Changes of CFTR functional measurements and clinical improvements in Cystic Fibrosis patients with non p.Gly551Asp gating mutations treated with ivacaftor

Myriam Mesbahi* and Michal Shteinberg*; Michael Wilschanski, Aurelie Hatton, Thao Nguyen–Khoa, Hannah Friedman, Michael Cohen, Virginie Escabasse, Muriel Le Bourgeois, VicenzinaLucidi, Isabelle Sermet-Gaudelus, Laurence Bassinet** and Galit Livnat**, *,**