June 2016
Title: Pancreatic Elastase-1 Quick Test for rapid assessment of pancreatic status in cystic fibrosis patients.
Authors Walkowiak J, Glapa A, Nowak JK, Bober L, Rohovyk N, Wenska-Chyży E, Sobkowiak P, Lisowska A
References J Cyst Fibros. 2016 Jun 7. pii: S1569-1993(16)30511-2.
Keywords Exocrine pancreatic insufficiency, Point-of-care, Qualitative test, Sensitivity, Specificity
June 2016
Title: Sino-nasal Inhalation of Isotonic versus Hypertonic Saline (6.0 %) in CF Patients with Chronic Rhinosinusitis – Results of a Multicentre, Prospective, Randomized, Double-blind, Controlled Trial
Authors Jochen G Mainz, Ulrike Schumacher, Katja Schädlich, Julia Hentschel, Christiane Koitschev, Assen Koitschev, Joachim Riethmüller, Freerk Prenzel, Olaf Sommerburg, Bärbel Wiedemann, Doris Staab, Wolfgang Gleiber, Rainald Fischer, James F Beck , Christin A
References J Cyst Fibros. 2016 Jun 4. pii: S1569-1993(16)30052-2
June 2016
Title: The Dynamics of Disease Progression in Cystic Fibrosis
Authors Adler FR, Liou TG
References PLoS One. 2016 Jun 1;11(6):e0156752. doi: 10.1371/journal.pone.0156752. eCollection 2016
Title: Cystic fibrosis in Latin America - Improving the awareness
Authors Luiz Vicente Ribeiro F. Silva Filho, Claudio Castaños, Héctor Hernán Ruíz
References J Cyst Fibros. 2016 Jun 1. pii: S1569-1993(16)30509-4.
Keywords Awareness, Diagnosis, Latin America, Management, Progress
May 2016
Title: Episodic oral antibiotic use in CF: discordance between the electronic medical record and self-report
Authors Lindsay J. Caverly, Tanner J. Caverly, Linda M. Kalikin, Bridget K. Foster, Richard H. Simon, John J. LiPuma
References J Cyst Fibros. 2016 May 4. pii: S1569-1993(16)30044-3
Keywords Bioelectrical impedance analysis, Body composition, Diaphragm, Fat-free mass, Lung function
Theme Epidemiology/Models of care
May 2016
Title: A false positive newborn screening result due to a complex allele carrying two frequent CF-causing variants.
Authors Bergougnoux A, Boureau-Wirth A, Rouzier C, Altieri JP, Verneau F, Larrieu L, Koenig M, Claustres M, Raynal C
References J Cyst Fibros. 2016 May;15(3):309-12
Keywords CFTR gene, Complex allele, False positive, Newborn screening
Title: A false positive newborn screening result due to a complex allele carrying two frequent CF-causing variants.
Authors Bergougnoux A, Boureau-Wirth A, Rouzier C, Altieri JP, Verneau F, Larrieu L, Koenig M, Claustres M, Raynal C
References J Cyst Fibros. 2016 May;15(3):309-12
Keywords CFTR gene, Complex allele, False positive, Newborn screening
April 2016
Title: Improving performance in the detection and management of cystic fibrosis-related diabetes in the Mountain West Cystic Fibrosis Consortium.
Authors Liou TG, Jensen JL, Allen SE, Brayshaw SJ, Brown MA, Chatfield B, Koenig J, McDonald C, Packer KA, Peet K, Radford P, Reineke LM, Otsuka K, Wagener JS, Young D, Marshall BC
References BMJ Open Diabetes Res Care. 2016 Apr 29;4(1):e000183. doi: 10.1136/bmjdrc-2015-000183.
Keywords Biomarker, Inflammation, Plasma, Pulmonary exacerbation
April 2016
Title: Improving performance in the detection and management of cystic fibrosis-related diabetes in the Mountain West Cystic Fibrosis Consortium
Authors Liou TG, Jensen JL, Allen SE, Brayshaw SJ, Brown MA, Chatfield B, Koenig J, McDonald C, Packer KA, Peet K, Radford P, Reineke LM, Otsuka K, Wagener JS, Young D, Marshall BC
References BMJ Open Diabetes Res Care. 2016 Apr 29;4(1):e000183. doi: 10.1136/bmjdrc-2015-000183. eCollection 2016.
