All Resources

This page provides filters and search facilities across all types of CF resources contained within the ECFS website.

Additionally, you can visit the specific resource type pages as follows:

More information on CF publications can be found here: Publications

October 2021

Title: Arm muscle area as an early indicator of worsening nutritional status in children - a single centre experience

Authors

Helmut Ellemunter, Markus Dumke, Gratiana Steinkamp

References

J Cyst Fibros. 2021 Oct 30;S1569-1993(21)02108-1. doi: 10.1016/j.jcf.2021.10.006.

Keywords

Anthropometric parameters, Arm muscle area, Fat-free mass, nutritional status, Skinfold measurements

Theme

Care of patients with CF, Nutrition/Gastroenterology

CF Research News Article

Scientific Abstract

October 2021

Title: Clofazimine has no influence on the blood concentrations of tezacaftor-ivacaftor in a patient with cystic fibrosis.

Authors

S E M Vonk, S W J Terheggen-Lagro, L M Mouissie, R A A Mathôt, E M Kemper, Amsterdam Mucociliary Clearance Disease (AMCD) research group

References

J Cyst Fibros. 2021 Oct 29;S1569-1993(21)02105-6. doi: 10.1016/j.jcf.2021.10.003.

Keywords

Clofazimine, Drug-drug interaction, Tezacaftor-ivacaftor

Theme

Care of patients with CF, Lung Disease and Infection

CF Research News Article

Scientific Abstract

October 2021

Title: The effect of CFTR modulation with elexacaftor-tezacaftor-ivacaftor on the anxiety sweat rate in people with cystic fibrosis

Authors

Sophia Theres Pallenberg, Sibylle Junge, Felix C Ringshausen, Annette Sauer-Heilborn, Gesine Hansen, Anna Maria Dittrich, Burkhard Tümmler, Manuel Nietert

References

J Cyst Fibros. 2021 Oct 28;S1569-1993(21)02107-X. doi: 10.1016/j.jcf.2021.10.005.

Keywords

CFTR modulator, Sweat rate assay, Sweat test

Theme

Diagnosis/Screening

CF Research News Article

Scientific Abstract

October 2021

Title: Exploring new treatment options for people with cystic fibrosis with severe stop mutations

Authors

E de Poel, S Spelier, S W F Suen, E Kruisselbrink, S Y Graeber, M A Mall, E J M Weersink, M M van der Eerden, G H Koppelman, C K van der Ent, J M Beekman

References

J Cyst Fibros. 2021 Oct 16;S1569-1993(21)01425-9. doi: 10.1016/j.jcf.2021.09.020.

Keywords

CFTR modulation, CFTR nonsense mutation, Intestinal organoids, nonsense mRNA mediated decay inhibition, Premature termination codon, Read-through

Theme

CFTR/Basic Science

CF Research News Article

Scientific Abstract

October 2021

Title: Damage in the cell lining of the airways in cystic fibrosis

Authors

Amandine M Collin, Marylène Lecocq, Bruno Detry, François M Carlier, Caroline Bouzin, Philippe de Sany, Delphine Hoton, Stijn Verleden, Antoine Froidure, Charles Pilette, Sophie Gohy

References

J Cyst Fibros. 2021 Oct 14;S1569-1993(21)01424-7. doi: 10.1016/j.jcf.2021.09.019.

Keywords

Epithelial differentiation, Epithelial-to-mesenchymal transition, Respiratory epithelium

Theme

CFTR/Basic Science, Lung Disease and Infection

CF Research News Article

Scientific Abstract

October 2021

Title: Is it possible to monitor young people with cystic fibrosis at home? Results of the CLIMB-CF study

Authors

C Edmondson, N Westrupp, P Seddon, C Olden, C Wallis, C Dawson, M Brodlie, F Baxter, J McCormick, S MacFarlane, D Rice, A Macleod, R Brooker, M Connon, S Ghayyda, L Blaikie, R Thursfield, L Brown, A Price, E Fleischer, J Itterman, D Hughes, P Barrett, , M Surette, C Donnelly, D Mateos-Corral, G Padley, J Wallenburg, K Brownlee, E W F W Alton, A Bush, J C Davies

References

J Cyst Fibros. 2021 Oct 8;S1569-1993(21)01423-5. doi: 10.1016/j.jcf.2021.09.018.

Keywords

anxiety, depression, Digital technology, Feasibility, Home monitoring

Theme

Care of patients with CF, Clinical Trials

CF Research News Article

Scientific Abstract

October 2021

Title: Lung infection by Pseudomonas aeruginosa in children with cystic fibrosis: risk factors and impact on lung function

Authors

Julie Mésinèle, Manon Ruffin, Astrid Kemgang, Loïc Guillot, Pierre-Yves Boëlle, Harriet Corvol

References

J Cyst Fibros. 2021 Oct 7;S1569-1993(21)01422-3. doi: 10.1016/j.jcf.2021.09.017.

Keywords

Children, Genetic modifiers, Lung function, Pseudomonas aeruginosa, Risk factors

Theme

Lung Disease and Infection

CF Research News Article

Scientific Abstract

October 2021

Title: A review of sweat testing in Ireland in the era of modern CF care

Authors

Barrie Maguire, Ophelia Blake, Gerard Boran, Ingrid Borovickova, Sabah Abdelfadil, Caroline Murray, Basil Elnazir, Barry Linnane

References

J Cyst Fibros. 2021 Oct 4;S1569-1993(21)01417-X. doi: 10.1016/j.jcf.2021.09.012.

Keywords

National survey, Newborn screening, Quantity not sufficient, sweat testing

Theme

Diagnosis/Screening

CF Research News Article

Scientific Abstract

October 2021

Title: Features of Salt Imbalance and Pseudo Barter Syndrome in hospitalized Children and Young Adults with Cystic Fibrosis.

Authors

Danish Abdul Aziz, Fatima Siddiqui, Quratulain Abbasi, Haissan Iftikhar, Shahira Shahid, Fatima Mir

References

J Cyst Fibros. 2021 Oct 2;S1569-1993(21)01418-1. doi: 10.1016/j.jcf.2021.09.013.

Keywords

Hypokalemic alkalosis, Hyponatremia, Pseudo-Bartter syndrom

Theme

Care of patients with CF, Endocrinology

CF Research News Article

Scientific Abstract