With the CF Research News, we aim to bridge the gap between people with CF and the researchers investigating CF and how best to treat those with the condition.
We want to provide access to patients, parents, relatives, friends and caregivers of patients with CF to all scientific work mainly published in the Journal of Cystic Fibrosis (JCF).

All PDF files published hereunder are lay version summaries of work published in the JCF.

June 2016

Title: Pancreatic Elastase-1 Quick Test for rapid assessment of pancreatic status in cystic fibrosis patients.
References
J Cyst Fibros. 2016 Jun 7. pii: S1569-1993(16)30511-2.

June 2016

Title: Sino-nasal Inhalation of Isotonic versus Hypertonic Saline (6.0 %) in CF Patients with Chronic Rhinosinusitis – Results of a Multicentre, Prospective, Randomized, Double-blind, Controlled Trial
References
J Cyst Fibros. 2016 Jun 4. pii: S1569-1993(16)30052-2
Theme
Clinical Trials

June 2016

Title: The Dynamics of Disease Progression in Cystic Fibrosis
References
PLoS One. 2016 Jun 1;11(6):e0156752. doi: 10.1371/journal.pone.0156752. eCollection 2016
Title: Cystic fibrosis in Latin America - Improving the awareness
References
J Cyst Fibros. 2016 Jun 1. pii: S1569-1993(16)30509-4.

May 2016

Title: Episodic oral antibiotic use in CF: discordance between the electronic medical record and self-report
References
J Cyst Fibros. 2016 May 4. pii: S1569-1993(16)30044-3
Theme
Epidemiology/Models of care

May 2016

Title: A false positive newborn screening result due to a complex allele carrying two frequent CF-causing variants.
References
J Cyst Fibros. 2016 May;15(3):309-12
Theme
Newborn screening
Title: A false positive newborn screening result due to a complex allele carrying two frequent CF-causing variants.
References
J Cyst Fibros. 2016 May;15(3):309-12
Theme
Newborn screening

April 2016

Title: Improving performance in the detection and management of cystic fibrosis-related diabetes in the Mountain West Cystic Fibrosis Consortium.
References
BMJ Open Diabetes Res Care. 2016 Apr 29;4(1):e000183. doi: 10.1136/bmjdrc-2015-000183.

April 2016

Title: Improving performance in the detection and management of cystic fibrosis-related diabetes in the Mountain West Cystic Fibrosis Consortium
References
BMJ Open Diabetes Res Care. 2016 Apr 29;4(1):e000183. doi: 10.1136/bmjdrc-2015-000183. eCollection 2016.

April 2016

Title: Prevalence of meconium ileus marks the severity of mutations of the Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) gene
References
Genet Med. 2016 Apr;18(4):333-40. doi: 10.1038/gim.2015.79

April 2016

Title: Controversies with Kalydeco: Newspaper Coverage in Canada and the Unites States of the Cystic Fibrosis “Wonder Drug”
References
J Cyst Fibros. 2016 Apr 14. pii: S1569-1993(16)30015-7
Theme
Epidemiology/Models of care
Title: Optimizing beta-lactam pharmacodynamics against Pseudomonas aeruginosa in adult cystic fibrosis patients.
References
J Cyst Fibros. 2016 Apr 27. pii: S1569-1993(16)30019-4.
Theme
Microbiology

March 2016

Title: The Geographic Impact on Hospitalization in Patients with Cystic Fibrosis.
References
J Pediatr. 2016 Mar;170:246-52.e1-4. doi: 10.1016/j.jpeds.2015.11.012. Epub 2015 Dec 13.

March 2016

Title: Short-term and long-term response to pulmonary exacerbation treatment in cystic fibrosis.
References
Thorax. 2016 Mar;71(3):223-9. doi: 10.1136/thoraxjnl-2014-206750. Epub 2015 Apr 24.

March 2016

Title: Comparison of two pancreatic enzyme products for exocrine insufficiency in patients with cystic fibrosis
References
J Cyst Fibros. 2016 Mar 21. pii: S1569-1993(16)30001-7
Theme
Nutrition/Gastroenterology
Title: Extensive cultivation of soil and water samples yields various pathogens in patients with cystic fibrosis but not Burkholderia multivorans.
References
J Cyst Fibros. 2016 Mar 17. pii: S1569-1993(16)30005-4
Theme
Microbiology
Title: Disease disclosure in individuals with cystic fibrosis: Association with psychosocial and health outcomes
References
J Cyst Fibros. 2016 Mar 17. pii: S1569-1993(16)30002-9
Title: Evaluation of a systems biology approach to identify pharmacological correctors of the mutant CFTR chloride channel
References
J Cyst Fibros. 2016 Mar 10. pii: S1569-1993(16)00057-6
Theme
CFTR/Basic Science

February 2016

Title: Assessing Differences in Mortality Rates and Risk Factors Between Hispanic and Non-Hispanic Patients With Cystic Fibrosis in California.
References
Chest. 2016 Feb;149(2):380-389. doi: 10.1378/chest.14-2189. Epub 2016 Jan 12.

