.008.
 
Keywords
Chronic rhinosinusitis, Epidemiology, Prevalence, Quality of life
Theme
Care of patients with CF, Pulmonology
PDF icon CF Research News Article
Scientific Abstract

May 2022

Title: Long-term health effects of real-world use of ivacaftor by people with cystic fibrosis who have non-G551D-CFTR gating mutations
Authors
Nicholas J. Simmonds, C. Kors van der Ent, Carla Colombo, Nils Kinnman, Cynthia DeSouza, Teja Thorat, Marci L. Chew, Keval Chandarana, Carlo Castellani
References
J Cyst Fibros. 2022 May 22;S1569-1993(22)00141-2. doi: 10.1016/j.jcf.2022.05.007.
Keywords
CFTR gating mutation, Healthcare resource utilization, Ivacaftor, Lung function, Real-world experience
Theme
Care of patients with CF, Pulmonology
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Scientific Abstract

May 2022

Title: Evaluation of a biochemical cystic fibrosis newborn screening protocol using IRT and PAP
Authors
Olaf Sommerburg, Mirjam Stahl, Susanne Hämmerling, Gwendolyn Gramer, Martina U Muckenthaler, Jürgen Okun, Dirk Kohlmüller, Margit Happich, Andreas E Kulozik, Marcus A Mall, Georg F Hoffmann
References
J Cyst Fibros. 2022 May;21(3):422-433. doi: 10.1016/j.jcf.2021.10.007. Epub 2021 Nov 9.
 
Keywords
Biochemical screening, genetic testing, Immuno reactive trypsinogene (IRT), Newborn screening (NBS), Pancreatitis associated protein (PAP)
Theme
False-positives, Newborn screening
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Scientific Abstract

May 2022

Title: The Association of Area Deprivation and State Child Health with Respiratory Outcomes of Pediatric Patients with Cystic Fibrosis in the United States
Authors
Gabriela Oates, Sarah Rutland, Lucia Juarez, Annabelle Friedman, Michael S Schechter
References
Pediatr Pulmonol. 2021 May;56(5):883-890. doi: 10.1002/ppul.25192. Epub 2020 Dec 14.
Keywords
social dimensions of pulmonary medicine
Theme
Care of patients with CF, Psychosocial, Pulmonology
PDF icon CF Research News Article
Scientific Abstract
Title: Adjusting the dose of triple therapy (Elexacaftor/Tezacaftor/Ivacaftor) to reduce mental health side effects
Authors
Spoletini G, Gillgrass L, Pollard K, Shaw N, Williams E, Etherington C, Clifton Ij, Peckham Dg
References
J Cyst Fibros. 2022 May 15;S1569-1993(22)00111-4. doi: 10.1016/j.jcf.2022.05.001. Online ahead of print.
 
Theme
Care of patients with CF, Psychosocial, Pulmonology
PDF icon CF Research News Article
Scientific Abstract

May 2022

Title: A rapid sweat test for chloride and bicarbonate to confirm the diagnosis of infants with cystic fibrosis
Authors
Stellena Mathiaparanam, Adriana Nori de Macedo, Biban Gill, Katherine Keenan, Tanja Gonska, Linda Pedder, Stephen Hill, Philip Britz-McKibbin
References
J Cyst Fibros. 2022 May 13;S1569-1993(22)00112-6. doi: 10.1016/j.jcf.2022.05.004.
Keywords
Bicarbonate, Capillary electrophoresis, Chloride, Confirmatory testing, Coulometric titration, Newborn screening, pilocarpine iontophoresis, Sweat
Theme
Diagnosis/Screening
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Scientific Abstract

May 2022

Title: Breakdown of lung proteins causes structural damage in cystic fibrosis lungs
Authors
Meghan R Pinezich, Manuel A Tamargo, Sharon Fleischer, Jonathan A Reimer, Maria R Hudock, Ahmed E Hozain, Sarah R Kaslow, Yuliya Tipograf, Rajesh Kumar Soni, Olimpia P Gavaudan, Brandon A Guenthart, Charles C Marboe, Matthew Bacchetta, John D O'Neill, N V
References
J Cyst Fibros. 2022 May 4;S1569-1993(22)00106-0. doi: 10.1016/j.jcf.2022.04.016.
Keywords
Basement membrane, Biomarkers, Extracellular matrix, Lung proteases
Theme
Imaging, Lung Disease and Infection
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Scientific Abstract
Title: Patients with F508del/5T;TG12 CFTR genotype
Authors
Antonella Tosco, Alice Castaldo, Carla Colombo, Laura Claut, Vincenzo Carnovale, Paola Iacotucci, Marco Lucarelli, Giuseppe Cimino, Benedetta Fabrizzi, Nicole Caporelli, Fabio Majo, Fabiana Ciciriello, Rita Padoan, Piercarlo Poli,, Giovanni Taccetti, Claudia Centrone, Rosaria Casciaro, Carlo Castellani, Donatello Salvatore, Carmela Colangelo, Paolo Bonomi, Giuseppe Castaldo, Vito Terlizzi
References
J Cyst Fibros. 2022 May 4;S1569-1993(22)00109-6. doi: 10.1016/j.jcf.2022.04.020.
Keywords
CBAVD, CFTR-RD, CRMS/CFSPID, FEV1, Outcomes, Spirometry
Theme
Care of patients with CF, Diagnosis/Screening
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Scientific Abstract

May 2022

Title: Respiratory viral infections and chest CT (computer tomography scan) changes in infants with CF
Authors
Don B Sanders, Ashley R Deschamp, Joseph E Hatch, James E Slaven, Netsanet Gebregziabher, Mariette Kemner-van de Corput, Harm A W M Tiddens, Tim Rosenow, Gregory A Storch, Graham L Hall, Stephen M Stick, Sarath Ranganathan, Thomas W Ferkol, Stephanie D D
References
J Cyst Fibros. 2022 May 3;S1569-1993(22)00103-5. doi: 10.1016/j.jcf.2022.04.014.
Keywords
Chest computed tomography, Newborn screening, Respiratory infection, Viruses
Theme
Care of patients with CF, Imaging, Lung Disease and Infection
PDF icon CF Research News Article
Scientific Abstract