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Home > Clinical response to lumacaftor-ivacaftor in patients with cystic fibrosis according to baseline lung function

Clinical response to lumacaftor-ivacaftor in patients with cystic fibrosis according to baseline lung function

Resource Type

CF Research News

Authors

Pierre-Régis Burgel, Isabelle Durieu, Raphaël Chiron, Laurent Mely, Anne Prevotat, Marlene Murris-Espin, Michele Porzio, Michel Abely, Philippe Reix9, Christophe Marguet, Julie Macey, Isabelle Sermet-Gaudelus, Harriet Corvol, Stéphanie Bui
Tiphaine Biouhee, Dominique Hubert, Anne Munck, Lydie Lemonnier, Clémence Dehillotte, Jennifer Da Silva, Jean-Louis Paillasseur, Clémence Martin, French Cystic Fibrosis Reference Network study group

References

J Cyst Fibros. 2020 Jun 23;S1569-1993(20)30752-9. doi: 10.1016/j.jcf.2020.06.012. Online ahead of print.

Document

PDF icon CF Research News Article [1]

Link

Scientific Abstract [2]

Date

Tuesday, June 23, 2020

Featured resource article

Yes

Resource - Guideline Type

Other Guidelines [3]
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Source URL:https://www.ecfs.eu/resource-article/cf-research-news/clinical-response-lumacaftor-ivacaftor-patients-cystic-fibrosis

Links
[1] https://www.ecfs.eu/sites/default/files/cf-research-article-files/JCF-D-20-00243R2_FINAL_Burgel_030920.pdf [2] https://pubmed.ncbi.nlm.nih.gov/32591294/ [3] https://www.ecfs.eu/resource-guideline-type/other-guidelines