All Resources

This page provides filters and search facilities across all types of CF resources contained within the ECFS website.

Additionally, you can visit the specific resource type pages as follows:

More information on CF publications can be found here: Publications

August 2016

Title: The changing prevalence of pulmonary infection in adults with cystic fibrosis: A longitudinal analysis
References
J Cyst Fibros. 2016 Aug 8. pii: S1569-1993(16)30567-7

August 2016

Title: Long-term work participation among cystic fibrosis patients undergoing lung transplantation
References
J Cyst Fibros. 2016 Aug 3. pii: S1569-1993(16)30564-1.
Theme
Epidemiology/Models of care

July 2016

Title: Hyperpolarized 129Xe for investigation of mild cystic fibrosis lung disease in pediatric patients.
References
J Cyst Fibros. 2016 Jul 28. pii: S1569-1993(16)30565-3.

July 2016

Title: Ivacaftor and symptoms of extra-oesophageal reflux in patients with cystic fibrosis and G551D mutation
References
J Cyst Fibros. 2016 Jul 27. pii: S1569-1993(16)30561-6
Theme
Nutrition/Gastroenterology

July 2016

Title: The Effects of Ivacaftor on CF Fatty Acid Metabolism: An Analysis from the GOAL Study
References
J Cyst Fibros. 2016 Jul 26. pii: S1569-1993(16)30563-X.
Theme
Nutrition/Gastroenterology

July 2016

Title: Limitations to providing adult cystic fibrosis care in Europe: Results of a care centre survey
References
J Cyst Fibros. 2016 Jul 25. pii: S1569-1993(16)30558-6
Theme
Epidemiology/Models of care

July 2016

Title: A Product of Immunoreactive Trypsinogen and Pancreatitis-Associated Protein as Second Tier Strategy in Cystic Fibrosis Newborn Screening
References
J Cyst Fibros. 2016 Jul 22. pii: S1569-1993(16)30559-8
Theme
Diagnosis/Screening

June 2016

Title: IL-22 exacerbates weight loss in a murine model of chronic pulmonary Pseudomonas aeruginosa infection
References
J Cyst Fibros. 2016 Jun 30. pii: S1569-1993(16)30553-7
Theme
Immunology
Title: A Novel Guluronate Oligomer Improves Intestinal Transit and Survival in Cystic Fibrosis Mice
References
J Cyst Fibros. 2016 Jun 30. pii: S1569-1993(16)30553-7
Theme
Nutrition/Gastroenterology

June 2016

Title: Triazole resistance in Aspergillus fumigatus isolates from patients with cystic fibrosis in Italy.
References
J Cyst Fibros. 2016 Jun 26. pii: S1569-1993(16)30551-3.
Theme
Microbiology

June 2016

Title: Longitudinal study of Stenotrophomonas maltophilia antibody levels and outcomes in cystic fibrosis patients.
References
J Cyst Fibros. 2016 Jun 23. pii: S1569-1993(16)30552-5.

June 2016

Title: Objective airway artery dimensions compared to CT scoring methods assessing structural cystic fibrosis lung disease
References
J Cyst Fibros. 2016 Jun 21. pii: S1569-1993(16)30522-7

June 2016

Title: Risk of asthma in heterozygous carriers for cystic fibrosis: a meta-analysis
References
J Cyst Fibros. 2016 Jun 17. pii: S1569-1993(16)30524-0
Theme
Epidemiology/Models of care
Title: Multiple Prevalent Fractures in Relation to Macroscopic Bone Architecture in Patients with Cystic Fibrosis
References
J Cyst Fibros. 2016 Jun 17. pii: S1569-1993(16)30547-1

June 2016

Title: Airway inflammation in mild cystic fibrosis.
References
J Cyst Fibros. 2016 Jun 10. pii: S1569-1993(16)30523-9
Title: Respiratory Pathogens Mediate the Association between Lung Function and Temperature in Cystic Fibrosis
References
J Cyst Fibros. 2016 Jun 10. pii: S1569-1993(16)30514-8.

