All Resources

This page provides filters and search facilities across all types of CF resources contained within the ECFS website.

Additionally, you can visit the specific resource type pages as follows:

More information on CF publications can be found here: Publications

April 2023

Title: Inhaled mRNA therapy for treatment of Cystic Fibrosis: Results of an Early Phase Clinical Trial
Authors
S M Rowe, J B Zuckerman, D Dorgan, J Lascano, K McCoy, M Jain, M S Schechter, S Lommatzsch, V Indihar, N Lechtzin, K McBennett, C Callison, C Brown, T G Liou, K D MacDonald, S Z Nasr, S Bodie, M Vaughn, E B Meltzer, A J Barbier
References
J Cyst Fibros. 2023 Apr 28;S1569-1993(23)00112-1. doi: 10.1016/j.jcf.2023.04.008
Keywords
Aerosol, Gene therapy, mRNA therapy
Theme
Care of patients with CF, Clinical Trials, Pulmonology
PDF icon CF Research News Article
Scientific Abstract

April 2023

Title: Variability of the sweat test in children with Cystic Fibrosis previously with an inconclusive diagnosis Vito Terlizzi, Daniela Dolce
Authors
Vito Terlizzi, Daniela Dolce
References
J Cyst Fibros. 2023 Apr 26;S1569-1993(23)00122-4. doi: 10.1016/j.jcf.2023.04.018.
Keywords
Coefficient of variation, inconclusive diagnosis, Outcomes, sweat chloride
Theme
Care of patients with CF, Diagnosis/Screening, Parents, Psychosocial
PDF icon CF Research News Article
Scientific Abstract

April 2023

Title: Is it cost-effective to use genetic tools to predict how well patients with cystic fibrosis will respond to treatment?
Authors
Yeva Sahakyan, Lusine Abrahamyan, Felix Ratjen, Christine Bear, Lisa Strug, Paul D W Eckford, John K Peel, Murray Krahn, Beate Sander
References
J Cyst Fibros. 2023 Apr 24;S1569-1993(23)00119-4. doi: 10.1016/j.jcf.2023.04.013.
Theme
Care of patients with CF, Epidemiology/Models of care
PDF icon CF Research News Article
Scientific Abstract
Title: Willingness of people taking elexacaftor/tezacaftor/ivacaftor to be in new CFTR modulator studies
Authors
D R VanDevanter, E T Zemanick, M W Konstan, C L Ren, K Odem-Davis, I Emerman, J Young, N Mayer-Hamblett, CHEC-SC Study Group
References
J Cyst Fibros. 2023 Apr 24;S1569-1993(23)00096-6. doi: 10.1016/j.jcf.2023.04.007.
Theme
Clinical Trials
PDF icon CF Research News Article
Scientific Abstract

April 2023

Title: The combination elexacaftor/tezacaftor/ivacaftor (eti) alters the lipid composition of the lung cells irrespective of CFTR mutation
Authors
Nara Liessi, Valeria Tomati, Valeria Capurro, Nicoletta Loberto, Mar Garcia-Aloy, Pietro Franceschi, Massimo Aureli, Nicoletta Pedemonte, Andrea Armirotti
References
J Cyst Fibros. 2023 Apr 21;S1569-1993(23)00115-7. doi: 10.1016/j.jcf.2023.04.012.
Keywords
dihydroceramides, lipidomics, off-target effect, sphingolipids, triple combination ETI
Theme
CFTR/Basic Science
PDF icon CF Research News Article
Scientific Abstract
Title: Cumulative ototoxicity of tobramycin
Authors
Justine Madaule, Félix Valenzuela, Marie Mittaine, Yohan Gallois, Blandine Baladi, Marlène Murris, Marie-Noelle Calmels, Didier Concordet, Peggy Gandia
References
J Cyst Fibros. 2023 Apr 21;S1569-1993(23)00092-9. doi: 10.1016/j.jcf.2023.04.002.
Keywords
Modelling, Ototoxicity, Personalised medicine, Tobramycin
Theme
Care of patients with CF, Lung Disease and Infection
PDF icon CF Research News Article
Scientific Abstract

April 2023

Title: A mobile app for self-management of CF and improved patient-centred care
Authors
Gabriela R Oates, Cathy Mims, Robin Geurs, Rikard Bergquist, Andreas Hager, Jennifer S Guimbellot, Anastasia M Hartzes, Hector H Gutierrez
References
J Cyst Fibros. 2023 Apr 19;S1569-1993(23)00113-3. doi: 10.1016/j.jcf.2023.04.009.
Keywords
Mobile health, Patient-centered care, Patient-generated health data, Satisfaction with care, Shared decision-making
Theme
Epidemiology/Models of care
PDF icon CF Research News Article
Scientific Abstract

April 2023

Title: Impact of the De-escalation of Supportive Therapies in Patients with Cystic Fibrosis Taking Elexacaftor, Tezacaftor, Ivacaftor
Authors
Emma L Guenther, Karen S McCoy, Mariah Eisner, Shasha Bai, Christopher J Nemastil, Kimberly J Novak, Terri Johnson, Emily M Stephan
References
J Cyst Fibros. 2023 Apr 15;S1569-1993(23)00082-6. doi: 10.1016/j.jcf.2023.03.018.
Theme
Care of patients with CF
PDF icon CF Research News Article
Scientific Abstract

April 2023

Title: Children and Adolescents with CF who have a patchy liver on a research ultrasound (US) are at increased risk of developing advanced CF liver disease
Authors
Marilyn J Siegel, Daniel H Leung, Jean P Molleston, Wen Ye, Shruti M Paranjape, A Jay Freeman, Joseph J Palermo, Janis Stoll, Prakash Masand, Boaz Karmazyn, Roger Harned, Simon C Ling, Oscar M Navarro, Wikrom Karnsakul, Adina Alazraki,, Sarah Jane Schwarzenberg, Alex J Towbin, Estella M Alonso, Jennifer L Nicholas, Nicole Green, Randolph K Otto, John C Magee, Michael R Narkewicz
References
J Cyst Fibros. 2023 Apr 7;S1569-1993(23)00083-8. doi: 10.1016/j.jcf.2023.03.019
Keywords
Cirrhosis, Cystic fibrosis liver disease
Theme
Imaging, Nutrition/Gastroenterology
PDF icon CF Research News Article
Scientific Abstract

April 2023

Title: Impact of unplanned pregnancies in cystic fibrosis
Authors
Giselle Peng, Jennifer L Taylor-Cousar, MinJae Lee, Ashley Keller, Natalie E West, Traci M Kazmerski, Jennifer L Goralski, Moira L Aitken, Andrea H Roe, Denis Hadjiliadis, Ahmet Uluer, Patrick A Flume, Sheila Mody, Leigh Ann Bray, Raksha Jain
References
J Cyst Fibros. 2023 Apr 5;S1569-1993(23)00084-X. doi: 10.1016/j.jcf.2023.03.020.
Keywords
Contraception, pregnancy, Pulmonary exacerbations, Unplanned
Theme
Care of patients with CF, Pregnancy with CF, Pulmonology
PDF icon CF Research News Article
Scientific Abstract