All Resources

This page provides filters and search facilities across all types of CF resources contained within the ECFS website.

Additionally, you can visit the specific resource type pages as follows:

More information on CF publications can be found here: Publications

May 2021

Title: The effect of lumacaftor-ivacaftor on mucus clearance

Authors

Scott H. Donaldson, Beth L. Laube, Peter Mogayzel, Timothy E. Corcoran, Joseph M. Pilewski, Agathe Ceppe, Jihong Wu, Pradeep G. Bhambhvani, Felix Ratjen, Scott D. Sagel, J.P. Clancy, Steven M. Rowe*, William D. Bennett* *on behalf of the PROSPECT Investig

References

J Cyst Fibros. 2021 May 31;S1569-1993(21)00131-4. doi: 10.1016/j.jcf.2021.05.004.

CF Research News Article

Scientific Abstract

May 2021

Title: How frequent is the condition of overweight among patients with cystic fibrosis in Italy?

Authors

Andrea Gramegna, Stefano Aliberti, Martina Contarini, Daniela Savi, Giovanni Sotgiu, Fabio Majo, Laura Saderi, Vincenzina Lucidi, Francesco Amati, Maria Pappalettera, Paolo Palange, Francesco Blasi

References

J Cyst Fibros. 2021 May 27;S1569-1993(21)00129-6. doi: 10.1016/j.jcf.2021.05.002.

Keywords

Adults, Overweight

CF Research News Article

Scientific Abstract

May 2021

Title: Sleep in children and youth with cystic fibrosis: A review of the research

Authors

Jordana McMurray, Kimberley Widger, Anne L Stephenson, Robyn Stremler

References

J Cyst Fibros. 2021 May 23;S1569-1993(21)00132-6. doi: 10.1016/j.jcf.2021.05.005.

CF Research News Article

Scientific Abstract

May 2021

Title: Early signs of Cystic Fibrosis Related Diabetes (CFRD) and low amount of the neuropeptide VIP in ΔF508-CF mice.

Authors

Anna Semaniakou, Frederic Chappe, Younes Anini, Valerie Chappe

References

J Cyst Fibros. 2021 May 22;S1569-1993(21)00133-8. doi: 10.1016/j.jcf.2021.05.006.

Keywords

Cystic fibrosis-related diabetes, Glucagon, Insulin, pancreas, Vasoactive Intestinal Peptide

CF Research News Article

Scientific Abstract

May 2021

Title: Pseudomonas aeruginosa infection, but not CFTR modulator therapy affects circulating regulatory T cells in an adult population with cystic fibrosis

Authors

Dirk Westhölter, Hendrik Beckert, Svenja Straßburg, Matthias Welsner, Sivagurunathan Sutharsan, Christian Taube, Sebastian Reuter

References

J Cyst Fibros. 2021 May 21;S1569-1993(21)00128-4. doi: 10.1016/j.jcf.2021.05.001.

Keywords

CFTR modulator therapy, Pseudomonas aeruginosa, Cytokines, lymphocytes, non-CF bronchiectasis, regulatory T cells

CF Research News Article

Scientific Abstract

May 2021

Title: Early acquisition and conversion of Pseudomonas aeruginosa in Hispanic youth with cystic fibrosis in the United States

Authors

Meghan E McGarry, Chiung-Yu Huang, Dennis W Nielson, Ngoc P Ly

References

J Cyst Fibros. 2021 May;20(3):424-431. doi: 10.1016/j.jcf.2020.10.002. Epub 2020 Nov 5.

Keywords

health disparities, Pseudomonas aeruginosa

Theme

Care of patients with CF, Lung Disease and Infection, Psychosocial

CF Research News Article

Scientific Abstract

Title: Mycobacterium abscessus smooth and rough colony variants in cystic fibrosis patients

Authors

Ana Victoria Gutiérrez, Sophie Alexandra Baron, Feyrouz Sonia Sardi, Jamal Saad, Bérengère Coltey, Martine Reynaud-Gaubert, Michel Drancourt

References

J Cyst Fibros. 2021 May;20(3):421-423. doi: 10.1016/j.jcf.2021.02.002.

