All Resources

This page provides filters and search facilities across all types of CF resources contained within the ECFS website.

Additionally, you can visit the specific resource type pages as follows:

More information on CF publications can be found here: Publications

March 2025

Title: What are the latest advances in Cystic fibrosis literatures in 2024?
Authors
Amel Alameeri, Burcu Capraz Yavuz, Francesca Lucca, Ivan Bambir, Paulina Famulska, Renata W․F․ Cohen
References
J Cyst Fibros. 2025 Mar;24(2):218-223. doi: 10.1016/j.jcf.2025.02.012. Epub 2025 Feb 18
Keywords
advances, literature, Review, 2024, knowledge, landscape, care
File Cystic fibrosis year in review 2024
Original manuscript citation in PubMed
Title: How sweat chloride levels relate to health improvements with CFTR modulators
Authors
Edith T Zemanick, Bonnie Ramsey, Dorota Sands, Edward F McKone, Isabelle Fajac, Jennifer L Taylor-Cousar, Marcus A Mall, Michael W Konstan, Nitin Nair, Jiaqiang Zhu, Emilio Arteaga-Solis, Fredrick Van Goor, Lisa McGarry, Valentin Prieto-Centurion,, Patrick R Sosnay, Carmen Bozic, David Waltz, Nicole Mayer-Hamblett
References
J Cyst Fibros. 2025 Mar;24(2):246-254. doi: 10.1016/j.jcf.2024.12.006. Epub 2025 Jan 3.
Keywords
CFTR function, CFTR modulators, clinical outcomes, sweat chloride
PDF icon CF Research News Article
Scientific Abstract
Title: AI-Powered Home Monitoring for Cystic Fibrosis Flare-Ups in Kids and Adults
Authors
Henryk Mazurek, Andrzej Emeryk, Kamil Janeczek, Eric Derom, Barbara Kuźnar-Kamińska, Tomasz Grzywalski, Adam Biniakowski, Krzysztof Szarzyński, Anna Pastusiak, Dominika Kaminiarczyk-Pyzałka, Dick Botteldooren, Honorata Hafke-Dys, Jędrzej Kociński
References
J Cyst Fibros. 2025 Mar;24(2):390-397. doi: 10.1016/j.jcf.2025.02.011. Epub 2025 Feb 18.
Keywords
AI-aided CF management, Cystic fibrosis exacerbation, Cystic fibrosis monitoring, Remote management of CF, hOme healthcare
PDF icon CF Research News Article
Scientific Abstract
Title: Mental health is related to adherence through self-efficacy and perceived barriers
Authors
Robin S Everhart, Milene T Saavedra, Christine R Ford, Sidney L Gibson, Felicia Reid, Emily F Muther, Christina L Duncan, Rachel Cravens, Angela Green, Kristin A Riekert
References
J Cyst Fibros. 2025 Mar;24(2):334-340. doi: 10.1016/j.jcf.2025.02.016. Epub 2025 Feb 22.
Keywords
Adherence, Barriers, mental health, Self-efficacy
PDF icon CF Research News Article
Scientific Abstract

March 2025

Title: Concentrations of elexacaftor-tezacaftor-ivacaftor After Lung Transplant
Authors
Guimbellot JS, Chalamalla A, Baker E, Ryan KJ, Dowell A, Abouelenein S, Bartlett LE, Bergeron J, Turner G, Acosta EP, Ramos KJ.
References

J Cyst Fibros. 2025 Mar 21:S1569-1993(25)00078-5. doi: 10.1016/j.jcf.2025.03.010. Epub ahead of print. PMID: 40121139.<

Keywords
Cystic Fibrosis; Elexacaftor; Ivacaftor; Lung transplant; Pharmacokinetics; Tacrolimus; Tezacaftor
Theme
Transplantation
PDF icon JCF-D-24-00577R1_FINAL_Guimbellot_230425.pdf
PubMed

March 2025

Title: Treating cystic fibrosis before birth: What we learned from an unsuccessful case
Authors
M Destoop, C Brantner, E B Wilms, Shaj Tytgat, B Peels, R van der Graaf, T B Y Liem, K M de Winter-de Groot
References
J Cyst Fibros. 2025 Mar 20:S1569-1993(25)00074-8. doi: 10.1016/j.jcf.2025.03.006.
Keywords
CFTR modulator therapy, In utero exposure, meconium ileus, pregnancy
PDF icon CF Research News Article
Scientific Abstract

March 2025

Title: Drug allergy to CFTR modulators – an international survey
Authors
Ruth M Urbantat, Laura Behan, Sebastian Wisniewski, Joshua Gardner, Mirjam Stahl, Marcus A Mall, Daniel Peckham, Dean J Naisbitt, Jobst F Roehmel
References
J Cyst Fibros. 2025 Mar 18:S1569-1993(25)00071-2. doi: 10.1016/j.jcf.2025.03.003.
Keywords
CFTR modulator withdrawal, Drug allergy, Drug allergy to CFTR modulator therapy, Immunogenic adverse events, Real-world data
PDF icon CF Research News Article
Scientific Abstract

March 2025

Title: Tracking the journey of elexacaftor-tezacaftor-ivacaftor in the bodies of children with cystic fibrosis
Authors
Steffie E M Vonk, Suzanne W J Terheggen-Lagro, Eric G Haarman, S Hashimoto, Anke H Maitland-van der Zee, Ron A A Mathôt, E Marleen Kemper; Amsterdam Mucociliary Clearance Disease (AMCD) research group
References
J Cyst Fibros. 2025 Mar 14:S1569-1993(25)00076-1. doi: 10.1016/j.jcf.2025.03.008.
Keywords
CFTR modulators, Elexacaftor-tezacaftor-ivacaftor, Pediatrics, Population
PDF icon CF Research News Article
Scientific Abstract

March 2025

Title: Lower inflammation is related to greater energy levels in adults with cystic fibrosis on elexacaftor/tezacaftor/ivacaftor
Authors
Jacob Gravelle, Sameer Desai, Kang Dong, Bradley S Quon
References
J Cyst Fibros. 2025 Mar 11:S1569-1993(25)00073-6. doi: 10.1016/j.jcf.2025.03.004.
Keywords
Elexacaftor, Fatigue, Systemic inflammation, Vitality
PDF icon CF Research News Article
Scientific Abstract

March 2025

Title: Do people with cystic fibrosis experience side effects from Elexacaftor/Tezacaftor/Ivacaftor because of high drug levels?
Authors
Syendon B C Baromeo, Renske van der Meer, Richard C J M van Rossen, Erik B Wilms
References
J Cyst Fibros. 2025 Mar 10:S1569-1993(25)00061-X. doi: 10.1016/j.jcf.2025.02.013.
Keywords
adverse events, Dose reduction, Drug concentration levels, Elexacaftor/tezacaftor/ivacaftor, Pharmacology
PDF icon CF Research News Article
Scientific Abstract

March 2025

Title: CFTR modulators and pregnancy outcomes: early findings from a nationwide cohort study
Authors
Laurent Chouchana, Mathis Collier, Clémence Martin, Pierre-Régis Burgel, Jean-Marc Treluyer
References
J Cyst Fibros. 2025 Mar 8:S1569-1993(25)00070-0. doi: 10.1016/j.jcf.2025.03.002.
Keywords
Birth defect, CFTR modulators, Drug safety, pregnancy, fetus
PDF icon CF Research News Article
Scientific Abstract