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Home > Use of LCI to monitor CFTR Modulator effect in people with CF

Use of LCI to monitor CFTR Modulator effect in people with CF

Resource Type

CF Research News

Authors

Philippe Reix, Aurélie Tatopoulos, Iulia Ioan, Muriel Le Bourgeois, Stéphanie Bui, Marie Luce Choukroun, Katia Bessaci-Kabouya, Michele Gerardin, Plamen Bokov, Jennifer Da Silva, Jean-Louis Paillasseur, Pierre Regis Burgel,
French Cystic Fibrosis Reference Network study group

References

J Cyst Fibros. 2021 Jun 25;S1569-1993(21)01286-8. doi: 10.1016/j.jcf.2021.06.002.

Document

PDF icon CF Research News Article [1]

Link

Scientific Abstract [2]

Keywords

CFTR modulators [3]
Lumacaftor [4]
Multiple breath washout [5]

Date

Friday, June 25, 2021

Featured resource article

Yes

Resource - Guideline Type

Other Guidelines [6]
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European Cystic Fibrosis Society (ECFS)

Source URL:https://www.ecfs.eu/resource-article/cf-research-news/use-lci-monitor-cftr-modulator-effect-people-cf

Links
[1] https://www.ecfs.eu/sites/default/files/cf-research-article-files/JCF-D-21-00178R2_FINAL_Reix_240721.pdf [2] https://pubmed.ncbi.nlm.nih.gov/34183285/ [3] https://www.ecfs.eu/research-article-keywords/cftr-modulators [4] https://www.ecfs.eu/research-article-keywords/lumacaftor [5] https://www.ecfs.eu/research-article-keywords/multiple-breath-washout [6] https://www.ecfs.eu/resource-guideline-type/other-guidelines