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Home > Rescue of CFTR NBD2 mutants N1303K and S1235R is influenced by the functioning of the autophagosome

Rescue of CFTR NBD2 mutants N1303K and S1235R is influenced by the functioning of the autophagosome

Resource Type

CF Research News

Authors

Liu Q, Sabirzhanova I, Yanda MK, Bergbower EAS, Boinot C, Guggino WB, Cebotaru L

References

J Cyst Fibros. 2018 Jun 20. pii: S1569-1993(18)30621-0. doi: 10.1016/j.jcf.2018.05.016.

Document

PDF icon CF Research News Article [1]

Link

Scientific Abstract [2]

Keywords

Autophagy [3]
CFTR [4]
Correctors [5]
Degradation [6]
Mutations [7]
Short circuit current [8]
Western blot [9]

Date

Monday, August 20, 2018

Featured resource article

Yes

Resource - Guideline Type

Other Guidelines [10]
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Source URL:https://www.ecfs.eu/resource-article/cf-research-news/rescue-cftr-nbd2-mutants-n1303k-and-s1235r-influenced-functioning

Links
[1] https://www.ecfs.eu/sites/default/files/cf-research-article-files/JCF-D-17-00085R3_FINAL_Cebotaru_130818_0.pdf [2] https://www.ncbi.nlm.nih.gov/pubmed/?term=Rescue%20of%20CFTR%20NBD2%20mutants%20N1303K%20and%20S1235R%20is%20influenced%20by%20the%20functioning%20of%20the%20autophagosome [3] https://www.ecfs.eu/research-article-keywords/autophagy [4] https://www.ecfs.eu/research-article-keywords/cftr [5] https://www.ecfs.eu/research-article-keywords/correctors [6] https://www.ecfs.eu/research-article-keywords/degradation [7] https://www.ecfs.eu/research-article-keywords/mutations [8] https://www.ecfs.eu/research-article-keywords/short-circuit-current [9] https://www.ecfs.eu/research-article-keywords/western-blot [10] https://www.ecfs.eu/resource-guideline-type/other-guidelines