February 2016

Title: Clinical outcomes in cystic fibrosis patients with Trichosporon respiratory infection
References
J Cyst Fibros. 2016 Feb 27. pii: S1569-1993(16)00037-0
Theme
Microbiology
Title: Safety and Efficacy of Prolonged Levofloxacin Inhalation Solution (1 APT-1026) Treatment for Cystic Fibrosis and Chronic Pseudomonas aeruginosa Airway Infection
References
J Cyst Fibros. 2016 Feb 26. pii: S1569-1993(16)00012-6
Theme
Clinical Trials
Title: The role of basophil activation test in allergic bronchopulmonary aspergillosis and Aspergillus fumigatus sensitization in cystic fibrosis patients
References
J Cyst Fibros. 2016 Feb 25. pii: S1569-1993(16)00016-3
Theme
Epidemiology/Models of care
Title: Glycated hemoglobin cannot yet be proposed as a screening tool for cystic fibrosis related diabetes
References
J Cyst Fibros. 2016 Feb 19. pii: S1569-1993(16)00017-5
Theme
Diagnosis/Screening
Title: International prospective study of distal intestinal obstruction syndrome in cystic fibrosis: associated factors and outcome.
References
J Cyst Fibros. 2016 Feb 23. pii: S1569-1993(16)00014-X.
Theme
Nutrition/Gastroenterology
Title: A Phase 3, Multi-center, Multinational, Randomized, Double-blind, Placebo-controlled Study to Evaluate the Efficacy and Safety of Levofloxacin Inhalation Solution (APT-1026) in Stable Cystic Fibrosis Patients
References
J Cyst Fibros. 2016 Feb 4. pii: S1569-1993(15)00276-3.
Theme
Clinical Trials

January 2016

Title: Measurement of fecal elastase improves performance of newborn screening for cystic fibrosis.
References
J Cyst Fibros. 2016 Jan 27. pii: S1569-1993(16)00002-3
Theme
Newborn screening

January 2016

Title: Microbiological yield from induced sputum compared to oropharyngeal swab in young children with cystic fibrosis
References
J Cyst Fibros. 2016 Jan 26. pii: S1569-1993(16)00008-4.
Theme
Microbiology

January 2016

Title: Host Response to Staphylococcus aureus Cytotoxins In Children with Cystic
References
J Cyst Fibros. 2016 Jan 25. pii: S1569-1993(15)00318-5
Theme
Microbiology

January 2016

Title: Ultrasound and magnetic resonance imaging assessment of joint disease in symptomatic patients with Cystic Fibrosis Arthropathy
References
J Cyst Fibros. 2016 Jan 19. pii: S1569-1993(15)00317-3
Theme
Imaging

January 2016

Title: Implementation of newborn screening for Cystic Fibrosis in Norway. Results from the first three years
References
J Cyst Fibros. 2016 Jan 12. pii: S1569-1993(15)00312-4
Theme
Newborn screening

January 2016

Title: YKL-40 as marker of severe lung disease in cystic fibrosis patients.
References
J Cyst Fibros. 2016 Jan 8. pii: S1569-1993(15)00315-X.
Theme
Immunology
Title: Distribution of the species of Achromobacter in a French Cystic Fibrosis centre and Multilocus Sequence Typing analysis reveal the predominance of A. xylosoxidans and clonal relationships between some clinical and environmental isolates
References
J Cyst Fibros. 2016 Jan 8. pii: S1569-1993(15)00281-7
Theme
Microbiology
Title: Gastric emptying and gastro-oesophageal reflux in children with cystic fibrosis
References
J Cyst Fibros. 2016 Jan 8. pii: S1569-1993(15)00287-8
Theme
Nutrition/Gastroenterology

January 2016

Title: Low sodium status in cystic fibrosis-as assessed by calculating fractional Na+ excretion-is associated with decreased growth parameters.
References
J Cyst Fibros. 2016 Jan 6. pii: S1569-1993(15)00282-9
Theme
Nutrition/Gastroenterology

