December 2015
Title: Preliminary Comparison of Normalized T1 and Non-Contrast Perfusion MRI Assessments of Regional Lung Disease in People with Cystic Fibrosis
Authors Shannon B. Donnola, Elliott C. Dasenbrook, David Weaver, Lan Lu, Karishma Gupta, Anjali Prabhakaran, Xin Yu, James F. Chmiel, Kimberly McBennett, Michael W. Konstan, Mitchell L. Drumm, Chris A. Flask
References J Cyst Fibros. 2015 Dec 21. pii: S1569-1993(15)00267-2
Keywords Imaging, Lung disease, Magnetic Resonance Imaging, Perfusion, Relaxometry
Title: Psychological resilience and intolerance of uncertainty in coping with cystic fibrosis
Authors Horst Mitmansgruber, Ulrike Smrekar, Bianca Rabanser, Thomas Beck, Johannes Eder, Helmut Ellemunter
References J Cyst Fibros. 2015 Dec 10. pii: S1569-1993(15)00269-6
Keywords Intolerance of uncertainty, Psychological well-being, Quality of life, Resilience
Title: Epidemic Pseudomonas aeruginosa Infection in Patients with Cystic Fibrosis is Not a Risk Factor for Poor Clinical Outcomes Following Lung Transplantation
Authors Julia Pritchard, Mitesh V. Thakrar, Ranjani Somayaji, Michael G. Surette, Harvey R. Rabin, Doug Helmersen, Dale Lien, Swathi Purighalla, Barbara Waddell, Michael D. Parkins
References J Cyst Fibros. 2015 Dec 2. pii: S1569-1993(15)00262-3
Keywords Bronchiectasis, Liverpool epidemic strain, Multi-drug resistant, Prairie Epidemic Strain, Transmissible, Transplant
Title: Bronchial epithelial cell lines and primary nasal epithelial cells from cystic fibrosis respond differently to cigarette smoke exposure
Authors Mark Thomas Shaw Williams, Francine de Courcey, David Comer, Joseph S Elborn, Madeleine Ennis
References J Cyst Fibros. 2015 Dec 1. pii: S1569-1993(15)00260-X
Keywords Airway, Bronchial, CSE, Cells, Cytokine, EGFR, Epithelial, F508del, Healthy, IL-8, Immortalised, Inflammation, Nasal, Patients, Primary, R117H, Release
November 2015
Title: Early Life Growth Trajectories in Cystic Fibrosis are Associated with Pulmonary Function at Age 6 Years.
Authors Sanders DB, Fink A, Mayer-Hamblett N, Schechter M, Sawicki GS, Rosenfeld M, Flume PA, Morgan WJ
References Journal of Pediatrics. 2015 Nov;167(5):1081-8.e1. PMID: 26340874
November 2015
Title: A Longitudinal Analysis of Chronic MRSA and Pseudomonas aeruginosa Co-infection in Cystic Fibrosis: A Single-Center Study
Authors Maret L. Maliniaka, Arlene A. Stecenkoa, Nael A. McCarty
References J Cyst Fibros. 2015 Nov 20. pii: S1569-1993(15)00258-1
Keywords Methicillin-resistant Staphylococcus aureus, Pseudomonas aeruginosa, Pulmonary function tests, Longitudinal studies, Epidemiology
October 2015
Title: Baseline Ultrasound and Clinical Correlates in Children with Cystic Fibrosis
Authors Leung DH, Ye W, Molleston JP, Weymann A, Ling S, Paranjape SM, Romero R, Schwarzenberg SJ, Palermo J, Alonso EM, Murray KF, Marshall BC, Sherker AH, Siegel MJ, Krishnamurthy R, Harned R, Karmazyn B, Magee JC, Narkewicz MR; Cystic Fibrosis Liver Disease Ne
References J Pediatr. 2015 Oct;167(4):862-868.e2. doi: 10.1016/j.jpeds.2015.06.062.
September 2015
Title: Genome-wide association meta-analysis identifies five modifier loci of lung disease severity in cystic fibrosis
Authors Corvol H, Blackman SM, Boëlle PY, Gallins PJ, Pace RG, Stonebraker JR, Accurso FJ, Clement A, Collaco JM, Dang H, Dang AT, Franca A, Gong J, Guillot L, Keenan K, Li W, Lin F, Patrone MV, Raraigh KS, Sun L, Zhou YH, O'Neal WK, Sontag MK, Levy H, Durie PR,
References Nat Commun. 2015 Sep 29;6:8382. doi: 10.1038/ncomms9382.
