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Home > Does the new CF treatment ETI protect bone health? Findings from a 3-year Danish study

Does the new CF treatment ETI protect bone health? Findings from a 3-year Danish study

Resource Type

CF Research News

Authors

Esben Herborg Henriksen, Bibi Uhre Nielsen, Camilla Bjørn Jensen, Thomas Bryrup, Christine Højte Dahl, Karlen Bader-Larsen, Christian Leo-Hansen, Mette Frahm Olsen
Majbritt Jeppesen, Peter Oturai, Peter Schwarz, Bente Langdahl, Thomas Almdal, Daniel Faurholt-Jepsen, Inger Hee Mabuza Mathiesen, and the TransformCF Study Group
TransformCF Study Group: Hans Kristian Råket Pedersen, Maria Hein Hegelund, Marianne Skov, Søren Jensen-Fangel, Tacjana Pressler, Tavs Qvist, Terese Katzenstein.

References

2026 Feb 18:S1569-1993(26)00031-7. doi: 10.1016/j.jcf.2026.02.002
Keywords: Bone mineral density; CFBD; CFTR modulator therapy; CFTR modulators; Cystic fibrosis; Cystic fibrosis bone disease; DXA; Elexacaftor/tezacaftor/ivacaftor; Endocrinology; 

Document

File JCF-D-25-00176R2_FINAL_Henriksen_2402026.docx [1]

Keywords

bone mineral density [2]
CFBD [3]
CFTR modulator therapy [4]
CFTR modulators [5]
Cystic fibrosis [6]
Cystic fibrosis bone disease [7]
DXA [8]
Elexacaftor/tezacaftor/ivacaftor [9]
Endocrinology [10]
Fat-soluble vitamins [11]
Micronutrients [12]
Osteoporosis [13]
Real world study [14]

Date

Sunday, February 22, 2026

Featured resource article

Yes

Resource - Guideline Type

Other Guidelines [15]
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European Cystic Fibrosis Society (ECFS)

Source URL:https://www.ecfs.eu/resource-article/cf-research-news/does-new-cf-treatment-eti-protect-bone-health-findings-3-year

Links
[1] https://www.ecfs.eu/sites/default/files/cf-research-article-files/JCF-D-25-00176R2_FINAL_Henriksen_2402026.docx [2] https://www.ecfs.eu/research-article-keywords/bone-mineral-density [3] https://www.ecfs.eu/research-article-keywords/cfbd [4] https://www.ecfs.eu/research-article-keywords/cftr-modulator-therapy [5] https://www.ecfs.eu/research-article-keywords/cftr-modulators [6] https://www.ecfs.eu/research-article-keywords/cystic-fibrosis [7] https://www.ecfs.eu/research-article-keywords/cystic-fibrosis-bone-disease [8] https://www.ecfs.eu/research-article-keywords/dxa [9] https://www.ecfs.eu/research-article-keywords/elexacaftortezacaftorivacaftor [10] https://www.ecfs.eu/research-article-keywords/endocrinology [11] https://www.ecfs.eu/research-article-keywords/fat-soluble-vitamins [12] https://www.ecfs.eu/research-article-keywords/micronutrients [13] https://www.ecfs.eu/research-article-keywords/osteoporosis [14] https://www.ecfs.eu/research-article-keywords/real-world-study [15] https://www.ecfs.eu/resource-guideline-type/other-guidelines