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Home > Lumacaftor-rescued F508del-CFTR has a modified bicarbonate permeability

Lumacaftor-rescued F508del-CFTR has a modified bicarbonate permeability

Resource Type

CF Research News

Authors

Loretta Ferrera, Debora Baroni and Oscar Moran

References

J Cyst Fibros. 2019 Feb 6. pii: S1569-1993(18)30927-5. doi: 10.1016/j.jcf.2019.01.012.

Document

PDF icon CF Research News Article [1]

Link

Scientific Abstract [2]

Keywords

CFTR-Corrector [3]
Ion permeability [4]
Patch-clamp [5]

Date

Wednesday, February 6, 2019

Featured resource article

Yes

Resource - Guideline Type

Other Guidelines [6]
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Source URL:https://www.ecfs.eu/resource-article/cf-research-news/lumacaftor-rescued-f508del-cftr-has-modified-bicarbonate

Links
[1] https://www.ecfs.eu/sites/default/files/cf-research-article-files/JCF-D-106-R2_FINAL_Ferrera_070319_0.pdf [2] https://www.ncbi.nlm.nih.gov/pubmed/?term=Lumacaftor-rescued%20F508del-CFTR%20has%20a%20modified%20bicarbonate%20permeability [3] https://www.ecfs.eu/research-article-keywords/cftr-corrector-0 [4] https://www.ecfs.eu/research-article-keywords/ion-permeability [5] https://www.ecfs.eu/research-article-keywords/patch-clamp [6] https://www.ecfs.eu/resource-guideline-type/other-guidelines