June 2016

Title: Bioelectrical impedance in young patients with cystic fibrosis: validation of a specific equation and clinical relevance
References
J Cyst Fibros. 2016 Jun 8. pii: S1569-1993(16)30053-4

June 2016

Title: Pancreatic Elastase-1 Quick Test for rapid assessment of pancreatic status in cystic fibrosis patients.
References
J Cyst Fibros. 2016 Jun 7. pii: S1569-1993(16)30511-2.

June 2016

Title: Sino-nasal Inhalation of Isotonic versus Hypertonic Saline (6.0 %) in CF Patients with Chronic Rhinosinusitis – Results of a Multicentre, Prospective, Randomized, Double-blind, Controlled Trial
References
J Cyst Fibros. 2016 Jun 4. pii: S1569-1993(16)30052-2
Theme
Clinical Trials

June 2016

Title: Cystic fibrosis in Latin America - Improving the awareness
References
J Cyst Fibros. 2016 Jun 1. pii: S1569-1993(16)30509-4.

May 2016

Title: Episodic oral antibiotic use in CF: discordance between the electronic medical record and self-report
References
J Cyst Fibros. 2016 May 4. pii: S1569-1993(16)30044-3
Theme
Epidemiology/Models of care

May 2016

Title: A false positive newborn screening result due to a complex allele carrying two frequent CF-causing variants.
References
J Cyst Fibros. 2016 May;15(3):309-12
Theme
Newborn screening
Title: A false positive newborn screening result due to a complex allele carrying two frequent CF-causing variants.
References
J Cyst Fibros. 2016 May;15(3):309-12
Theme
Newborn screening

April 2016

Title: Improving performance in the detection and management of cystic fibrosis-related diabetes in the Mountain West Cystic Fibrosis Consortium.
References
BMJ Open Diabetes Res Care. 2016 Apr 29;4(1):e000183. doi: 10.1136/bmjdrc-2015-000183.

April 2016

Title: Prevalence of meconium ileus marks the severity of mutations of the Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) gene
References
Genet Med. 2016 Apr;18(4):333-40. doi: 10.1038/gim.2015.79

April 2016

Title: Clinical Practice Guidelines from the Cystic Fibrosis Foundation for Preschoolers with Cystic Fibrosis
References
Pediatrics. 2016 April; 137(4), DOI:10.1542/peds.2015-1784
Theme
Care of patients with CF, Clinical Trials, Pregnancy with CF
Title: Controversies with Kalydeco: Newspaper Coverage in Canada and the Unites States of the Cystic Fibrosis “Wonder Drug”
References
J Cyst Fibros. 2016 Apr 14. pii: S1569-1993(16)30015-7
Theme
Epidemiology/Models of care
Title: Optimizing beta-lactam pharmacodynamics against Pseudomonas aeruginosa in adult cystic fibrosis patients.
References
J Cyst Fibros. 2016 Apr 27. pii: S1569-1993(16)30019-4.
Theme
Microbiology

March 2016

Title: The Geographic Impact on Hospitalization in Patients with Cystic Fibrosis.
References
J Pediatr. 2016 Mar;170:246-52.e1-4. doi: 10.1016/j.jpeds.2015.11.012. Epub 2015 Dec 13.

March 2016

Title: Short-term and long-term response to pulmonary exacerbation treatment in cystic fibrosis.
References
Thorax. 2016 Mar;71(3):223-9. doi: 10.1136/thoraxjnl-2014-206750. Epub 2015 Apr 24.