April 2016
Title: Prevalence of meconium ileus marks the severity of mutations of the Cystic Fibrosis Transmembrane Conductance Regulator (CFTR) gene
Authors Dupuis A, Keenan K, Ooi CY, Dorfman R, Sontag MK, Naehrlich L, Castellani C, Strug, LJ Rommens JM, Gonska T
References Genet Med. 2016 Apr;18(4):333-40. doi: 10.1038/gim.2015.79
April 2016
Title: Controversies with Kalydeco: Newspaper Coverage in Canada and the Unites States of the Cystic Fibrosis “Wonder Drug”
Authors Christen Rachul, Maeghan Toews, Timothy Caulfield
References J Cyst Fibros. 2016 Apr 14. pii: S1569-1993(16)30015-7
Theme Epidemiology/Models of care
Title: Optimizing beta-lactam pharmacodynamics against Pseudomonas aeruginosa in adult cystic fibrosis patients.
Authors Thompson RZ, Martin CA, Burgess DR, Rutter WC, Burgess DS
References J Cyst Fibros. 2016 Apr 27. pii: S1569-1993(16)30019-4.
Keywords Beta-lactam, Continuous-infusion, Pharmacodynamics, Pharmacokinetics, Prolonged infusion, Pseudomonas aeruginosa
March 2016
Title: The Geographic Impact on Hospitalization in Patients with Cystic Fibrosis.
Authors Kopp BT, Nicholson L, Paul G, Tobias J, Ramanathan C, Hayes D Jr
References J Pediatr. 2016 Mar;170:246-52.e1-4. doi: 10.1016/j.jpeds.2015.11.012. Epub 2015 Dec 13.
March 2016
Title: Short-term and long-term response to pulmonary exacerbation treatment in cystic fibrosis.
Authors Heltshe SL, Goss CH, Thompson V, Sagel SD, Sanders DB, Marshall BC, Flume PA
References Thorax. 2016 Mar;71(3):223-9. doi: 10.1136/thoraxjnl-2014-206750. Epub 2015 Apr 24.
March 2016
Title: Comparison of two pancreatic enzyme products for exocrine insufficiency in patients with cystic fibrosis
Authors C.J. Taylor, R. Thieroff-Ekerdt, S. Shiff, L. Magnus, R. Fleming, C. Gommoll
References J Cyst Fibros. 2016 Mar 21. pii: S1569-1993(16)30001-7
Keywords Clinical trial, Enzepi, Exocrine pancreatic insufficiency (EPI), Pancreatic enzyme product (PEP), Zenpep
Theme Nutrition/Gastroenterology
Title: Extensive cultivation of soil and water samples yields various pathogens in patients with cystic fibrosis but not Burkholderia multivorans.
Authors Charlotte Peeters, Eliza Depoorter, Jessy Praet, Peter Vandamme
References J Cyst Fibros. 2016 Mar 17. pii: S1569-1993(16)30005-4
Keywords Burkholderia multivorans, Gram-negative non-fermenters, Isolation, Rapidly growing mycobacteria, Soil, Water
Title: Disease disclosure in individuals with cystic fibrosis: Association with psychosocial and health outcomes
Authors Adrienne P. Borschuk, Robin S. Everhart, Michelle N. Eakin, Devin Rand-Giovannetti, Belinda Borrelli, Kristin A. Riekert
References J Cyst Fibros. 2016 Mar 17. pii: S1569-1993(16)30002-9
Keywords Disclosure, Medication adherence, Self-efficacy, Social support
Title: Evaluation of a systems biology approach to identify pharmacological correctors of the mutant CFTR chloride channel
Authors Pesce E, Gorrieri G, Sirci F, Napolitano F, Carrella D, Caci E, Tomati V, Zegarra-Moran O, di Bernardo D, Galietta LJ
References J Cyst Fibros. 2016 Mar 10. pii: S1569-1993(16)00057-6
Keywords CFTR, Chloride channel, Corrector, F508del, Systems biology
February 2016
Title: Epidemiology of the Respiratory Bacteriology of Patients with Cystic Fibrosis
Authors Salsgiver EL, Fink AK, Knapp EA, LiPuma JJ, Olivier KN, Marshall BC, Saiman L. Changing
References Chest. 2016 Feb;149(2):390-400. doi: 10.1378/chest.15-0676.
