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Home > Disease Progression in Patients with Cystic Fibrosis Treated with Ivacaftor: Data From National US and UK Registries

Disease Progression in Patients with Cystic Fibrosis Treated with Ivacaftor: Data From National US and UK Registries

Resource Type

CF Research News

Authors

Volkova N, Moy K, Evans J, Campbell D, Tian S, Simard C, Higgins M, Konstan MW, Sawicki GS, Elbert A, Charman SC, Marshall BC, Bilton D

References

J Cyst Fibros. 2019 Jun 10. pii: S1569-1993(19)30767-2. doi: 10.1016/j.jcf.2019.05.015. 

Document

PDF icon CF Research News Article [1]

Link

Scientific Abstract [2]

Keywords

CF complications [3]
CF disease progression [4]
CFTR [5]
CFTR modulator [6]
Ivacaftor [7]

Date

Monday, June 10, 2019

Featured resource article

Yes

Resource - Guideline Type

Other Guidelines [8]
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European Cystic Fibrosis Society (ECFS)

Source URL:https://www.ecfs.eu/resource-article/cf-research-news/disease-progression-patients-cystic-fibrosis-treated-ivacaftor

Links
[1] https://www.ecfs.eu/sites/default/files/cf-research-article-files/JCF-D-19-00040R1_FINAL_Volkva_150719.pdf [2] https://www.ncbi.nlm.nih.gov/pubmed/?term=Disease%20Progression%20in%20Patients%20with%20Cystic%20Fibrosis%20Treated%20With%20Ivacaftor%3A%20Data%20From%20National%20US%20and%20UK%20Registries [3] https://www.ecfs.eu/research-article-keywords/cf-complications [4] https://www.ecfs.eu/research-article-keywords/cf-disease-progression [5] https://www.ecfs.eu/research-article-keywords/cftr [6] https://www.ecfs.eu/research-article-keywords/cftr-modulator [7] https://www.ecfs.eu/research-article-keywords/ivacaftor [8] https://www.ecfs.eu/resource-guideline-type/other-guidelines