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Home > Limited impact of CFTR modulator on exercise capacity: physical activity remains crucial

Limited impact of CFTR modulator on exercise capacity: physical activity remains crucial

Resource Type

CF Research News

Authors

Mariangela Retucci, Andrea Gramegna, Simone Gambazza, Martina Santambrogio, Gianmarco Putti, Alessandra Mariani, Maria Chiara Russo, Marco Vicenzi, Valeria Daccò, Francesco Blasi

References

2025 Oct 16:S1569-1993(25)02489-0. doi: 10.1016/j.jcf.2025.10.005.

Document

File JCF-D-25-00106R2_FINAL_Gramegna_01122025.docx [1]

Keywords

CFTR modulators [2]
CPET [3]
Cardiopulmonary exercise testing [4]
ETI [5]
cardio metabolic [6]
Exercise [7]
maximum workload [8]
muscular [9]

Date

Wednesday, October 15, 2025

Featured resource article

Yes

Resource - Guideline Type

Other Guidelines [10]
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European Cystic Fibrosis Society (ECFS)

Source URL:https://www.ecfs.eu/resource-article/cf-research-news/limited-impact-cftr-modulator-exercise-capacity-physical-activity

Links
[1] https://www.ecfs.eu/sites/default/files/cf-research-article-files/JCF-D-25-00106R2_FINAL_Gramegna_01122025.docx [2] https://www.ecfs.eu/research-article-keywords/cftr-modulators [3] https://www.ecfs.eu/research-article-keywords/cpet [4] https://www.ecfs.eu/research-article-keywords/cardiopulmonary-exercise-testing [5] https://www.ecfs.eu/research-article-keywords/eti [6] https://www.ecfs.eu/research-article-keywords/cardio-metabolic [7] https://www.ecfs.eu/research-article-keywords/exercise [8] https://www.ecfs.eu/research-article-keywords/maximum-workload [9] https://www.ecfs.eu/research-article-keywords/muscular [10] https://www.ecfs.eu/resource-guideline-type/other-guidelines