November 2019
Title: Antimicrobial Susceptibility Testing in Cystic Fibrosis: A Delphi approach to defining best practices
Authors Edith Zemanick, Pierre–Régis Burgel, Giovanni Taccetti, Alison Holmes, Felix Ratjen, Catherine A Byrnes, Valerie J. Waters, Scott C. Bell, Donald R. VanDevanter, J. Stuart Elborn, Patrick A. Flume, on behalf of the Antimicrobial Resistance International Working Group in Cystic Fibrosis
References J Cyst Fibros. 2019 Oct 31. pii: S1569-1993(19)30919-1. doi: 10.1016/j.jcf.2019.10.006.
November 2019
Title: Ivacaftor in Cystic Fibrosis With Residual Function: Lung Function Results From an N-of-1 Study
Authors Jerry A. Nick, Connie St. Clair, Marion C. Jones, Lan Lan, Mark Higgins
References J Cyst Fibros. 2019 Nov 26. pii: S1569-1993(19)30897-5. doi: 10.1016/j.jcf.2019.09.013.
Keywords Bayesian hierarchical model, Cystic fibrosis transmembrane conductance regulator, forced expiratory volume, Ivacaftor, Residual CFTR function
November 2019
Title: Integrating the multiple breath washout test into international multicentre trials.
Authors Saunders C, Jensen R, Robinson PD, Stanojevic S, Klingel M, Short C, Davies JC, Ratjen F
References J Cyst Fibros. 2019 Nov 23. pii: S1569-1993(19)30968-3. doi: 10.1016/j.jcf.2019.11.006.
Keywords Multiple breath washout, MBW, Clinical trial endpoint, Lung clearance index, LCI
November 2019
Title: Answering the call to address cystic fibrosis treatment burden in the era of highly effective CFTR modulator therapy
Authors Alex H. Gifford, Nicole Mayer-Hamblett, Kelsie Pearson, David P. Nichols
References J Cyst Fibros 2019 Nov 21 - DOI: 10.1016/j.jcf.2019.11.007
Keywords Modulator, Survey, Treatment burden, Withdrawal study.
Title: Streptococcus pseudopneumoniae, an opportunistic pathogen in patients with cystic fibrosis
Authors Chloé Dupont, Anne-Laure Michon, Marion Normandin, Guillaume Salom, Marie Latypov, Raphaël Chiron, Hélène Marchandin
References J Cyst Fibros. 2019 Nov 20. pii: S1569-1993(19)30966-X. doi: 10.1016/j.jcf.2019.11.004.
Keywords Exacerbation, Identification, Opportunistic pathogen, Resistance, Streptococcus pseudopneumoniae
November 2019
Title: Clustered randomized controlled trial of a clinic-based problem-solving intervention to improve adherence in adolescents with cystic fibrosis
Authors Alexandra L Quittner, Michelle N Eakin, Adrianne N Alpern, Alana K Ridge, Katherine A McLean, Andrew Bilderback, Kristen K Criado, Shang-En Chung, Kristin A Riekert
References J Cyst Fibros. 2019 Nov;18(6):879-885. doi: 10.1016/j.jcf.2019.05.004. Epub 2019 May 15
Keywords Adherence, Adolescents, Education, Problem-solving
Title: Lavage lipidomics signatures in children with cystic fibrosis and protracted bacterial bronchitis
Authors Elias Seidl, Hannah Kiermeier, Gerhard Liebisch, Manfred Ballmann, Sebastian Hesse, Karl Paul-Buck, Felix Ratjen, Ernst Rietschel, Matthias Griese
References J Cyst Fibros. 2019 Nov;18(6):790-795. doi: 10.1016/j.jcf.2019.04.012. Epub 2019 Apr 25.
Keywords Bronchoalveolar lavage, Children, infants, Lipids
Title: The role of endothelial cells in cystic fibrosis
Authors Declercq, M; Treps, L; Carmeliet, P, Witters, P.
References J Cyst Fibros. 2019 Nov;18(6):752-761. doi: 10.1016/j.jcf.2019.07.005
Keywords Angiogenesis, Coagulation, Endothelial barrier, Endothelial cells, Inflammation, Vascular tone
November 2019
Title: Can Exercise Replace Airway Clearance Techniques in Cystic Fibrosis? A Survey of Patients and Healthcare Professionals
Authors N J Rowbotham, S J Smith, G Davies, T Daniels, Z C Elliott, K Gathercole, O C Rayner, A R Smyth
References J Cyst Fibros 2019 Nov 15 - DOI: 10.1016/j.jcf.2019.10.026
Keywords Airway clearance techniques, Co-production, Exercise, Priority setting
November 2019
Title: Characterising burden of treatment in cystic fibrosis to identify priority areas for clinical trials
Authors Gwyneth Davies, Nicola J Rowbotham, Sherie Smith, Zoe C Elliot, Katie Gathercole, Oli Rayner, Paul A Leighton, Sophie Herbert, Alistair JA Duff, Suja Chandran, Tracey Daniels, Edward F Nash, Alan R Smyth
References J Cyst Fibros. 2019 Nov 14. pii: S1569-1993(19)30961-0. doi: 10.1016/j.jcf.2019.10.025
Keywords Clinical trial, Co-production, Priority setting, Treatment burden
November 2019
Title: Prevalence and factors associated with overweight and obesity in adults with cystic fibrosis: A single-center analysis
Authors Harindhanavudhi T, Wang Q, Dunitz J, Moran A, Moheet A
References J Cyst Fibros. 2019 Nov 11. pii: S1569-1993(19)30922-1. doi: 10.1016/j.jcf.2019.10.004.
Keywords obesity, Prevalence
November 2019
Title: Regional differences in infection and structural lung disease in infants and young children with cystic fibrosis
Authors Regional differences in infection and structural lung disease in infants and young children with cystic fibrosis. Carzino R, Frayman KB, King L, Vidmar S, Ranganathan S; AREST CF.
References J Cyst Fibros. 2019 Nov 6. pii: S1569-1993(19)30933-6. doi: 10.1016/j.jcf.2019.10.018.
Keywords Bronchiectasis, Bronchoalveolar lavage, Chest computed tomography, Pro-inflammatory microbes, Right middle lobe and lingula
November 2019
Title: Insights into the variability of Nasal Potential Difference, a biomarker of CFTR activity
Authors Spyridoula Kyrilli, Theophraste Henry, Michael Wilschanski, Isabelle Fajac, Jane C Davies, Jean-Philippe Jais, Isabelle Sermet-Gaudelus
References J Cyst Fibros. 2019 Nov 4. pii: S1569-1993(19)30899-9. doi: 10.1016/j.jcf.2019.09.015.
Keywords Biomarker, Nasal potential difference
November 2019
Title: The implications of dysglycaemia on aerobic exercise and ventilatory function in cystic fibrosis
Authors Adam J. Causer, Janis K. Shute, Michael H. Cummings, Anthony I. Shepherd, Samuel R. Wallbanks, Mark I. Allenby, Irantzu Arregui-Fresneda, Victoria Bright, Mary P. Carroll, Gary Connett, Thomas Daniels, Tom Meredith, and Zoe L. Saynor
References J Cyst Fibros . 2019 Nov 2;S1569-1993(19)30895-1. doi: 10.1016/j.jcf.2019.09.014.
Keywords Cardiorespiratory fitness, Cystic fibrosis-related diabetes, Maximal oxygen uptake, Respiratory disease