Keywords Pseudomonas aeruginosa, Staphylococcus aureus, registry
Title: Assessing Differences in Mortality Rates and Risk Factors Between Hispanic and Non-Hispanic Patients With Cystic Fibrosis in California.
Authors Buu MC, Sanders LM, Mayo JA, Milla CE, Wise PH
References Chest. 2016 Feb;149(2):380-389. doi: 10.1378/chest.14-2189. Epub 2016 Jan 12.
Keywords ethnicity, health disparities, pediatric pulmonology
February 2016
Title: Clinical outcomes in cystic fibrosis patients with Trichosporon respiratory infection
Authors Charles R. Esther, Rongpong Plongla, Alan Kerr, Feng-Chang Lin, Peter Gilligan
References J Cyst Fibros. 2016 Feb 27. pii: S1569-1993(16)00037-0
Keywords Chryseobacterium, Lung function
Title: Safety and Efficacy of Prolonged Levofloxacin Inhalation Solution (1 APT-1026) Treatment for Cystic Fibrosis and Chronic Pseudomonas aeruginosa Airway Infection
Authors J. Stuart Elborn, Patrick A. Flume, Fredric Cohen, Jeffery Loutit, Donald R. VanDevanter
References J Cyst Fibros. 2016 Feb 26. pii: S1569-1993(16)00012-6
Title: The role of basophil activation test in allergic bronchopulmonary aspergillosis and Aspergillus fumigatus sensitization in cystic fibrosis patients
Authors Anna Katelari, Marianna Tzanoudaki, Maria Noni, Maria Kanariou, Maria Theodoridou, Emmanuel Kanavakis, Stavros-Eleftherios Doudounakis, Christina Kanaka-Gantenbein
References J Cyst Fibros. 2016 Feb 25. pii: S1569-1993(16)00016-3
Keywords Allergic bronchopulmonary aspergillosis, Aspergillus fumigatus, Aspergillus fumigatus sensitization, Basophil activation test
Theme Epidemiology/Models of care
Title: Glycated hemoglobin cannot yet be proposed as a screening tool for cystic fibrosis related diabetes
Authors Boudreau V, Coriati A, Desjardins K, Rabasa-Lhoret R
References J Cyst Fibros. 2016 Feb 19. pii: S1569-1993(16)00017-5
Keywords Adult, CFRD, Glycated hemoglobin, Oral glucose tolerance test
Theme Diagnosis/Screening
Title: International prospective study of distal intestinal obstruction syndrome in cystic fibrosis: associated factors and outcome.
Authors Anne Munck, Corinne Alberti, Carla Colombo, Nataliya Kashirskaya, Helmut Ellemunter, Maria Fotoulaki, Roderick Houwen, Eddy Robberecht, Priscilla Boizeau, Michael Wilschanski on behalf of the CF/Pancreas ESPGHAN Working Group and DIOS Study Group
References J Cyst Fibros. 2016 Feb 23. pii: S1569-1993(16)00014-X.
Keywords Abdominal pain, Distal intestinal obstruction syndrome, Incidence
Theme Nutrition/Gastroenterology
Title: A Phase 3, Multi-center, Multinational, Randomized, Double-blind, Placebo-controlled Study to Evaluate the Efficacy and Safety of Levofloxacin Inhalation Solution (APT-1026) in Stable Cystic Fibrosis Patients
Authors Patrick A. Flume, Donald R. VanDevanter, Elizabeth E. Morgan, Michael N. Dudley, Jeffery S. Loutit, Scott C. Bell, Eitan Kerem, Rainald Fischer, Alan R. Smyth, Shawn D. Aaron, Douglas Conrad, David E. Geller, J. Stuart Elborn on behalf of the APT investigators
References J Cyst Fibros. 2016 Feb 4. pii: S1569-1993(15)00276-3.
Keywords Aerosol, Antibiotics, Fluoroquinolone, Pseudomonas
January 2016
Title: Measurement of fecal elastase improves performance of newborn screening for cystic fibrosis.
Authors Barben J, Rueegg CS, Jurca M, Spalinger J, Kuehni CE, Swiss Cystic Fibrosis Screening Group
References J Cyst Fibros. 2016 Jan 27. pii: S1569-1993(16)00002-3
Keywords CFSPID, Fecal elastase, Newborn screening
January 2016
Title: Microbiological yield from induced sputum compared to oropharyngeal swab in young children with cystic fibrosis
Authors Marco Zampoli, Komala Pillay, Henri Carrara, Heather J Zar, Brenda Morrow
References J Cyst Fibros. 2016 Jan 26. pii: S1569-1993(16)00008-4.
