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Home > The Proteostatic Network Chaperome is Downregulated in F508del Homozygote Cystic Fibrosis

The Proteostatic Network Chaperome is Downregulated in F508del Homozygote Cystic Fibrosis

Resource Type

CF Research News

Authors

Marc A Sala, Michael Alexander, Basil Khuder, Yuliya Politanska, Hiam Abdala-Valencia, G R Scott Budinger, Jing Liu, Manu Jain, Paul A Reyfman

References

J Cyst Fibros. 2021 Mar;20(2):356-363. doi: 10.1016/j.jcf.2020.12.018. Epub 2021 Jan 23.

Document

PDF icon CF Research News Article [1]

Link

Scientific Abstract [2]

Keywords

Chaperones [3]
Ionocyte [4]
nasal epithelium [5]
Proteostasis [6]
Transcriptomic [7]

Date

Saturday, March 20, 2021

Featured resource article

Yes

Resource - Guideline Type

Other Guidelines [8]
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Source URL:https://www.ecfs.eu/resource-article/cf-research-news/proteostatic-network-chaperome-downregulated-f508del-homozygote

Links
[1] https://www.ecfs.eu/sites/default/files/cf-research-article-files/JCF-D-20-00263R2_FINAL_Jain_110321.pdf [2] https://pubmed.ncbi.nlm.nih.gov/33495079/ [3] https://www.ecfs.eu/research-article-keywords/chaperones [4] https://www.ecfs.eu/research-article-keywords/ionocyte [5] https://www.ecfs.eu/research-article-keywords/nasal-epithelium [6] https://www.ecfs.eu/research-article-keywords/proteostasis [7] https://www.ecfs.eu/research-article-keywords/transcriptomic [8] https://www.ecfs.eu/resource-guideline-type/other-guidelines