December 2015

Title: Preliminary Comparison of Normalized T1 and Non-Contrast Perfusion MRI Assessments of Regional Lung Disease in People with Cystic Fibrosis
References
J Cyst Fibros. 2015 Dec 21. pii: S1569-1993(15)00267-2
Theme
Imaging
Title: Psychological resilience and intolerance of uncertainty in coping with cystic fibrosis
References
J Cyst Fibros. 2015 Dec 10. pii: S1569-1993(15)00269-6
Title: Epidemic Pseudomonas aeruginosa Infection in Patients with Cystic Fibrosis is Not a Risk Factor for Poor Clinical Outcomes Following Lung Transplantation
References
J Cyst Fibros. 2015 Dec 2. pii: S1569-1993(15)00262-3
Title: Bronchial epithelial cell lines and primary nasal epithelial cells from cystic fibrosis respond differently to cigarette smoke exposure
References
J Cyst Fibros. 2015 Dec 1. pii: S1569-1993(15)00260-X
Theme
CFTR/Basic Science

November 2015

Title: Early Life Growth Trajectories in Cystic Fibrosis are Associated with Pulmonary Function at Age 6 Years.
References
Journal of Pediatrics. 2015 Nov;167(5):1081-8.e1. PMID: 26340874

October 2015

Title: Baseline Ultrasound and Clinical Correlates in Children with Cystic Fibrosis
References
J Pediatr. 2015 Oct;167(4):862-868.e2. doi: 10.1016/j.jpeds.2015.06.062.

September 2015

Title: Genome-wide association meta-analysis identifies five modifier loci of lung disease severity in cystic fibrosis
References
Nat Commun. 2015 Sep 29;6:8382. doi: 10.1038/ncomms9382.

September 2015

Title: Outcomes and Treatment of Chronic Methicillin-Resistant Staphylococcus aureus Differs by Staphylococcal Cassette Chromosome mec (SCCmec) Type in Children With Cystic Fibrosis
References
J Pediatric Infect Dis Soc. 2015 Sep;4(3):225-31. doi: 10.1093/jpids/piu048. Epub 2014 Jun 9.

August 2015

Title: Rate of Uptake of Ivacaftor Use after U.S. Food and Drug Administration Approval among Patients Enrolled in the U.S. Cystic Fibrosis Foundation Patient Registry
References
Ann Am Thorac Soc. 2015 Aug;12(8):1146-52. doi: 10.1513/AnnalsATS.201504-214OC

May 2015

Title: Effect of treatment of cystic fibrosis pulmonary exacerbations on systemic inflammation.
References
Ann Am Thorac Soc. 2015 May;12(5):708-17

May 2015

Title: Outcomes of infants with indeterminate diagnosis detected by cystic fibrosis newborn screening.
References
Pediatrics. 2015 Jun;135(6):e1386-92. doi: 10.1542/peds.2014-3698. Epub 2015 May 11.

March 2015

Title: Comparison of WHO and CDC growth charts in predicting pulmonary outcomes in cystic fibrosis
References
J Pediatr Gastroenterol Nutr. 2015 Mar;60(3):378-83. doi: 10.1097/MPG.0000000000000610.

January 2015

Title: Characterization of Missing Data in Clinical Registry Studies.
References
Ther Innov Regul Sci. 2015 Jan;49(1):146-154. doi: 10.1177/2168479014532259.

December 2014

Title: Gender Differences in Outcomes of Patients with Cystic Fibrosis
References
J Womens Health (Larchmt). 2014 Dec;23(12):1012-20. doi: 10.1089/jwh.2014.4985.

March 2014

Title: Antimicrobial susceptibility and molecular typing of MRSA in cystic fibrosis.
References
Pediatr Pulmonol. 2014 Mar;49(3):230-7. doi: 10.1002/ppul.22815

December 2013

Title: A semiparametric approach to estimate rapid lung function decline in cystic fibrosis
References
Ann Epidemiol. 2013 Dec;23(12):771-7. doi: 10.1016/j.annepidem.2013.08.009. Epub 2013 Oct 5

October 2013

Title: Genetic modifiers of cystic fibrosis-related diabetes.
References
Diabetes. 2013 Oct;62(10):3627-35. doi: 10.2337/db13-0510. 

June 2013

Title: Season is associated with Pseudomonas aeruginosa acquisition in young children with cystic fibrosis.
References
Clin Microbiol Infect. 2013 Nov;19(11):E483-9. doi: 10.1111/1469-0691.12272. Epub 2013 Jun 25.

November 2011

Title: Effect of temperature on cystic fibrosis lung disease and infections: a replicated cohort study.
References
PLoS One. 2011;6(11):e27784. doi: 10.1371/journal.pone.0027784. Epub 2011 Nov 1

January 2004

Title: Effect of ambient air pollution on pulmonary exacerbations and lung function in cystic fibrosis.
References
Am J Respir Crit Care Med. 2004 Apr 1;169(7):816-21. Epub 2004 Jan 12.