Published on European Cystic Fibrosis Society (ECFS) (https://www.ecfs.eu)

Home > Lumacaftor/ivacaftor in patients with cystic fibrosis and advanced lung disease homozygous for F508del-CFTR

Lumacaftor/ivacaftor in patients with cystic fibrosis and advanced lung disease homozygous for F508del-CFTR

Resource Type

CF Research News

Authors

Jennifer L. Taylor-Cousar, Manu Jain, Tara Lynn Barto, Tarik Haddad, Jeffrey Atkinson, Simon Tian, Rui Tang, Gautham Marigowda, David Waltz, Joseph Pilewski on behalf of the VX14-809-106 Investigator Group

References

J Cyst Fibros. 2017 Nov 7. pii: S1569-1993(17)30891-3. doi: 10.1016/j.jcf.2017.09.012

Document

PDF icon CF Research News Article [1]

Link

Scientific Abstract [2]

Keywords

Advanced lung disease [3]
F508del [4]
Ivacaftor [5]
Lumacaftor [6]
Severe lung dysfunction [7]

Date

Tuesday, November 7, 2017

Featured resource article

Yes

Resource - Guideline Type

Other Guidelines [8]
Source URL: https://www.ecfs.eu/resource-article/cf-research-news/lumacaftorivacaftor-patients-cystic-fibrosis-and-advanced-lung

Links
[1] https://www.ecfs.eu/sites/default/files/cf-research-article-files/JCF-D-17-00239R1_FINAL_Taylor-Cousarj_25112017.pdf
[2] https://www.ncbi.nlm.nih.gov/pubmed/?term=Lumacaftor/ivacaftor%20in%20patients%20with%20cystic%20fibrosis%20and%20advanced%20lung%20disease%20homozygous%20for%20F508del-CFTR
[3] https://www.ecfs.eu/research-article-keywords/advanced-lung-disease
[4] https://www.ecfs.eu/research-article-keywords/f508del
[5] https://www.ecfs.eu/research-article-keywords/ivacaftor
[6] https://www.ecfs.eu/research-article-keywords/lumacaftor
[7] https://www.ecfs.eu/research-article-keywords/severe-lung-dysfunction
[8] https://www.ecfs.eu/resource-guideline-type/other-guidelines