Keywords Induced sputum, Oropharyngeal swab, Young children
January 2016
Title: Host Response to Staphylococcus aureus Cytotoxins In Children with Cystic
Authors Ashley D. Chadha, Isaac P. Thomsen, Natalia Jimenez-Truque, Nicole R. Soper, Lauren S. Jones, Andrew G. Sokolow, Victor J. Torres, C. Buddy Creech
References J Cyst Fibros. 2016 Jan 25. pii: S1569-1993(15)00318-5
Keywords Exotoxins, LukAB, Serology, Staphylococcus aureus
January 2016
Title: Ultrasound and magnetic resonance imaging assessment of joint disease in symptomatic patients with Cystic Fibrosis Arthropathy
Authors G Fitch, K Williams, JE Freeston, S Dass, A Grainger, R Hodgson, L Horton, P Whitaker, D Peckham
References J Cyst Fibros. 2016 Jan 19. pii: S1569-1993(15)00317-3
Keywords Arthropathy, Joint count, MRI, Ultrasound
January 2016
Title: Implementation of newborn screening for Cystic Fibrosis in Norway. Results from the first three years
Authors Emma Lundmana, H. Junita Gaupa, Egil Bakkeheimb, Edda J. Olafsdottird, Terje Rootweltc, Olav Trond Storrøstenb, Rolf D. Pettersena
References J Cyst Fibros. 2016 Jan 12. pii: S1569-1993(15)00312-4
Keywords Newborn screening
January 2016
Title: YKL-40 as marker of severe lung disease in cystic fibrosis patients.
Authors Leonardi S, Parisi GF, Capizzi A, Manti S, Cuppari C, Scuderi MG, Rotolo N, Lanzafame A, Musumeci M, Salpietro C
References J Cyst Fibros. 2016 Jan 8. pii: S1569-1993(15)00315-X.
Keywords Acute pulmonary exacerbation, Lung function decline, Pulmonary pseudomonas infection, YKL-40
Title: Distribution of the species of Achromobacter in a French Cystic Fibrosis centre and Multilocus Sequence Typing analysis reveal the predominance of A. xylosoxidans and clonal relationships between some clinical and environmental isolates
Authors Lucie Amoureux, Julien Bador, Fatma Bounoua Zouak, Angélique Chapuis, Claire deCurraize, Catherine Neuwirth
References J Cyst Fibros. 2016 Jan 8. pii: S1569-1993(15)00281-7
Keywords Achromobacter spp., Cystic fibrosis, Environment, Epidemiology, Genotyping, MLST, nNrdA
Title: Gastric emptying and gastro-oesophageal reflux in children with cystic fibrosis
Authors Hauser B, De Schepper J, Malfroot A, De Wachter E, De Schutter I, Keymolen K, Vandenplas Y
References J Cyst Fibros. 2016 Jan 8. pii: S1569-1993(15)00287-8
Keywords (13)C-gastric emptying breath test, Children, Gastric emptying, Gastro-oesophageal reflux, Multichannel intraluminal impedance-pH monitoring
Theme Nutrition/Gastroenterology
January 2016
Title: Low sodium status in cystic fibrosis-as assessed by calculating fractional Na+ excretion-is associated with decreased growth parameters.
