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Home > Changes of CFTR functional measurements and clinical improvements in Cystic Fibrosis patients with non p.Gly551Asp gating mutations treated with ivacaftor

Changes of CFTR functional measurements and clinical improvements in Cystic Fibrosis patients with non p.Gly551Asp gating mutations treated with ivacaftor

Resource Type

CF Research News

Authors

Myriam Mesbahi* and Michal Shteinberg*; Michael Wilschanski, Aurelie Hatton, Thao Nguyen–Khoa, Hannah Friedman, Michael Cohen, Virginie Escabasse, Muriel Le Bourgeois, VicenzinaLucidi, Isabelle Sermet-Gaudelus, Laurence Bassinet** and Galit Livnat**, *,**

References

J Cyst Fibros. 2017 Jan;16(1):45-48

Document

PDF icon JCF-D-16-00131R3_FINAL_Sermet-Gaudelus_04012017.pdf [1]

Link

Scientific abstract [2]

Keywords

CFTR modulators [3]
Evaporimetry; Ivacaftor [4]
Nasal potential difference [5]
Short circuit current [6]

Date

Thursday, January 12, 2017

Featured resource article

Yes

Resource - Guideline Type

Other Guidelines [7]
Source URL:https://www.ecfs.eu/resource-article/cf-research-news/changes-cftr-functional-measurements-and-clinical-improvements

Links
[1] https://www.ecfs.eu/sites/default/files/cf-research-article-files/JCF-D-16-00131R3_FINAL_Sermet-Gaudelus_04012017.pdf [2] https://www.ncbi.nlm.nih.gov/pubmed/?term=Changes%20of%20CFTR%20functional%20measurements%20and%20clinical%20improvements%20in%20Cystic%20Fibrosis%20patients%20with%20non%20p.Gly551Asp%20gating%20mutations%20treated%20with%20ivacaftor [3] https://www.ecfs.eu/research-article-keywords/cftr-modulators [4] https://www.ecfs.eu/research-article-keywords/evaporimetry-ivacaftor [5] https://www.ecfs.eu/research-article-keywords/nasal-potential-difference [6] https://www.ecfs.eu/research-article-keywords/short-circuit-current [7] https://www.ecfs.eu/resource-guideline-type/other-guidelines