All Resources

This page provides filters and search facilities across all types of CF resources contained within the ECFS website.

Additionally, you can visit the specific resource type pages as follows:

More information on CF publications can be found here: Publications

April 2022

Title: Use of the CFTR modulator combination elexacaftor/tezacaftor/ivacaftor after lung transplant

Authors

Kathleen J. Ramos, Jennifer S. Guimbellot, Maryam Valapour, Lauren E. Bartlett, Travis Hee Wai, Joseph M. Pilewski, Albert Faro, Joshua M. Diamond for the CFLTC Study Group

References

J Cyst Fibros. 2022 Apr 23;S1569-1993(22)00098-4. doi: 10.1016/j.jcf.2022.04.009.

Keywords

Cystic fibrosis transmembrane conductance regulator, Lung transplantation, Trikafta

Theme

Care of patients with CF, Diabetes, Lung Disease and Infection, Nutrition/Gastroenterology, Transplantation

CF Research News Article

Scientific Abstract

April 2022

Title: How the number of kinds of antibiotics chosen to treat Pseudomonas during an exacerbation affect recovery

Authors

D.R. VanDevanter, N.E. West, D.B. Sanders, M. Skalland, C.H. Goss, P.A. Flume, S.L. Heltshe

References

J Cyst Fibros. 2022 Apr 21;S1569-1993(22)00096-0. doi: 10.1016/j.jcf.2022.04.006.

Keywords

antipseudomonal classes, P. aeruginosa, Pulmonary exacerbation

Theme

Care of patients with CF, Lung Disease and Infection, Pulmonology

CF Research News Article

Scientific Abstract

April 2022

Title: Coping and Length of Life in Cystic Fibrosis

Authors

Janice Abbott, Margaret A. Hurley, Helen Chadwick, Daniel Peckham

References

J Cyst Fibros. 2022 Apr 20;S1569-1993(22)00100-X. doi: 10.1016/j.jcf.2022.04.011.

Keywords

Cox model, Coping, optimism, Survival

Theme

Care of patients with CF, Psychosocial

CF Research News Article

Scientific Abstract

April 2022

Title: Onset of high blood pressure might be possible after the start of elexacaftor/tezacaftor/ivacaftor in adults with cystic fibrosis.

Authors

Andrea Gramegna, Claudia De Petro, Gloria Leonardi, Martina Contarini, Francesco Amati, Roberto Meazza, Stefano Carugo, Francesco Blasi

References

J Cyst Fibros. 2022 Apr 18;S1569-1993(22)00099-6. doi: 10.1016/j.jcf.2022.04.010.

Keywords

adverse events, Elexacaftor/tezacaftor/ivacaftor, Systemic arterial hypertension

Theme

Care of patients with CF, Endocrinology

CF Research News Article

Scientific Abstract

April 2022

Title: Current Prices versus Minimum Costs of Production for CFTR Modulators

Authors

Jonathan Guo, Junzheng Wang, Jingchun Zhang, Joseph Fortunak, Andrew Hill

References

J Cyst Fibros. 2022 Apr 16;S1569-1993(22)00090-X. doi: 10.1016/j.jcf.2022.04.007.

Keywords

CFTR modulator, ; Cystic fibrosis transmembrane conductance regulator, Elexacaftor/tezacaftor/ivacaftor, Kaftrio, Trikafta

Theme

Care of patients with CF, Psychosocial

CF Research News Article

Scientific Abstract

Title: How ivacaftor changes inflammation and protein levels in the bloodstream of people with CF and the G551D mutation

Authors

Jordana E. Hoppe, Brandie D. Wagner, J. Kirk Harris, Steven M. Rowe, Sonya L Heltshe, Emily M. DeBoer, Scott D. Sagel

References

J Cyst Fibros. 2022 Apr 16;S1569-1993(22)00089-3. doi: 10.1016/j.jcf.2022.03.012.

Keywords

CFTR modulation, Extrapulmonary, Inflammation, Proteomics

Theme

Care of patients with CF, Endocrinology, Nutrition/Gastroenterology, Pulmonology

CF Research News Article

Scientific Abstract

April 2022

Title: Inflammation and infection change what mucus is made of, how much gets made, and how much it can dissolve

Authors

Matthew R Markovetz, Ian C Garbarine, Cameron B Morrison, William J Kissner, Ian Seim, M Gregory Forest, Micah J Papanikolas, Ronit Freeman, Agathe Ceppe, Andrew Ghio, Neil E Alexis, Stephen M Stick, Camille Ehre, Richard C Boucher, Charles R Esther, Marianne S Muhlebach, David B Hill

References

J Cyst Fibros. 2022 Apr 15;S1569-1993(22)00097-2. doi: 10.1016/j.jcf.2022.04.008.

Keywords

Airway mucus, Gel-forming mucins, Infection, Microrheology, Mucus flakes

Theme

CFTR/Basic Science, Lung Disease and Infection

CF Research News Article

Scientific Abstract

April 2022

Title: Immune response after COVID-19 vaccination in cystic fibrosis patients

Authors

Athanasios Michos, Filippos Filippatos, Elisabeth-Barbara Tatsi, Charilaos Dellis, Vasiliki Efthymiou, Ioanna Zarkada, Evgenia Troupi, Vasiliki Syriopoulou, Ioanna Loukou

References

J Cyst Fibros. 2022 Apr 14;S1569-1993(22)00094-7. doi: 10.1016/j.jcf.2022.04.004.

Keywords

Antibody, BNT162b2, COVID-19, Neutralizing, SARS-CoV-2, Vaccine

Theme

Care of patients with CF, Immunology

CF Research News Article

Scientific Abstract

April 2022

Title: Maternal Trikafta use during pregnancy and breastfeeding improved outcomes for a baby with CF

Authors

Sylvia Szentpetery, Kimberly Foil, Sara Hendrix, Sue Gray, Christina Mingora, Barbara Head, Donna Johnson, Patrick A Flume

References

J Cyst Fibros. 2022 Apr 11;S1569-1993(22)00095-9. doi: 10.1016/j.jcf.2022.04.005.

Keywords

CFTR modulators, pregnancy

Theme

Care of patients with CF, Parents, Pregnancy with CF

CF Research News Article

Scientific Abstract

April 2022

Title: Magnetic Resonance Imaging Detects Improvements of Pulmonary and Paranasal Sinus Abnormalities in Response to Elexacaftor/Tezacaftor/Ivacaftor Therapy in Adults with Cystic Fibrosis

Authors

Lena Wucherpfennig, Simon M. F. Triphan, Sabine Wege, Hans-Ulrich Kauczor, Claus P. Heussel, Niclas Schmitt, Felix Wuennemann, Victoria L. Mayer, Olaf Sommerburg, Marcus A. Mall, Monika Eichinger, Mark O. Wielpütz

References

J Cyst Fibros. 2022 Apr 7;S1569-1993(22)00088-1. doi: 10.1016/j.jcf.2022.03.011.

Keywords

Airway disease, Functional MRI, Lung perfusion, Mucus obstruction, CFTR-modulator

CF Research News Article

Scientific Abstract