Authors Knepper C, Ellemunter H, Eder J, Niedermayr K, Haerter B, Hofer P, Scholl-Bürgi S, Müller T, Heinz-Erian P
References J Cyst Fibros. 2016 Jan 6. pii: S1569-1993(15)00282-9
Keywords Fractional sodium excretion, Growth retardation, Normonatremic sodium depletion
Theme Nutrition/Gastroenterology
December 2015
Title: Preliminary Comparison of Normalized T1 and Non-Contrast Perfusion MRI Assessments of Regional Lung Disease in People with Cystic Fibrosis
Authors Shannon B. Donnola, Elliott C. Dasenbrook, David Weaver, Lan Lu, Karishma Gupta, Anjali Prabhakaran, Xin Yu, James F. Chmiel, Kimberly McBennett, Michael W. Konstan, Mitchell L. Drumm, Chris A. Flask
References J Cyst Fibros. 2015 Dec 21. pii: S1569-1993(15)00267-2
Keywords Imaging, Lung disease, Magnetic Resonance Imaging, Perfusion, Relaxometry
Title: Psychological resilience and intolerance of uncertainty in coping with cystic fibrosis
Authors Horst Mitmansgruber, Ulrike Smrekar, Bianca Rabanser, Thomas Beck, Johannes Eder, Helmut Ellemunter
References J Cyst Fibros. 2015 Dec 10. pii: S1569-1993(15)00269-6
Keywords Intolerance of uncertainty, Psychological well-being, Quality of life, Resilience
Title: Epidemic Pseudomonas aeruginosa Infection in Patients with Cystic Fibrosis is Not a Risk Factor for Poor Clinical Outcomes Following Lung Transplantation
Authors Julia Pritchard, Mitesh V. Thakrar, Ranjani Somayaji, Michael G. Surette, Harvey R. Rabin, Doug Helmersen, Dale Lien, Swathi Purighalla, Barbara Waddell, Michael D. Parkins
References J Cyst Fibros. 2015 Dec 2. pii: S1569-1993(15)00262-3
Keywords Bronchiectasis, Liverpool epidemic strain, Multi-drug resistant, Prairie Epidemic Strain, Transmissible, Transplant
Title: Bronchial epithelial cell lines and primary nasal epithelial cells from cystic fibrosis respond differently to cigarette smoke exposure
Authors Mark Thomas Shaw Williams, Francine de Courcey, David Comer, Joseph S Elborn, Madeleine Ennis
References J Cyst Fibros. 2015 Dec 1. pii: S1569-1993(15)00260-X
Keywords Airway, Bronchial, CSE, Cells, Cytokine, EGFR, Epithelial, F508del, Healthy, IL-8, Immortalised, Inflammation, Nasal, Patients, Primary, R117H, Release
November 2015
Title: Early Life Growth Trajectories in Cystic Fibrosis are Associated with Pulmonary Function at Age 6 Years.
Authors Sanders DB, Fink A, Mayer-Hamblett N, Schechter M, Sawicki GS, Rosenfeld M, Flume PA, Morgan WJ
References Journal of Pediatrics. 2015 Nov;167(5):1081-8.e1. PMID: 26340874
November 2015
Title: A Longitudinal Analysis of Chronic MRSA and Pseudomonas aeruginosa Co-infection in Cystic Fibrosis: A Single-Center Study
Authors Maret L. Maliniaka, Arlene A. Stecenkoa, Nael A. McCarty
References J Cyst Fibros. 2015 Nov 20. pii: S1569-1993(15)00258-1
Keywords Methicillin-resistant Staphylococcus aureus, Pseudomonas aeruginosa, Pulmonary function tests, Longitudinal studies, Epidemiology
October 2015
Title: Baseline Ultrasound and Clinical Correlates in Children with Cystic Fibrosis
Authors Leung DH, Ye W, Molleston JP, Weymann A, Ling S, Paranjape SM, Romero R, Schwarzenberg SJ, Palermo J, Alonso EM, Murray KF, Marshall BC, Sherker AH, Siegel MJ, Krishnamurthy R, Harned R, Karmazyn B, Magee JC, Narkewicz MR; Cystic Fibrosis Liver Disease Ne
References J Pediatr. 2015 Oct;167(4):862-868.e2. doi: 10.1016/j.jpeds.2015.06.062.
September 2015
Title: Genome-wide association meta-analysis identifies five modifier loci of lung disease severity in cystic fibrosis
Authors Corvol H, Blackman SM, Boëlle PY, Gallins PJ, Pace RG, Stonebraker JR, Accurso FJ, Clement A, Collaco JM, Dang H, Dang AT, Franca A, Gong J, Guillot L, Keenan K, Li W, Lin F, Patrone MV, Raraigh KS, Sun L, Zhou YH, O'Neal WK, Sontag MK, Levy H, Durie PR,
References Nat Commun. 2015 Sep 29;6:8382. doi: 10.1038/ncomms9382.
September 2015
Title: Outcomes and Treatment of Chronic Methicillin-Resistant Staphylococcus aureus Differs by Staphylococcal Cassette Chromosome mec (SCCmec) Type in Children With Cystic Fibrosis
Authors Heltshe SL, Saiman L, Popowitch EB, Miller MB, Kloster M, Thompson V, Ferkol TW, Hoover WC, Schechter MS, Muhlebach MS.
