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Home > Pulmonary surfactant dysfunction in pediatric cystic fibrosis: Mechanisms and reversal with a lipid-sequestering drug.

Pulmonary surfactant dysfunction in pediatric cystic fibrosis: Mechanisms and reversal with a lipid-sequestering drug.

Resource Type

CF Research News

Authors

Gunasekara L, Al-Saiedy M, Green F, Pratt R, Bjornson C, Yang A, Michael Schoel W, Mitchell I, Brindle M, Montgomery M, Keys E, Dennis J, Shrestha G, Amrein M.

References

J Cyst Fibros. 2017 Jun 7. pii: S1569-1993(17)30151-0.

Document

PDF icon CF Research News Article [1]

Link

Scientific Abstract [2]

Keywords

Cholesterol [3]
oxidative stress [4]
Free fatty acids [5]
Genotypes [6]
Infection [7]
Inflammation [8]
Lung surfactant [9]
Phospholipids [10]
Surface tension [11]

Date

Wednesday, June 7, 2017

Featured resource article

Yes

Resource - Guideline Type

Other Guidelines [12]
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Source URL:https://www.ecfs.eu/resource-article/cf-research-news/pulmonary-surfactant-dysfunction-pediatric-cystic-fibrosis

Links
[1] https://www.ecfs.eu/sites/default/files/cf-research-article-files/JCF-D-16-00397R1_FINAL_Green_06062017.pdf [2] https://www.ncbi.nlm.nih.gov/pubmed/?term=Pulmonary%20Surfactant%20Dysfunction%20in%20Pediatric%20Cystic%20Fibrosis%3A%20Mechanisms%20and%20Reversal%20with%20a%20Lipid-Sequestering%20Drug [3] https://www.ecfs.eu/research-article-keywords/cholesterol [4] https://www.ecfs.eu/research-article-keywords/oxidative-stress [5] https://www.ecfs.eu/research-article-keywords/free-fatty-acids [6] https://www.ecfs.eu/research-article-keywords/genotypes [7] https://www.ecfs.eu/research-article-keywords/infection [8] https://www.ecfs.eu/research-article-keywords/inflammation [9] https://www.ecfs.eu/research-article-keywords/lung-surfactant [10] https://www.ecfs.eu/research-article-keywords/phospholipids [11] https://www.ecfs.eu/research-article-keywords/surface-tension [12] https://www.ecfs.eu/resource-guideline-type/other-guidelines