European Cystic Fibrosis Society (ECFS)
Published on European Cystic Fibrosis Society (ECFS) (https://www.ecfs.eu)

Home > Retrospective observational study of French patients with cystic fibrosis and a Gly551Asp-CFTR mutation after 1 and 2 years of treatment with ivacaftor in a real-world setting

Retrospective observational study of French patients with cystic fibrosis and a Gly551Asp-CFTR mutation after 1 and 2 years of treatment with ivacaftor in a real-world setting

Resource Type

CF Research News

Authors

Hubert D, Dehillotte C, Munck A, David V, Baek J, Mely L, Dominique S, Ramel S, Danner Boucher I, Lefeuvre S, Reynaud Q, Colomb-Jung V, Bakouboula P, Lemonnier L

References

J Cyst Fibros. 2017 Jul 12. pii: S1569-1993(17)30816-0. doi: 10.1016/j.jcf.2017.07.001

Document

PDF icon CF Research News Article [1]

Link

Scientific Abstract [2]

Keywords

CFTR modulators [3]
Lumacaftor [4]

Date

Wednesday, July 12, 2017

Featured resource article

Yes

Resource - Guideline Type

Other Guidelines [5]
Terms & Conditions Privacy policy  Accessibility Sitemap Contact 
© EUROPEAN CYSTIC FIBROSIS SOCIETY 2025. All rights reserved. Website by VidaVia (link is external)
European Cystic Fibrosis Society (ECFS)

Source URL:https://www.ecfs.eu/resource-article/cf-research-news/retrospective-observational-study-french-patients-cystic-fibrosis

Links
[1] https://www.ecfs.eu/sites/default/files/cf-research-article-files/JCF-D-17-00105R2_FINAL_Hubert_21102017.pdf [2] https://www.ncbi.nlm.nih.gov/pubmed/?term=Retrospective%20observational%20study%20of%20French%20patients%20with%20cystic%20fibrosis%20and%20a%20Gly551Asp-CFTR%20mutation%20after%201%20and%202%20years%20of%20treatment%20with%20ivacaftor%20in%20a%20real-world%20setting [3] https://www.ecfs.eu/research-article-keywords/cftr-modulators [4] https://www.ecfs.eu/research-article-keywords/lumacaftor [5] https://www.ecfs.eu/resource-guideline-type/other-guidelines