All Resources

This page provides filters and search facilities across all types of CF resources contained within the ECFS website.

Additionally, you can visit the specific resource type pages as follows:

More information on CF publications can be found here: Publications

December 2021

Title: Treatment of Idiopathic Chronic Pancreatitis (ICP) with ivacaftor in a Cystic Fibrosis (CF) carrier who also had a second inherited risk factor for pancreatitis called Methylmalonic Acidemia

Authors

Tin-Yun Tang, Vincent B Cruz, Laura L Konczal

References

J Cyst Fibros. 2021 Dec 30;S1569-1993(21)02174-3. doi: 10.1016/j.jcf.2021.12.013.

Theme

Nutrition/Gastroenterology

CF Research News Article

Scientific Abstract

December 2021

Title: Antisense oligonucleotide as a novel therapy for people with CF affected by the W1282X mutation

Authors

Yifat S. Oren, Ofra Avizur-Barchad, Efrat Ozeri-Galai, Renana Elgrabli, Meital R. Schirelman, Tehilla Blinder, Chava D. Stampfer, Merav Ordan, Onofrio Laselva, Malena Cohen-Cymberknoh, Eitan Kerem, Christine E Bear, Batsheva Kerem

References

J Cyst Fibros. 2021 Dec 28;S1569-1993(21)02172-X. doi: 10.1016/j.jcf.2021.12.012.

Keywords

Antisense oligonucleotides, drug development, Exon skipping

Theme

CFTR/Basic Science

CF Research News Article

Scientific Abstract

Title: Is Body Mass Index Associated with Better Lung Function in Children with Pancreatic-Sufficient Cystic Fibrosis?

Authors

Ankitha Madde, William Okoniewski, Don B Sanders, Clement L Ren, Daniel J Weiner, Erick Forno

References

J Cyst Fibros. 2021 Dec 28;S1569-1993(21)02173-1. doi: 10.1016/j.jcf.2021.12.014.

Keywords

BMI, FEV1, Lung function, Nutrition, pancreatic insufficiency

Theme

Care of patients with CF, Lung Disease and Infection, Nutrition/Gastroenterology

CF Research News Article

Scientific Abstract

December 2021

Title: Looking at lung disease over time in young children with CF

Authors

Alan S Brody, Rui Huang, Bin Zhang, Frederick R Long, Scott W Powers

References

J Cyst Fibros. 2021 Dec 24;S1569-1993(21)02168-8. doi: 10.1016/j.jcf.2021.12.009.

Theme

Imaging, Lung Disease and Infection, Pulmonology

Scientific Abstract

Title: Looking at lung disease over time in young children with CF

Authors

Alan S Brody, Rui Huang, Bin Zhang, Frederick R Long, Scott W Powers

References

J Cyst Fibros. 2021 Dec 24;S1569-1993(21)02168-8. doi: 10.1016/j.jcf.2021.12.009.

Keywords

Bronchiectasis, Child, Computed tomography, Outcome measures, Pulmonary cystic fibrosis, Preschool

CF Research News Article

Scientific Abstract

Title: Results of a clinical evaluation of the safety and efficacy of the therapeutic drug candidate Roscovitine in people with cystic fibrosis.

Authors

Laurent Meijer, Geneviève Hery-Arnaud, Cyril Leven, Emmanuel Nowak, Sophie Hillion, Yves Renaudineau, Isabelle Durieu, Raphaël Chiron, Anne Prevotat, Isabelle Fajac, Dominique Hubert, Marlène Murris-Espin, Sandrine Huge, Isabelle Danner-Boucher, , Bruno Ravoninjatovo, Sylvie Leroy, Julie Macey, Thierry Urban, Gilles Rault, Dominique Mottier, Rozenn Le Berre

References

J Cyst Fibros. 2021 Dec 24;S1569-1993(21)02167-6. doi: 10.1016/j.jcf.2021.10.013.

Keywords

Clinical trial, Inflammation, Pseudomonas aeruginosa, Roscovitine, Seliciclib

Theme

Lung Disease and Infection, Microbiology

CF Research News Article

Scientific Abstract

December 2021

Title: A simple blood test to detect how severe liver disease is in children with CF

Authors

Diego A Calvopina, Peter J Lewindon, Louise E Ramm, Charlton Noble, Gunter F Hartel, Daniel H Leung, Grant A Ramm

References

J Cyst Fibros. 2021 Dec 22;S1569-1993(21)02171-8. doi: 10.1016/j.jcf.2021.10.014.

Keywords

Children, cystic fibrosis-associated liver disease, Liver fibrosis, multilobular cirrhosis, Serum biomarker

Theme

Biomarkers, Nutrition/Gastroenterology

CF Research News Article

Scientific Abstract

December 2021

Title: Advanced but not mild liver disease is a predictor of decreased survival in children with cystic fibrosis, with far greater impact in females: A 27-year real-life cohort study

Authors

Marilisa Baldissera, Peter J Lewindon, Louise E Ramm, Gunter F Hartel, Rita Mattiello, Grant A Ramm

References

J Cyst Fibros. 2021 Dec 20;S1569-1993(21)02156-1. doi: 10.1016/j.jcf.2021.11.015.

