March 2023
Title: How the discovery of new white blood cell subtypes can improve our understanding of lung disease progression in adult CF patients?
Authors Murru Andréa, Vadeboncoeur Nathalie, Therrien Andrée-Anne, Coderre Lise, Vaillancourt Myriam, Labrecque Marie-Michèle, Berthiaume Yves, Bouvet Guillaume, Adam Damien, Brochiero Emmanuelle, Lesage Sylvie, Flamand Nicolas, Bilodeau Lara, Maria J Fernandes
References J Cyst Fibros. 2023 Mar 25;S1569-1993(23)00072-3. doi: 10.1016/j.jcf.2023.03.009.
Keywords Lung function, Neutrophil, Neutrophil sub-populations, Pulmonary exacerbation
Theme CFTR/Basic Science, Immunology, Lung Disease and Infection
March 2023
Title: Autoimmunity (a condition where the body's immune system mistakes its own healthy tissues as foreign and attacks them) in People with Cystic Fibrosis
Authors Christina Chadwick, Heather Lehman, Shelby Luebbert, Rabheh Abdul-Aziz, Drucy Borowitz
References J Cyst Fibros. 2023 Mar 23;S1569-1993(23)00071-1. doi: 10.1016/j.jcf.2023.03.007.
Keywords Arthritis, Autoimmune disease, autoimmunity, Celiac disease, Crohn's disease, Vasculitis
Title: Cervical mucus quality in females with and without cystic fibrosis
Authors Andrea H Roe, Nathanael Koelper, Arden McAllister, Kurt T Barnhart, Courtney A Schreiber, Denis Hadjiliadis
References J Cyst Fibros. 2023 Mar 23;S1569-1993(23)00077-2. doi: 10.1016/j.jcf.2023.03.013.
Theme Endocrinology, Pregnancy with CF
Title: What do dietitians, doctors and physiotherapists think about the management of people with CF who are living with overweight and obesity?
Authors Joanna E Snowball, William G Flight, Laura Heath, Dimitrios A Koutoukidis
References J Cyst Fibros. 2023 Mar 23;S1569-1993(23)00075-9. doi: 10.1016/j.jcf.2023.03.011.
Keywords CFTR modulators, obesity, Overweight, Qualitative interviews, Weight management
Theme Care of patients with CF, Nutrition/Gastroenterology
March 2023
Title: Year in Review (2022): Modulators and COVID-19: the story does on
Authors Stefanie Dillenhoefer, Dorothy Grogono, Ana Morales-Tirado
References J Cyst Fibros. 2023 Mar;22(2):188-192. doi: 10.1016/j.jcf.2023.03.001. Epub 2023 Mar 6.
Theme Bone health, Care of patients with CF, Imaging, Lung Disease and Infection, Nutrition/Gastroenterology, Psychosocial, Pulmonology, Transplantation
Title: Effects of elexacaftor/tezacaftor/ivacaftor on liver tests in cystic fibrosis
Authors Daniel H Tewkesbury, Varinder Athwal, Rowland J Bright-Thomas, Andrew M Jones, Peter J Barry
References J Cyst Fibros. 2023 Mar;22(2):256-262. doi: 10.1016/j.jcf.2023.01.007. Epub 2023 Jan 19.
Theme CFTR/Basic Science, Nutrition/Gastroenterology
Title: Sharing decisions about family goals: A study exploring women’s experiences and needs for support.
Authors Denitza Williams, Oluwaseun B Esan, Daniela K Schlüter, David Taylor-Robinson, Shantini Paranjothy, Jamie Duckers, Natalie Goodchild, Rhiannon Phillips
References J Cyst Fibros. 2023 Mar;22(2):207-216. doi: 10.1016/j.jcf.2023.02.007. Epub 2023 Feb 28.
Keywords Mixed-method, Person-centred care, Pre-conception, Reproductive goals, Shared decision-making
Theme Care of patients with CF, Pregnancy with CF, Psychosocial
Title: An overview of CFTR modulators and pancreas function
Authors Mitchell L Ramsey, Susan S Li, Luis F Lara, Yevgeniya Gokun, Venkata S Akshintala, Darwin L Conwell, John Heintz, Stephen E Kirkby, Karen S McCoy, Georgios I Papachristou, Alpa Patel, Vikesh K Singh, Phil A Hart
References J Cyst Fibros. 2023 Mar;22(2):193-200. doi: 10.1016/j.jcf.2022.08.008.
