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Home > Long term clinical effectiveness of ivacaftor in people with the G551D CFTR mutation

Long term clinical effectiveness of ivacaftor in people with the G551D CFTR mutation

Resource Type

CF Research News

Authors

J S Guimbellot, A Baines, A Paynter, S L Heltshe, J VanDalfsen, M Jain, S M Rowe, S D Sagel, GOAL-e2 Investigators

References

J Cyst Fibros. 2020 Nov 25;S1569-1993(20)30911-5. doi: 10.1016/j.jcf.2020.11.008. 

Document

PDF icon CF Research News Article [1]

Link

Scientific Abstract [2]

Keywords

CFTR [3]
Ivacaftor; Lung function [4]
Pseudomonas aeruginosa [5]
Quality of life [6]
sweat chloride [7]

Date

Wednesday, November 25, 2020

Featured resource article

Yes

Resource - Guideline Type

Other Guidelines [8]
Source URL:https://www.ecfs.eu/resource-article/cf-research-news/long-term-clinical-effectiveness-ivacaftor-people-g551d-cftr

Links
[1] https://www.ecfs.eu/sites/default/files/cf-research-article-files/JCF-D-20-00325R1_FINAL_Guimbellot_180221.pdf [2] https://pubmed.ncbi.nlm.nih.gov/33249004/ [3] https://www.ecfs.eu/research-article-keywords/cftr [4] https://www.ecfs.eu/research-article-keywords/ivacaftor-lung-function [5] https://www.ecfs.eu/research-article-keywords/pseudomonas-aeruginosa [6] https://www.ecfs.eu/research-article-keywords/quality-life [7] https://www.ecfs.eu/research-article-keywords/sweat-chloride [8] https://www.ecfs.eu/resource-guideline-type/other-guidelines