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Home > Females with Cystic Fibrosis have a larger decrease in sweat chloride in response to lumacaftor/ivacaftor compared to males

Females with Cystic Fibrosis have a larger decrease in sweat chloride in response to lumacaftor/ivacaftor compared to males

Resource Type

CF Research News

Authors

B L Aalbers, R W Hofland, I Bronsveld, K M de Winter-de Groot, H G M Arets, A C de Kiviet, M M M van Oirschot-van de Ven, M A Kruijswijk, S Schotman, S Michel, C K van der Ent, H G M Heijerman

References

J Cyst Fibros. 2020 May 21;S1569-1993(20)30135-1. doi: 10.1016/j.jcf.2020.05.004

Document

PDF icon CF Research News Article [1]

Link

Scientific Abstract [2]

Keywords

BMI [3]
CFTR modulators [4]
Lumacaftor/ivacator [5]
sweat chloride [6]
Sweat test [7]
Treatment response [8]
ppFEV1 [9]

Date

Thursday, May 21, 2020

Featured resource article

Yes

Resource - Guideline Type

Other Guidelines [10]
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European Cystic Fibrosis Society (ECFS)

Source URL:https://www.ecfs.eu/resource-article/cf-research-news/females-cystic-fibrosis-have-larger-decrease-sweat-chloride

Links
[1] https://www.ecfs.eu/sites/default/files/cf-research-article-files/JCF-D-20-00084R2_Aalbers_FINAL_110720.pdf [2] https://pubmed.ncbi.nlm.nih.gov/32448708/ [3] https://www.ecfs.eu/research-article-keywords/bmi [4] https://www.ecfs.eu/research-article-keywords/cftr-modulators [5] https://www.ecfs.eu/research-article-keywords/lumacaftorivacator [6] https://www.ecfs.eu/research-article-keywords/sweat-chloride [7] https://www.ecfs.eu/research-article-keywords/sweat-test [8] https://www.ecfs.eu/research-article-keywords/treatment-response [9] https://www.ecfs.eu/research-article-keywords/ppfev1 [10] https://www.ecfs.eu/resource-guideline-type/other-guidelines