All Resources

This page provides filters and search facilities across all types of CF resources contained within the ECFS website.

Additionally, you can visit the specific resource type pages as follows:

More information on CF publications can be found here: Publications

November 2020

Title: Updated guidance on the care of children with an inconclusive diagnosis after newborn screening

Authors

Jürg Barben, Carlo Castellani, Anne Munck, Jane C Davies, Karin M de Winter-de Groot, Silvia Gartner, Nataliya Kashirskaya, Barry Linnane, Sarah J Mayell, Susanna McColley, Chee Y Ooi, Marijke Proesmans, Clement L Ren, Danieli Salinas, Dorota Sands, Isabelle Sermet-Gaudelus, Olaf Sommerburg, Kevin W Southern. For the European CF Society Neonatal Screening Working Group (ECFS NSWG)

References

J Cyst Fibros. 2020 Nov 27;S1569-1993(20)30909-7. doi: 10.1016/j.jcf.2020.11.006.

Keywords

CFSPID, CRMS, Management, Newborn screening

CF Research News Article

Scientific Abstract

November 2020

Title: The cystic fibrosis gut as a potential source of multidrug resistant pathogens

Authors

Steven L Taylor, Lex E X Leong, Sarah K Sims, Rebecca L Keating, Lito E Papanicolas, Alyson Richard, Fredrick M Mobegi, Steve Wesselingh, Lucy D Burr, Geraint B Rogers

References

J Cyst Fibros. 2020 Nov 26;S1569-1993(20)30912-7. doi: 10.1016/j.jcf.2020.11.009.

Keywords

Anti-bacterial agents, Drug resistance, microbiota, Resistome

CF Research News Article

Scientific Abstract

Title: Prostaglandin E2 and phagocytosis of inhaled particulate matter by airway macrophages in cystic fibrosis

Authors

Norrice M Liu, Lisa Miyashita, Marek Sanak, Benjamin Barratt, Jonathan Grigg

References

J Cyst Fibros. 2020 Nov 26;S1569-1993(20)30913-9. doi: 10.1016/j.jcf.2020.11.010.

Keywords

Airway macrophage, Particulate matter, Phagocytosis, Prostaglandin E2

CF Research News Article

Scientific Abstract

November 2020

Title: Long term clinical effectiveness of ivacaftor in people with the G551D CFTR mutation

Authors

J S Guimbellot, A Baines, A Paynter, S L Heltshe, J VanDalfsen, M Jain, S M Rowe, S D Sagel, GOAL-e2 Investigators

References

J Cyst Fibros. 2020 Nov 25;S1569-1993(20)30911-5. doi: 10.1016/j.jcf.2020.11.008.

Keywords

CFTR, Ivacaftor; Lung function, Pseudomonas aeruginosa, Quality of life, sweat chloride

CF Research News Article

Scientific Abstract

Title: Lumacaftor/ivacaftor in people with cystic fibrosis with an A455E-CFTR mutation

Authors

Gitte Berkers, Renske van der Meer, Harry Heijerman, Jeffrey M Beekman, Sylvia F Boj, Robert G J Vries, Peter van Mourik, Jamie R Doyle, Paul Audhya, Zheng Jason Yuan, Nils Kinnman, C Kors van der Ent

References

J Cyst Fibros. 2020 Nov 25;S1569-1993(20)30910-3. doi: 10.1016/j.jcf.2020.11.007.

Keywords

A455E–CFTR, Crossover study, Cystic fibrosis, Lumacaftor/ivacaftor

CF Research News Article

Scientific Abstract

November 2020

Title: Long-term azithromycin use is not associated with QT prolongation in children with cystic fibrosis

Authors

Amalia S Magaret, Jack Salerno, Jason F Deen, Margaret Kloster, Nicole Mayer-Hamblett, Bonnie W Ramsey, Dave P Nichols

References

J Cyst Fibros. 2020 Nov 24;S1569-1993(20)30908-5. doi: 10.1016/j.jcf.2020.11.005.

Keywords

Azithromycin, Pulmonary exacerbation, QT prolongation

CF Research News Article

Scientific Abstract

November 2020

Title: Outcomes and endpoints reported in studies of pulmonary exacerbations in people with cystic fibrosis (CF): a systematic review

Authors

Charlie McLeod, Jamie Wood, André Schultz, Richard Norman, Sherie Smith, Christopher C Blyth, Steve Webb, Alan R Smyth, Thomas L Snelling

References

J Cyst Fibros. 2020 Nov;19(6):858-867. doi: 10.1016/j.jcf.2020.08.015. Epub 2020 Nov 13.