March 2016

Title: Comparison of two pancreatic enzyme products for exocrine insufficiency in patients with cystic fibrosis
References
J Cyst Fibros. 2016 Mar 21. pii: S1569-1993(16)30001-7
Theme
Nutrition/Gastroenterology
Title: Extensive cultivation of soil and water samples yields various pathogens in patients with cystic fibrosis but not Burkholderia multivorans.
References
J Cyst Fibros. 2016 Mar 17. pii: S1569-1993(16)30005-4
Theme
Microbiology
Title: Disease disclosure in individuals with cystic fibrosis: Association with psychosocial and health outcomes
References
J Cyst Fibros. 2016 Mar 17. pii: S1569-1993(16)30002-9
Title: Evaluation of a systems biology approach to identify pharmacological correctors of the mutant CFTR chloride channel
References
J Cyst Fibros. 2016 Mar 10. pii: S1569-1993(16)00057-6
Theme
CFTR/Basic Science

February 2016

Title: Assessing Differences in Mortality Rates and Risk Factors Between Hispanic and Non-Hispanic Patients With Cystic Fibrosis in California.
References
Chest. 2016 Feb;149(2):380-389. doi: 10.1378/chest.14-2189. Epub 2016 Jan 12.

February 2016

Title: Clinical outcomes in cystic fibrosis patients with Trichosporon respiratory infection
References
J Cyst Fibros. 2016 Feb 27. pii: S1569-1993(16)00037-0
Theme
Microbiology
Title: Safety and Efficacy of Prolonged Levofloxacin Inhalation Solution (1 APT-1026) Treatment for Cystic Fibrosis and Chronic Pseudomonas aeruginosa Airway Infection
References
J Cyst Fibros. 2016 Feb 26. pii: S1569-1993(16)00012-6
Theme
Clinical Trials
Title: The role of basophil activation test in allergic bronchopulmonary aspergillosis and Aspergillus fumigatus sensitization in cystic fibrosis patients
References
J Cyst Fibros. 2016 Feb 25. pii: S1569-1993(16)00016-3
Theme
Epidemiology/Models of care
Title: Glycated hemoglobin cannot yet be proposed as a screening tool for cystic fibrosis related diabetes
References
J Cyst Fibros. 2016 Feb 19. pii: S1569-1993(16)00017-5
Theme
Diagnosis/Screening
Title: International prospective study of distal intestinal obstruction syndrome in cystic fibrosis: associated factors and outcome.
References
J Cyst Fibros. 2016 Feb 23. pii: S1569-1993(16)00014-X.
Theme
Nutrition/Gastroenterology
Title: A Phase 3, Multi-center, Multinational, Randomized, Double-blind, Placebo-controlled Study to Evaluate the Efficacy and Safety of Levofloxacin Inhalation Solution (APT-1026) in Stable Cystic Fibrosis Patients
References
J Cyst Fibros. 2016 Feb 4. pii: S1569-1993(15)00276-3.
Theme
Clinical Trials

January 2016

Title: Measurement of fecal elastase improves performance of newborn screening for cystic fibrosis.
References
J Cyst Fibros. 2016 Jan 27. pii: S1569-1993(16)00002-3
Theme
Newborn screening

January 2016

Title: Microbiological yield from induced sputum compared to oropharyngeal swab in young children with cystic fibrosis
References
J Cyst Fibros. 2016 Jan 26. pii: S1569-1993(16)00008-4.
Theme
Microbiology

January 2016

Title: Host Response to Staphylococcus aureus Cytotoxins In Children with Cystic
References
J Cyst Fibros. 2016 Jan 25. pii: S1569-1993(15)00318-5
Theme
Microbiology

January 2016

Title: Ultrasound and magnetic resonance imaging assessment of joint disease in symptomatic patients with Cystic Fibrosis Arthropathy
References
J Cyst Fibros. 2016 Jan 19. pii: S1569-1993(15)00317-3
Theme
Imaging

January 2016

Title: Implementation of newborn screening for Cystic Fibrosis in Norway. Results from the first three years
References
J Cyst Fibros. 2016 Jan 12. pii: S1569-1993(15)00312-4
Theme
Newborn screening

