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Home > Recovery of lung function following a pulmonary exacerbation in patients with cystic fibrosis and the G551D-CFTR mutation treated with ivacaftor.

Recovery of lung function following a pulmonary exacerbation in patients with cystic fibrosis and the G551D-CFTR mutation treated with ivacaftor.

Resource Type

CF Research News

Authors

Flume PA, Wainwright CE, Tullis ED, Rodriguez S, Niknian M, Higgins M, Davies JC, Wagener JS

References

J Cyst Fibros. 2017 Jun 24. pii: S1569-1993(17)30770-1. doi: 10.1016/j.jcf.2017.06.002

Document

PDF icon CF Research News Article [1]

Link

Scientific Abstract [2]

Keywords

Cystic fibrosis transmembrane conductance regulator [3]
Ivacaftor [4]
Pulmonary exacerbations [5]
Pulmonary function [6]

Date

Saturday, June 24, 2017

Featured resource article

Yes

Resource - Guideline Type

Other Guidelines [7]
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European Cystic Fibrosis Society (ECFS)

Source URL:https://www.ecfs.eu/resource-article/cf-research-news/recovery-lung-function-following-pulmonary-exacerbation-patients

Links
[1] https://www.ecfs.eu/sites/default/files/cf-research-article-files/JCF-D-17-00110R1_FINAL_Flume_23072017.pdf [2] https://www.ncbi.nlm.nih.gov/pubmed/?term=Recovery%20of%20lung%20function%20following%20a%20pulmonary%20exacerbation%20in%20patients%20with%20cystic%20fibrosis%20and%20the%20G551D-CFTR%20mutation%20treated%20with%20ivacaftor [3] https://www.ecfs.eu/research-article-keywords/cystic-fibrosis-transmembrane-conductance-regulator [4] https://www.ecfs.eu/research-article-keywords/ivacaftor [5] https://www.ecfs.eu/research-article-keywords/pulmonary-exacerbations [6] https://www.ecfs.eu/research-article-keywords/pulmonary-function [7] https://www.ecfs.eu/resource-guideline-type/other-guidelines