Keywords

Endpoint measure, Outcome assessment, Outcome variables, Patient reported outcome measures, Pulmonary exacerbation

Theme

Clinical Trials

CF Research News Article

Scientific Abstract

Title: Laboratory reporting on the clinical spectrum of CFTR p.Arg117His: still room for improvement

Authors

Nele Laudus, Marie-Pierre Audrézet, Emmanuelle Girodon, Michael A Morris, Dragica Radojkovic, Caroline Raynal, Manuela Seia, Alexandra Štambergová, Heike Torkler, Raina Yamamoto, Elisabeth M C Dequeker

References

J Cyst Fibros. 2020 Nov;19(6):969-974. doi: 10.1016/j.jcf.2020.05.005. Epub 2020 Jun 3

Keywords

CFTR-related disorders, External quality assessment, P.Arg117His

Theme

Care of patients with CF, Diagnosis/Screening

CF Research News Article

Scientific Abstract

November 2020

Title: Impact of Socioeconomic Position on Access to the U.S. Lung Transplant Waiting List in a Matched Cystic Fibrosis Cohort

Authors

Carli J Lehr, Aliza K Fink, Melissa Skeans, Albert Faro, Gabriela Fernandez, Elliott Dasenbrook, Maryam Valapour

References

Ann Am Thorac Soc. 2020 Nov;17(11):1384-1392. doi: 10.1513/AnnalsATS.202001-030OC

Keywords

Socioeconomic position, transplantation

Theme

Care of patients with CF, Psychosocial, Transplantation

CF Research News Article

Scientific Abstract

November 2020

Title: Predicting effects of mutations on CFTR’s mRNA

Authors

Natacha Martin, Anne Bergougnoux, Nesrine Baatallah, Benoit Chevalier, Jessica Varilh, David Baux, Bruno Costes, Pascale Fanen, Caroline Raynal, Isabelle Sermet-Gaudelus, Emmanuelle Girodon, Magali Taulan-Cadars, Alexandre Hinzpeter

References

J Cyst Fibros. 2020 Dec 16;S1569-1993(20)30935-8. doi: 10.1016/j.jcf.2020.12.003.

Keywords

CFTR, Exon skipping, In silico predictions, Minigene, Splicing

CF Research News Article

Scientific Abstract

November 2020

Title: Defective immunometabolism pathways in cystic fibrosis macrophages

Authors

Kaitlin Hamilton, Kathrin Krause, Asmaa Badr, Kylene Daily, Shady Estfanous, Mostafa Eltobgy, Arwa Abu Khweek, Midhun N K Anne, Cierra Carafice, Daniel Baetzhold, Jeffrey R Tonniges, Xiaoli Zhang, Mikhail A Gavrilin, Narasimham L Parinandi, Amal O Amer

References

J Cyst Fibros. 2020 Nov 15;S1569-1993(20)30880-8. doi: 10.1016/j.jcf.2020.10.006.

Keywords

Bacterial infection, Immunometabolism, Macrophage, Mitochondria, Reactive oxygen species

CF Research News Article

Scientific Abstract

November 2020

Title: Airway epithelial stem cell chimerism in cystic fibrosis lung transplant recipients

Authors

Don Hayes J, Rachael E Rayner, Cynthia L Hill, Alfahdah Alsudayri, Mahelet Tadesse, Scott W Lallier, Hemant Parekh, Guy N Brock, Estelle Cormet-Boyaka, Susan D Reynolds

References

J Cyst Fibros. 2020 Nov 10;S1569-1993(20)30881-X. doi: 10.1016/j.jcf.2020.09.013.

Keywords

Airway epithelial stem cell, Basal cell, Chronic lung allograft dysfunction, Lung transplant

CF Research News Article

Scientific Abstract

November 2020

Title: The virtual CF clinic – what this means for sputum microbiology

Authors

John E Moore, B Cherie Millar, John McCaughan, Damian O'Neill, Jane Bell, Amanda Crossan, Jacqueline C Rendall

References

J Cyst Fibros. 2020 Nov 6;S1569-1993(20)30879-1. doi: 10.1016/j.jcf.2020.10.005.

Keywords

COVID19, Mail, Post, Sputum microbiology, Transportation, Virtual clinic

CF Research News Article

Scientific Abstract

November 2020

Title: Early acquisition and conversion of Pseudomonas aeruginosa in Hispanic youth with cystic fibrosis in the United States

Authors

Meghan E McGarry, Chiung-Yu Huang, Dennis W Nielson, Ngoc P Ly

References

J Cyst Fibros. 2020 Nov 5;S1569-1993(20)30876-6. doi: 10.1016/j.jcf.2020.10.002.

Keywords

health disparities, Pseudomonas aeruginosa

CF Research News Article

Scientific Abstract

November 2020

Title: The global impact of SARS-CoV-2 in 181 people with cystic fibrosis

Authors

Elliot McClenaghan, Rebecca Cosgriff, Keith Brownlee, Susannah Ahern, Pierre-Régis Burgel, Catherine A Byrnes, Carla Colombo, Harriet Corvol, Stephanie Y Cheng, Géraldine Daneau, Alexander Elbert, Albert Faro, Christopher H Goss, Vincent Gulmans, Hector Gutierrez, Isabelle de Monestrol, Andreas Jung, Lutz Nährlich, Nataliya Kashirskaya, Bruce C Marshall, Edward McKone, Peter G Middleton, Pedro Mondejar-Lopez, M Dolores Pastor-Vivero, Rita Padoan, Samar Rizvi, Rasa Ruseckaite, Marco Salvatore, Anne L Stephenson, Luiz Vicente R da Silva Filho, Joel Melo, Marco Zampoli, Siobhán B Carr, Global Registry Harmonization Group

References

J Cyst Fibros. 2020 Nov 4;S1569-1993(20)30877-8. doi: 10.1016/j.jcf.2020.10.003

Keywords

COVID-19, Coronavirus, SARS-CoV-2, Transplant

CF Research News Article

Scientific Abstract