January 2016

Title: YKL-40 as marker of severe lung disease in cystic fibrosis patients.
References
J Cyst Fibros. 2016 Jan 8. pii: S1569-1993(15)00315-X.
Theme
Immunology
Title: Distribution of the species of Achromobacter in a French Cystic Fibrosis centre and Multilocus Sequence Typing analysis reveal the predominance of A. xylosoxidans and clonal relationships between some clinical and environmental isolates
References
J Cyst Fibros. 2016 Jan 8. pii: S1569-1993(15)00281-7
Theme
Microbiology
Title: Gastric emptying and gastro-oesophageal reflux in children with cystic fibrosis
References
J Cyst Fibros. 2016 Jan 8. pii: S1569-1993(15)00287-8
Theme
Nutrition/Gastroenterology

January 2016

Title: Low sodium status in cystic fibrosis-as assessed by calculating fractional Na+ excretion-is associated with decreased growth parameters.
References
J Cyst Fibros. 2016 Jan 6. pii: S1569-1993(15)00282-9
Theme
Nutrition/Gastroenterology

January 2016

Title: International Committee on Mental Health in Cystic Fibrosis: CFF and ECFS consensus statements for screening and treating depression and anxiety
References
Thorax.2016; 71(1):26-34
Theme
Psychosocial
Title: Antibiotic treatment for Burkholderia cepacia complex in people with cystic fibrosis experiencing a pulmonary exacerbation
References
Horsley A, Jones AM, Lord R. Antibiotic treatment for Burkholderia cepacia complex in people with cystic fibrosis experiencing a pulmonary exacerbation. Cochrane Database of Systematic Reviews 2016, Issue 1. Art. No.: CD009529. DOI: 10.1002/14651858.CD009529.pub3
Theme
Lung Disease and Infection
Title: US CFF and ECFS consensus recommendations for the management of non-tuberculous mycobacteria in individuals with cystic fibrosis: executive summary
References
Thorax. 2016; 71(1):88-90
Theme
Lung Disease and Infection
Title: US CFF and ECFS consensus recommendations for the management of non-tuberculous mycobacteria in individuals with cystic fibrosis
References
Thorax. 2016; 71:i1-i22
Theme
Lung Disease and Infection

December 2015

Title: Preliminary Comparison of Normalized T1 and Non-Contrast Perfusion MRI Assessments of Regional Lung Disease in People with Cystic Fibrosis
References
J Cyst Fibros. 2015 Dec 21. pii: S1569-1993(15)00267-2
Theme
Imaging
Title: Psychological resilience and intolerance of uncertainty in coping with cystic fibrosis
References
J Cyst Fibros. 2015 Dec 10. pii: S1569-1993(15)00269-6
Title: Epidemic Pseudomonas aeruginosa Infection in Patients with Cystic Fibrosis is Not a Risk Factor for Poor Clinical Outcomes Following Lung Transplantation
References
J Cyst Fibros. 2015 Dec 2. pii: S1569-1993(15)00262-3
Title: Bronchial epithelial cell lines and primary nasal epithelial cells from cystic fibrosis respond differently to cigarette smoke exposure
References
J Cyst Fibros. 2015 Dec 1. pii: S1569-1993(15)00260-X
Theme
CFTR/Basic Science

November 2015

Title: Cystic Fibrosis Screen Positive, Inconclusive Diagnosis (CFSPID): a new designation and management recommendations for infants with an inconclusive diagnosis following newborn screening
References
Journal of Cystic Fibrosis. 2015 Nov;14(6):706-713
Theme
Diagnosis/Screening

October 2015

Title: Baseline Ultrasound and Clinical Correlates in Children with Cystic Fibrosis
References
J Pediatr. 2015 Oct;167(4):862-868.e2. doi: 10.1016/j.jpeds.2015.06.062.

