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Home > Lung Function Decline is Delayed But Not Decreased in Patients With Cystic Fibrosis and the R117H Gene Mutation

Lung Function Decline is Delayed But Not Decreased in Patients With Cystic Fibrosis and the R117H Gene Mutation

Resource Type

CF Research News

Authors

Jeffrey S. Wagener, Stefanie J. Millar, Nicole Mayer-Hamblett, Gregory S. Sawicki, Edward F. McKone6, Christopher H. Goss, Michael W. Konstan, Wayne J. Morgan, David J. Pasta2, Richard B. Moss

References

J Cyst Fibros. 2017 Oct 31. pii: S1569-1993(17)30912-8. doi: 10.1016/j.jcf.2017.10.003

Document

PDF icon CF Research News Article [1]

Link

Scientific Abstract [2]

Keywords

F508del [3]
Lung function [4]
Lung function decline [5]
R117H [6]

Date

Tuesday, October 31, 2017

Featured resource article

Yes

Resource - Guideline Type

Other Guidelines [7]
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European Cystic Fibrosis Society (ECFS)

Source URL:https://www.ecfs.eu/resource-article/cf-research-news/lung-function-decline-delayed-not-decreased-patients-cystic

Links
[1] https://www.ecfs.eu/sites/default/files/cf-research-article-files/JCF-D-17-00248R1_FINAL_Wagener_19112017.pdf [2] https://www.ncbi.nlm.nih.gov/pubmed/29100868 [3] https://www.ecfs.eu/research-article-keywords/f508del [4] https://www.ecfs.eu/research-article-keywords/lung-function [5] https://www.ecfs.eu/research-article-keywords/lung-function-decline [6] https://www.ecfs.eu/research-article-keywords/r117h [7] https://www.ecfs.eu/resource-guideline-type/other-guidelines