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Home > Orkambi may improve liver disease in people with CF

Orkambi may improve liver disease in people with CF

Resource Type

CF Research News

Authors

David Drummond, Jérémy Dana, Laureline Berteloot, Elena K. Schneider-Futschik, Frédérique Chedevergne, Céline Bailly-Botuha, Thao Nguyen-Khoa, Muriel Le Bourgeois, Dominique Debray, Muriel Girard, Isabelle Sermet-Gaudelus

References

J Cyst Fibros. 2021 Aug 25;S1569-1993(21)01337-0. doi: 10.1016/j.jcf.2021.07.018.

Document

PDF icon CF Research News Article [1]

Link

Scientific Abstract [2]

Keywords

CFTR modulator [3]
Cystic-fibrosis liver disease [4]
Cirrhosis [5]
hepatobiliary [6]
liver enzymes; pediatrics [7]

Date

Wednesday, August 25, 2021

Featured resource article

Yes

Resource - Guideline Type

Other Guidelines [8]
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European Cystic Fibrosis Society (ECFS)

Source URL:https://www.ecfs.eu/resource-article/cf-research-news/orkambi-may-improve-liver-disease-people-cf

Links
[1] https://www.ecfs.eu/sites/default/files/cf-research-article-files/JCF-D-20-00563R3_FINAL_Sermet-Gaudelus_290821.pdf [2] https://pubmed.ncbi.nlm.nih.gov/34454846/ [3] https://www.ecfs.eu/research-article-keywords/cftr-modulator [4] https://www.ecfs.eu/research-article-keywords/cystic-fibrosis-liver-disease-0 [5] https://www.ecfs.eu/research-article-keywords/cirrhosis [6] https://www.ecfs.eu/research-article-keywords/hepatobiliary [7] https://www.ecfs.eu/research-article-keywords/liver-enzymes-pediatrics [8] https://www.ecfs.eu/resource-guideline-type/other-guidelines