Keywords Acute pancreatitis, Exocrine pancreatic insufficiency, Fecal elastase, Lipase, Trypsin
Theme Care of patients with CF, Nutrition/Gastroenterology
Title: Two-year follow-up results from an ongoing study on the safety and effectiveness of elexacaftor/tezacaftor/ivacaftor when used in real-world settings by people with cystic fibrosis
Authors Julie K Bower, Nataliya Volkova, Neil Ahluwalia, Gurvaneet Sahota, Fengjuan Xuan, Anna Chin, Tanya G Weinstock, Josh Ostrenga, Alexander Elbert
References J Cyst Fibros. 2023 Mar 22;S1569-1993(23)00066-8. doi: 10.1016/j.jcf.2023.03.002.
Keywords Elexacaftor, Ivacaftor, Real-world, registry, Tezacaftor
Theme Clinical Trials, Pulmonology
March 2023
Title: A letter in response to the recently published article entitled “Effect of elexacaftor/tezacaftor/ivacaftor on annual rate of lung function decline in people with cystic fibrosis
Authors Zhe Hui Hoo, Lana Yh Lai, Robert D Sandler, Tracey E Daniels, Sophie Dawson, Marlene Hutchings, Martin J Wildman
References J Cyst Fibros. 2023 Mar 20;S1569-1993(23)00076-0. doi: 10.1016/j.jcf.2023.03.012.
March 2023
Title: Postage of sputum samples from home to clinic can be used for microbiology surveillance
Authors Lauren Hatfield, Brooke Bianco, Helen Gavillet, Phillipa Burns, Damian Rivett, Matthew Smith, Andrew Jones, Christopher van der Gast, Alexander Horsley
References J Cyst Fibros. 2023 Mar 16;S1569-1993(23)00073-5. doi: 10.1016/j.jcf.2023.03.008.
Keywords Airway infection, microbiology, Remote monitoring, Sputum, Telemedicine
March 2023
Title: Understanding Medical Traumatic Stress in Cystic Fibrosis from the Viewpoints of Patients, Families, and Providers
Authors Addison A Cuneo, Simon Outram, Meghan L Marsac, Siena Vendlinski, Melvin B Heyman, Ngoc Ly, Emily von Scheven, Emily R Perito
References J Cyst Fibros. 2023 Mar 14;S1569-1993(22)01427-8. doi: 10.1016/j.jcf.2022.12.008.
Keywords Chronic illness, Iatrogenic trauma, Medical traumatic stress, Trauma-informed medical care
March 2023
Title: Association between nebulizer therapies adherence and visit-to-visit variability of lung function in patients with cystic fibrosis
Authors David Drummond, Pauline Whelan, Matthew Sperrin
References J Cyst Fibros. 2023 Mar 13;S1569-1993(23)00070-X. doi: 10.1016/j.jcf.2023.03.006.
Keywords Adherence, Forced expiratory volume in one second, Lung function tests
March 2023
Title: How does telehealth impact the health of children with cystic fibrosis
Authors Kristene Rimbaldo, Katherine B Frayman, Shivanthan Shanthikumar
References J Cyst Fibros. 2023 Mar 6;S1569-1993(23)00068-1. doi: 10.1016/j.jcf.2023.03.003.
Keywords COVID-19, Spirometry, Telehealth.
Theme Care of patients with CF, Epidemiology/Models of care
March 2023
Title: Models of Cystic Fibrosis care after lung transplant
Authors Edward McKone, Kathleen Ramos, Cecilia Chaparro, Joshua Blatter, Ramsey Hachem, Michael Anstead, Fanny Vlahos, Abby Thaxton, Sarah Hempstead, Thomas Daniels, Michelle Murray, Amparo Sole, Robin Vos, Erin Tallarico, Albert Faro, Joseph M Pilewski
References J Cyst Fibros. 2023 Mar 5;S1569-1993(23)00059-0. doi: 10.1016/j.jcf.2023.02.011.
Theme Care of patients with CF, Epidemiology/Models of care, Transplantation
