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Home > Real-life acute lung function changes after lumacaftor/ivacaftor first administration in pediatric patients with cystic fibrosis

Real-life acute lung function changes after lumacaftor/ivacaftor first administration in pediatric patients with cystic fibrosis

Resource Type

CF Research News

Authors

Aurélie Labaste, Camille Olhmann, Catherine Mainguy, Virginie Jubin, Marie Perceval, Laurianne Coutier, Philippe Reix

References

J Cyst Fibros. 2017 May 18. pii: S1569-1993(17)30153-4. doi: 10.1016/j.jcf.2017.05.002. 

Document

PDF icon CF Research News Article [1]

Link

Scientific Abstract [2]

Keywords

Acute [3]
Airway obstruction [4]
Bronchoconstriction [5]
Lumacaftor [6]
Modulators [7]
Pediatric [8]

Date

Thursday, May 18, 2017

Featured resource article

Yes

Resource - Guideline Type

Other Guidelines [9]
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Source URL:https://www.ecfs.eu/resource-article/cf-research-news/real-life-acute-lung-function-changes-after-lumacaftorivacaftor

Links
[1] https://www.ecfs.eu/sites/default/files/cf-research-article-files/JCF-D-17-00069R1_FINAL_Reix_16072017.pdf [2] https://www.ncbi.nlm.nih.gov/pubmed/?term=Real-life%20acute%20lung%20function%20changes%20after%20lumacaftor/ivacaftor%20first%20administration%20in%20pediatric%20patients%20with%20cystic%20fibrosis [3] https://www.ecfs.eu/research-article-keywords/acute [4] https://www.ecfs.eu/research-article-keywords/airway-obstruction [5] https://www.ecfs.eu/research-article-keywords/bronchoconstriction [6] https://www.ecfs.eu/research-article-keywords/lumacaftor [7] https://www.ecfs.eu/research-article-keywords/modulators [8] https://www.ecfs.eu/research-article-keywords/pediatric [9] https://www.ecfs.eu/resource-guideline-type/other-guidelines