Keywords

Children, Cohort studies, liver disease, mortality

Theme

Diabetes, Nutrition/Gastroenterology

CF Research News Article

Scientific Abstract

Title: Improving conclusions after newborn screening for babies with no clear diagnosis

Authors

Aurelie Hatton, Anne Bergougnoux, Katarzyna Zybert, Benoit Chevalier, Myriam Mesbahi, Jean Pierre Altéri, Katarzyna Walicka-Serzysko, Magdalena Postek, Magali Taulan-Cadars, Aleksander Edelman, Alexandre Hinzpeter, Mireille Claustres, Emmanuelle Girodon, , Caroline Raynal, Isabelle Sermet-Gaudelus, Dorota Sands

References

J Cyst Fibros. 2021 Dec 20;S1569-1993(21)02169-X. doi: 10.1016/j.jcf.2021.12.010

Keywords

CFTR, Functional tests, neonatal screening

Theme

Newborn screening

CF Research News Article

Scientific Abstract

December 2021

Title: Measuring inflammation in blood during exacerbation treatment

Authors

D R VanDevanter, S L Heltshe, M Skalland, N E West, D B Sanders, C H Goss, P A Flume

References

J Cyst Fibros. 2021 Dec 18;S1569-1993(21)02160-3. doi: 10.1016/j.jcf.2021.12.003.

Keywords

C-reactive protein, Clinical response, Pulmonary exacerbation

Theme

Biomarkers, Care of patients with CF, Lung Disease and Infection, Pulmonology

CF Research News Article

Scientific Abstract

December 2021

Title: Magnetic resonance imaging of the gastrointestinal tract shows reduced small bowel motility and altered chyme in cystic fibrosis compared to controls

Authors

Neele S Dellschaft, Christabella Ng, Caroline Hoad, Luca Marciani, Robin Spiller, Iain Stewart, Alex Menys, Helen Barr, Penny A Gowland, Giles Major, Alan R Smyth

References

J Cyst Fibros. 2021 Dec 15;S1569-1993(21)02166-4. doi: 10.1016/j.jcf.2021.12.007.

Keywords

Gastrointestinal tract, Magnetic Resonance Imaging

Theme

Imaging, Nutrition/Gastroenterology

CF Research News Article

Scientific Abstract

Title: Nutritional health and lung transplantation in cystic fibrosis

Authors

Ann L. Jennerich, Joseph B. Pryor, Travis Y. Hee Wai, Siddhartha G. Kapnadak, Moira L. Aitken, Christopher H. Goss, Kathleen J. Ramos

References

J Cyst Fibros. 2021 Dec 15;S1569-1993(21)02159-7. doi: 10.1016/j.jcf.2021.12.001.

Keywords

Lung diseases, Lung transplantation, nutritional status, Survival analysis

Theme

Care of patients with CF, Nutrition/Gastroenterology, Transplantation

CF Research News Article

Scientific Abstract

December 2021

Title: Two cases of heart attacks in young women with cystic fibrosis and diabetes

Authors

Sirisha Reddy Thambuluru, Sayyad Kyazimzade, Katherine A Despotes, Deepa Kirk, Jennifer L Goralski

References

J Cyst Fibros. 2021 Dec 12;S1569-1993(21)02154-8. doi: 10.1016/j.jcf.2021.11.013.

Keywords

Coronary artery disease, Cystic fibrosis related diabetes, Dyslipidemia, myocardial infarction

Theme

Diabetes

CF Research News Article

Scientific Abstract

December 2021

Title: Bacterial communities relate to gut function and transit in the cystic fibrosis gut

Authors

Ryan Marsh, Helen Gavillet, Liam Hanson, Christabella Ng, Mandisa Mitchell-Whyte, Giles Major, Alan R Smyth, Damian Rivett, Christopher van der Gast

References

J Cyst Fibros. 2021 Dec 8;S1569-1993(21)02155-X. doi: 10.1016/j.jcf.2021.11.014.

Keywords

Antibiotics, Dysbiosis, Gut microbiome, Gut microbiota, Intestinal physiology, MRI

Theme

Imaging, Microbiology, Nutrition/Gastroenterology

CF Research News Article

Scientific Abstract

December 2021

Title: A new path for CF clinical trials through the use of historical controls

Authors

Amalia S Magaret, Mark Warden, Noah Simon, Sonya Heltshe, George Z Retsch-Bogart, Bonnie W Ramsey, Nicole Mayer-Hamblett

References

J Cyst Fibros. 2021 Dec 5;S1569-1993(21)02138-X. doi: 10.1016/j.jcf.2021.11.007.

Keywords

Clinical development, External controls, Pulmonary exacerbations, Real world data

Theme

Clinical Trials, Epidemiology/Models of care

CF Research News Article

Scientific Abstract