October 2015

Title: Statement on Exercise Testing in Cystic Fibrosis
References
Respiration. 2015;90:332-351
Theme
Physiotherapy/Exercise testing
Title: International Committee on Mental Health in Cystic Fibrosis: Cystic Fibrosis Foundation and European Cystic Fibrosis Society consensus statements for screening and treating depression and anxiety
References
doi:10.1136/thoraxjnl-2015-207488

May 2015

Title: Effect of treatment of cystic fibrosis pulmonary exacerbations on systemic inflammation.
References
Ann Am Thorac Soc. 2015 May;12(5):708-17

December 2014

Title: CFF pulmonary guideline. Pharmacologic approaches to prevention and eradication of initial Pseudomonas aeruginosa infection
References
Annals of the American Thoracic Society. 2014; 11(10):1640-1650
Theme
Lung Disease and Infection

November 2014

Title: Aspergillus and cystic fibrosis: old disease – new classifications
References
Current Opinion in Pulmonary Medicine. 2014; 20:632-638
Theme
Lung Disease and Infection

September 2014

Title: Management of cystic fibrosis-related diabetes in children and adolescents ISAPD Clinical Practice Consensus Guidelines 2014 Compendium)
References
Pediatric Diabetes. 2014: 15 (Suppl.20): 65-76
Theme
Diabetes

August 2014

Title: Infection prevention and control guideline for cystic fibrosis: 2013 update.
References
Infection Control and Hospital Epidemilogy
Theme
Lung Disease and Infection

May 2014

Title: Vitamin A supplementation for cystic fibrosis
References
Bonifant CM, Shevill E, Chang AB. Vitamin A supplementation for cystic fibrosis. Cochrane Database of Systematic Reviews 2014, Issue 5. Art. No.: CD006751. DOI: 10.1002/14651858.CD006751.pub4
Theme
Nutrition/Gastroenterology
Title: Vitamin D supplementation
References
Ferguson JH, Chang AB. Vitamin D supplementation for cystic fibrosis. Cochrane Database of Systematic Reviews 2014, Issue 5. Art. No.: CD007298. DOI: 10.1002/14651858.CD007298.pub4
Theme
Nutrition/Gastroenterology
Title: European Cystic Fibrosis Society Standards of Care: Quality Management in cystic fibrosis
References
Journal of Cystic Fibrosis. 2014 May;13 Suppl 1:S43-S59
Theme
Care of patients with CF, Clinical Trials, Pregnancy with CF
Title: European Cystic Fibrosis Society Standards of Care: Best Practice guidelines
References
Journal of Cystic Fibrosis. 2014 May;13 Suppl 1:S23-S42
Theme
Care of patients with CF, Clinical Trials, Pregnancy with CF
Title: European Cystic Fibrosis Society Standards of Care: Framework for the Cystic Fibrosis Centre
References
Journal of Cystic Fibrosis. 2014 May;13 Suppl 1:S3-S22
Theme
Care of patients with CF, Clinical Trials, Pregnancy with CF

March 2014

Title: Practical Guidelines: Lung Transplantation in Patients with Cystic Fibrosis
References
Pulmonary Medicine. 2014:621342. doi: 10.1155/2014/621342. Epub 2014 Mar 30. Review
Theme
Transplantation

October 2013

Title: Genetic modifiers of cystic fibrosis-related diabetes.
References
Diabetes. 2013 Oct;62(10):3627-35. doi: 10.2337/db13-0510. 

October 2013

Title: Culture-based diagnostic microbiology in cystic fibrosis: Can we simplify the complexity?
References

September 2013

Title: Treatment of pulmonary exacerbations in cystic fibrosis
References
European Respiratory Review. 2013 Sep;22:205-216
Theme
Lung Disease and Infection

June 2013

Title: Drug induced complications; can we do more?
References

April 2013

Title: Cystic Fibrosis Pulmonary Guidelines chronic medications for maintenance of lung health
References
American Journal of Respiratory and Critical Care Medicine. 2013; 187:680-689
Theme
Lung Disease and Infection
Title: Update on cystic fibrosis-related diabetes
References
Title: A review of renal disease in cystic fibrosis
References

February 2013

Title: Molecular detection of CF lung pathogens: Current status and future potential
References