References J Pediatric Infect Dis Soc. 2015 Sep;4(3):225-31. doi: 10.1093/jpids/piu048. Epub 2014 Jun 9.
Keywords PVL, Panton-Valentine leukocidin, SCCmec type, methicillin-resistant Staphylococcus aureus; pulmonary exacerbation
August 2015
Title: Rate of Uptake of Ivacaftor Use after U.S. Food and Drug Administration Approval among Patients Enrolled in the U.S. Cystic Fibrosis Foundation Patient Registry
Authors Sawicki GS, Dasenbrook E, Fink AK, Schechter MS
References Ann Am Thorac Soc. 2015 Aug;12(8):1146-52. doi: 10.1513/AnnalsATS.201504-214OC
Keywords Ivacaftor, patient registry
June 2015
Title: Multicenter Observational Study on Factors and Outcomes Associated with Various Methicillin-Resistant Staphylococcus aureus Types in Children with Cystic Fibrosis
Authors Muhlebach MS, Heltshe SL, Popowitch EB, Miller MB, Thompson V, Kloster M, Ferkol T, Hoover WC, Schechter MS, Saiman L; STAR-CF Study Team
References Ann Am Thorac Soc. 2015 Jun;12(6):864-71.
Keywords Panton–Valentine leukocidin, SCCmec type, clinic visits, Methicillin-resistant Staphylococcus aureus, risk factor
May 2015
Title: Fine particulate matter exposure and initial Pseudomonas aeruginosa acquisition in cystic fibrosis.
Authors Psoter KJ, De Roos AJ, Mayer JD, Kaufman JD, Wakefield J, Rosenfeld M.
References Ann Am Thorac Soc. 2015 Mar;12(3):385-91. doi: 10.1513/AnnalsATS
Keywords Pseudomonas aeruginosa, ambient air pollution, Epidemiology, Fine particulate matter
Title: Effect of treatment of cystic fibrosis pulmonary exacerbations on systemic inflammation.
Authors Sagel SD, Thompson V, Chmiel JF, Montgomery GS, Nasr SZ, Perkett E, Saavedra MT, Slovis B, Anthony MM, Emmett P, Heltshe SL.
References Ann Am Thorac Soc. 2015 May;12(5):708-17
Keywords Biomarker, Plasma, Pulmonary exacerbation
May 2015
Title: Outcomes of infants with indeterminate diagnosis detected by cystic fibrosis newborn screening.
Authors Ren CL, Fink AK, Petren K, Borowitz DS, McColley SA, Sanders DB, Rosenfeld M, Marshall BC.
References Pediatrics. 2015 Jun;135(6):e1386-92. doi: 10.1542/peds.2014-3698. Epub 2015 May 11.
March 2015
Title: Comparison of WHO and CDC growth charts in predicting pulmonary outcomes in cystic fibrosis
Authors Machogu E, Cao Y, Miller T, Simpson P, Levy H, Quintero D, Goday PS.
References J Pediatr Gastroenterol Nutr. 2015 Mar;60(3):378-83. doi: 10.1097/MPG.0000000000000610.
January 2015
Title: Characterization of Missing Data in Clinical Registry Studies.
Authors Mendelsohn AB, Dreyer NA, Mattox PW, Su Z, Swenson A, Li R, Turner JR, Velentgas P.
References Ther Innov Regul Sci. 2015 Jan;49(1):146-154. doi: 10.1177/2168479014532259.
Keywords missing data, missingness, observational, registry, research, studies
December 2014
Title: Gender Differences in Outcomes of Patients with Cystic Fibrosis
Authors Harness-Brumley CL, Elliott AC, Rosenbluth DB, Raghavan D, Jain R.
References J Womens Health (Larchmt). 2014 Dec;23(12):1012-20. doi: 10.1089/jwh.2014.4985.
December 2014
Title: Improvements in lung function and height among cohorts of 6-year-olds with cystic fibrosis from 1994 to 2012
Authors VanDevanter DR, Pasta DJ, Konstan MW.
References J Pediatr. 2014 Dec;165(6):1091-1097.e2. doi: 10.1016/j.jpeds.2014.06.061
June 2014
Title: Differential geographical risk of initial Pseudomonas aeruginosa acquisition in young U.S. children with cystic fibrosis.
Authors Psoter KJ, Rosenfeld M, De Roos AJ, Mayer JD, Wakefield J.
