All Resources

This page provides filters and search facilities across all types of CF resources contained within the ECFS website.

Additionally, you can visit the specific resource type pages as follows:

More information on CF publications can be found here: Publications

April 2018

Title: Eradication of early P. aeruginosa infection in children <7 years of age with cystic fibrosis: The early study

Authors

Felix Ratjen, Alexander Moeller, Martha L.McKinney, Irina Asherova, Nipa Alon, Robert Maykutn, Gerhild Angyalosi

References

https://doi.org/10.1016/j.jcf.2018.04.002

Keywords

Early eradication, Paediatric patient, Placebo-controlled, Recurrence, Tobramycin inhalation solution

CF Research News Article

Scientific Abstract

April 2018

Title: Pulmonary exacerbations and acute declines in lung function in patients with cystic fibrosis

Authors

Wagener JS, Williams MJ, Millar SJ, Morgan WJ, Pasta DJ, Konstan MW

References

J Cyst Fibros. 2018 Apr 20. pii: S1569-1993(18)30026-2. doi: 10.1016/j.jcf.2018.02.003.

Keywords

Lung function, Pulmonary exacerbations

CF Research News Article

Scientific Abstract

Title: Effectiveness of ivacaftor in cystic fibrosis patients with non-G551D gating mutations.

Authors

Guimbellot J, Solomon GM, Baines A, Heltshe SL, VanDalfsen J, Joseloff E, Sagel SD, Rowe SM; GOALe(2) Investigators.

References

J Cyst Fibros. 2018 Apr 20. pii: S1569-1993(18)30090-0. doi: 10.1016/j.jcf.2018.04.004.

Keywords

CFTR potentiator, clinical trials, Gating mutation, Ivacaftor

CF Research News Article

Scientific Abstract

Title: The CF Canada-Sick Kids Program in individual CF therapy: A resource for the advancement of personalized medicine in CF.

Authors

Eckford PDW, McCormack J, Munsie L, He G, Stanojevic S, Pereira SL, Ho K, Avolio J, Bartlett C, Yang JY, Wong AP, Wellhauser L, Huan LJ, Jiang JX, Ouyang H, Du K, Klingel M, Kyriakopoulou L, Gonska T, Moraes TJ, Strug LJ, Rossant J, Ratjen F, Bear CE

References

J Cyst Fibros. 2018 Apr 20. pii: S1569-1993(18)30086-9. doi: 10.1016/j.jcf.2018.03.013.

Keywords

Clinical outcome data, Cultures, Drug responses, Nasal, Patient-specific primary tissues, Pluripotent stem cells, Precision medicine, RNAseq, Resource for discovery, Whole genome sequencing

CF Research News Article

Scientific Abstract

April 2018

Title: Insights into the cystic fibrosis care in Eastern Europe: results of survey

Authors

Walicka-Serzysko K, Peckova M, Noordhoek JJ, Sands D, Drevinek P

References

J Cyst Fibros. 2018 Apr 19. pii: S1569-1993(18)30088-2. doi: 10.1016/j.jcf.2018.04.003.

Keywords

Eastern Europe; Standards of care

CF Research News Article

Scientific Abstract

April 2018

Title: CFTR rescue with VX-809 and VX-770 favors the repair of primary airway epithelial cell cultures from patients with class II mutations in the presence of Pseudomonas aeruginosa exoproducts.

Authors

Adam D, Bilodeau C, Sognigbé L, Maillé É, Ruffin M, Brochiero E.

References

J Cyst Fibros. 2018 Apr 13. pii: S1569-1993(18)30082-1. doi: 10.1016/j.jcf.2018.03.010.

Keywords

Airway epithelial repair, CFTR rescue, Integrity, Orkambi, Pseudomonas aeruginosa

CF Research News Article

Scientific Abstract

April 2018

Title: Establishing the diagnosis of chronic colonization with Pseudomonas aeruginosa of cystic fibrosis patients: Comparison of the European consensus criteria with genotyping of P. aeruginosa isolates

Authors

Jonckheere L, Schelstraete P, Van Simaey L, Van Braeckel E, Willekens J, Van Daele S, De Baets F, Vaneechoutte M

References

J Cyst Fibros. 2018 Apr 11. pii: S1569-1993(18)30074-2. doi: 10.1016/j.jcf.2018.03.004.

Keywords

European consensus criteria (ECC), Genotyping (GT), McRAPD, Pseudomonas aeruginosa

CF Research News Article

Scientific Abstract