September 2015
Title: Outcomes and Treatment of Chronic Methicillin-Resistant Staphylococcus aureus Differs by Staphylococcal Cassette Chromosome mec (SCCmec) Type in Children With Cystic Fibrosis
Authors Heltshe SL, Saiman L, Popowitch EB, Miller MB, Kloster M, Thompson V, Ferkol TW, Hoover WC, Schechter MS, Muhlebach MS.
References J Pediatric Infect Dis Soc. 2015 Sep;4(3):225-31. doi: 10.1093/jpids/piu048. Epub 2014 Jun 9.
Keywords PVL, Panton-Valentine leukocidin, SCCmec type, methicillin-resistant Staphylococcus aureus; pulmonary exacerbation
August 2015
Title: Rate of Uptake of Ivacaftor Use after U.S. Food and Drug Administration Approval among Patients Enrolled in the U.S. Cystic Fibrosis Foundation Patient Registry
Authors Sawicki GS, Dasenbrook E, Fink AK, Schechter MS
References Ann Am Thorac Soc. 2015 Aug;12(8):1146-52. doi: 10.1513/AnnalsATS.201504-214OC
Keywords Ivacaftor, patient registry
June 2015
Title: Multicenter Observational Study on Factors and Outcomes Associated with Various Methicillin-Resistant Staphylococcus aureus Types in Children with Cystic Fibrosis
Authors Muhlebach MS, Heltshe SL, Popowitch EB, Miller MB, Thompson V, Kloster M, Ferkol T, Hoover WC, Schechter MS, Saiman L; STAR-CF Study Team
References Ann Am Thorac Soc. 2015 Jun;12(6):864-71.
Keywords Panton–Valentine leukocidin, SCCmec type, clinic visits, Methicillin-resistant Staphylococcus aureus, risk factor
May 2015
Title: Fine particulate matter exposure and initial Pseudomonas aeruginosa acquisition in cystic fibrosis.
Authors Psoter KJ, De Roos AJ, Mayer JD, Kaufman JD, Wakefield J, Rosenfeld M.
References Ann Am Thorac Soc. 2015 Mar;12(3):385-91. doi: 10.1513/AnnalsATS
Keywords Pseudomonas aeruginosa, ambient air pollution, Epidemiology, Fine particulate matter
Title: Effect of treatment of cystic fibrosis pulmonary exacerbations on systemic inflammation.
Authors Sagel SD, Thompson V, Chmiel JF, Montgomery GS, Nasr SZ, Perkett E, Saavedra MT, Slovis B, Anthony MM, Emmett P, Heltshe SL.
References Ann Am Thorac Soc. 2015 May;12(5):708-17
Keywords Biomarker, Plasma, Pulmonary exacerbation
May 2015
Title: Outcomes of infants with indeterminate diagnosis detected by cystic fibrosis newborn screening.
Authors Ren CL, Fink AK, Petren K, Borowitz DS, McColley SA, Sanders DB, Rosenfeld M, Marshall BC.
References Pediatrics. 2015 Jun;135(6):e1386-92. doi: 10.1542/peds.2014-3698. Epub 2015 May 11.
March 2015
Title: Comparison of WHO and CDC growth charts in predicting pulmonary outcomes in cystic fibrosis
Authors Machogu E, Cao Y, Miller T, Simpson P, Levy H, Quintero D, Goday PS.
References J Pediatr Gastroenterol Nutr. 2015 Mar;60(3):378-83. doi: 10.1097/MPG.0000000000000610.
January 2015
Title: Characterization of Missing Data in Clinical Registry Studies.
Authors Mendelsohn AB, Dreyer NA, Mattox PW, Su Z, Swenson A, Li R, Turner JR, Velentgas P.
References Ther Innov Regul Sci. 2015 Jan;49(1):146-154. doi: 10.1177/2168479014532259.
Keywords missing data, missingness, observational, registry, research, studies
December 2014
Title: Gender Differences in Outcomes of Patients with Cystic Fibrosis
Authors Harness-Brumley CL, Elliott AC, Rosenbluth DB, Raghavan D, Jain R.
References J Womens Health (Larchmt). 2014 Dec;23(12):1012-20. doi: 10.1089/jwh.2014.4985.
December 2014
Title: Improvements in lung function and height among cohorts of 6-year-olds with cystic fibrosis from 1994 to 2012
Authors VanDevanter DR, Pasta DJ, Konstan MW.
References J Pediatr. 2014 Dec;165(6):1091-1097.e2. doi: 10.1016/j.jpeds.2014.06.061
June 2014
Title: Differential geographical risk of initial Pseudomonas aeruginosa acquisition in young U.S. children with cystic fibrosis.
