European Cystic Fibrosis Society (ECFS)
Published on European Cystic Fibrosis Society (ECFS) (https://www.ecfs.eu)

Home > The relationship between ivacaftor and lung function variability

The relationship between ivacaftor and lung function variability

Resource Type

CF Research News

Authors

Rhonda D Szczesniak, Eleni-Rosalina Andrinopoulou, Hancheng Li, Raksha Jain, Nicole Mayer-Hamblett, Josh Ostrenga, Anushka K Palipana, David J Pasta, Margaret Rosenfeld, Jonathan Todd, Elizabeth A Cromwell, Wayne J Morgan

References

J Cyst Fibros. 2025 Feb 9:S1569-1993(25)00047-5. doi: 10.1016/j.jcf.2025.01.014.

Document

PDF icon CF Research News Article [1]

Link

Scientific Abstract [2]

Keywords

FEV1 [3]
Highly effective modulator [4]
Longitudinal [5]
mutation [6]
patient registry [7]
Stability [8]

Date

Sunday, February 9, 2025

Featured resource article

Yes

Resource - Guideline Type

Other Guidelines [9]
Terms & Conditions Privacy policy  Accessibility Sitemap Contact 
© EUROPEAN CYSTIC FIBROSIS SOCIETY 2025. All rights reserved. Website by VidaVia (link is external)
European Cystic Fibrosis Society (ECFS)

Source URL:https://www.ecfs.eu/resource-article/cf-research-news/relationship-between-ivacaftor-and-lung-function-variability

Links
[1] https://www.ecfs.eu/sites/default/files/cf-research-article-files/JCF-D-24-00405R1_FINAL_Szczesniak_160225%20%28002%29.pdf [2] https://pubmed.ncbi.nlm.nih.gov/39929763/ [3] https://www.ecfs.eu/research-article-keywords/fev1 [4] https://www.ecfs.eu/research-article-keywords/highly-effective-modulator [5] https://www.ecfs.eu/research-article-keywords/longitudinal [6] https://www.ecfs.eu/research-article-keywords/mutation [7] https://www.ecfs.eu/research-article-keywords/patient-registry [8] https://www.ecfs.eu/research-article-keywords/stability [9] https://www.ecfs.eu/resource-guideline-type/other-guidelines