Keywords

Mycobacterium abscessus, Rough variant, Smooth variant, Whole genome sequencing

Theme

Care of patients with CF, Microbiology

CF Research News Article

Scientific Abstract

Title: SARS-CoV2 infection in CF patient colonized by Burkholderia cenocepacia

Authors

C Olcese, R Casciaro, D Pirlo, C Debbia, E Castagnola, F Cresta, C Castellani

References

J Cyst Fibros. 2021 May;20(3):e29-e31. doi: 10.1016/j.jcf.2021.03.024. Epub 2021 Apr 8.

Keywords

Burkholderia cepacia, Pulmonary exacerbation, SARS-CoV-2 COVID-19

CF Research News Article

Scientific Abstract

May 2021

Title: Quality of life and health outcomes in children with CF aged 5 years

Authors

Joyce Cheney, Suzanna Vidmar, Nicholas Gailer, Claire Wainwright, Tonia A Douglas, Australasian Cystic Fibrosis Bronchoalveolar Lavage (ACFBAL) study group

References

J Cyst Fibros. 2020 May;19(3):483-491. doi: 10.1016/j.jcf.2020.02.022. Epub 2020 Mar 9.

Keywords

Children, Exacerbations, health-related quality of life, Lung function, Preschool, Pulmonary

CF Research News Article

Scientific Abstract

May 2021

Title: Boosting the rescue of faulty CFTR with phosphate

Authors

Vinciane Saint‐Criq, Yiting Wang, Livia Delpiano, JinHeng Lin, David N. Sheppard, Michael A. Gray

References

J Cyst Fibros. 2021 May 18;S1569-1993(21)00123-5. doi: 10.1016/j.jcf.2021.04.013.

Keywords

Airway epithelia, CFTR correctors, Elexacaftor-tezacaftor-ivacaftor (Trikafta), F508del-CFTR, Phosphate, SLC34A2

CF Research News Article

Scientific Abstract

May 2021

Title: CF Pancreatic Duct Secretions Can Alter Islet Function

Authors

Pavana G. Rotti, Idil A, Evans, Yulong Zhang, Bo Liang, Nathan Cunicelli, Yunxia O’Malley, Andrew W. Norris, Aliye Uc, John F. Engelhardt

References

J Cyst Fibros. 2021 May 17;S1569-1993(21)00120-X. doi: 10.1016/j.jcf.2021.04.010.

Keywords

Cystic fibrosis related diabetes, ductal cells, pancreas, proteome, secretome

CF Research News Article

Scientific Abstract

Title: Focusing on tiny compounds in exhaled breath, can they help detect bacteria in people with cystic fibrosis?

Authors

Renate Kos, Paul Brinkman, Anne H Neerincx, Tamara Paff, Marije G Gerritsen, Ariana Lammers, Aletta D Kraneveld, Harry G M Heijerman, Hettie M Janssens, Jane C Davies, Christof J Majoor, Els J Weersink, Peter J Sterk, Eric G Haarman, Lieuwe D Bos, Anke H Maitland-van der Zee, Amsterdam Mucociliary Clearance Disease (AMCD) Research Group and the Amsterdam UMC Breath Research Group

References

J Cyst Fibros. 2021 May 17;S1569-1993(21)00125-9. doi: 10.1016/j.jcf.2021.04.015.

Keywords

Exhaled biomarkers, Pseudomonas aeruginosa, VOC

CF Research News Article

Scientific Abstract

Title: Aquagenic wrinkling in children under two years of age: Could this be a potential clinical referral tool for cystic fibrosis among non-screened populations?

Authors

Grace R Paul, Shasha Bai, Kenneth Jackson, Karen S McCoy

References

J Cyst Fibros. 2021 May 17;S1569-1993(21)00112-0. doi: 10.1016/j.jcf.2021.04.002.

Keywords

Aquagenic wrinkling, CF early diagnosis, Nutrition, Time to wrinkle

CF Research News Article

Scientific Abstract

May 2021

Title: How does infection with Pseudomonas and Aspergillus affect people with cystic fibrosis? A study using UK registry data.

Authors

Dominic A Hughes, Olga Archangelidi, Matthew Coates, Darius Armstrong-James, Stuart J Elborn, Siobhán B Carr, Jane C Davies

References

J Cyst Fibros. 2021 May 3;S1569-1993(21)00117-X. doi: 10.1016/j.jcf.2021.04.007.

Keywords

Aspergillus, Infection, Pseudomonas, registry

CF Research News Article

Scientific Abstract