Authors Psoter KJ, Rosenfeld M, De Roos AJ, Mayer JD, Wakefield J.
References Am J Epidemiol. 2014 Jun 15;179(12):1503-13. doi: 10.1093/aje/kwu077.
Keywords Bayesian hierarchical spatial models, Pseudomonas aeruginosa, Weibull regression, interval censoring, intrinsic conditional autoregression
March 2014
Title: Antimicrobial susceptibility and molecular typing of MRSA in cystic fibrosis.
Authors Champion EA, Miller MB, Popowitch EB, Hobbs MM, Saiman L, Muhlebach MS; STAR-CF Study Team.
References Pediatr Pulmonol. 2014 Mar;49(3):230-7. doi: 10.1002/ppul.22815
Keywords Panton-Valentine leukocidin, community MRSA, hospital MRSA, multi-center study, spa-typing; staphylococcal cassette chromosome mec
March 2014
Title: Modeling the impact of antibiotic exposure on human microbiota
Authors Zhao J, Murray S, Lipuma JJ.
References Sci Rep. 2014 Mar 11;4:4345. doi: 10.1038/srep04345
January 2014
Title: Effects of puberty on cystic fibrosis related pulmonary exacerbations in women versus men
Authors Sutton S, Rosenbluth D, Raghavan D, Zheng J, Jain
References Pediatr Pulmonol. 2014 Jan;49(1):28-35. doi: 10.1002/ppul.22767
Keywords Exacerbation, gender disparity, puberty
December 2013
Title: A semiparametric approach to estimate rapid lung function decline in cystic fibrosis
Authors Szczesniak RD, McPhail GL, Duan LL, Macaluso M, Amin RS, Clancy JP
References Ann Epidemiol. 2013 Dec;23(12):771-7. doi: 10.1016/j.annepidem.2013.08.009. Epub 2013 Oct 5
Keywords Epidemiologic methods, Nonlinear models, Spline regression
October 2013
Title: Genetic modifiers of cystic fibrosis-related diabetes.
Authors Blackman SM, Commander CW, Watson C, Arcara KM, Strug LJ, Stonebraker JR, Wright FA, Rommens JM, Sun L, Pace RG, Norris SA, Durie PR, Drumm ML, Knowles MR, Cutting GR.
References Diabetes. 2013 Oct;62(10):3627-35. doi: 10.2337/db13-0510.
June 2013
Title: Season is associated with Pseudomonas aeruginosa acquisition in young children with cystic fibrosis.
Authors Psoter KJ, De Roos AJ, Wakefield J, Mayer J, Rosenfeld M.
References Clin Microbiol Infect. 2013 Nov;19(11):E483-9. doi: 10.1111/1469-0691.12272. Epub 2013 Jun 25.
Keywords Acquisition, Pseudomonas aeruginosa, Climate, Seasonality
November 2011
Title: Effect of temperature on cystic fibrosis lung disease and infections: a replicated cohort study.
Authors Collaco JM, McGready J, Green DM, Naughton KM, Watson CP, Shields T, Bell SC, Wainwright CE; ACFBAL Study Group, Cutting GR
References PLoS One. 2011;6(11):e27784. doi: 10.1371/journal.pone.0027784. Epub 2011 Nov 1
September 2011
Title: A Novel Lung Disease Phenotype Adjusted for Mortality Attrition for Cystic Fibrosis Genetic Modifier Studies
Authors Taylor C, Commander CW, Collaco JM, Strug LJ, Li W, Wright FA, Webel AD, Pace RG, Stonebraker JR, Naughton K, Dorfman R, Sandford A, Blackman SM, Berthiaume Y, Paré P, Drumm ML, Zielenski J, Durie P, Cutting GR, Knowles MR, Corey M.
References Pediatr Pulmonol. 2011 Sep;46(9):857-69. doi: 10.1002/ppul.21456
January 2006
Title: Clinical trial participants compared with nonparticipants in cystic fibrosis
Authors Goss CH, Rubenfeld GD, Ramsey BW, Aitken ML.
References Am J Respir Crit Care Med. 2006 Jan 1;173(1):98-104
January 2004
Title: Effect of ambient air pollution on pulmonary exacerbations and lung function in cystic fibrosis.
Authors Goss CH, Newsom SA, Schildcrout JS, Sheppard L, Kaufman JD
References Am J Respir Crit Care Med. 2004 Apr 1;169(7):816-21. Epub 2004 Jan 12.
