Lumacaftor/ivacaftor in patients with cystic fibrosis and advanced lung disease homozygous for F508del-CFTR
Lung Function Decline is Delayed But Not Decreased in Patients With Cystic Fibrosis and the R117H Gene Mutation
Bile salt stimulated lipase, Cystic fibrosis, Enzyme therapy, NMR spectroscopy, Pancreatic insufficiency, Titrimetric enzyme assay
Age-related levels of fecal M2-pyruvate kinase in children with cystic fibrosis and healthy children 0 to 10years old.
End-of-life practice patterns at U.S. adult cystic fibrosis care centers: A national retrospective chart review.
Retrospective observational study of French patients with cystic fibrosis and a Gly551Asp-CFTR mutation after 1 and 2 years of treatment with ivacaftor in a real-world setting