December 2012

Title: Antibiotic treatment for nontuberculous mycobacteria lung infection in people with cystic fibrosis
References
Waters V, Ratjen F. Antibiotic treatment for nontuberculous mycobacteria lung infection in people with cystic fibrosis. Cochrane Database of Systematic Reviews 2012, Issue 12. Art. No.: CD010004. DOI: 10.1002/14651858.CD010004.pub2
Theme
Lung Disease and Infection
Title: Treatment of lung infection in patients with cystic fibrosis: Current and future strategies
References
Journal of Cystic Fibrosis. 2012 Dec;11(6):461-479
Theme
Lung Disease and Infection
Title: Nutritional intervention in patients with Cystic Fibrosis: A systematic review
References

November 2012

Title: Report of the workshop on endpoints for cystic fibrosis clinical trials
References
Title: Treatment of lung infection in patients with cystic fibrosis:Current and future strategies
References
Journal of Cystic Fibrosis 2012; 11 : 461-79 

September 2012

Title: Lung function is abnormal in 3-month-old infants with cystic fibrosis diagnosed by newborn screening
References
Title: Measures of body habitus are associated with lung function in adults with cystic fibrosis: A population-based study
References

June 2012

Title: Antifungal therapies for allergic bronchopulmonary aspergillosis in people with cystic fibrosis
References
Elphick HE, Southern KW. Antifungal therapies for allergic bronchopulmonary aspergillosis in people with cystic fibrosis. Cochrane Database of Systematic Reviews 2012, Issue 6. Art. No.: CD002204. DOI: 10.1002/14651858.CD002204.pub2
Theme
Lung Disease and Infection

April 2012

Title: Vitamin D supplementation for cystic fibrosis
References
Ferguson JH, Chang AB. Vitamin D supplementation for cystic fibrosis. Cochrane Database of Systematic Reviews 2012, Issue 4. Art. No.: CD007298. DOI: 10.1002/14651858.CD007298.pub3
Theme
Nutrition/Gastroenterology
Title: An update on the screening, diagnosis, management, and treatment of vitamin D deficiency in individuals with cystic fibrosis: evidence-based recommendations from the Cystic Fibrosis Foundation
References
The Journal of Clinical Endocrinology and Metabolism. 2012 Apr; 97(4):1082-93.
Theme
Bone health
Title: Cystic fibrosis research in allied health and nursing professions
References

December 2011

Title: Chronic Cystic Fibrosis Respiratory Infections: Where do we go from here?
References

August 2011

Title: Infection prevention and control in cystic fibrosis
References
Curr Opin Infect Dis. 2011 Aug;24(4):390-395
Theme
Lung Disease and Infection

June 2011

Title: Guidelines for the diagnosis and management of distal intestinal obstruction syndrome in cystic fibrosis patients
References
Journal of Cystic Fibrosis. 2011 Jun;10 Suppl 2:S24-28
Theme
Nutrition/Gastroenterology
Title: Best practice guidance for the diagnosis and management of cystic fibrosis-associated liver disease
References
Journal of Cystic Fibrosis. 2011 Jun; 10 Suppl 2: S29-36
Theme
Nutrition/Gastroenterology
Title: Recommendations for the classification of diseases as CFTR-related disorders
References
Journal of Cystic Fibrosis. 2011 Volume 10 Suppl 2:S86-S102
Theme
Diagnosis/Screening
Title: Guideline on the design and conduct of cystic fibrosis clinical trials: the European Cystic Fibrosis Society-Clinical Trials Network (ECFS-CTN)
References
Journal of Cystic Fibrosis. 2011 Jun; 10 Suppl 2: S67-74
Theme
Care of patients with CF, Clinical Trials, Pregnancy with CF
Title: European cystic fibrosis bone mineralisation guidelines
References
Journal of Cystic Fibrosis. 2011 Jun;10 Suppl 2:S16-23
Theme
Bone health
Title: Developing new products in cystic fibrosis: Needs and obstacles for activities of small and middle-sized companies
References
Journal of Cystic Fibrosis Volume 10 (2011) S103-S109