European Cystic Fibrosis Society (ECFS)
Published on European Cystic Fibrosis Society (ECFS) (https://www.ecfs.eu)

Home > Bone demineralization is improved by ivacaftor in patients with cystic fibrosis carrying the p.Gly551Asp mutation

Bone demineralization is improved by ivacaftor in patients with cystic fibrosis carrying the p.Gly551Asp mutation

Resource Type

CF Research News

Authors

Isabelle Sermet-Gaudelus
Martial Delion
Isabelle Durieu
Jacky Jacquot
Dominique Hubert

References

J Cyst Fibros. 2016 Oct 10. pii: S1569-1993(16)30605-1

Document

PDF icon CF Research News article [1]

Link

Scientific abstract [2]

Theme

CFTR/Basic Science [3]

Keywords

Bone density [4]
CFTR corrector [5]
RANKL [6]

Date

Monday, October 10, 2016

Featured resource article

Yes
Terms & Conditions Privacy policy  Accessibility Sitemap Contact 
© EUROPEAN CYSTIC FIBROSIS SOCIETY 2025. All rights reserved. Website by VidaVia (link is external)
European Cystic Fibrosis Society (ECFS)

Source URL:https://www.ecfs.eu/resource-article/cf-research-news/bone-demineralization-improved-ivacaftor-patients-cystic-fibrosis

Links
[1] https://www.ecfs.eu/sites/default/files/cf-research-article-files/JCF-D-16-00118R2_FINAL_Sermet-Gaudelus_13112016.pdf [2] https://www.ncbi.nlm.nih.gov/pubmed/?term=Bone%20demineralization%20is%20improved%20by%20ivacaftor%20in%20patients%20with%20cystic%20fibrosis%20carrying%20the%20p.Gly551Asp%20mutation [3] https://www.ecfs.eu/research-article-themes/cftrbasic-science [4] https://www.ecfs.eu/research-article-keywords/bone-density [5] https://www.ecfs.eu/research-article-keywords/cftr-corrector [6] https://www.ecfs.eu/research-article-keywords/rankl