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Home > Assessing novel modulator therapy in children with cystic fibrosis using xenon gas MRI during multiple-breath washout

Assessing novel modulator therapy in children with cystic fibrosis using xenon gas MRI during multiple-breath washout

Resource Type

CF Research News

Authors

Faiyza Alam, Samal Munidasa, Brandon Zanette, Sharon Braganza, Daniel Li, Renee Jensen, Marie-Pier Dumas, Felix Ratjen, Giles Santyr

References

J Cyst Fibros. 2024 Sep 30:S1569-1993(24)01789-2. doi: 10.1016/j.jcf.2024.09.021.

Document

PDF icon CF Research News Article [1]

Link

Scientific Abstract [2]

Keywords

Fractional ventilation [3]
Hyperpolarized (129)Xe [4]
Lung clearance index [5]
Multiple-breath washout [6]
Pediatric; elexacaftor/tezacaftor/ivacaftor [7]

Date

Monday, September 30, 2024

Featured resource article

Yes

Resource - Guideline Type

Other Guidelines [8]
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Source URL:https://www.ecfs.eu/resource-article/cf-research-news/assessing-novel-modulator-therapy-children-cystic-fibrosis-using

Links
[1] https://www.ecfs.eu/sites/default/files/JCF-D-24-00133R2_FINAL_Alam_201024.pdf [2] https://pubmed.ncbi.nlm.nih.gov/39353741/ [3] https://www.ecfs.eu/research-article-keywords/fractional-ventilation [4] https://www.ecfs.eu/research-article-keywords/hyperpolarized-129xe [5] https://www.ecfs.eu/research-article-keywords/lung-clearance-index [6] https://www.ecfs.eu/research-article-keywords/multiple-breath-washout-0 [7] https://www.ecfs.eu/research-article-keywords/pediatric-elexacaftortezacaftorivacaftor [8] https://www.ecfs.eu/resource-guideline-type/other-guidelines