References Am J Epidemiol. 2014 Jun 15;179(12):1503-13. doi: 10.1093/aje/kwu077.
Keywords Bayesian hierarchical spatial models, Pseudomonas aeruginosa, Weibull regression, interval censoring, intrinsic conditional autoregression
March 2014
Title: Antimicrobial susceptibility and molecular typing of MRSA in cystic fibrosis.
Authors Champion EA, Miller MB, Popowitch EB, Hobbs MM, Saiman L, Muhlebach MS; STAR-CF Study Team.
References Pediatr Pulmonol. 2014 Mar;49(3):230-7. doi: 10.1002/ppul.22815
Keywords Panton-Valentine leukocidin, community MRSA, hospital MRSA, multi-center study, spa-typing; staphylococcal cassette chromosome mec
March 2014
Title: Modeling the impact of antibiotic exposure on human microbiota
Authors Zhao J, Murray S, Lipuma JJ.
References Sci Rep. 2014 Mar 11;4:4345. doi: 10.1038/srep04345
January 2014
Title: Effects of puberty on cystic fibrosis related pulmonary exacerbations in women versus men
Authors Sutton S, Rosenbluth D, Raghavan D, Zheng J, Jain
References Pediatr Pulmonol. 2014 Jan;49(1):28-35. doi: 10.1002/ppul.22767
Keywords Exacerbation, gender disparity, puberty
December 2013
Title: A semiparametric approach to estimate rapid lung function decline in cystic fibrosis
Authors Szczesniak RD, McPhail GL, Duan LL, Macaluso M, Amin RS, Clancy JP
References Ann Epidemiol. 2013 Dec;23(12):771-7. doi: 10.1016/j.annepidem.2013.08.009. Epub 2013 Oct 5
Keywords Epidemiologic methods, Nonlinear models, Spline regression
October 2013
Title: Genetic modifiers of cystic fibrosis-related diabetes.
Authors Blackman SM, Commander CW, Watson C, Arcara KM, Strug LJ, Stonebraker JR, Wright FA, Rommens JM, Sun L, Pace RG, Norris SA, Durie PR, Drumm ML, Knowles MR, Cutting GR.
References Diabetes. 2013 Oct;62(10):3627-35. doi: 10.2337/db13-0510.
June 2013
Title: Season is associated with Pseudomonas aeruginosa acquisition in young children with cystic fibrosis.
Authors Psoter KJ, De Roos AJ, Wakefield J, Mayer J, Rosenfeld M.
References Clin Microbiol Infect. 2013 Nov;19(11):E483-9. doi: 10.1111/1469-0691.12272. Epub 2013 Jun 25.
Keywords Acquisition, Pseudomonas aeruginosa, Climate, Seasonality
November 2011
Title: Effect of temperature on cystic fibrosis lung disease and infections: a replicated cohort study.
Authors Collaco JM, McGready J, Green DM, Naughton KM, Watson CP, Shields T, Bell SC, Wainwright CE; ACFBAL Study Group, Cutting GR
References PLoS One. 2011;6(11):e27784. doi: 10.1371/journal.pone.0027784. Epub 2011 Nov 1
September 2011
Title: A Novel Lung Disease Phenotype Adjusted for Mortality Attrition for Cystic Fibrosis Genetic Modifier Studies
Authors Taylor C, Commander CW, Collaco JM, Strug LJ, Li W, Wright FA, Webel AD, Pace RG, Stonebraker JR, Naughton K, Dorfman R, Sandford A, Blackman SM, Berthiaume Y, Paré P, Drumm ML, Zielenski J, Durie P, Cutting GR, Knowles MR, Corey M.
References Pediatr Pulmonol. 2011 Sep;46(9):857-69. doi: 10.1002/ppul.21456
January 2006
Title: Clinical trial participants compared with nonparticipants in cystic fibrosis
Authors Goss CH, Rubenfeld GD, Ramsey BW, Aitken ML.
References Am J Respir Crit Care Med. 2006 Jan 1;173(1):98-104
January 2004
Title: Effect of ambient air pollution on pulmonary exacerbations and lung function in cystic fibrosis.
Authors Goss CH, Newsom SA, Schildcrout JS, Sheppard L, Kaufman JD
References Am J Respir Crit Care Med. 2004 Apr 1;169(7):816-21. Epub 2004 Jan 12.
