Recovery of lung function following a pulmonary exacerbation in patients with cystic fibrosis and the G551D-CFTR mutation treated with ivacaftor.
Immediate Effects of Lumacaftor/Ivacaftor Administration on Lung Function in Patients with Severe Cystic Fibrosis Lung Disease
Correlation of sweat chloride and percent predicted FEV1 in cystic fibrosis patients treated with ivacaftor
Therapeutic benefit observed with the CFTR potentiator, ivacaftor, in a CF patient homozygous for the W1282X CFTR nonsense mutation
Creation and characterization of an airway epithelial cell line for stable expression of CFTR variants
CFTR potentiator therapy ameliorates impaired insulin secretion in CF patients with a gating mutation
Alterations in blood leukocytes of G551D-bearing cystic fibrosis patients undergoing treatment with ivacaftor.
